Abstract:
:A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy and clinical management of the patient is discussed together with an overview of the existing literature.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Singla M,Al-Radi O,Mertens Ldoi
10.1007/s00246-012-0483-5subject
Has Abstractpub_date
2013-01-01 00:00:00pages
1941-4issue
8eissn
0172-0643issn
1432-1971journal_volume
34pub_type
杂志文章abstract::Twelve years after an apparently successful surgical correction of infradiaphragmatic (obstructed) total anomalous pulmonary venous drainage, a 12-year-old boy developed evidence of pulmonary artery hypertension secondary to pulmonary venous obstruction due to an apparent lack of growth at the anastomotic site. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02080561
更新日期:1988-01-01 00:00:00
abstract::The outcome in a series of 23 cases of tetralogy of Fallot diagnosed prenatally was compared to published figures for this condition when (a) identified postnatally or (b) treated surgically. There was a marked difference in the survival between these groups, with the highest mortality (75%) occurring when the diagnos...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00788220
更新日期:1992-01-01 00:00:00
abstract::A 12-year-old male presented with a 6-week history of apparent digital vasculitis with color changes of the distal fingers and erythematous macules of the palms and soles. Physical examination revealed skin findings of Carney complex and an abnormal cardiac examination. Echocardiography demonstrated a large left atria...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-1238-3
更新日期:2006-03-01 00:00:00
abstract::Severe atrioventricular valve (AVV) or semilunar valve (SLV) regurgitation in the setting of a single ventricle physiology may proceed to valve replacement if repair strategies fail. Outcome data for these children are limited. We present transplant-free survival of a case series of children with single ventricle phys...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02234-9
更新日期:2020-01-01 00:00:00
abstract::Two-dimensional echocardiography was performed on a patient with criss-cross atrioventricular (AV) relationship and ventriculo-arterial discordance. A systematic approach from the subcostal area revealed the complex cardiac pathology including the criss-cross AV relationship of right and left heart, indicating that th...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02427034
更新日期:1982-01-01 00:00:00
abstract::Congenital left ventricular diverticulum is a rare cardiac malformation. The incidence of left ventricular diverticulum is reported to be 0.05% of all congenital heart malformations. This case series comprised three infants with the diagnosis of congenital left ventricular diverticulum determined by echocardiography. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0153-7
更新日期:2012-04-01 00:00:00
abstract::Previous studies have indicated the importance of allometric scaling of VO2max for body size. However, no information is available on adjusting maximal cardiac output (Qmax) and stroke volume (SVmax) for body dimensions. The allometric exponent b was determined for the equation Y = aXb (where Y is the physiological ou...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章
doi:10.1007/s002460010102
更新日期:2000-09-01 00:00:00
abstract::The outcome of children born with cyanotic congenital heart disease has markedly improved over the years. Follow up is recommended for most post-operated cases as complications may occur over long term. One of the complications is the development of ventricular dysfunction, often seen after a successful Fontan surgery...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0531-1
更新日期:2013-04-01 00:00:00
abstract::Cardiac surgery for congenital heart disease often necessitates a period of myocardial ischemia during cardiopulmonary bypass and cardioplegic arrest, followed by reperfusion after aortic cross-clamp removal. In experimental models, myocardial ischemia-reperfusion is associated with significant oxidative stress and ve...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1345-3
更新日期:2016-04-01 00:00:00
abstract::A premature child with congenital complete heart block had an epicardial single-chamber pacemaker implanted at 2 days of age. At 21 months of age, while sitting or standing, the patient's right anterior thigh muscles contracted at her pulse rate. Surgical exploration revealed a free-floating pacemaker in her peritoneu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900430
更新日期:1999-03-01 00:00:00
abstract::Noninvasive measurement of cardiac output (CO) and particularly stroke volume (SV) remain difficult but potentially valuable. These variables can be particularly challenging to measure in children with congenital heart disease (CHD). Impedance cardiography (IC) is a technique shown to be accurate in measuring SV in ad...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1456-x
更新日期:2016-12-01 00:00:00
abstract::Congenital diverticulum of the ventricle is a rare disease, but most cases of congenital left ventricular diverticula are asymptomatic. We present a child with congenital left ventricular diverticulum whose routine electrocardiographic examination showed T-wave inversion in inferior and V4 to V6 leads. He was successf...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-010-9719-4
更新日期:2010-08-01 00:00:00
abstract::Rho-kinase (ROCK) belongs to the AGC (protein kinase A/protein kinase G/protein kinase C, PKA/PKG/PKC) family of serine/threonine kinases and is a major downstream effector of small GTPase RhoA. Rho-kinase is involved in a wide range of fundamental cellular functions such as contraction, adhesion, migration, and proli...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-011-9920-0
更新日期:2011-03-01 00:00:00
abstract::Mammalian cardiomyocytes withdraw from the cell cycle soon after birth. This process is called terminal differentiation. The c-kit, a receptor tyrosine kinase, is expressed on cardiomyocytes immediately after birth but for only a few days. In mice with genetic c-kit dysfunction, adult cardiomyocytes are phenotypically...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9366-1
更新日期:2009-07-01 00:00:00
abstract::The original version of the article unfortunately contained an alignment error in Table 1. The correct version of Table 1 is given below. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章,已发布勘误
