Abstract：
:From 1981 through June 1989, 59 children had surgery for a complete atrioventricular (AV) canal defect at Oregon Health Sciences University. We compared the morbidity, mortality, and hemodynamic status of 47 children with and 12 without Down's syndrome through review of operative, clinical, and cardiac catheterization records. Overall, 10 children with Down's syndrome have died, nine from cardiac cause within 90 days of surgery. The 2-year survival of these children was 77 +/- 6% as compared to 100% in children without Down's syndrome (p = 0.08). Early age at surgery, the surgical anatomy of the AV canal, and gender had no significant effect on survival. Before surgery, the hemodynamic status of Down's syndrome and non-Down's syndrome children did not differ; in a small group of post-operative catheterization, right heart pressures and pulmonary vascular resistance remained significantly higher in the Down's syndrome as compared to non-Down's syndrome children. These trends to higher mortality and poorer postoperative hemodynamics in children with Down's syndrome may necessitate closer follow-up if confirmed in other cohorts.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Morris CD,Magilke D,Reller Mdoi
10.1007/BF00798209subject
Has Abstractpub_date
1992-04-01 00:00:00pages
80-4issue
2eissn
0172-0643issn
1432-1971journal_volume
13pub_type
杂志文章abstract：:The purpose of this study was to describe the long-term outcome of infants with hypoplastic left heart syndrome (HLHS) who underwent placement of internal pulmonary artery bands as part of a transcatheter palliation procedure followed by primary heart transplantation. Transcatheter palliation included stenting of the ...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-009-9424-3
更新日期：2009-05-01 00:00:00
abstract：:Internationally, there have been isolated case reports published of children presenting with dilated cardiomyopathy (DCM) in the setting of undiagnosed rickets. Although there has been an increased prevalence of rickets in the United States, there has been only one documented case of associated DCM. At our institution...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-009-9444-z
更新日期：2009-08-01 00:00:00
abstract：:We present a case of congenital pulmonary systemic collateral vein associated with truncus arteriosus. Pulmonary systemic collateral vein with nonobstructed left atrial egress is different from those with obstructed left atrial egress in that it is functionally redundant. Including this case, 8 patients among 33 repor...
journal_title：Pediatric cardiology
pub_type： 杂志文章,评审
doi：10.1007/s00246-002-0439-2
更新日期：2004-01-01 00:00:00
abstract：:Postoperative arrhythmia is a common complication after open heart surgery in children. JET is the most common and dangerous arrhythmia. We aimed to assess safety and efficacy of prophylactic amiodarone in preventing JET in children underwent cardiac surgery and to assess risk factors for JET among our patients. In to...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-016-1343-5
更新日期：2016-04-01 00:00:00
abstract：:Screening with portable echocardiography has uncovered a large burden of latent rheumatic heart disease (RHD) among asymptomatic children in endemic regions, the significance of which remains unclear. This study aimed to determine the 2-year outcomes for children with latent RHD diagnosed by echocardiographic screenin...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-014-0925-3
更新日期：2014-10-01 00:00:00
abstract：:The longer survival of patients with Duchenne muscular dystrophy due to advances in clinical care has increased the incidence of Duchenne muscular dystrophy-associated cardiomyopathy, a nearly consistent feature in the third decade of life. A 26-year-old patient with Duchenne muscular dystrophy experienced severe acut...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-019-02072-9
更新日期：2019-03-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-009-9603-2
更新日期：2010-05-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-015-1327-x
更新日期：2016-04-01 00:00:00
abstract：:Rhabdomyoma is the most common primary cardiac tumor in infants and children and is often associated with tuberous sclerosis. Surgical resection may be indicated and, if so, is usually curative. We describe a rhabdomyoma in an infant who presented with severe myocardial ischemia necessitating orthotopic heart transpla...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/BF00794197
更新日期：1995-07-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 临床试验,杂志文章
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更新日期：2010-10-01 00:00:00
abstract：:Congenital diverticulum of the ventricle is a rare disease, but most cases of congenital left ventricular diverticula are asymptomatic. We present a child with congenital left ventricular diverticulum whose routine electrocardiographic examination showed T-wave inversion in inferior and V4 to V6 leads. He was successf...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-010-9719-4
更新日期：2010-08-01 00:00:00
abstract：:Since its first description in Japan 30 years ago, Kawasaki disease has been reported worldwide. Although an infectious etiology is suspected based on the epidemiology and clinical features, a causative agent has not been identified. The majority of the morbidity and mortality associated with this condition is attribu...
