Prognosis in fetal tetralogy of Fallot.

abstract：:Warfarin dosing is challenging due to a multitude of factors affecting its pharmacokinetics (PK) and pharmacodynamics (PD). A novel personalised dosing algorithm predicated on a warfarin PK/PD model and incorporating CYP2C9 and VKORC1 genotype information has been developed for children. The present prospective, obser...

journal_title：Pediatric cardiology

authors： Al-Metwali BZ,Rivers P,Goodyer L,O'Hare L,Young S,Mulla H

更新日期：2019-12-01 00:00:00

abstract：OBJECTIVE:Heterotaxy syndrome is associated with complex cardiac malformations and cardiac conduction system abnormalities. Those with right atrial isomerism (RAI) have dual sinus nodes and dual atrioventricular nodes predisposing them to supraventricular tachycardia (SVT). Those with left atrial isomerism (LAI) lack a...

journal_title：Pediatric cardiology

authors： Ozawa Y,Asakai H,Shiraga K,Shindo T,Hirata Y,Hirata Y,Inuzuka R

更新日期：2019-06-01 00:00:00

abstract：:In this report, we describe a case of coarctation of the aorta, congenital aortic stenosis with bicuspid valve, and supravalvar aortic stenosis with left coronary artery ostial stenosis. The child underwent staged treatment using a hybrid approach employing both surgical and interventional cardiology methods. A single...

journal_title：Pediatric cardiology

authors： Goel P,Madhu Sankar N,Rajan S,Cherian KM

更新日期：2001-01-01 00:00:00

abstract：:The primary objective was to create a clinically relevant model of right ventricular hypertension and to study right ventricular myocardial pathophysiology in growing organism. The secondary objective was to analyse the effect of oral enoximone (phosphodiesterase inhibitor) therapy on right ventricular haemodynamic pa...

journal_title：Pediatric cardiology

authors： Kobr J,Slavik Z,Uemura H,Saeed I,Furck A,Pizingerová K,Fremuth J,Tonar Z

更新日期：2016-12-01 00:00:00

abstract：:Marfan syndrome (MS) is a connective tissue disease involving the cardiovascular, ocular, and the musculoskeletal systems. MS has variable phenotypic expression and is most often diagnosed in adult life. Infantile-onset MS is rare and is associated with severe cardiovascular manifestations; there is an extremely high ...

journal_title：Pediatric cardiology

authors： Strigl S,Quagebeur JM,Gersony WM

更新日期：2007-09-01 00:00:00

abstract：:A varying degree of impairment of ventricular performance is observed over the long-term after surgery for a congenital heart defect (CHD). Impaired ventricular performance has been shown to be of prognostic value for increased risk of cardiovascular events in adult CHD patients. This emphasizes the importance of deli...

journal_title：Pediatric cardiology

authors： Klitsie LM,Roest AA,Blom NA,ten Harkel AD

更新日期：2014-01-01 00:00:00

abstract：:Magnetic resonance imaging (MRI) is a powerful tool which enables the visualization of anatomy and the assessment of many physiological aspects of organ function. MRI and magnetic resonance angiography and magnetic resonance spectroscopy will play critical roles in cardiac applications during the next millennium. Thus...

journal_title：Pediatric cardiology

authors： Mulkern RV,Chung T

更新日期：2000-01-01 00:00:00

abstract：:During the development of so-called aneurysmal transformation of perimembranous ventricular septal defects (pmVSD), tricuspid valve (TV) morphology and function may be altered resulting in left ventricular (LV) to right atrial (RA) shunting. The feasibility and outcome of interventional closure of these pmVSD has not ...

journal_title：Pediatric cardiology

authors： Kerst G,Moysich A,Ho SY,Apitz C,Latus H,Schranz D

更新日期：2015-10-01 00:00:00

abstract：:Previous studies have evaluated left ventricular dimensions in children using two-dimensional echocardiography, but there is little information on gender differences and on the longitudinal development of the dimensions of the left ventricle. Our objective was to assess, by two-dimensional echocardiography, the normal...

journal_title：Pediatric cardiology

authors： Nagasawa H,Arakaki Y,Yamada O,Nakajima T,Kamiya T

更新日期：1996-05-01 00:00:00

abstract：OBJECTIVES:The aim of this article is to examine the frequency, timing of formation of aneurysm of the ventricular membranous septum (AVMS), and prognosis in patients with a perimembranous ventricular septal defect (VSD). PATIENTS:One hundred forty-eight patients were diagnosed with a perimembranous VSD within 90 days...

