Carney complex presenting with Raynaud's phenomenon and erythematous macules of the extremities.

abstract：BACKGROUND:Cardiac magnetic resonance imaging (MRI) is an important diagnostic tool for congenital heart disease (CHD), as reflected by class 1 recommendations for the use of cardiac MRI by various consensus panels. However, little is known about the safety and clinical utility of cardiac MRI for these critically ill i...

journal_title：Pediatric cardiology

authors： Sarikouch S,Schaeffler R,Körperich H,Dongas A,Haas NA,Beerbaum P

更新日期：2009-02-01 00:00:00

abstract：:The clinical and pathological features of primary pulmonary artery sarcoma in two children are reported. The first patient presented with right ventricular outflow obstruction and underwent successful surgical resection of his tumor. The second patient developed cardiac arrest following a relatively short period of sy...

journal_title：Pediatric cardiology

authors： Farooki ZQ,Chang CH,Jackson WL,Clapp SK,Hakimi M,Arciniegas E,Pinsky WW

更新日期：1988-01-01 00:00:00

abstract：:A 6-year-old girl with evidence of a parahisian accessory pathway on a baseline electrocardiogram underwent successful catheter ablation using magnetic navigation. Magnetic remote controlled ablation eliminated the parahisian pathway with the first radiofrequency application. A second anterolaterally located concealed...

journal_title：Pediatric cardiology

authors： Mantziari L,Rigby M,Till J,Ernst S

更新日期：2013-03-01 00:00:00

abstract：:Despite improved outcomes following modifications to the Fontan technique, significant morbidity and mortality persist. We sought to determine if abnormal pre-Fontan catheterization hemodynamic data will predict postoperative prolonged hospital stay (PHLOS) and adverse post-discharge outcomes. This is a retrospective ...

journal_title：Pediatric cardiology

authors： Guruchandrasekar SH,Dakin H,Kadochi M,Bhatia A,Bardales L,Johnston M,Piggott KD

更新日期：2020-12-01 00:00:00

abstract：:Cardiac intervention remains controversial in patients with trisomy 13 and 18 and little is known about factors that may affect outcomes. The goal of this study was to evaluate preoperative factors and surgical approach with respect to outcomes in these patients. Patients with congenital heart disease and trisomy 13 o...

journal_title：Pediatric cardiology

authors： Peterson R,Calamur N,Fiore A,Huddleston C,Spence K

更新日期：2018-01-01 00:00:00

abstract：:The case is described of a 14-year-old boy who had a hepatoma with a right atrial extension. He presented with edema, abdominal pain, and ascites. Two-dimensional echocardiography showed a right atrial tumor that had invaded from the inferior vena cava as an extension into the right atrium of the hepatoma. ...

journal_title：Pediatric cardiology

authors： Imamoğlu A,Akalin H,Corapçioğlu T,Girgin N,Mengübaş K,Erol C

更新日期：1989-10-01 00:00:00

abstract：:Mammalian cardiomyocytes withdraw from the cell cycle soon after birth. This process is called terminal differentiation. The c-kit, a receptor tyrosine kinase, is expressed on cardiomyocytes immediately after birth but for only a few days. In mice with genetic c-kit dysfunction, adult cardiomyocytes are phenotypically...

journal_title：Pediatric cardiology

authors： Naqvi N,Li M,Yahiro E,Graham RM,Husain A

更新日期：2009-07-01 00:00:00

abstract：:This report describes an unusual case with tortuosity of the great vessels in a neonate who presented at birth with cyanosis. The diagnosis was made with magnetic resonance imaging (MRI), then confirmed by genetic analysis. ...

journal_title：Pediatric cardiology

authors： Pilati M,Luciani GB,Prioli MA,Puppini G

更新日期：2009-11-01 00:00:00

abstract：:In contrast to the percentile-based definitions of elevated blood pressure (BP) and hypertension for children and adolescents of all ages in the 2004 fourth report, the 2017 American Academy of Pediatrics (AAP) BP guideline recommends a change to single BP cut-offs for clinical diagnosis (120/< 80-129/< 80 mmHg for el...

journal_title：Pediatric cardiology

authors： Liu Q,Hou Y,Yang L,Zhao M,Li S,Xi B

更新日期：2019-04-01 00:00:00

abstract：:A surge in cortisol levels is seen after surgery with cardiopulmonary bypass (CPB). Based on evidence of attenuation of the cortisol response to repeated stress in other settings, we hypothesized that the magnitude of cortisol increase in children after a second exposure to CPB would be reduced. Serial cortisol levels...

