Anterosuperior diverticula of the right ventricle: morphological spectrum and long-term outcome of a distinct cardiac anomaly.

Abstract:

:Right-ventricular diverticula (RVD), although rare, have particular characteristics. Our study describes the morphology of anterosuperior diverticula of the right ventricle (RV) and patient outcome for this anomaly. Retrospective analysis was performed on all patients with anterosuperior RVD diagnosed in two tertiary referral centres. From January 1982 to December 2012, five patients were diagnosed with anterosuperior RVD (median 4 months). Four patients had perimembranous ventricular septal defects (VSDs) with no clinical symptoms related to RVD. Communication of the RVD with the RV was located either close to the VSD (two patients) or in the anterior free wall of the RV opposite the VSD (two patients). In the remaining patient, the diverticulum was connected with the left ventricle (LV) by a tunnel-like structure originating from the left-ventricular outflow tract; the RVD communicated with the RV by way of a restrictive opening. Four patients underwent surgical repair including patch closure of the VSD (one patient) and patch closure of the VSD through an incision of the RVD followed by plication of the diverticulum or closure of its communication with the RV (three patients). All patients remained asymptomatic during a median follow-up of 14.8 years. Anterosuperior RVD is a specific congenital cardiovascular anomaly frequently associated with additional congenital heart disease. There are significant variations in how the RVD communicates with the RV with each requiring a different surgical repair strategy. According to the experience in our small cohort, the long-term prognosis of patients with anterosuperior RVD appears excellent after surgical correction of associated congenital heart disease.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Wiegand G,Rauch R,Singer H,Koch A,Hofbeck M

doi

10.1007/s00246-014-0885-7

subject

Has Abstract

pub_date

2014-08-01 00:00:00

pages

983-9

issue

6

eissn

0172-0643

issn

1432-1971

journal_volume

35

pub_type

杂志文章
  • Interrupted aortic arch in infancy: a 10-year experience.

    abstract::Fifty infants with interrupted aortic arch (IAA), admitted between 1979 and 1988, were reviewed. They usually presented early in severe cardiac failure or shock. In the initial 5-year period, 17 of the 21 infants underwent diagnostic or confirmatory cardiac catheterization, in contrast with the latter 5 years when onl...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF00838779

    authors: Menahem S,Rahayoe AU,Brawn WJ,Mee RB

    更新日期:1992-10-01 00:00:00

  • Evaluation of Impedance Cardiography for Measurement of Stroke Volume in Congenital Heart Disease.

    abstract::Noninvasive measurement of cardiac output (CO) and particularly stroke volume (SV) remain difficult but potentially valuable. These variables can be particularly challenging to measure in children with congenital heart disease (CHD). Impedance cardiography (IC) is a technique shown to be accurate in measuring SV in ad...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-016-1456-x

    authors: Ebrahim M,Hegde S,Printz B,Abcede M,Proudfoot JA,Davis C

    更新日期:2016-12-01 00:00:00

  • Recurrent congenital left atrial aneurysm in a newborn.

    abstract::Recurrent congenital left atrial aneurysm presenting in a newborn as cardiac tamponade is described. Such a presentation has not been previously reported. ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s002469900269

    authors: Mansour E,Aldousany A,Arce O,Subramanian S,Ashraf MH

    更新日期:1998-03-01 00:00:00

  • Contractility reserve in children undergoing dialysis by dobutamine stress echocardiography.

    abstract::Left ventricular hypertrophy is an adaptive mechanism in children undergoing chronic dialysis to improve contractility at rest. The aim of this study was to determine the left ventricular performance and contractility reserve by "dobutamine stress echocardiography" in children undergoing chronic dialysis. Thirty-five ...

    journal_title:Pediatric cardiology

    pub_type: 临床试验,杂志文章

    doi:10.1007/s00246-010-9721-x

    authors: Mese T,Guven B,Yilmazer MM,Serdaroglu E,Tavli V,Haydar A,Bak M

    更新日期:2010-10-01 00:00:00

  • The Significance of Crochetage on the R wave of an Electrocardiogram for the Early Diagnosis of Pediatric Secundum Atrial Septal Defect.

    abstract::The purpose of this study was to test the hypothesis that the incidence of crochetage on the R wave in inferior limb leads can be used for the diagnosis of pediatric secundum atrial septal defect (ASD). Two hundred fifty-six children with secundum ASD (case cohort) and 256 age- and gender-matched children without hear...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-018-1857-0

    authors: Shen L,Liu J,Li JK,Xu M,Yuan L,Zhang GQ,Wang JY,Huang YJ

    更新日期:2018-06-01 00:00:00

  • False aneurysm following modified Blalock-Taussig shunt.

