Abstract:
:Hirayama disease is a nonprogressive, asymmetric amyotrophy of the hands and forearms, possibly caused by compression of the lower cervical cord on neck flexion. The authors used phase-contrast MR angiography to study a patient with this disorder and observed abnormal spinal epidural venous dilation on neck flexion. In addition to mechanical compression of the lower cervical cord, venous congestion in the spinal canal may have a role in promoting anterior horn damage.
journal_name
Neurologyjournal_title
Neurologyauthors
Baba Y,Nakajima M,Utsunomiya H,Tsuboi Y,Fujiki F,Kusuhara T,Yamada Tdoi
10.1212/01.wnl.0000120665.81001.40subject
Has Abstractpub_date
2004-04-27 00:00:00pages
1426-8issue
8eissn
0028-3878issn
1526-632Xjournal_volume
62pub_type
杂志文章相关文献
NEUROLOGY文献大全abstract:OBJECTIVE:To validate the Narcolepsy Severity Scale (NSS), a brief clinical instrument to evaluate the severity and consequences of symptoms in patients with narcolepsy type 1 (NT1). METHODS:A 15-item scale to assess the frequency and severity of excessive daytime sleepiness, cataplexy, hypnagogic hallucinations, slee...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0000000000003787
更新日期:2017-04-04 00:00:00
abstract:OBJECTIVES:This study aims to investigate if patients with inflammatory neuropathies and tremor have evidence of dysfunction in the cerebellum and interactions in sensorimotor cortex compared to nontremulous patients and healthy controls. METHODS:A prospective data collection study investigating patients with inflamma...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0b013e318292a2b8
更新日期:2013-05-14 00:00:00
abstract::We report a family with Machado-Joseph disease (MJD) that was previously diagnosed with dentatorubral-pallidoluysian atrophy (DRPLA), on the basis of the neuropathologic findings. Because the clinical and pathologic reevaluation strongly suggested a diagnosis of MJD, we conducted a genetic study in the family. Two pat...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.46.4.1154
更新日期:1996-04-01 00:00:00
abstract::Migraine and the MELAS (mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes) syndrome have some clinical features in common. First, cerebral infarctions, most often in the posterior cerebral regions, which are a main symptom of MELAS, may complicate migraine. Second, migrainous headache w...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.46.6.1735
更新日期:1996-06-01 00:00:00
abstract:OBJECTIVE:We tested the hypothesis that admission serum magnesium levels are associated with hematoma volume, hematoma growth, and functional outcomes in patients with intracerebral hemorrhage (ICH). METHODS:Patients presenting with spontaneous ICH were enrolled in an observational cohort study that prospectively coll...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0000000000004249
更新日期:2017-08-22 00:00:00
abstract::In 17 patients with cough syncope, electroencephalograms showed normal interictal recordings in 12 patients, minimally abnormal recordings in 4, and a moderately abnormal recording in 1. Fourteen episodes of cough syncope (six patients) were recorded, with the EEGs showing diffuse theta and delta slowing during the ep...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.34.3.371
更新日期:1984-03-01 00:00:00
abstract:OBJECTIVE:To examine associations of orthostatic hypotension (OH) with dementia and long-term cognitive decline and to update previously published results in the same cohort for stroke with an additional 16 years of follow-up. METHODS:We analyzed data from 11,709 participants without a history of coronary heart diseas...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0000000000006027
更新日期:2018-08-21 00:00:00
abstract::This is a report on hepatic adverse events associated with dantrolene therapy. All cases reported to the manufacturer are included, from all sources, through 1987. Of 122 cases containing sufficient data to analyze, 47 patients had asymptomatic transaminase elevations, 12 had additional mild (less than or equal to 2.5...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.40.9.1427
更新日期:1990-09-01 00:00:00
abstract:OBJECTIVE:To characterize the molecular basis of a novel fast-channel congenital myasthenic syndrome. METHODS:We used the candidate gene approach to identify the pathogenic mutation in the acetylcholine receptor (AChR) ε subunit, genetically engineered the mutant AChR into HEK cells, and evaluated the level of express...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0b013e31825b5bda
