Renal artery stenosis associated with epidermal nevus syndrome.

Abstract:

:Epidermal nevus syndrome is an unusual neurocutaneous disorder in which epidermal nevi are associated with abnormalities of the skeleton and central nervous system, including the eyes and somtimes the cardiovascular system. We treated a patient in whom the latter included renal artery stenosis. An 18-year-old man with epidermal nevi was diagnosed as having the syndrome based on the additional presence of scoliosis, an arachnoid cyst in the middle cranial fossa, and microphthalmos. Hypertension was diagnosed when the patient was 15 years old. The plasma renin activity (9.7 ng/ml/h) was elevated. Right renal artery stenosis was demonstrated by angiography, and the abdominal aorta was narrowed distal to the ostium of the superior mesenteric artery. The plasma renin activity in the right renal vein (16 ng/ml/h) was higher than contralaterally (10 ng/ml/h). Several cardiovascular manifestations have been reported as a complication of epidermal nevus syndrome. Hypertension in an individual with epidermal nevi and congenital anomalies should prompt a search for a vascular anomaly.

journal_name

Nephron

journal_title

Nephron

authors

Aizawa K,Nakamura T,Ohyama Y,Saito Y,Hoshino J,Kanda T,Sumino H,Nagai R

doi

10.1159/000045540

subject

Has Abstract

pub_date

2000-01-01 00:00:00

pages

67-70

issue

1

eissn

1660-8151

issn

2235-3186

pii

45540

journal_volume

84

pub_type

杂志文章

相关文献

NEPHRON文献大全
  • Effect of intravenous 1-alpha-hydroxyvitamin D3 on secondary hyperparathyroidism in chronic uremic patients on maintenance hemodialysis.

    abstract::The effect of intravenous 1 alpha(OH)D3 on circulating intact parathyroid hormone (PTH) and COOH-terminal immunoreactive PTH was examined in 21 patients on chronic hemodialysis. The patients were treated for 3 months with increasing doses of 1 alpha(OH)D3 under careful control of serum Ca2+. 1 alpha(OH)D3 was given in...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000185744

    authors: Brandi L,Daugaard H,Tvedegaard E,Storm T,Olgaard K

    更新日期:1989-01-01 00:00:00

  • Serum leptin concentrations in patients on hemodialysis.

    abstract::Serum leptin concentrations in normal humans have been reported to correlate with the body mass index (BMI) as well as with the body fat mass. In this study, we measured serum leptin concentrations in 107 patients on hemodialysis, 30 of whom had diabetes mellitus as the cause, and examined the clinical significance. F...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000045122

    authors: Nakazono H,Nagake Y,Ichikawa H,Makino H

    更新日期:1998-09-01 00:00:00

  • Fibroadhesive form of tuberculous peritonitis: chyloperitoneum in a patient undergoing automated peritoneal dialysis.

    abstract::Chyloperitoneum is a rare condition in patients undergoing peritoneal dialysis. We report here a patient who developed chylous ascites during the course of tuberculous peritonitis. The diagnosis was confirmed by cultures of dialysate and peritoneal biopsy, and laparoscopy revealed severe hyperemia and intestine adhesi...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000188969

    authors: Huang CH,Chen HS,Chen YM,Tsai TJ

    更新日期:1996-01-01 00:00:00

  • Uremic pruritus and skin mast cells.

    abstract::The number of mast cells in the skin was evaluated in 25 patients with end-stage renal failure on different treatment modality (conservative, hemodialysis and peritoneal dialysis). According to the presence of pruritus, uremic patients were divided into two groups: group A, 13 patients with diffuse pruritus, and group...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000186826

    authors: Dimković N,Djukanović L,Radmilović A,Bojić P,Juloski T

    更新日期:1992-01-01 00:00:00

  • The herbal medicine Sairei-to inhibits proliferation of rat mesangial cells.

    abstract:BACKGROUND:The herbal medicine Sairei-to is efficacious in renal diseases where mesangial proliferation is a key event. We examined whether Sairei-to inhibits proliferation of cultured rat mesangial cells and investigated its mechanism of action. METHODS:The effect of Sairei-to on [(3)H]-thymidine incorporation stimul...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000064112

    authors: Awazu M,Fujita H,Omori S,Hida M

    更新日期:2002-01-01 00:00:00

  • Usefulness of a highly sensitive urinary and serum IL-6 assay in patients with diabetic nephropathy.

    abstract:BACKGROUND/AIM:Interleukin-6 (IL-6) promotes the growth of renal mesangial cells. IL-6 may play a major role in such mesangial proliferation, but there has been little research on IL-6 in relation to diabetic nephropathy because of the difficulty in measuring urinary and serum IL-6 levels. Using a newly developed, high...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000045634

    authors: Shikano M,Sobajima H,Yoshikawa H,Toba T,Kushimoto H,Katsumata H,Tomita M,Kawashima S