    abstract::A 3 1/2-year-old female child presented with massive hemoptysis 5 months after a modified Blalock-Taussig (BT) shunt for double-outlet right ventricle with pulmonary stenosis. Computerized tomographic scan and angiography showed a false aneurysm of the subclavian artery at the insertion of the shunt. Successful surgic...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-001-0043-x

    authors: Parvathy U,Balakrishnan KR,Ranjith MS,Moorthy JS

    更新日期:2002-03-01 00:00:00

  • Prevalence of obesity among patients with congenital and acquired heart disease.

    abstract::Overweight and obesity rates have risen dramatically in the United States, with subsequent detrimental comorbidity risks. The rates for obesity among children with congenital and acquired heart disease have rarely been reported. A retrospective cross-sectional study was conducted to determine the prevalence of overwei...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-011-0049-y

    authors: Shustak RJ,McGuire SB,October TW,Phoon CK,Chun AJ

    更新日期:2012-01-01 00:00:00

  • Decision-Making in the Catheter Laboratory: The Most Important Variable in Successful Outcomes.

    abstract::Increasingly the importance of how and why we make decisions in the medical arena has been questioned. Traditionally the aeronautical and business worlds have shed a light on this complex area of human decision-making. In this review we reflect on what we already know about the complexity of decision-making in additio...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章,评审

    doi:10.1007/s00246-020-02295-1

    authors: Duignan S,Walsh KP,McMahon CJ

    更新日期:2020-03-01 00:00:00

  • Anomalous origin of left pulmonary artery from aorta with atrial septal defect.

    abstract::Anomalous origin of left pulmonary artery (ALPA) from aorta with atrial septal defect (ASD) is a rare congenital cardiac malformation. We report a case of ALPA from the aorta with ASD in a 1.8-kg baby. Repair was needed at an early age due to progressive congestive heart failure. Surgical correction was performed with...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-008-9234-z

    authors: Lee JH,Jung TE,Lee YH

    更新日期:2008-07-01 00:00:00

  • Avoiding compression of extracardiac valved conduits.

    abstract::Extracardiac valved conduits are routinely employed in the correction of complex congenital heart lesions. Compression of a conduit and/or of the heart may present serious operative and postoperative complications. We believe its occurrence can be minimized and hemodynamic results improved by adhering to simple surgic...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF02242263

    authors: Dunn JM,Stark J,de Leval M

    更新日期:1983-07-01 00:00:00

  • Hemodynamic assessment in patients with one-and-a-half ventricle repair revealed by four-dimensional flow magnetic resonance imaging.

    abstract::We report hemodynamic findings in two patients with pulmonary atresia and intact ventricular septum (PAIVS) after "one-and-a-half ventricle repair" and placement of a bidirectional Glenn shunt using four-dimensional (4D) flow magnetic resonance imaging. Quantification of flow and analysis of flow patterns revealed the...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0288-6

    authors: Uribe S,Bächler P,Valverde I,Crelier GR,Beerbaum P,Tejos C,Irarrazaval P

    更新日期:2013-02-01 00:00:00

  • Congenitally corrected transposition of the great arteries in a patient with cor triatriatum: a rare combination.

    abstract::Congenitally corrected transposition of the great arteries is a rare anomaly that is thought to arise from a defect in looping of the primitive cardiac tube. Cor triatriatum is another rare congenital cardiac anomaly due to faulty incorporation of the common pulmonary vein into the left atrium. We present a rare case ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-011-9912-0

    authors: Jayranganath M,Subramanian A,Manjunath CN

    更新日期:2011-04-01 00:00:00

  • Increased α1-antitrypsin levels in acute-phase Kawasaki disease as shown by SELDI-TOF MS analysis.

    abstract::Various agents have been suggested as causal or associated factors in the pathogenesis of Kawasaki disease (KD); however, the underlying factors of KD remain unknown. Plasma exchange is one of the most effective treatments for the acute phase of KD. This indicates that plasma may contain factors associated with the pa...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0329-1

    authors: Kanai T,Shiraishi H,Uehara R,Ito T,Momoi MY

    更新日期:2012-12-01 00:00:00

  • Early detection of anomalous origin of left coronary artery from the right pulmonary artery after successful repair of critical coarctation of the aorta.

