Complex transposition with interrupted right aortic arch and partial Di George syndrome: successful palliation with combined medical and surgical therapy.

abstract：:Pediatric primary cardiomyopathy is rare but serious, having high mortality; hypertrophic and dilated types are the most common. Its etiology has been mainly considered idiopathic; however, next generation sequencing techniques have revealed nearly half of idiopathic pediatric cases arose from specific genetic mutatio...

journal_title：Pediatric cardiology

authors： Rojnueangnit K,Sirichongkolthong B,Wongwandee R,Khetkham T,Noojarern S,Khongkraparn A,Wattanasirichaigoon D

更新日期：2020-01-01 00:00:00

abstract：:14-year-old white male with a past medical history of congenital bicuspid aortic valve, Streptococcus viridans endocarditis, and pulmonary valve homograft presented with culture-negative endocarditis. Molecular studies identified the causative organism as Bartonella henselae and subsequent serologic studies supported ...

journal_title：Pediatric cardiology

authors： Pitchford CW,Creech CB 2nd,Peters TR,Vnencak-Jones CL

更新日期：2006-11-01 00:00:00

abstract：:We present two term neonates in which intravenous indomethacin usage was associated with successful closure of a persistently patent arterial duct. Both children had congenital heart disease with high pulmonary blood flow following surgical placement of contralateral systemic-pulmonary artery shunts. ...

journal_title：Pediatric cardiology

authors： Vandekerckhove K,Macrae D,Slavik Z

更新日期：2005-09-01 00:00:00

abstract：:Previous studies showed the reliability of cardiac magnetic resonance imaging (cMRI) in the quantification of aortic valve stenosis in adults. The aim of this retrospective study was to assess the ability of cMRI in the quantification of congenital aortic valve stenosis (CAS) in children. Nineteen patients (mean age 1...

journal_title：Pediatric cardiology

authors： Sirin S,Nassenstein K,Neudorf U,Jensen CJ,Mikat C,Schlosser T

更新日期：2014-06-01 00:00:00

abstract：:After surgical repair of an aortic coarctation a term infant presented with severe pulmonary hypertension and cyanosis unresponsive to treatment including extracorporeal membrane oxygenation. The atypical clinical course became apparent once the accompanying diagnosis of congenital alveolar capillary dysplasia with mi...

journal_title：Pediatric cardiology

authors： Gamillscheg A,Zobel G,Spuller E,Reiterer F,Beitzke A

更新日期：2008-01-01 00:00:00

abstract：:A fetal echocardiographic scan was performed when routine prenatal ultrasound screening failed to identify four cardiac chambers. The scan showed a single ventricle with an associated circoid varicosity. Because of these anomalies, amniocentesis was suggested and trisomy 18 confirmed. The presence of major cardiac str...

journal_title：Pediatric cardiology

authors： Duncan WJ,George D,Ezzat W,Wallace K,Van den Beuken B

更新日期：1993-01-01 00:00:00

abstract：:Postoperative coarctation (CoA) patients are often found to have signs of persistent myocardial dysfunction. M-mode echocardiography was performed to study left ventricular (LV) size, mass, and systolic function and Doppler ultrasonography to study LV filling and flow velocity in the LV outflow tract and aorta in 28 "...

journal_title：Pediatric cardiology

authors： Sigurdardóttir LY,Helgason H

更新日期：1997-03-01 00:00:00

abstract：:Pulmonary arterial hypertension (PAH) is a major cause of morbidity and mortality among patients with congenital heart disease (CHD). This study was designed to determine biomarker levels in patients with PAH associated with CHD (PAH-CHD) and CHD patients without PAH and to investigate the relationship of these potent...

journal_title：Pediatric cardiology

authors： Sanli C,Oguz D,Olgunturk R,Tunaoglu FS,Kula S,Pasaoglu H,Gulbahar O,Cevik A

更新日期：2012-12-01 00:00:00

abstract：:The proximal course of an anomalously arising coronary artery is a decisive factor in the surgical approach for tetralogy of Fallot (TOF). Studies have shown that echocardiography provides a good anatomic definition of the ostium and proximal epicardial course of coronary arteries [1, 2]. This report describes a case ...

journal_title：Pediatric cardiology

authors： Deepa S,Bijulal S,Baiju DS,Thomas M

更新日期：2013-01-01 00:00:00

abstract：:The effect of patent ductus arteriosus (PDA) treatment with cyclooxygenase (COX) inhibitors (indomethacin [INDO] and ibuprofen [IBU]) on regional oxygenation requires further clarification. The authors hypothesized that both INDO and IBU reduce regional tissue oxygenation in preterm neonates with PDA but that the risk...