    更新日期:2000-05-01 00:00:00

  • Effect of parathyroid hormone on antioxidant enzyme activity and lipid peroxidation of erythrocytes in five-sixths nephrectomized rats.

    abstract::The purpose of the study was to investigate the effects of parathyroid hormone (PTH) infusion on antioxidant enzyme activity and lipid peroxidation of erythrocytes in five-sixths nephrectomized (Nx) rats. Five-sixths Nx rats had a higher osmotic fragility in red blood cells (RBC). Thyroparathyroidectomy (TPTX) effecti...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000189046

    authors: Chen SM,Young TK

    更新日期:1996-01-01 00:00:00

  • Effect of chronic fluoride exposure in uremic rats.

    abstract::This study was conducted to test the hypothesis that the margin of safe fluoride exposure is narrowed in rats that are physiologically compromised by renal dysfunction. The study objective was to determine whether increases in fluoride retention and tissue fluoride levels in rats with surgically induced renal insuffic...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000044888

    authors: Dunipace A,Brizendine E,Wilson M,Zhang W,Wilson C,Katz B,Kafrawy A,Stookey G

    更新日期:1998-01-01 00:00:00

  • Post-obstruction diuresis: influence of renal prostaglandins.

    abstract::The possible role of altered renal prostaglandin metabolism in the generation of post-obstruction diuresis (POD) was examined in 16 adult male Sprague-Dawley rats. Inhibition of cyclooxygenase by the administration of a combination of two nonsteroidal anti-inflammatory drugs (NSAID), meclofenamate and indomethacin in ...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000186766

    authors: Kauker ML,Zawada ET

    更新日期:1992-01-01 00:00:00

  • Combined chemotherapy and radiotherapy for esophageal carcinoma in a hemodialyzed patient. Long-term survival.

    abstract::The use of antimitotic chemotherapy in hemodialysis patients is not yet well codified, and each individual decision remains difficult. We report the case of a 68-year-old hemodialyzed man who developed a squamous cell carcinoma of the upper third of the esophagus. Necessarily disabling surgery was rejected, and three ...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000189461

    authors: Rebibou JM,Chauffert B,Dumas M,Mousson C,Bone MC,Tanter Y,Rifle G

    更新日期:1996-01-01 00:00:00

  • Antioxidant enzymes activity in polymorphonuclear leukocytes in chronic renal failure.

    abstract::In the present study, activity of polymorphonuclear leukocyte (PMNL) intracellular antioxidant enzymes, i.e. catalase, superoxide dismutase (SOD) and glutathione peroxidase (GPX), was assessed in CRF patients on hemodialysis (HD), or continuous ambulatory peritoneal dialysis (CAPD) and in healthy controls. The activit...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000188708

    authors: Shurtz-Swirski R,Mashiach E,Kristal B,Shkolnik T,Shasha SM

    更新日期:1995-01-01 00:00:00

  • Prolactin status in experimentally induced acute renal failure in the rat.

    abstract::Serum prolactin levels were elevated in male Sprague-Dawley rats with acute renal failure induced by glycerol administration. Specific prolactin binding to kidney membrane preparations was reduced in glycerol and antirat glomerular basement membrane serum-treated rats, after morphological and biochemical acute renal f...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000182078

    authors: Dobbie JW,Mountjoy K,Cowden EA,Allison ME,Ratcliffe JG

    更新日期:1981-01-01 00:00:00

  • Effect of sodium bicarbonate preloading on ischemic renal failure.

    abstract::Rats pretreated with sodium bicarbonate were functionally protected from the damage of bilateral renal artery occlusion. The rise in serum creatinine (day 1 minus day 0) during the first 24 h after ischemia was 2.88 +/- 0.28 mg% in the bicarbonate-loaded animals versus 3.90 +/- 0.26 mg% in their matched controls (p le...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000183915

    authors: Atkins JL

    更新日期:1986-01-01 00:00:00

  • Two distinct epithelial responses may compensate for the ureteral obstruction in early and late phase of unilateral ureteral obstruction-treated rat: cellular proliferation in acute phase and osteopontin expression in chronic phase.

    abstract::In order to clarify cellular responses in dilated renal tubules in the acute and chronic phase of ureteral obstruction, we investigated the expression of proliferating cell nuclear antigen and osteopontin (OPN) in unilateral ureteral obstruction (UUO)-treated rat kidneys. The results showed that renal epithelial cells...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000190298

    authors: Sakai T,Tanaka H,Shirasawa T

    更新日期:1997-01-01 00:00:00

  • Stimulation of polymorphonuclear leukocyte chemotaxis by cold precipitable complexes containing DNA-anti-DNA in active nephritis of systemic lupus erythematosus.

