The role of the epinephrine test in the diagnosis and management of children suspected of having congenital long QT syndrome.

abstract：:Hyperplastic left heart syndrome (HLHS) patients are palliated by creating a Fontan-type circulation passing from different surgical stages. The aim of this work is to describe the evolution of ventricular energetics parameters in HLHS patients during the different stages of palliation including the hybrid, the Norwoo...

journal_title：Pediatric cardiology

authors： Di Molfetta A,Iacobelli R,Guccione P,Di Chiara L,Rocchi M,Cobianchi Belisari F,Campanale M,Gagliardi MG,Filippelli S,Ferrari G,Amodeo A

更新日期：2017-12-01 00:00:00

abstract：:This study examined the age-related criteria of signal-averaged electrocardiographic (SA-ECG) parameters in children. SA-ECGs were obtained in 82 healthy volunteers in six groups depending on age (group 1: 1 day to < 1 month; group 2: 1 month to < 1 year; group 3: 1 to < 6 years; group 4: 6 to < 12 years; group 5: 12 ...

journal_title：Pediatric cardiology

authors： Hayabuchi Y,Matsuoka S,Kubo M,Akita H,Kuroda Y

更新日期：1994-05-01 00:00:00

abstract：:For premature infants with congenital heart disease (CHD), it may be unclear when the burdens of treatment outweigh potential benefits. Parents may thus have to choose between comfort care at birth and medical stabilization until surgical repair is feasible. Better defined outcome data, including risk factors for mort...

journal_title：Pediatric cardiology

authors： Lynema S,Fifer CG,Laventhal NT

更新日期：2016-06-01 00:00:00

abstract：:The HOXA1 gene plays a fundamental role in embryonic morphogenesis. Recent studies in humans and mice have indicated that HOXA1 plays a previously unrecognized role in cardiovascular system development. Congenital heart disease (CHD), particularly ventricular septal defect (VSD), might be a clinically isolated manifes...

journal_title：Pediatric cardiology

authors： Liu J,Wang B,Chen X,Li H,Wang J,Cheng L,Ma X,Gao B

更新日期：2013-02-01 00:00:00

abstract：:Nesiritide is a synthetic form of B-type natriuretic peptide. It is approved for the treatment of acute exacerbations of congestive heart failure in hospitalized adult patients. It is currently under investigation for use in other settings and other patient populations. This article describes administration of nesirit...

journal_title：Pediatric cardiology

authors： Reynolds EW,Conely ET,Vranicar M

更新日期：2007-05-01 00:00:00

abstract：:Dextro-transposition of the great arteries (D-TGA) is one of the most common cyanotic heart lesions. The arterial switch operation (ASO) is the preferred surgical palliation for D-TGA. One of the primary concerns following the ASO is complications arising from the coronary artery transfer. There is a need for myocardi...

journal_title：Pediatric cardiology

authors： Noel CV,Krishnamurthy R,Masand P,Moffett B,Schlingmann T,Cheong BY,Krishnamurthy R

更新日期：2018-08-01 00:00:00

abstract：:Enlarged bronchial arteries and/or systemic-to-pulmonary collaterals have been frequently demonstrated in association with transposition of the great arteries. They are usually clinically silent, although they might be large enough to cause accelerated pulmonary vascular obstructive disease or symptomatic cardiac volu...

journal_title：Pediatric cardiology

authors： Santoro G,Carrozza M,Russo MG,Calabrò R

更新日期：2008-07-01 00:00:00

abstract：BACKGROUND:Cardiac magnetic resonance imaging (MRI) is an important diagnostic tool for congenital heart disease (CHD), as reflected by class 1 recommendations for the use of cardiac MRI by various consensus panels. However, little is known about the safety and clinical utility of cardiac MRI for these critically ill i...

journal_title：Pediatric cardiology

authors： Sarikouch S,Schaeffler R,Körperich H,Dongas A,Haas NA,Beerbaum P

更新日期：2009-02-01 00:00:00

abstract：:This study identified tracheobronchial cartilage calcification in children with congenital heart disease. Calcification of the tracheobronchial airways has been found previously in adults receiving warfarin and in children receiving warfarin after mitral valve replacement. A 9-year-old girl who had received a Fontan r...

journal_title：Pediatric cardiology

authors： Eckersley L,Stirling J,Occleshaw C,Wilson N

更新日期：2014-08-01 00:00:00

abstract：:Atrioventricular block has been described in association with cases of long QT syndrome and mortality is increased in this subgroup. We describe an infant with congenital QT prolongation and atrioventricular block with normal cardiac function, leading to the initial diagnosis of long QT syndrome. She subsequently deve...