doi:10.1007/s00246-018-1978-5
更新日期:2019-01-01 00:00:00
abstract::The slip ring and nutate/rotate configuration of the new, fourth-generation, computed tomography (CT) (TCT-900S, Toshiba Medical Company) makes it possible to scan consecutively 25 slices every 75 s. This scanner also rapidly provides hemodynamic and multiplanar reconstruction images. Studies were performed on 13 chil...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02309917
更新日期:1989-04-01 00:00:00
abstract::A 2-year-old girl with cor triatriatum with unroofed coronary sinus and persistent left superior vena cava underwent preoperative radiofrequency catheter ablation for atrial tachycardia attack that developed after admission to our hospital. The procedure was not successful. Cryoablation was successfully performed duri...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-002-0376-0
更新日期:2003-09-01 00:00:00
abstract::The congenital anomaly of aortopulmonary window is rare. Its combination with interruption of the aortic arch has been previously recognized and reported in infants and children. Early and complete repair of such a congenital anomaly may prevent progression to cardiac failure and premature death. We describe the succe...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/BF02505097
更新日期:1996-03-01 00:00:00
abstract::This study is presented to identify and characterize the spectrum of the cardiovascular anomalies in children presenting with Williams-Beuren syndrome and cardiovascular anomalies at The Hospital for Sick Children, Toronto from 1966 to 1988. Forty-nine children were diagnosed and followed. The female to male ratio was...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02310569
更新日期:1991-10-01 00:00:00
abstract::A varying degree of impairment of ventricular performance is observed over the long-term after surgery for a congenital heart defect (CHD). Impaired ventricular performance has been shown to be of prognostic value for increased risk of cardiovascular events in adult CHD patients. This emphasizes the importance of deli...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-013-0802-5
更新日期:2014-01-01 00:00:00
abstract::Routine use of intraoperative transesophageal echocardiography (TEE) is a safe monitoring and diagnostic method during pediatric congenital cardiac surgery. However, the question of whether intraoperative TEE is accurate and cost effective for patients with tetralogy of Fallot (TOF) has not been raised. This study aim...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0423-4
更新日期:2013-02-01 00:00:00
abstract::Coronary artery anatomy represents a challenging and, often, determining predictor of outcome in an arterial switch operation (ASO). Impact of specific coronary artery variants, such as single, intramural and inverted, on time-related events following ASO, is, yet, to be determined. We sought to compare early and late...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1543-z
更新日期:2017-03-01 00:00:00
abstract::We describe two cases of left-side pulmonary vein obstruction observed after the arterial switch operation (Jatene) for D-transposition of the great arteries. This appears to be related to left-sided pulmonary vein obstruction occurring coincidently with D-transposition of the great arteries, rather than a consequence...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900180
更新日期:1997-07-01 00:00:00
abstract::We describe the first report of an infant who was born with hypoplastic left heart syndrome and significant pulmonary stenosis. He was successfully palliated with multiple cardiac catheterization interventions while waiting for cardiac transplantation. This unusual constellation of heart defects is an entity that is r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0856-5
更新日期:2005-09-01 00:00:00
abstract::The current pulse-oximetry screening (POS) protocol for detection of critical congenital heart defects (CCHDs) is recommended only for newborns in well-infant and intermediate care nurseries, and there is no evidence-based protocol for infants discharged from the neonatal intensive care unit (NICU). The objectives of ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0793-2
更新日期:2014-03-01 00:00:00
abstract::The development of Leadless cardiac pacemakers avoids the inherent complications that may occur secondary to lead insertion. A large number of devices have been inserted in adult patients although data in pediatric patients are lacking. We aimed to assess our experience with the Leadless device in the pediatric popula...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02277-y
更新日期:2020-04-01 00:00:00
abstract::Patency of the ductus arteriosus (PDA) is a common finding in small premature infants. Recently pulsed-Doppler-cross sectional echocardiography (PD-CSE) has been successfully used in these patients. We report a case of a premature infant with an unusual PD-CSE pattern. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02279882
更新日期:1988-01-01 00:00:00
abstract::The aim of the study is to identify reliable quantitative fetal echocardiographic predictors for postnatal development of coarctation (CoA). In this retrospective study, we included 65 fetuses with a prenatally suspected, isolated CoA, born 2010-2018. Dimensions of the cardiac structures, aortic, and ductal arches exp...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02509-6
更新日期:2020-12-23 00:00:00
abstract::Two cases of arrhythmogenic right ventricular dysplasia (ARVD) in siblings are reported. In the boy, 14 years old, the clinical history, ECG, echocardiography, and histopathological findings were consistent with ARVD. Premature ventricular contractions of left bundle branch block (LBBB) pattern were recorded but no ve...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02239576
更新日期:1990-04-01 00:00:00
abstract::Myocardial contractility and relaxation are highly dependent on calcium homeostasis. Immature myocardium, as in pediatric patients, is thought to be more dependent on extracellular calcium for optimal function. For this reason, intravenous calcium chloride infusions may improve myocardial function in the pediatric pat...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1322-2
更新日期:2016-03-01 00:00:00