journal_title：Pediatric cardiology

authors： Bangalore H,Checchia PA,Ocampo EC,Heinle JS,Minard CG,Shekerdemian LS

更新日期：2019-01-01 00:00:00

abstract：:The mechanism of heart failure in patients with enterovirus 71 rhombencephalitis (brain stem encephalitis) remains unknown. Our previous reports hypothesized that a catecholamine storm induced by rhombencephalitis may account for the heart failure. The aim of this study was to develop a novel feline model of norepinep...

journal_title：Pediatric cardiology

authors： Fu YC,Chi CS,Lin NN,Cheng CC,Jan SL,Hwang B,Hsu SL,Gong CL,Chen YT,Chiu YT

更新日期：2006-09-01 00:00:00

abstract：:A five-day-old infant with transposition of the great arteries, ventricular septal defect, and an interrupted right aortic arch underwent successful balloon septostomy, pulmonary artery banding, and aortic arch repair. The infant also had abnormal facies with severe refractory hypocalcemia and depressed T-lymphocyte n...

journal_title：Pediatric cardiology

authors： Duncan WJ,Tyrrell MJ,Bharadwaj B,Rosenberg AM,Schroeder ML,Bingham WT

更新日期：1984-07-01 00:00:00

abstract：:A reduced exercise capacity is a common finding in adult congenital heart disease and is associated with cardiovascular morbidity and mortality. However, data on exercise capacity in patients after repair of coarctation of the aorta (CoA) are scarce. Furthermore, a high rate of exercise-induced hypertension has been d...

journal_title：Pediatric cardiology

authors： Dijkema EJ,Sieswerda GT,Breur JMPJ,Haas F,Slieker MG,Takken T

更新日期：2019-10-01 00:00:00

abstract：:Device closure of atrial septal defects (ASDs) is rapidly becoming routine in children. Comparisons are often made to older surgical series with higher morbidities. However outcomes including reintervention, late failure, and the need for long-term follow-up must be considered and compared to those of a current surgic...

journal_title：Pediatric cardiology

authors： Baskett RJ,Tancock E,Ross DB

更新日期：2003-09-01 00:00:00

abstract：:In the fetus, the cardiac neural crest gives rise to both the thymus and the conotruncus of the heart. In newborn screening for severe T-cell lymphopenia neonates with congenital heart defects may be detected. In this study, we investigated the occurrence of T-cell lymphopenia in neonates with or without 22q11.2 delet...

journal_title：Pediatric cardiology

authors： Gul KA,Strand J,Pettersen RD,Brun H,Abrahamsen TG

更新日期：2020-04-01 00:00:00

abstract：:Azygos continuation of inferior venacava (IVC) is well known in association with interrupted IVC. We report azygos connection of uninterrupted IVC in a young child with complex univentricular heart. This peculiar anatomy was made suitable for univentricular repair by combining percutaneous device closure of prehepatic...

journal_title：Pediatric cardiology

authors： Chaudhuri M,Shivanna D,Jayranganath M,Chandra S

更新日期：2011-01-01 00:00:00

abstract：:Paroxysmal non-reentrant supraventricular tachycardia due to double ventricular response through antegrade dual atrioventricular nodal pathways by a single atrial excitation has been reported in limited adult cases but not in pediatric patients with structurally normal hearts or with congenital heart defects. We repor...

journal_title：Pediatric cardiology

authors： Takahashi K,Nakayashiro M,Ganaha H

更新日期：2013-03-01 00:00:00

abstract：:The HOXA1 gene plays a fundamental role in embryonic morphogenesis. Recent studies in humans and mice have indicated that HOXA1 plays a previously unrecognized role in cardiovascular system development. Congenital heart disease (CHD), particularly ventricular septal defect (VSD), might be a clinically isolated manifes...

journal_title：Pediatric cardiology

authors： Liu J,Wang B,Chen X,Li H,Wang J,Cheng L,Ma X,Gao B

更新日期：2013-02-01 00:00:00

abstract：:A newborn infant with familial Wolff-Parkinson-White (WPW) syndrome presented with a supraventricular tachycardia of 300 beats/min, refractory to digoxin and flecainide administration. Serial electropharmacologic tests were performed via the esophagus before and during oral therapy with verapamil at 40, 80, and 60 mg ...

journal_title：Pediatric cardiology

authors： Colloridi V,Boscioni M,Patruno N,Pulignano G,Critelli G

更新日期：1990-10-01 00:00:00

abstract：:The proximal course of an anomalously arising coronary artery is a decisive factor in the surgical approach for tetralogy of Fallot (TOF). Studies have shown that echocardiography provides a good anatomic definition of the ostium and proximal epicardial course of coronary arteries [1, 2]. This report describes a case ...