journal_title：Pediatric cardiology

authors： Miyake T,Shinohara T,Nakamura Y,Fukuda T,Tasato H,Toyohara K,Tanihira Y

更新日期：2004-07-01 00:00:00

abstract：:Congenital heart defect (CHD) represents the most prevalent birth defect, and accounts for substantial morbidity and mortality in humans. Aggregating evidence demonstrates the genetic basis for CHD. However, CHD is a heterogeneous disease, and the genetic determinants underlying CHD in most patients remain unknown. In...

journal_title：Pediatric cardiology

authors： Lu CX,Wang W,Wang Q,Liu XY,Yang YQ

更新日期：2018-04-01 00:00:00

abstract：:We present a 2-month-old male infant with thrombosis in the superior vena cava and pericardium due to transient protein C deficiency. Protein C deficiency was related to sepsis and hepatitis-induced liver function impairment. The patient's cardiac anatomy was otherwise normal. The patient was referred to us with signs...

journal_title：Pediatric cardiology

authors： Demir T,Celkan T,Ahunbay G,Babaoglu A,Besikci R

更新日期：2006-07-01 00:00:00

abstract：:Fetal atrioventricular dissociation is a dysrhythmia associated with significant antenatal and postnatal morbidity and mortality. We present a case of a 19-week-old fetus with atrioventricular dissociation, which spontaneously resolved. The mother had no signs of autoimmune disease. The fetus had an uneventful gestati...

journal_title：Pediatric cardiology

authors： Boris JR,Drose JA,Schaffer MS,Shaffer EM

更新日期：1998-11-01 00:00:00

abstract：:We report a 4-month-old infant with torsade de pointes secondary to procainamide treatment. The infant presented with atrial flutter and converted to normal sinus rhythm with intravenous procainamide. Oral procainamide therapy was initiated as the infusion was tapered, and the patient subsequently developed incessant ...

journal_title：Pediatric cardiology

authors： Bell D,Thoele DG,Mander G,Bauman JL

更新日期：1995-03-01 00:00:00

abstract：:This report describes a rare case of complete transposition of the great arteries (TGA) with an intramural right coronary artery arising well above the sinotubular junction. Additionally in this case, the left circumflex artery arose anomalously as a branch from the right coronary. Identification of this anatomic anom...

journal_title：Pediatric cardiology

authors： Johnson JA,Burkhart HM,O'Leary PW

更新日期：2012-01-01 00:00:00

abstract：:Right ventricular (RV) function as assessed by deformation has been evaluated prenatally and after palliation in hypoplastic left heart syndrome (HLHS). However, limited data exist about the immediate postnatal cardiac adaptation and RV function in HLHS. We compared echocardiographic measures of cardiac performance in...

journal_title：Pediatric cardiology

authors： Altit G,Bhombal S,Chock VY,Tacy TA

更新日期：2019-01-01 00:00:00

abstract：:A case of cerebral hemorrhage associated with sildenafil (Revatio) use in an infant is presented. Sildenafil is increasingly used in the treatment of primary and secondary pulmonary arterial hypertension and pulmonary arteriovenous fistula. In the reported case, sildenafil used to treat pulmonary arteriovenous fistula...

journal_title：Pediatric cardiology

authors： Samada K,Shiraishi H,Aoyagi J,Momoi MY

更新日期：2009-10-01 00:00:00

abstract：:Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluati...

journal_title：Pediatric cardiology

authors： Kim JJ,Valdes SO,Kertesz NJ,Cannon BC

更新日期：2008-09-01 00:00:00

abstract：:A fetal echocardiographic scan was performed when routine prenatal ultrasound screening failed to identify four cardiac chambers. The scan showed a single ventricle with an associated circoid varicosity. Because of these anomalies, amniocentesis was suggested and trisomy 18 confirmed. The presence of major cardiac str...

journal_title：Pediatric cardiology

authors： Duncan WJ,George D,Ezzat W,Wallace K,Van den Beuken B

更新日期：1993-01-01 00:00:00

abstract：:Interventional occluder implantation has become the preferred mode of treatment in children with clinically significant atrial septal defect (ASD). The continuous increase in the number of patients treated calls for long-term data on device integrity and biocompatibility. We report a child who underwent successful int...