journal_title：Pediatric cardiology

authors： Walls J,Dipchand A,Sanatani S

更新日期：2006-01-01 00:00:00

abstract：:This prospective observational study conducted in a neonatal intensive care unit aimed to evaluate echocardiographic changes provoked by anemia and transfusion of packed red blood cells (pRBCs) in premature infants. In this study, 32 anemic premature infants had serial echocardiographic assessment of left ventricular ...

journal_title：Pediatric cardiology

authors： Radicioni M,Troiani S,Mezzetti D

更新日期：2012-04-01 00:00:00

abstract：:Previous studies showed the reliability of cardiac magnetic resonance imaging (cMRI) in the quantification of aortic valve stenosis in adults. The aim of this retrospective study was to assess the ability of cMRI in the quantification of congenital aortic valve stenosis (CAS) in children. Nineteen patients (mean age 1...

journal_title：Pediatric cardiology

authors： Sirin S,Nassenstein K,Neudorf U,Jensen CJ,Mikat C,Schlosser T

更新日期：2014-06-01 00:00:00

abstract：:The vertebrate heart is innervated by the sympathetic and parasympathetic components of the peripheral autonomic nervous system, which regulates its contractile rate and force. Understanding the mechanisms that control sympathetic neuronal growth, differentiation, and innervation of the heart may provide insight into ...

journal_title：Pediatric cardiology

authors： Vincentz JW,Rubart M,Firulli AB

更新日期：2012-08-01 00:00:00

abstract：:Balloon angioplasty for native coarctation of the aorta in infants and children is gaining acceptance as an alternative to surgery in discrete membranous obstruction. The aim of this study was to assess the immediate and intermediate-term effectiveness and safety of balloon angioplasty in infants and children with dis...

journal_title：Pediatric cardiology

authors： Massoud Iel S,Farghly HE,Abdul-Monem A,Botros N,Kassem A,Magraby AE,Dawood A,Abdul-Hakam M

更新日期：2008-05-01 00:00:00

abstract：:Ruptured sinus Valsalva aneurysm (SVA) in a patient with tetralogy of Fallot is a very rare cardiac complication. This report describes the case of a 10-year-old Hispanic girl who presented to her cardiologist for a routine transthoracic echocardiography (TTE), which showed a ruptured sinus of Valsalva, with left-to-r...

journal_title：Pediatric cardiology

authors： Mithani AA,Polimenakos AC,Santucci BA

更新日期：2013-01-01 00:00:00

abstract：:Limited data exist on the impact of prenatal diagnosis and outcomes of fetal truncus arteriosus (TA). We sought to assess prenatal diagnostic accuracy and prenatal outcomes in fetuses with TA and compare postnatal outcomes in neonates with prenatally and postnatally diagnosed TA. Records were reviewed for patients dia...

journal_title：Pediatric cardiology

authors： Swanson TM,Selamet Tierney ES,Tworetzky W,Pigula F,McElhinney DB

更新日期：2009-04-01 00:00:00

abstract：:Currently, it is clear that primary hypertension begins in childhood and that it contributes to the early development of chronic kidney disease (CKD). Hypertension also increases the risk of cardiovascular morbidity and mortality, and that risk rises as blood pressure levels escalate. As among adult patients, overweig...

journal_title：Pediatric cardiology

authors： Assadi F

更新日期：2012-10-01 00:00:00

abstract：:Sudden death accounts for up to 43% of all deaths in patients with familial dysautonomia (FD). The classic features of FD, namely, autonomic dysfunction, high blood pressure, and blood pressure labiality, are all risk factors for cardiac remodeling and hypertrophy. Myocardial remodeling and hypertrophy are independent...

journal_title：Pediatric cardiology

authors： Nussinovitch U,Katz U,Nussinovitch M,Blieden L,Nussinovitch N

更新日期：2009-11-01 00:00:00

abstract：:A 12-year-old male presented with a 6-week history of apparent digital vasculitis with color changes of the distal fingers and erythematous macules of the palms and soles. Physical examination revealed skin findings of Carney complex and an abnormal cardiac examination. Echocardiography demonstrated a large left atria...

journal_title：Pediatric cardiology

authors： Mirkinson LJ,Ratnayaka K,Sable CA,Gaskin PR

更新日期：2006-03-01 00:00:00

abstract：:The authors present an unusual complication of the balloon atrial septostomy procedure performed in a neonate with D-transposition of the great arteries. Cardiac tamponade developed shortly after the balloon atrial septostomy procedure and the infant was found to have a tear in the superior aspect of the left atrium, ...