更新日期:2012-07-31 00:00:00
abstract::An improved agarose gel electrophoretic technique was used to fractionate serum and cerebrospinal fluid (CSF) proteins in patients with presenile dementia. The CSF electrophoretic patterns demonstrated three abnormal bands in the gamma-globulin region in five out of eight of these patients. ...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.30.8.882
更新日期:1980-08-01 00:00:00
abstract::Salla disease is a lysosomal storage disorder associated with increased urinary excretion of free sialic acid. The main clinical features in 34 patients were severe psychomotor retardation of early onset, ataxia, athetosis, rigidity, spasticity, and impaired speech. Growth retardation, thick calvarium, and exotropia w...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.33.1.57
更新日期:1983-01-01 00:00:00
abstract:OBJECTIVE:To report long-term safety and efficacy outcomes of a large cohort of patients with medically refractory isolated dystonia treated with subthalamic nucleus (STN) deep brain stimulation (DBS). METHODS:Twenty patients (12 male, 8 female; mean age 49 ± 16.3 years) with medically refractory isolated dystonia wer...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0000000000003451
更新日期:2017-01-03 00:00:00
abstract::Four toluene abusers had evidence of severe multifocal central nervous system damage. Impairment of cognitive, cerebellar, brainstem, auditory, and pyramidal tract function, as well as CT evidence of cerebral cortical, cerebellar, and brainstem atrophy, have been noted. In addition, we found opsoclonus, ocular flutter...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.33.10.1337
更新日期:1983-10-01 00:00:00
abstract::Rosenthal fibers are present in several neurologic disorders. Their occurrence in widespread subependymal, subpial, and perivascular locations is thought to be diagnostic of Alexander's disease, but they have also been reported in rare adult cases. Some of these patients were neurologically intact with severe systemic...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.42.9.1733
更新日期:1992-09-01 00:00:00
abstract::We sought to determine whether geriatric patients with late-life-onset major depression have more subcortical hyperintensities on MRI and greater cognitive impairment than age-matched geriatric patients with early-life-onset major depression, suggesting that subcortical disease may be etiologic in late-life depression...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.46.6.1567
更新日期:1996-06-01 00:00:00
abstract::Intracranial EEG recording is often required to identify an area of the brain for resective surgery for intractable epilepsy. We simultaneously compared bilaterally placed depth and limited subdural electrode EEG to determine the most effective method of recording seizures from the temporal lobes. Localized complex pa...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.39.11.1497
更新日期:1989-11-01 00:00:00
abstract::Ullrich disease is a form of congenital muscular dystrophy characterized clinically by generalized muscle weakness, contractures of the proximal joints, and hyperflexibility of the distal joints from birth or early infancy. Recently, mutations of the collagen VI gene have been associated with Ullrich disease. The auth...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.59.6.920
更新日期:2002-09-24 00:00:00
abstract::Recent clinical neuropathologic reports are inconsistent with previous models of how pontine neural circuits generate saccadic eye movements. We present a hypothetical explanation of these and other clinical and experimental findings based on a new model that accurately predicts the eye signs in pontine lesions. ...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.39.7.994
更新日期:1989-07-01 00:00:00
abstract:OBJECTIVE:The primary objective of this research was to characterize the movement disorders associated with FOXG1 mutations. METHODS:We identified patients with FOXG1 mutations who were referred to either a tertiary movement disorder clinic or tertiary epilepsy service and retrospectively reviewed medical records, cli...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/WNL.0000000000002585
更新日期:2016-05-10 00:00:00
