Abstract：
:The Hermansky-Pudlak Syndrome, a "tyrosinase positive' form of oculocutaneous albinism, is a triad comprising albinism, a hemorrhagic diathesis and ceroid-lipofuscin storage. A pedigree is presented showing consanguinity with a pattern of pseudodominance. Electroretinography in two isolated Hermansky-Pudlak subjects was distinctly abnormal, showing decreased rod and cone responses (as well as abnormal flicker fusion responses) in one patient, and reduced photopic and scotopic responses in another. The decreased ERG responses are discussed with reference to the known retinal abnormalities in both generalized oculocutaneous albinism and Batten's disease, another ceroid-lipofuscin storage disorder.
journal_name
Int Ophthalmoljournal_title
International ophthalmologyauthors
Fagadau WR,Heinemann MH,Cotlier Edoi
10.1007/BF00139585subject
Has Abstractpub_date
1981-08-01 00:00:00pages
113-22issue
1-2eissn
0165-5701issn
1573-2630journal_volume
4pub_type
杂志文章abstract：:The clinical and pathological presentation of Behçet's disease are discussed. Necrotising arteriolitis and phlebitis with thromboses are demonstrated when a rare enucleation specimen became available for examination in this condition. Immunohistochemical studies show mural IgG, IgA, and C3 deposits in episcleral and s...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/BF00128365
更新日期：1985-03-01 00:00:00
abstract：:The authors reviewed their experience with 429 cases of orbital exenteration between 1963 and 1993. Apart from the 22 cases operated in concert with other physicians, 407 cases were operated by an ophthalmologist and spontaneous granulation technique was used. Total or eyelid-sacrificing exenteration was carried out f...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/BF00133735
更新日期：1995-01-01 00:00:00
abstract：BACKGROUND:Rhegmatogenous retinal detachment associated with choroidal detachment (RRDCD) refers to the detachment of the ciliary body and choroid from the sclera along with retinal detachment. The recovery of visual function is often far worse after surgical treatment of RRDCD than following anatomical reduction for c...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-020-01433-1
更新日期：2020-10-01 00:00:00
abstract：PURPOSE:To compare the systemic and ocular characteristics and laboratory findings of patients developing toxic anterior segment syndrome (TASS) after uneventful phaco surgery with unaffected subjects undergoing the same surgery in the same session. DESIGN:A retrospective case-control study. METHODS:The study group c...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-016-0418-x
更新日期：2018-02-01 00:00:00
abstract：:We describe the first two cases of diffuse unilateral subacute neuroretinitis (DUSN) in the UK successfully treated with albendazole. Two patients are described who presented with unilateral reduction in vision, with clusters of yellow-white retinal lesions fading and reappearing in new locations of the fundus over a ...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-010-9358-z
更新日期：2010-10-01 00:00:00
abstract：:In a study of 95 patients with intraocular foreign body injuries presenting in the eight year period from 1978-1986 we found the overall visual results to be good with 62% of patients achieving a final visual acuity of 6/18 or better. The factors leading to a poor visual result were a large intraocular foreign body, p...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/BF00137136
更新日期：1988-01-01 00:00:00
abstract：PURPOSE:To describe the incidence of, and risk factors associated with, diabetic retinopathy in diabetic persons assessed at a Saudi diabetes centre. METHODS:Five hundred and two patients with diabetes mellitus assessed by our service were studied. There were 174 patients (34.7%) with insulin-dependent diabetes mellit...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1023/a:1006240928938
更新日期：1998-01-01 00:00:00
abstract：:This study aimed to monitor the graft-host junction's (GHJ's) apposition with anterior segment optical coherence tomogram after penetrating keratoplasty (PK) and correlate the analysis with the preoperative diagnosis. Fifty-one eyes of 50 patients with various preoperative diagnosis of adherent leucoma, pseudophakic b...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-016-0269-5
更新日期：2017-04-01 00:00:00
abstract：:I have developed two protective caps that fit on the viewing windows of the indirect ophthalmoscope. These caps contain filters that absorb the argon laser beam and protect the operator's eyes during endolaser treatment. ...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/BF00225937
