Abstract:
:We present a clinical and morphological study concerning a kindred with slowly progressive X-linked muscular dystrophy (Becker type). Five males were affected; one died of heart failure at age 16. Severe and early cardiac disorder is unusual in this type of muscular dystrophy, and death at such an early age had not been reported previously. In the other patients of the kindred, cardiac abnormalities, if present at all, were nonspecific. Another unusual feature in this kindred was severe muscle pain at an early stage of the disease, a feature that cannot yet be explained.
journal_name
Neurologyjournal_title
Neurologyauthors
Kuhn E,Fiehn W,Schröder JM,Assmus H,Wagner Adoi
10.1212/wnl.29.8.1144subject
Has Abstractpub_date
1979-08-01 00:00:00pages
1144-9issue
8eissn
0028-3878issn
1526-632Xjournal_volume
29pub_type
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