    abstract::DNA-anti-DNA cold precipitable complexes (CPC) isolated from 21 patients with systemic lupus erythematosus were tested for their ability to stimulate polymorphonuclear leukocyte (PMN) chemotaxis and to activate complement in vitro. The complexes activated complement in 20 out of 21 cases and stimulated PMN chemotaxis ...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000182509

    authors: Losito A,Cecchini C,Pittavini L,Zampi I

    更新日期:1982-01-01 00:00:00

  • Prevalence of hypocitraturia and hypopyrophosphaturia in recurrent calcium stone formers: as isolated defects or associated with other metabolic abnormalities.

    abstract::Several underlying metabolic abnormalities may be present in patients with recurrent calcium calculus disease (RCCD). The aim of this study was to determine the prevalence of deficiencies of 2 well-known potent inhibitors of crystal formation and growth, citrate and pyrophosphate, in the various metabolic subgroups an...

    journal_title:Nephron

    pub_type: 临床试验,杂志文章

    doi:10.1159/000186179

    authors: Laminski NA,Meyers AM,Sonnekus MI,Smyth AE

    更新日期:1990-01-01 00:00:00

  • Renal transplantation in diabetes mellitus. Influence of preexisting vascular disease on outcome.

    abstract::We reviewed the recommendations and outcomes for all patients with diabetes mellitus and end-stage renal disease referred to the Medical Center Hospital of Vermont from 1971 through December 1983. During this period, we recommended transplantation in 53 of 73 patients evaluated. Thirty-two transplants were performed i...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000183693

    authors: Rimmer JM,Sussman M,Foster R,Gennari FJ

    更新日期:1986-01-01 00:00:00

  • Radial artery pseudoaneurysm complicating a Brescia-Cimino dialysis fistula.

    abstract::The authors describe an unusual case of radial artery pseudoaneurysm in a patient with a Brescia-Cimino fistula. Evaluation of a pulsatile mass on the patient's forearm which occurred after hemodialysis led to a nondiagnostic fistulogram. Color flow ultrasound was helpful in identifying the nature of the abnormality, ...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000188958

    authors: Labus TP,Trerotola SO,Savader SJ

    更新日期:1996-01-01 00:00:00

  • Recovery of decreased ability of peripheral-blood mononuclear cells from chronic renal failure to produce interleukin-1 alpha and beta after renal transplantation.

    abstract::The ability of cultured peripheral-blood mononuclear cells (PBMC) to release interleukin-1 alpha and beta (IL-1 alpha, IL-1 beta) in response to concanavalin A (con A) was investigated in patients with chronic renal failure (CRF) and in renal transplant recipients. Mean IL-1 alpha level released by PBMC of healthy sub...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000186478

    authors: Kang XX,Hirano T,Oka K,Tamaki T,Sakurai E,Kaji N,Yoshida M,Kozaki M

    更新日期:1991-01-01 00:00:00

  • Preventive effect of ulinastatin on renal scarring in rat model of pyelonephritis induced by direct or ascending infection with Serratia marcescens or Escherichia coli.

    abstract::Renal scarring is considered to be a characteristic of reflux nephropathy. The effects of ulinastatin, a strong inhibitor of polymorphonuclear leukocyte elastase, on renal scarring following direct parenchymal or intravesical ascending infection by Serratia marcescens or Escherichia coli were determined. Four days of ...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000188362

    authors: Matsumoto T,Haraoka M,Mizunoe Y,Takahashi K,Kubo S,Sakumoto M,Tanaka M,Kumazawa J

    更新日期:1995-01-01 00:00:00

  • Fungal peritonitis in patients on continuous ambulatory peritoneal dialysis. Three recoveries in 5 cases without catheter removal.

    abstract::We attempted to treat 5 patients on CAPD with fungal peritonitis without removing the catheter. In 1 case, amphotericin B caused a severe chemical peritonitis. The other 4 patients received amphotericin B intravenously and miconazole or flucytosine intraperitoneally. Recovery was obtained in 3 cases without removing t...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000183582

    authors: Benevent D,Peyronnet P,Lagarde C,Leroux-Robert C

    更新日期:1985-01-01 00:00:00

  • Development and Internal Validation of a Prediction Model to Estimate the Probability of Left-Ventricular Diastolic Dysfunction in Stable Maintenance Hemodialysis Patients without Clinical Heart Failure.

    abstract:OBJECTIVE:To develop and internally validate a multivariable prediction model based on simple clinical record data and laboratory tests and to estimate the probability of left-ventricular diastolic dysfunction (LVDD) in stable maintenance hemodialysis (MHD) patients without clinical heart failure. DESIGN:Cross-section...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000499605

    authors: Sun L,Ji Y,Wang Y,Zhu D,Chen F,Zhang N,Shen E,Wang X

    更新日期:2019-01-01 00:00:00

  • [Regulation of erythropoietin synthesis].

