Abstract：
:Tricuspid valve malformation is a rare congenital heart disease. Prenatal diagnosis of Ebstein's anomaly (EA) and tricuspid valve dysplasia (TVD) is associated with high mortality. There are conflicting reports concerning accurate prognostication after diagnosis in utero. The aim of our study was to assess prognostic factors based on our experience. We reviewed 37 fetuses between 1984 and June 2010 comprising 26 cases of EA and 11 cases of TVD. There were 10 terminations, 5 intrauterine deaths, 8 neonatal deaths, and 14 survivors. We found that the major prognostic factor for outcome was the flow pattern through the pulmonary valve on the first echocardiogram. Retrograde flow was strongly correlated with fetal or neonatal death (p = 8 × 10(-5)), and anterograde flow predicted good outcome (p = 8 × 10(-5)). In contrast, cardiothoracic indexes, right to left-ventricular ratio, and Celermajer index were not useful prognostic markers. The Simpson Andrews Sharland score, which was more complex, was well correlated with our series. Flow through the pulmonary valve on the first echocardiogram is a simple and excellent prognostic factor when major tricuspid valve disease is diagnosed in utero. Fetuses should be monitored throughout pregnancy, particularly those with retrograde ductus arteriosus, because several hemodynamic factors may worsen the prognosis.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Barre E,Durand I,Hazelzet T,David Ndoi
10.1007/s00246-012-0355-zsubject
Has Abstractpub_date
2012-12-01 00:00:00pages
1391-6issue
8eissn
0172-0643issn
1432-1971journal_volume
33pub_type
杂志文章abstract：:At the University of California Davis Medical Center, a screening fetal ultrasound examination (level I or II) incorporates a comprehensive segmental evaluation of the fetal heart. This study evaluated the reliability of the fetal ultrasound exam in the detection of abnormal heart anatomy. Our retrospective study revi...
journal_title：Pediatric cardiology
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journal_title：Pediatric cardiology
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更新日期：2009-07-01 00:00:00
abstract：:Sudden cardiac death in young competitive athletes is tragic and usually due to unsuspected cardiovascular disease. Screening programs for athletes remain debatable, and restriction of athletes from sports can have physical, emotional, and legal ramifications. In this article, we review the epidemiology of the more co...
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pub_type： 杂志文章,评审
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journal_title：Pediatric cardiology
pub_type： 杂志文章
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pub_type： 杂志文章,多中心研究
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journal_title：Pediatric cardiology
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更新日期：2014-08-01 00:00:00
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pub_type： 杂志文章,随机对照试验
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更新日期：2005-09-01 00:00:00
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journal_title：Pediatric cardiology
pub_type： 杂志文章
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更新日期：1994-11-01 00:00:00
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pub_type： 杂志文章,评审
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更新日期：2010-11-01 00:00:00
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journal_title：Pediatric cardiology
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更新日期：1985-01-01 00:00:00
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更新日期：2003-09-01 00:00:00
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abstract：:This prospective observational study conducted in a neonatal intensive care unit aimed to evaluate echocardiographic changes provoked by anemia and transfusion of packed red blood cells (pRBCs) in premature infants. In this study, 32 anemic premature infants had serial echocardiographic assessment of left ventricular ...
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