Double-outlet right ventricle without interventricular communication: an unusual and challenging problem.

Abstract:

:A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy and clinical management of the patient is discussed together with an overview of the existing literature.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Singla M,Al-Radi O,Mertens L

doi

10.1007/s00246-012-0483-5

subject

Has Abstract

pub_date

2013-01-01 00:00:00

pages

1941-4

issue

8

eissn

0172-0643

issn

1432-1971

journal_volume

34

pub_type

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