    abstract::The main regulatory hormone for the control of erythropoiesis is erythropoietin (EPO). This glycoprotein has a molecular weight of 34,000 daltons, about 40% of which is represented by carbohydrates. EPO leads to an enhanced mitosis and differentiation of erythroid precursors (colony-forming unit erythroid) in the bone...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000185562

    authors: Bauer C,Kurtz A,Eckardt KU,Tannahill L

    更新日期:1989-01-01 00:00:00

  • Declining Estimated Glomerular Filtration Rate and Its Association with Mortality and Comorbidity Over 10 Years in Elderly Women.

    abstract:BACKGROUND/AIMS:Renal function deteriorates with age, but a few studies have addressed this longitudinally in elderly women. Our objective was, using 5 estimated glomerular filtration rates (eGFR)-equations, to evaluate changes in renal function and association with adverse outcomes for a decade in 75-year-old women. ...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000435790

    authors: Malmgren L,McGuigan FE,Berglundh S,Westman K,Christensson A,Åkesson K

    更新日期:2015-01-01 00:00:00

  • Lipophilic antioxidants and iron status in ESRD patients on hemodialysis.

    abstract::Cardiovascular disease remains the major cause of mortality in hemodialysis patients. Abnormal oxidative stress and impaired antioxidant defense may contribute to accelerated atherogenesis associated with uremia. As oxidative modification of lipids appears to be a prerequisite for the development of atherosclerotic le...

    journal_title:Nephron

    pub_type: 临床试验,杂志文章

    doi:10.1159/000045830

    authors: Lim PS,Chan EC,Lu TC,Yu YL,Kuo SY,Wang TH,Wei YH

    更新日期:2000-12-01 00:00:00

  • Membranous glomerulonephritis associated with renal cell carcinoma: failure to detect a nephritogenic tumor antigen.

    abstract::A 57-year-old man with renal cell carcinoma associated with membranous glomerulonephropathy (MGN) developed a transient amelioration of the nephrotic syndrome after excision of the tumor. We tried to identify a nephritogenic tumor antigen using the immunoblotting technique in this patient with MGN, since previous stud...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000049047

    authors: Togawa A,Yamamoto T,Suzuki H,Watanabe K,Matsui K,Nagase M,Hishida A

    更新日期:2002-02-01 00:00:00

  • Peritonitis in continuous ambulatory peritoneal dialysis: analysis of an 8-year experience.

    abstract::Experiences with peritonitis in a continuous ambulatory peritoneal dialysis (CAPD) program at a single center over 8 years were reviewed. Home-acquired peritonitis rates have been less than 1 episode per patient year since 1982. Gram-positive organisms continue to account for most episodes in a similar proportion. Act...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000183807

    authors: Prowant B,Nolph K,Ryan L,Twardowski Z,Khanna R

    更新日期:1986-01-01 00:00:00

  • Trajectory of Estimated Glomerular Filtration Rate Predicts Renal Injury in Children with Multicystic Dysplastic Kidney.

    abstract:BACKGROUND/AIMS:Children with a solitary functioning kidney have a risk of renal injury caused by hyperfiltration. Timely intervention with renin-angiotensin inhibitors may be beneficial. We examined whether trajectory of estimated glomerular filtration rate (eGFR) would predict renal injury, defined as microalbuminuri...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000490200

    authors: Matsumura K,Sugii K,Awazu M

    更新日期:2018-01-01 00:00:00

  • Chromoblastomycosis in a renal transplant patient.

    abstract::Chromoblastomycosis is a rare, deep mycosis seen mostly in tropical and subtropical regions. We have encountered a kidney transplant recipient with this subcutaneous mycosis developing as an asymptomatic mass in the right forearm. The lesion recurred after an initial local excision, but it is now apparently cured 10 m...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000183468

    authors: Morales LA,González ZA,Santiago-Delpín EA

    更新日期:1985-01-01 00:00:00

  • Urinary fibrinogen and fibrin fragments in children with renal disease.

    abstract::Fibrinogen fragments (X, Y, D and E) and fibrin fragments (D-dimer and E) were examined in the urine of 52 patients with various types of renal diseases. One or more of the fibrinogen fragments were detectable in all the urine specimens. D-Dimer together with fibrinogen fragments was found in 38 of the 52 patients. Th...

    journal_title:Nephron

    pub_type: 杂志文章

    doi:10.1159/000182833

    authors: Yoshioka K,Iseki T,Akano N,Uraoka Y,Miyata H,Maki S

    更新日期:1982-01-01 00:00:00