Abstract:
:The occurrence of familial heart disease in association with tricuspid atresia is rare. The first reported instance of tricuspid atresia and Ebstein's anomaly in siblings is presented. The presence of these two distinct pathologic variants of tricuspid valve malformations in siblings suggests that these malformations result from a common abnormality occurring during the development of the inlet portion of the right ventricle.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Grant JWdoi
10.1007/s002469900072subject
Has Abstractpub_date
1996-09-01 00:00:00pages
327-9issue
5eissn
0172-0643issn
1432-1971journal_volume
17pub_type
杂志文章abstract::Children with trisomy 21 have a high incidence of congenital heart disease that frequently requires surgical repair. These patients often require multiple and higher dosage sedatives during the postoperative period. Dexmedetomidine is an alpha(2)-adrenergic receptor agonist that has sedative, analgesic, and anxiolytic...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0072-6
更新日期:2007-09-01 00:00:00
abstract::Aortopulmonary window is a relatively uncommon congenital heart defect. We report on a patient with a small aortopulmonary window, who presented with an asymptomatic murmur and in whom catheter closure was successfully performed with an Amplatzer Duct Occluder. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-002-0307-0
更新日期:2003-05-01 00:00:00
abstract::A 39-week-old phenotypically female infant was born with hypoplastic left heart syndrome and expired on the third day of life. An autopsy revealed the patient to also have male pseudohermaphroditism and uterus bicornis bicollis. The association of hypoplastic left heart syndrome and male pseudohermaphroditism has been...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00795715
更新日期:1995-09-01 00:00:00
abstract::The most common modes of medical education for congenital heart disease (CHD) rely heavily on 2-dimensional imaging. Three-dimensional (3D) printing technology allows for the creation of physical cardiac models that can be used for teaching trainees. 3D printed cardiac models were created for the following lesions: pu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02146-8
更新日期:2019-08-01 00:00:00
abstract::A patient with pulmonary valve stenosis associated with pseudohypertrophic muscular dystrophy is reported. The anomalies were detected by two-dimensional echocardiography and elevated serum enzymes, conformed by right ventriculography and muscles biopsy. The association between these two pathologies is unknown. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-0051-x
更新日期:2002-03-01 00:00:00
abstract::We aimed to investigate the complications after epicardial pacemaker (PM) implantation in neonates and infants and their relationship with factors such as device size and patient size. Between May 2010 and July 2018, 55 patients under 1 year of age who underwent epicardial PM placement were retrospectively evaluated. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02306-1
更新日期:2020-04-01 00:00:00
abstract::Modifications of the Fontan operation can afford excellent palliation for many patients with a variety of forms of single ventricle. In properly selected patients who are good candidates, early and late survival can be as high as 95-97%. However, mortality is considerably higher for patients with risk factors for poor...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-007-9003-4
更新日期:2007-11-01 00:00:00
abstract::Fetal interventions have been performed for some congenital heart diseases. However, these procedures have not gained wide acceptance due to concerns about their efficacy and safety. The aim of this study was to report on a preliminary experience with fetal cardiac interventions in Brazil. Twenty-two cardiac intervent...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0792-3
更新日期:2014-03-01 00:00:00
abstract::Dextro-transposition of the great arteries (D-TGA) is one of the most common cyanotic heart lesions. The arterial switch operation (ASO) is the preferred surgical palliation for D-TGA. One of the primary concerns following the ASO is complications arising from the coronary artery transfer. There is a need for myocardi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1890-z
更新日期:2018-08-01 00:00:00
abstract::Right ventricular (RV) pacing can be associated with impairment of left ventricular (LV) function due to electrical dyssynchrony and myocardial remodeling (Janousek et al. in J Cardiovasc Electrophysiol 15:470-474, 2004). RV-pacing induced ventricular dysfunction is reversible by techniques such as biventricular pacin...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1629-2
更新日期:2017-08-01 00:00:00
abstract::Although the Fontan operation can improve outcomes, surviving patients still face Fontan-associated liver disease (FALD). The aim of this study was to determine the associated factors of FALD in relation to ultrasound liver elastography. A cross-sectional study was conducted for all patients on whom an ultrasound uppe...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02422-y
更新日期:2020-12-01 00:00:00
abstract::Nesiritide is a synthetic form of B-type natriuretic peptide. It is approved for the treatment of acute exacerbations of congestive heart failure in hospitalized adult patients. It is currently under investigation for use in other settings and other patient populations. This article describes administration of nesirit...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0064-6
更新日期:2007-05-01 00:00:00
abstract::Ductal stenting (DS) palliates duct-dependent lesions using coronary stents. Sirolimus-eluting stents have replaced bare-metal stents in coronary interventions. Concerns exist about sirolimus levels in neonates. Therapeutic immunosuppressive sirolimus level is 5-15 ng/ml. After neonatal DS, drug levels were assessed a...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02381-4
更新日期:2020-10-01 00:00:00
abstract::This paper reviews the initial experience of radical correction of truncus arteriosus in the Soviet Union. The anatomy, hemodynamics, diagnosis and surgical technique are described in detail. Five patients were operated on; three survived. The two deaths in this series were due to mistakes in evaluating the indication...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02424960
更新日期:1984-04-01 00:00:00