journal_title：Pediatric cardiology

authors： Bhatt M,Petrova A,Mehta R

更新日期：2012-12-01 00:00:00

abstract：:Percutaneous balloon aortic valvuloplasty was attempted in an eight-month-old infant with severe aortic valve stenosis. The procedure resulted in a fall in the resting transvalvular systolic pressure gradient from 106 mmHg to 40 mmHg and no aortic regurgitation. Clinical and Doppler echocardiography findings suggest p...

journal_title：Pediatric cardiology

authors： Sánchez GR,Mehta AV,Ewing LL,Brickley SE,Anderson TM,Black IF

更新日期：1985-01-01 00:00:00

abstract：:Anatomic evidence of intrauterine closure of ventricular septal defects (VSDs) has been reported rarely. Between 1985 and 1990, 112 autopsies were performed at the Mayo Clinic on third trimester stillborns and infants who died during the first week of life. There were 21 (19%) cases of congenital heart disease. VSD wa...

journal_title：Pediatric cardiology

authors： Nir A,Driscoll DJ,Edwards WD

更新日期：1994-01-01 00:00:00

abstract：:Once a mainstay in the treatment of neonates with d-transposition of the great arteries (d-TGA), the application of balloon atrial septostomy (BAS) in the d-TGA population has become more selective. Currently, there is no clear evidence for or against a selective BAS strategy. The aims of this single-center retrospect...

journal_title：Pediatric cardiology

authors： Zaleski KL,McMullen CL,Staffa SJ,Thiagarajan RR,Maschietto N,DiNardo JA,Nasr VG

更新日期：2021-01-25 00:00:00

abstract：:A neonate with pulmonary interstitial glycogenosis, pulmonary hypertension, and hypertrophic cardiomyopathy is described. The fatal outcome for this patient contrasts with the reported favorable prognosis associated with isolated pulmonary interstitial glycogenosis. To the authors' knowledge, the association of pulmon...

journal_title：Pediatric cardiology

authors： Alkhorayyef A,Ryerson L,Chan A,Phillipos E,Lacson A,Adatia I

更新日期：2013-02-01 00:00:00

abstract：:This study examined the age-related criteria of signal-averaged electrocardiographic (SA-ECG) parameters in children. SA-ECGs were obtained in 82 healthy volunteers in six groups depending on age (group 1: 1 day to < 1 month; group 2: 1 month to < 1 year; group 3: 1 to < 6 years; group 4: 6 to < 12 years; group 5: 12 ...

journal_title：Pediatric cardiology

authors： Hayabuchi Y,Matsuoka S,Kubo M,Akita H,Kuroda Y

更新日期：1994-05-01 00:00:00

abstract：:Mid-cavity obstruction of the systemic venous atrium developed after the Mustard operation in a child with transposition of the great arteries. Balloon dilatation (BD) was performed twice, to a maximum theoretical transverse diameter of 18 mm. Each time obstruction was initially relieved, but recurred within months. T...

journal_title：Pediatric cardiology

authors： Waldman JD,Waldman J,Jones MC

更新日期：1983-04-01 00:00:00

abstract：:In the fetus, the cardiac neural crest gives rise to both the thymus and the conotruncus of the heart. In newborn screening for severe T-cell lymphopenia neonates with congenital heart defects may be detected. In this study, we investigated the occurrence of T-cell lymphopenia in neonates with or without 22q11.2 delet...

journal_title：Pediatric cardiology

authors： Gul KA,Strand J,Pettersen RD,Brun H,Abrahamsen TG

更新日期：2020-04-01 00:00:00

abstract：:The epidemiologic data for pediatric hypertrophic cardiomyopathy (HCM) needs to be periodically updated as diagnostic techniques and management strategies improve. Herein, the incidence, prevalence, and mortality rates of pediatric HCM in a population-based treatment system are described. Patients aged ≤ 17 years and ...

journal_title：Pediatric cardiology

authors： Nandi D,Hayes EA,Wang Y,Jerrell JM

更新日期：2020-10-03 00:00:00

abstract：:Right-ventricular diverticula (RVD), although rare, have particular characteristics. Our study describes the morphology of anterosuperior diverticula of the right ventricle (RV) and patient outcome for this anomaly. Retrospective analysis was performed on all patients with anterosuperior RVD diagnosed in two tertiary ...

journal_title：Pediatric cardiology

authors： Wiegand G,Rauch R,Singer H,Koch A,Hofbeck M

更新日期：2014-08-01 00:00:00

abstract：:Various agents have been suggested as causal or associated factors in the pathogenesis of Kawasaki disease (KD); however, the underlying factors of KD remain unknown. Plasma exchange is one of the most effective treatments for the acute phase of KD. This indicates that plasma may contain factors associated with the pa...

journal_title：Pediatric cardiology

authors： Kanai T,Shiraishi H,Uehara R,Ito T,Momoi MY

更新日期：2012-12-01 00:00:00

abstract：:Kawasaki disease (KD) is a self-limiting systemic vasculitis of unknown etiology. KD is often complicated by coronary artery aneurysms (CAAs), which develop in about 20-25% of untreated children and 3-5% of children treated with intravenous immunoglobulin therapy. To identify the risk loci for CAA susceptibility in pa...

journal_title：Pediatric cardiology

authors： Kwon YC,Kim JJ,Yu JJ,Yun SW,Yoon KL,Lee KY,Kil HR,Kim GB,Han MK,Song MS,Lee HD,Ha KS,Sohn S,Hong YM,Jang GY,Lee JK,Korean Kawasaki Disease Genetics Consortium.