journal_title：Pediatric cardiology

authors： Blanchard WB,Knauf DG,Victorica BE

更新日期：1983-04-01 00:00:00

abstract：:We measured the coronary flow reserve in a 13-year-old girl with the rare anomaly of an absent left circumflex coronary artery. Although the coronary flow volume of the right coronary artery was at the same level as that of the left anterior descending coronary artery, the coronary flow reserve of the patient's right ...

journal_title：Pediatric cardiology

authors： Itoi T,Oka T,Hamaoka K

更新日期：2001-03-01 00:00:00

abstract：:Pulmonary artery banding (PAB) is used as a surgical palliation to reduce excessive pulmonary blood flow caused by congenital heart defects. Due to the lack of microscopic studies dealing with the tissue remodeling caused by contemporary PAB materials, this study aimed to assess histologic changes associated with PAB ...

journal_title：Pediatric cardiology

authors： Nedorost L,Uemura H,Furck A,Saeed I,Slavik Z,Kobr J,Tonar Z

更新日期：2013-10-01 00:00:00

abstract：:Congenital aneurysms of the thoracic venous system are rare. In particular, innominate venous aneurysms are extremely rare. We describe a 16-year-old girl whose chest x-ray suggested a mediastinal tumor. Three-dimensional contrast-enhancement magnetic resonance venography showed a giant sacciform aneurysm of the left ...

journal_title：Pediatric cardiology

authors： Tsuji A,Katada Y,Tanimoto M,Fujita I

更新日期：2004-07-01 00:00:00

abstract：:A primary rhabdomyosarcoma of the heart observed in a 3-week-old infant, provides an opportunity to review this rare clinical entity; 61 reported cases are collated. The more common sites are right ventricle, left atrium, and right atrium; the tumour may protrude into the cavity and cause obstruction. Echocardiography...

journal_title：Pediatric cardiology

authors： Schmaltz AA,Apitz J

更新日期：1982-01-01 00:00:00

abstract：:Color-coded two-dimensional (2D) echocardiography confirmed the presence of severe congenital mitral regurgitation in an 8-month-old infant. Intraoperative inspection revealed an isolated perforation in the anterior leaflet. ...

journal_title：Pediatric cardiology

authors： Schranz D,Oelert H,Iversen S,Schuind A,Huth R,Jüngst BK,Stopfkuchen H,Erbel R

更新日期：1990-04-01 00:00:00

abstract：:During the development of so-called aneurysmal transformation of perimembranous ventricular septal defects (pmVSD), tricuspid valve (TV) morphology and function may be altered resulting in left ventricular (LV) to right atrial (RA) shunting. The feasibility and outcome of interventional closure of these pmVSD has not ...

journal_title：Pediatric cardiology

authors： Kerst G,Moysich A,Ho SY,Apitz C,Latus H,Schranz D

更新日期：2015-10-01 00:00:00

abstract：:This report describes the case of two pediatric patients who demonstrated echocardiographic evidence of pulmonary hypertension (PH) during the acute phase of Kawasaki disease. The etiology of PH development in this setting is currently unknown, but the authors hypothesize that pulmonary vasculitis may play a significa...

journal_title：Pediatric cardiology

authors： Nicholson GT,Samai C,Kanaan U

更新日期：2013-01-01 00:00:00

abstract：:Previous studies have indicated the importance of allometric scaling of VO2max for body size. However, no information is available on adjusting maximal cardiac output (Qmax) and stroke volume (SVmax) for body dimensions. The allometric exponent b was determined for the equation Y = aXb (where Y is the physiological ou...

journal_title：Pediatric cardiology

authors： Rowland T,Goff D,Martel L,Ferrone L,Kline G

更新日期：2000-09-01 00:00:00

abstract：:We report hemodynamic findings in two patients with pulmonary atresia and intact ventricular septum (PAIVS) after "one-and-a-half ventricle repair" and placement of a bidirectional Glenn shunt using four-dimensional (4D) flow magnetic resonance imaging. Quantification of flow and analysis of flow patterns revealed the...

journal_title：Pediatric cardiology

authors： Uribe S,Bächler P,Valverde I,Crelier GR,Beerbaum P,Tejos C,Irarrazaval P

更新日期：2013-02-01 00:00:00

abstract：:Children with trisomy 21 have a high incidence of congenital heart disease that frequently requires surgical repair. These patients often require multiple and higher dosage sedatives during the postoperative period. Dexmedetomidine is an alpha(2)-adrenergic receptor agonist that has sedative, analgesic, and anxiolytic...

journal_title：Pediatric cardiology

authors： Kalyanaraman M,Costello JL,Starr JP

更新日期：2007-09-01 00:00:00