journal_title：Pediatric cardiology

authors： Zhu W,Neubauer H

更新日期：2010-10-01 00:00:00

abstract：:A 6-year-old girl was found to have a combination of accessory mitral valve tissue and subaortic membrane. The association caused left ventricular outflow tract obstruction leading to severe left ventricular dysfunction. Surgical relief of the obstruction resulted in immediate improvement of ventricular function. ...

journal_title：Pediatric cardiology

authors： Assaqqat M,Galal MO,Baslaim G

更新日期：2002-01-01 00:00:00

abstract：:Pulmonary artery thrombosis in neonates occurs rarely. This report describes the case of a term infant with a pulmonary artery thrombosis presenting as persistent pulmonary hypertension of the newborn. The risk factors identified in the case included maternal diabetes and heterozygous factor V Leiden deficiency. The p...

journal_title：Pediatric cardiology

authors： Sawyer T,Antle A,Studer M,Thompson M,Perry S,Mahnke CB

更新日期：2009-05-01 00:00:00

abstract：:In this article we report the first case of Q fever endocarditis in a 13 years old child with a percutaneous pulmonary Melody® valve. The patient had a new onset of Melody valve dysfunction associated with the combination of hepatosplenomegaly and pancytopenia but was afebrile. Although blood cultures were negative, w...

journal_title：Pediatric cardiology

authors： Jalal Z,Duperril M,Séguéla PE,Melenotte C,Chabaneix J,Raoult D,Thambo JB

更新日期：2018-01-01 00:00:00

abstract：:Fluid overload and prolonged mechanical ventilation lead to worse outcomes in critically ill children. However, the association between these variables in children following congenital heart surgery is unknown. The objectives of this study were to describe the association between fluid overload and duration of mechani...

journal_title：Pediatric cardiology

authors： Sampaio TZ,O'Hearn K,Reddy D,Menon K

更新日期：2015-12-01 00:00:00

abstract：:A 5-year-old boy born with a congenital heart defect had insertion of an epicardial pacemaker that was found on routine evaluation to have been displaced into the rectovesical pouch. He underwent transvenous insertion of another pacemaker, and the displaced pacemaker was successfully retrieved by laparoscopy without i...

journal_title：Pediatric cardiology

authors： Kravarusic D,Chirdan L,Freud E

更新日期：2011-12-01 00:00:00

abstract：:The purpose of this study was to describe the long-term outcome of infants with hypoplastic left heart syndrome (HLHS) who underwent placement of internal pulmonary artery bands as part of a transcatheter palliation procedure followed by primary heart transplantation. Transcatheter palliation included stenting of the ...

journal_title：Pediatric cardiology

authors： Miyamoto SD,Pietra BA,Chan KC,Ivy DD,Mashburn C,Campbell DN,Mitchell MB,Boucek MM

更新日期：2009-05-01 00:00:00

abstract：:Modifications of the Fontan operation can afford excellent palliation for many patients with a variety of forms of single ventricle. In properly selected patients who are good candidates, early and late survival can be as high as 95-97%. However, mortality is considerably higher for patients with risk factors for poor...

journal_title：Pediatric cardiology

authors： Driscoll DJ

更新日期：2007-11-01 00:00:00

abstract：:Double outlet right ventricle (DORV) was produced experimentally in the chick embryo by preventing the incorporation of the posteromedial conus into the left ventricle. This was accomplished by placing a ligature around the caudal end of the conus at a stage in which it is exclusively continuous with the right ventric...

journal_title：Pediatric cardiology

authors： Arteaga M,de la Cruz MV,Sanchez C,Diaz GF

更新日期：1982-01-01 00:00:00

abstract：:This case report describes a boy who had Kawasaki disease (KD) at age 12 months and had a recurrence one year later. The coronary arteries were normal following the initial episode; however, during the second episode he developed coronary aneurysms. Gallium-67 radionuclide imaging, echocardiography, and angiography we...

journal_title：Pediatric cardiology

authors： Vargo TA,Huhta JC,Moore WH,Person DA,Edwards MS

更新日期：1986-01-01 00:00:00

abstract：:Exercise testing can highlight repolarisation abnormalities in adults with coronary artery disease. Late after Kawasaki disease (KD), increased QT dispersion (QTd) has been reported on resting ECG in children, but there are no reported studies of QTd during exercise. Our objective was to determine the pattern of QTd r...

journal_title：Pediatric cardiology

authors： Gravel H,Dahdah N,Fournier A,Mathieu MÈ,Curnier D

更新日期：2012-06-01 00:00:00