更新日期：2019-03-01 00:00:00

abstract：:Although recognized by pediatric cardiac surgeons, aortic insufficiency as a technical complication after tetralogy of Fallot repair is poorly documented, especially if it occurs late. The case of a boy with aortic insufficiency 10 years after complete tetralogy repair is described. No documentation in the literature ...

journal_title：Pediatric cardiology

authors： Bilfinger TV,Seifert FC,Vallone AM,Biancaniello TM

更新日期：1994-03-01 00:00:00

abstract：:We report hemodynamic findings in two patients with pulmonary atresia and intact ventricular septum (PAIVS) after "one-and-a-half ventricle repair" and placement of a bidirectional Glenn shunt using four-dimensional (4D) flow magnetic resonance imaging. Quantification of flow and analysis of flow patterns revealed the...

journal_title：Pediatric cardiology

authors： Uribe S,Bächler P,Valverde I,Crelier GR,Beerbaum P,Tejos C,Irarrazaval P

更新日期：2013-02-01 00:00:00

abstract：:Our purpose was to evaluate the impact of suspicion or confirmation of heart disease on the physical and psychosocial health of children. We utilized the Child Health Questionnaire (CHQ PF-50). Children ages 5 to 18 years attending a general cardiology clinic were eligible. Those with primary noncardiac diagnoses unre...

journal_title：Pediatric cardiology

authors： Walker RE,Gauvreau K,Jenkins KJ

更新日期：2004-01-01 00:00:00

abstract：:Five patients with ventricular inversion, corrected transposition of the great arteries, and atresia of the left-sided atrioventricular (tricuspid) valve have been observed. Three patients died in infancy, two had large interatrial communications, one with an early stage of arterial-type hypertensive pulmonary vascula...

journal_title：Pediatric cardiology

authors： Tazelaar HD,Moore GW,Hutchins GM

更新日期：1986-01-01 00:00:00

abstract：:A 2-year-old girl with cor triatriatum with unroofed coronary sinus and persistent left superior vena cava underwent preoperative radiofrequency catheter ablation for atrial tachycardia attack that developed after admission to our hospital. The procedure was not successful. Cryoablation was successfully performed duri...

journal_title：Pediatric cardiology

authors： Sato T,Suzuki K,Umemura J,Takahashi Y,Tomimoto K

更新日期：2003-09-01 00:00:00

abstract：:The occurrence of familial heart disease in association with tricuspid atresia is rare. The first reported instance of tricuspid atresia and Ebstein's anomaly in siblings is presented. The presence of these two distinct pathologic variants of tricuspid valve malformations in siblings suggests that these malformations ...

journal_title：Pediatric cardiology

authors： Grant JW

更新日期：1996-09-01 00:00:00

abstract：:Noonan syndrome is an autosomal dominant disease that manifests a wide variety of clinical characteristics. The syndrome is also associated with some cardiac defects. Half of all Noonan syndrome cases are caused by mutations in the PTPN11 gene, but only limited data are available regarding aortic involvement in these ...

journal_title：Pediatric cardiology

authors： Jefferies JL,Belmont JW,Pignatelli R,Towbin JA,Craigen WJ

更新日期：2010-01-01 00:00:00

abstract：:Renovascular hypertension is an uncommon disease, but it causes 5-10% of all childhood hypertension. The most common cause of renal artery stenosis is fibromuscular dysplasia, resulting in at least 60% of renovascular hypertension cases. This report describes a case of a renal artery stenosis confirmed by multidetecto...

journal_title：Pediatric cardiology

authors： Kim HJ,Son JS,Kim KS

更新日期：2011-06-01 00:00:00

abstract：:Left-ventricular noncompaction (LVNC) is an echocardiographic finding of increasing frequency in pediatrics; however, predictors of outcomes have been difficult to identify. We conducted a retrospective review of pediatric patients at the Morgan Stanley Children's Hospital of New York from January of 1993 to September...

journal_title：Pediatric cardiology

authors： Zuckerman WA,Richmond ME,Singh RK,Carroll SJ,Starc TJ,Addonizio LJ

更新日期：2011-04-01 00:00:00