Abstract:
:We describe a new case of isolated Langerhans cell histiocytosis (LCH) of the hypothalamus. A 53-year-old female patient presented with polydipsia, headache, anorexia, and fatigue. Neurological imaging revealed a mass projecting from the hypothalamus into the third ventricle. Gross total removal of the tumor was performed. Light microscopy showed LCH, and immunohistochemical studies revealed S-100 and CD1a immunoreactivity in the Langerhans cells. Although the most common CNS site for LCH is the hypothalamus, isolated hypothalamic LCH, confirmed by biopsy, is very rare. The residual mass appeared to remit spontaneously 3.5 years after surgery, with regrowth 3 years later.
journal_name
Brain Tumor Patholjournal_title
Brain tumor pathologyauthors
Horiguchi K,Fujii T,Nakazato Ydoi
10.1007/BF02484517keywords:
subject
Has Abstractpub_date
2004-01-01 00:00:00pages
97-101issue
2eissn
1433-7398issn
1861-387Xjournal_volume
21pub_type
杂志文章abstract::We observed the histopathological and physiological characteristics of adrenocorticotropic hormone (ACTH)-secreting adenoma cells derived from a rapidly growing pituitary adenoma, which have firm cell attachment and well-preserved hormonal function in a relatively longterm culture. Corticotrophs, obtained from a 43-ye...
journal_title:Brain tumor pathology
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journal_title:Brain tumor pathology
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更新日期:2011-02-01 00:00:00
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journal_title:Brain tumor pathology
pub_type: 杂志文章
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更新日期:2019-07-01 00:00:00
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journal_title:Brain tumor pathology
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journal_title:Brain tumor pathology
pub_type: 杂志文章,评审
doi:10.1007/s10014-018-0327-y
更新日期:2018-10-01 00:00:00
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journal_title:Brain tumor pathology
pub_type: 杂志文章
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journal_title:Brain tumor pathology
pub_type: 杂志文章
doi:10.1007/BF02478945
更新日期:2003-01-01 00:00:00
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journal_title:Brain tumor pathology
pub_type: 杂志文章
doi:10.1007/s10014-012-0098-9
更新日期:2013-01-01 00:00:00
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pub_type: 杂志文章
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journal_title:Brain tumor pathology
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journal_title:Brain tumor pathology
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journal_title:Brain tumor pathology
pub_type: 杂志文章,评审
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abstract::Papillary tumor of the pineal region (PTPR) was recently added to the 2007 WHO classification of tumors of the central nervous system as a rare pineal tumor. We present a case of a 17-year-old man who developed a 3-cm pineal tumor that was incompletely excised following two operations. The pathological findings presen...
journal_title:Brain tumor pathology
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更新日期:2009-01-01 00:00:00
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