abstract:OBJECTIVE:To evaluate the safety and efficacy of 60 Hz deep brain stimulation (DBS) of the globus pallidus internus (GPi) in 15 consecutive patients with primary dystonia. METHODS:We conducted a retrospective analysis of clinic charts relative to 15 consecutive patients with medically refractory primary dystonia who u...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/01.wnl.0000267430.95106.ff
更新日期:2007-08-14 00:00:00
abstract::A 71-year-old man developed severe limb, bulbar, and respiratory weakness over 18 months. A muscle biopsy showed only a moderate degree of type 2 atrophy, but immunocytochemistry showed absence of chondroitin sulfate C glycosaminoglycan in the endomysium. Prednisone produced a marked increase in strength. Diffuse loss...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.50.2.526
更新日期:1998-02-01 00:00:00
abstract:BACKGROUND:Physicians are often asked to predict outcome after acute stroke. Very little information is available that can reliably predict the likelihood of severe disability or death. OBJECTIVE:To develop a practical method for predicting a poor outcome after acute ischemic stroke. METHODS:Data from the placebo arm...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.55.7.952
更新日期:2000-10-10 00:00:00
abstract::Serum from 35 cases of naturally occurring acquired canine myasthenia gravis (MG) were assayed for patterns of autoantibody specificities against canine acetylcholine receptor (AChR) using monoclonal antibodies (mAbs) and antiserum against defined regions of the AChR as competitive inhibitors of autoantibody binding. ...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.38.9.1417
更新日期:1988-09-01 00:00:00
abstract:BACKGROUND:Despite convenience, accessibility, and strong correlation to severity of Alzheimer disease (AD) pathology, medial temporal lobe atrophy (MTA) has not been used as a criterion in the diagnosis of prodromal and probable AD. METHODS:Using a newly validated visual rating system, mean MTA scores of three bilate...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/01.wnl.0000336925.79704.9f
更新日期:2008-12-09 00:00:00
abstract::Plasma levels of six short-chain fatty acids (SCFA) were measured in 23 Reye's syndrome patients. In sequential measurements, only propionic acid correlated closely with neurologic severity. Although admission SCFA levels were slightly elevated, there were no significant differences between patients grouped by severit...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.34.6.831
更新日期:1984-06-01 00:00:00
abstract::The electronic medical record (EMR) is changing the landscape of medical practice in the modern age. Increasing emphasis on quality metric reporting, data-driven documentation, and timely coding and billing are pressuring institutions across the country to adopt the latest EMR technology. The impact of these systems o...
journal_title:Neurology
pub_type: 杂志文章,评审
doi:10.1212/WNL.0000000000000819
更新日期:2014-09-23 00:00:00
abstract::Diffusion-weighted MRI (DWI) was used in three patients with autopsy-proven sporadic Creutzfeldt-Jakob disease (CJD) to provide a rapid noninvasive way to make this sometimes confusing diagnosis. DWI prompted the diagnosis of CJD at an early stage and appears to be particularly useful for monitoring the progression of...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.52.1.205
更新日期:1999-01-01 00:00:00
abstract:OBJECTIVE:To investigate whether admission hyperglycemia predicts poststroke infections and, if so, whether poststroke infections modify the effect of admission hyperglycemia on functional outcome in ischemic stroke. METHODS:We used data from acute ischemic stroke patients in the Preventive Antibiotics in Stroke Study...
journal_title:Neurology
pub_type: 杂志文章,多中心研究,随机对照试验
doi:10.1212/WNL.0000000000003811
更新日期:2017-04-11 00:00:00
abstract::A 16-year-old male with a 9-year history of spontaneously arrested hydrocephalus was noted to have hydrosyringomyelia and increased intracranial pressure shortly after sustaining minor head trauma. His symptoms resolved completely following ventriculoperitoneal shunt replacement. Hydrosyringomyelia may occur in the se...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.38.4.652
更新日期:1988-04-01 00:00:00
abstract::The authors analyzed the association of L-carnitine treatment with hepatic survival in 92 patients with severe, symptomatic, valproate-induced hepatotoxicity. Forty-eight percent of the 42 patients treated with L-carnitine survived, but only 10% of the 50 patients treated solely with aggressive supportive care survive...
journal_title:Neurology
pub_type: 杂志文章
doi:10.1212/wnl.56.10.1405
更新日期:2001-05-22 00:00:00