更新日期：1986-04-01 00:00:00
abstract：:The purpose of this study was to compare the keratometry (K) values obtained by the Scheimpflug camera combined with placido-disk corneal topography (Sirius) and optical biometry (Lenstar) for intraocular lens (IOL) power calculation before the cataract surgery, and to evaluate the accuracy of postoperative refraction...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-016-0330-4
更新日期：2017-08-01 00:00:00
abstract：PURPOSE:Our purpose is to describe a safe and easy technique for the removal of the BrightOcular cosmetic iris implants. Our technique involves cutting the implant into five parts rather than removal as a whole with less intraocular manipulation and no rotation of the implant. METHODS:We have used this technique in tw...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-020-01328-1
更新日期：2020-06-01 00:00:00
abstract：PURPOSE:To report a case of bilateral Terson Syndrome with sub inner limiting membrane hemorrhage associated with a rare finding: perimacular fold. METHODS:The patient, a 34 years old female with aneurysmal subarachnoid hemorrhage and bilateral Terson syndrome was admitted to the Ophthalmology department, complaining ...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-018-0822-5
更新日期：2019-02-01 00:00:00
abstract：PURPOSE:Regional variations of the preoperative biometry can affect the refractive accuracy of cataract surgery. We aimed to compare the preoperative biometric data for cataract surgery between two domestic institutions. METHODS:We retrospectively reviewed the preoperative biometric data of 673 consecutive eyes underg...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-020-01476-4
更新日期：2020-11-01 00:00:00
abstract：PURPOSE:The objective of this study is to examine the morphometry of the lacrimal drainage system with reference to bony landmarks in the vicinity. METHODS:Twenty midsaggitalized heads obtained from sixteen preserved cadavers were studied. Measurements involved detailed morphometry of anterior and posterior lacrimal c...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-017-0753-6
更新日期：2018-12-01 00:00:00
abstract：PURPOSE:To determine whether gene polymorphisms which are associated with age-related macular degeneration (AMD) influence treatments' response and specifically the antioxidant supplementation in dry AMD patients, as well as the anti-vascular endothelial growth factor (anti-VEGF) therapy in neovascular AMD patients. M...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-019-01274-7
更新日期：2020-04-01 00:00:00
abstract：PURPOSE:To identify baseline optical coherence tomography (OCT) factors in ischemic central retinal vein occlusion (CRVO) that predict response to bevacizumab injections. METHODS:Patients underwent OCT at diagnosis and the central macular thickness, subretinal fluid width and height as well as the presence of intraret...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-020-01604-0
更新日期：2020-10-22 00:00:00
abstract：PURPOSE:To explore the protective effect of probucol on human retinal Müller cells cultured in high glucose. METHODS:Primary Müller cells from human retinas were cultured in complete DMEM. Third-generation Müller cells were identified using glutamine synthetase (GS) antibody and randomly divided into three groups: nor...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-019-01130-8
更新日期：2019-12-01 00:00:00
abstract：PURPOSE:To gain an insight into the manufacturing and fitting of artificial eyes in children and potential improvements to the process. METHOD:An online qualitative survey was distributed to 39 ocularists/prosthetists in Europe and Canada. Participants were recruited through purposive sampling, specifically maximum va...
journal_title：International ophthalmology
pub_type： 杂志文章,多中心研究
doi：10.1007/s10792-016-0383-4
更新日期：2017-10-01 00:00:00
abstract：:Preliminary results of a larger investigation on correlation between Retinal Nerve Fiber Layer Defects (RNFL) and Automated Perimetry (AP) are presented. A group of ocular hypertensive patients was recruited and a cross-section, randomized study was carried out. The group was composed of 54 eyes from 28 patients; 15 m...
journal_title：International ophthalmology
pub_type： 临床试验,杂志文章,随机对照试验
doi：10.1007/BF00917968
更新日期：1992-09-01 00:00:00
abstract：PURPOSE:Proliferative vitreoretinopathy in the inferior retina remains clinically challenging. Heavier-than-water intraocular tamponades have been developed to improve inferior tamponading properties, and their chemical compositions have been substantially improved over the years, in parallel with developments in vitre...