abstract::Unilateral absence of a pulmonary artery is a rare anomaly. Patients may present with hemoptysis, recurrent respiratory infections, pulmonary hypertension, or congestive heart failure. This report describes the case of a missing right pulmonary artery associated with anomalous left pulmonary venous connection not prev...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0110-x
更新日期:2012-01-01 00:00:00
abstract::Sudden cardiac death in young competitive athletes is tragic and usually due to unsuspected cardiovascular disease. Screening programs for athletes remain debatable, and restriction of athletes from sports can have physical, emotional, and legal ramifications. In this article, we review the epidemiology of the more co...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-012-0170-6
更新日期:2012-03-01 00:00:00
abstract::A 10-month-old boy was referred for tachypnea and heart murmur. An echocardiogram showed unexplained left heart dilation without evidence of an intracardiac shunt. A 64-slice computed tomographic contrast-enhanced angiography showed a large tortuous anomalous artery arising from the descending thoracic aorta and suppl...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9287-z
更新日期:2009-01-01 00:00:00
abstract::Anomalous origin of left pulmonary artery (ALPA) from aorta with atrial septal defect (ASD) is a rare congenital cardiac malformation. We report a case of ALPA from the aorta with ASD in a 1.8-kg baby. Repair was needed at an early age due to progressive congestive heart failure. Surgical correction was performed with...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9234-z
更新日期:2008-07-01 00:00:00
abstract::Respiratory viral infections in infants undergoing congenital heart surgery lead to prolonged intubation time, hospital (HLOS) and cardiac intensive care unit length of stay (CICU LOS). The objective of this study was to evaluate the prevalence of respiratory viruses using molecular testing in otherwise healthy infant...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1994-5
更新日期:2019-02-01 00:00:00
abstract::A neonate with pulmonary interstitial glycogenosis, pulmonary hypertension, and hypertrophic cardiomyopathy is described. The fatal outcome for this patient contrasts with the reported favorable prognosis associated with isolated pulmonary interstitial glycogenosis. To the authors' knowledge, the association of pulmon...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0311-y
更新日期:2013-02-01 00:00:00
abstract:BACKGROUND:This study aimed to provide descriptive information about off-label treatment practice with clopidogrel in a pediatric population. METHODS:Patients less than 18 years of age prescribed clopidogrel between March 2002 and August 2005 were retrospectively identified at Children's Hospital, Boston. Data from th...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9289-x
更新日期:2009-02-01 00:00:00
abstract::From 1981 through June 1989, 59 children had surgery for a complete atrioventricular (AV) canal defect at Oregon Health Sciences University. We compared the morbidity, mortality, and hemodynamic status of 47 children with and 12 without Down's syndrome through review of operative, clinical, and cardiac catheterization...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00798209
更新日期:1992-04-01 00:00:00
abstract::This study aimed to clarify the characteristics of pulmonary arterial resistance (Rp)-compliance (Cp) coupling in individuals with Down syndrome (DS), who have increased risks of pulmonary arterial hypertension (PAH). We performed cardiac catheterization before and after corrective surgery in 85 DS infants and 85 cont...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02080-9
更新日期:2019-04-01 00:00:00
abstract::The American Academy of Pediatrics (AAP) recommends that any child diagnosed with hypertension have an echocardiogram to evaluate for the presence of left-ventricular (LV) hypertrophy (LVH) and advocates that LVH is an indication to initiate or intensify antihypertensive therapy. However, there is no consensus on the ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0829-7
更新日期:2014-04-01 00:00:00
abstract::The longer survival of patients with Duchenne muscular dystrophy due to advances in clinical care has increased the incidence of Duchenne muscular dystrophy-associated cardiomyopathy, a nearly consistent feature in the third decade of life. A 26-year-old patient with Duchenne muscular dystrophy experienced severe acut...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02072-9
更新日期:2019-03-01 00:00:00
abstract::Systemic candidiasis developed in a seven-week-old premature baby after 6 weeks treatment with antibiotics for suspected septicemia. At that time the echocardiogram showed a dense layer of echoes posteriorly to the anterior tricuspid leaflet during atrial systole. The diagnosis of Candida endocarditis with vegetations...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02281007
更新日期:1983-01-01 00:00:00
abstract::This study identified tracheobronchial cartilage calcification in children with congenital heart disease. Calcification of the tracheobronchial airways has been found previously in adults receiving warfarin and in children receiving warfarin after mitral valve replacement. A 9-year-old girl who had received a Fontan r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0880-z
更新日期:2014-08-01 00:00:00
abstract::The aim of this study is to evaluate the relationship between maternal single nucleotide polymorphisms (SNPs) of methylenetetrahydrofolate reductase (MTHFR) gene with plasma homocysteine (HCY) level and offspring congenital heart diseases (CHDs). 338 mothers with offspring CHDs as case group and 306 mothers of normal ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02449-1
更新日期:2020-11-21 00:00:00
abstract::Our purpose was to evaluate the impact of suspicion or confirmation of heart disease on the physical and psychosocial health of children. We utilized the Child Health Questionnaire (CHQ PF-50). Children ages 5 to 18 years attending a general cardiology clinic were eligible. Those with primary noncardiac diagnoses unre...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0348-z
更新日期:2004-01-01 00:00:00
abstract:INTRODUCTION:Newborns with congenital diaphragmatic hernia (CDH) have varying degrees of pulmonary hypoplasia and pulmonary hypertension (PH), and there is limited evidence that cardiac dysfunction is present. We sought to study early neonatal biventricular function and performance in these patients by reviewing early ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1850-7
更新日期:2018-06-01 00:00:00