journal_title：Pediatric cardiology
pub_type： 杂志文章,评审
doi：10.1007/s002469900436
更新日期：1999-05-01 00:00:00
abstract：:For some congenital heart lesions, higher institutional surgical volume has been associated with better survival than in lower volume centers. The relationship between institutional surgical volume and mortality in infants after total anomalous pulmonary vein return (TAPVR) repair has not been well explored. The Texas...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-019-02224-x
更新日期：2020-01-01 00:00:00
abstract：:In this article we report the first case of Q fever endocarditis in a 13 years old child with a percutaneous pulmonary Melody® valve. The patient had a new onset of Melody valve dysfunction associated with the combination of hepatosplenomegaly and pancytopenia but was afebrile. Although blood cultures were negative, w...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-017-1723-5
更新日期：2018-01-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/BF02310569
更新日期：1991-10-01 00:00:00
abstract：:The hospitalization of a child for cardiac surgery is known to be a stressful experience for parents. However, little is known about the time course or the relationships between parental stress and the child's actual or perceived recovery. This research aimed to investigate pre- and postoperative parental stress and t...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-010-9726-5
更新日期：2010-10-01 00:00:00
abstract：:To assess the prevalence, history, and treatment of arrhythmias, in particular preexcitation and Wolff-Parkinson-White (WPW) syndrome, in patients with Ebstein anomaly (EA) during childhood and adolescence, we performed a multicenter retrospective study of all consecutive live-born patients with EA, diagnosed, and fol...
journal_title：Pediatric cardiology
pub_type： 杂志文章,多中心研究
doi：10.1007/s00246-009-9590-3
更新日期：2010-02-01 00:00:00
abstract：:While exercise stress testing (EST) is an important tool, little is known about its use for determining ischemia in patients with hypoplastic left heart syndrome (HLHS) and Fontan palliation. We sought to determine the frequency of ST segment changes during EST in HLHS patients after Fontan and examine results of furt...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-015-1312-4
更新日期：2016-03-01 00:00:00
abstract：:Sudden cardiac death in young competitive athletes is tragic and usually due to unsuspected cardiovascular disease. Screening programs for athletes remain debatable, and restriction of athletes from sports can have physical, emotional, and legal ramifications. In this article, we review the epidemiology of the more co...
journal_title：Pediatric cardiology
pub_type： 杂志文章,评审
doi：10.1007/s00246-012-0170-6
更新日期：2012-03-01 00:00:00
abstract：:Tricuspid valve malformation is a rare congenital heart disease. Prenatal diagnosis of Ebstein's anomaly (EA) and tricuspid valve dysplasia (TVD) is associated with high mortality. There are conflicting reports concerning accurate prognostication after diagnosis in utero. The aim of our study was to assess prognostic ...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-012-0355-z
更新日期：2012-12-01 00:00:00
abstract：:This study reviewed different types of primary cardiac and mediastinal tumors in infants and children as well as their clinical presentation and management. Altogether, 34 consecutive patients followed from 1976 through December 2005 were analyzed. Of these 34 patients, 14 (41%) underwent surgery and 20 (59%) with rha...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-008-9256-6
更新日期：2008-11-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/BF00795379
更新日期：1993-10-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章,评审
doi：10.1007/s00246-003-0593-1
更新日期：2004-05-01 00:00:00
abstract：:The patient safety movement and human factors studies are becoming an increasingly important part of everyday clinical practice. Pediatric cardiac surgery is a high-risk field that is very much dependent on safe practices and continuous research into improvement of outcomes. This article reviews the main research fram...
journal_title：Pediatric cardiology
pub_type： 杂志文章,评审
doi：10.1007/s00246-006-1448-3
更新日期：2007-03-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-015-1208-3
更新日期：2015-12-01 00:00:00
abstract：:Cardiac involvement of Duchenne and Becker muscular dystrophies (DMD/BMD) is the most common cause of fatal outcomes. It is still unclear whether some DMD/BMD gene mutations might be predictive of cardiac involvement. In this study, we provide a comprehensive overview on genotypes of cardiac disease in DMD/BMD. We sys...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-020-02470-4
更新日期：2020-10-09 00:00:00
abstract：:Cardiopulmonary bypass (CPB) reduces coagulation factor levels through hemodilution and consumption. Differences in CPB-induced alterations of factor XIII (FXIII) levels in children with cyanotic and acyanotic congenital heart defects (CHDs) are not well characterized. FXIII activity (determined by Berichrom assay), p...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-014-0903-9
更新日期：2014-10-01 00:00:00
abstract：:Previous studies showed the reliability of cardiac magnetic resonance imaging (cMRI) in the quantification of aortic valve stenosis in adults. The aim of this retrospective study was to assess the ability of cMRI in the quantification of congenital aortic valve stenosis (CAS) in children. Nineteen patients (mean age 1...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-013-0851-9
更新日期：2014-06-01 00:00:00
abstract：:Our objective was to understand the scope of pediatric heart failure (HF) and the current staffing environment of HF programs. An online survey was distributed to members of the Pediatric Heart Transplant Study and the Pediatric Council of the International Society for Heart and Lung Transplantation. All participants ...
journal_title：Pediatric cardiology
pub_type： 杂志文章,多中心研究
doi：10.1007/s00246-017-1756-9
更新日期：2018-02-01 00:00:00
abstract：:Chylous effusions frequently occur after cardiac surgery due to severe damage to the lymphatic system, thus indicating that the insertion of a chest tube may be necessary. Factor XIII (FXIII) is discussed as being essential for wound healing. The aim of this retrospective study was to evaluate whether the application ...
journal_title：Pediatric cardiology
pub_type： 杂志文章
doi：10.1007/s00246-005-0993-5
更新日期：2006-01-01 00:00:00