journal_title：International ophthalmology
pub_type： 杂志文章,评审
doi：10.1007/s10792-017-0489-3
更新日期：2018-04-01 00:00:00
abstract：:The purpose of this study was to evaluate the presence of Toxoplasmosis gondii in samples of peripheral blood from patients with varying etiologies of uveitis. Whole blood from patients with different forms of uveitis was tested for the presence of T. gondii using real-time PCR targeting the well-characterized 529 bp ...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-016-0221-8
更新日期：2017-02-01 00:00:00
abstract：:The choroidal vascular bed has many interesting features such as relatively wide but flat capillaries, fenestrated capillary walls and an enormous blood flow. The high flow rate results in a high oxygen tension in the tissue and is also of importance in the temperature control of the eye. The capillary wall is permeab...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/BF00127638
更新日期：1983-02-01 00:00:00
abstract：PURPOSE:To report two cases of ciliochoroidal effusion after the usage of topiramate. CASES:Two middle-aged women experienced sudden onset of acute glaucoma and acquired myopia after taking topiramate. Ultrasound biomicroscopy demonstrated bilateral ciliochoroidal effusion and angle closure. The A-scan ultrasonography...
journal_title：International ophthalmology
pub_type： 杂志文章,评审
doi：10.1007/s10792-017-0740-y
更新日期：2018-12-01 00:00:00
abstract：:To assess the effect of intravitreal dexamethasone implant (Ozurdex) for the treatment of macular edema secondary to retinal vein occlusion (RVO) resistant to repeated intravitreal ranibizumab injection. Retrospective review of 11 patients (11 eyes) with ranibizumab-resistant macular edema secondary to RVO. Macular ed...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-016-0226-3
更新日期：2017-02-01 00:00:00
abstract：:To report the clinical and microbiological characteristics of infectious endophthalmitis after Boston type I keratoprosthesis (B-K-Pro) implantation. Retrospective analysis of 136 eyes that received a B-K-Pro type 1 between 1999 and 2012 was performed. Five eyes with a diagnosis of exogenous endophthalmitis after B-K-...
journal_title：International ophthalmology
pub_type： 杂志文章,评审
doi：10.1007/s10792-014-9994-9
更新日期：2015-10-01 00:00:00
abstract：PURPOSE:The purpose of the study was to assess adjuvant treatment with topical nonsteroidal anti-inflammatory drugs (NSAIDs) (0.9 % bromfenac, 0.1 % nepafenac, 0.5 % indomethacin, or 0.1 % diclofenac) in addition to topical steroidal treatment with 0.1 % dexamethasone and 0.3 % netilmicin for prevention of cystoid macu...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-016-0374-5
更新日期：2017-10-01 00:00:00
abstract：PURPOSE:To perform vector analysis of changes in corneal astigmatism and evaluate changes in corneal topographic parameters following the lateral tarsal strip (LTS) procedure in patients with involutional ectropion or entropion. METHODS:Nineteen eyes of 15 patients (10 eyes with ectropion and 9 eyes with entropion) we...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-018-0987-y
更新日期：2019-08-01 00:00:00
abstract：:A 17-year-old female presented to our hospital with fatigue, arthralgia and fever associated with non-granulomatous anterior uveitis in the left eye. Blood tests revealed renal failure and a renal biopsy showed acute tubulointerstitial nephritis. Findings were consistent with tubulointerstitial nephritis and uveitis (...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-013-9820-9
更新日期：2014-06-01 00:00:00
abstract：:Glycated proteins formed by the Maillard reaction were measured by furosine determination in human normal lenses and in senile and diabetic cataracts. Furosine, an hydrolysis product of fructose-lysine adduct formed in the early stages of the Maillard reaction, was measured by high performance liquid chromatography (H...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/BF00951795
更新日期：1994-01-01 00:00:00
abstract：PURPOSE:To evaluate the cognitive performance of patients with glaucoma and compare it to individuals with Alzheimer's disease (AD). METHODS:This is a prospective, cross-sectional and case-control study. All subjects were assessed using the Mini-Mental State Examination (MMSE) and its subtests verbal fluency, word lis...
journal_title：International ophthalmology
pub_type： 杂志文章
doi：10.1007/s10792-017-0658-4
更新日期：2018-10-01 00:00:00