journal_title：Pediatric cardiology

authors： Deepa S,Bijulal S,Baiju DS,Thomas M

更新日期：2013-01-01 00:00:00

abstract：:Acute kidney injury (AKI) is a potential complication for children with congenital heart disease (CHD) after cardiopulmonary bypass (CPB) surgery. This study was designed to investigate and compare the predictive values of urinary biomarkers for AKI after CPB surgery in infants and young children and to determine the ...

journal_title：Pediatric cardiology

authors： Zheng J,Xiao Y,Yao Y,Xu G,Li C,Zhang Q,Li H,Han L

更新日期：2013-04-01 00:00:00

abstract：:We report a newborn with a congenital aneurysm of the muscular interventricular septum, a conduction system abnormality involving variable left and right bundle branch block, and an abnormality of the short arm of chromosome 20, This combination of anomalies has not been previously reported. To date, the infant has pr...

journal_title：Pediatric cardiology

authors： Wong SH,Coleman DM,Aftimos S

更新日期：2007-01-01 00:00:00

abstract：:In a patient with single ventricle, mitral atresia, common atrium, pulmonary stenosis, azygos continuation of the inferior vena cava and bilateral systemic artery--pulmonary artery anastomoses, the systemic veins were connected directly to the pulmonary arteries to achieve physiologic repair; the child was discharged ...

journal_title：Pediatric cardiology

authors： Waldman JD,Lamberti JJ

更新日期：1986-01-01 00:00:00

abstract：:For adults with sickle cell disease (SCD), cardiac changes are well described and may account for up to one-fourth of disease-related mortality. Much less is known about heart disease in pediatric SCD patients. This retrospective study analyzed a contemporary cohort of children with SCD followed at a single tertiary c...

journal_title：Pediatric cardiology

authors： Doshi AR,Pauliks LB

更新日期：2013-04-01 00:00:00

abstract：:The objective of this study was to investigate the association between red blood cell (RBC) transfusion and hematocrit values with outcomes in infants undergoing Norwood operation. This study included infants ≤2 months of age who underwent Norwood operation with either a modified Blalock-Taussig shunt or a right ventr...

journal_title：Pediatric cardiology

authors： Gupta P,King C,Benjamin L,Goodhart T,Robertson MJ,Gossett JM,Pesek GA,DasGupta R

更新日期：2015-08-01 00:00:00

abstract：:In 19 consecutive children with aortic valve stenosis, the left ventricle was entered retrogradely with a Gensini catheter guided by a tip-deflector guidewire which could produce any desirable degree of curvature at its tip. In all patients, the aortic valve was retrogradely traversed for measurement of the pressure g...

journal_title：Pediatric cardiology

authors： Lau KC,Leung MP,Lo RN

更新日期：1986-01-01 00:00:00

abstract：:Ventricular dysfunction in patients after Fontan-like operations (FLOs) is a serious complication that might contribute to poor long-term results. Ischemic heart disease will have debilitating consequences on a Fontan heart. Ten patients (15.8 +/- 5.01 years) after FLO had transesophageal echocardiography and cardiac ...

journal_title：Pediatric cardiology

authors： Hauser M,Bengel FM,Kühn A,Sauer U,Nekolla SG,Eicken A,Schwaiger M,Hess J

更新日期：2003-07-01 00:00:00

abstract：:Aortopulmonary window is a relatively uncommon congenital heart defect. We report on a patient with a small aortopulmonary window, who presented with an asymptomatic murmur and in whom catheter closure was successfully performed with an Amplatzer Duct Occluder. ...

journal_title：Pediatric cardiology

authors： Atiq M,Rashid N,Kazmi KA,Qureshi SA

更新日期：2003-05-01 00:00:00

abstract：:The data on the outcomes of children with heart disease and Down syndrome receiving extracorporeal membrane oxygenation (ECMO) for cardiac or respiratory failure are limited. This study aimed to evaluate morbidity and mortality associated with ECMO in children with Down syndrome and heart disease. Children younger tha...

journal_title：Pediatric cardiology

authors： Gupta P,Gossett JM,Rycus PT,Prodhan P

更新日期：2014-12-01 00:00:00

abstract：:There has been substantial controversy regarding treatment of congenital heart defects in infants with trisomies 13 and 18. Most reports have focused on surgical outcomes versus expectant treatment, and rarely there has been an effort to consolidate existing evidence into a more coherent way to help clinicians with de...

journal_title：Pediatric cardiology

authors： Carvajal HG,Callahan CP,Miller JR,Rensink BL,Eghtesady P

更新日期：2020-10-01 00:00:00