    abstract::Left ventricular (LV) function is impaired by increased afterload in neonates with severe coarctation of the aorta, which may result in endocardial fibroelastosis. Repair of the coarctation usually solves the problem, with LV function normalizing after a few weeks. This report describes a patient who underwent success...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-009-9595-y

    authors: Celik L,Becker V,Hammel D,Nürnberg JH

    更新日期:2010-02-01 00:00:00

  • Radiofrequency catheter ablation of tachycardia in patients with congenital heart disease.

    abstract::Patients with anomalies of the heart frequently suffer from arrhythmias that either are associated with a congenital heart defect or result from the course of the disease. For most of the bradyarrhythmias, appropriate timing of the initiation of treatment is more challenging than its eventual execution. In the case of...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章,评审

    doi:10.1007/s002460010134

    authors: Hebe J,Hansen P,Ouyang F,Volkmer M,Kuck KH

    更新日期:2000-11-01 00:00:00

  • Double-outlet right ventricle without interventricular communication: an unusual and challenging problem.

    abstract::A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0483-5

    authors: Singla M,Al-Radi O,Mertens L

    更新日期:2013-01-01 00:00:00

  • Horseshoe lung associated with unique left pulmonary vein: an unreported association.

    abstract::Horseshoe lung is a rare malformation that is often associated with lung hypoplasia and/or vascular anomalies. We describe a 10-year-old girl with horseshoe lung and unique left pulmonary vein. This is the first reported case with this vascular feature. The patient presented with signs and symptoms of severe pulmonary...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-010-9735-4

    authors: Salerno T,Guccione P,Malena S,Cutrera R

    更新日期:2010-08-01 00:00:00

  • Heart transplantation in an infant with rhabdomyoma.

    abstract::Rhabdomyoma is the most common primary cardiac tumor in infants and children and is often associated with tuberous sclerosis. Surgical resection may be indicated and, if so, is usually curative. We describe a rhabdomyoma in an infant who presented with severe myocardial ischemia necessitating orthotopic heart transpla...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF00794197

    authors: Demkow M,Sorensen K,Whitehead BF,Rees PG,Sullivan ID,Elliott MJ,de Leval MR

    更新日期:1995-07-01 00:00:00

  • Patient safety and human factors in pediatric cardiac surgery.

    abstract::The patient safety movement and human factors studies are becoming an increasingly important part of everyday clinical practice. Pediatric cardiac surgery is a high-risk field that is very much dependent on safe practices and continuous research into improvement of outcomes. This article reviews the main research fram...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章,评审

    doi:10.1007/s00246-006-1448-3

    authors: Bacha EA

    更新日期:2007-03-01 00:00:00

  • Restricting sports for athletes with heart disease: are we saving lives, avoiding lawsuits, or just promoting obesity and sedentary living?

    abstract::Sudden cardiac death in young competitive athletes is tragic and usually due to unsuspected cardiovascular disease. Screening programs for athletes remain debatable, and restriction of athletes from sports can have physical, emotional, and legal ramifications. In this article, we review the epidemiology of the more co...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章,评审

    doi:10.1007/s00246-012-0170-6

    authors: Vaseghi M,Ackerman MJ,Mandapati R

    更新日期:2012-03-01 00:00:00

  • Dilated cardiomyopathy masquerading as long QT syndrome.

    abstract::Atrioventricular block has been described in association with cases of long QT syndrome and mortality is increased in this subgroup. We describe an infant with congenital QT prolongation and atrioventricular block with normal cardiac function, leading to the initial diagnosis of long QT syndrome. She subsequently deve...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-005-1114-1

    authors: Walls J,Dipchand A,Sanatani S

    更新日期:2006-01-01 00:00:00

  • Magnetocardiographic localization of ventricular pre-excitation in a child with a congenital heart defect.

    abstract::Magnetocardiographic mapping was performed on a 2-year-old boy who suffered from the Wolff-Parkinson-White syndrome in association with a complex congenital heart defect. The pre-excitation site was determined noninvasively from the measured cardiac magnetic fields. The location was in the same anatomic region as foun...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF02310333

    authors: Nenonen J,Rovamo L,Toivonen L,Ilmoniemi R,Järvinen A,Leiniö M,Montonen J,Nisula L

    更新日期:1995-01-01 00:00:00

  • Scimitar variant.

    abstract::In the classic scimitar syndrome, a pulmonary vein draining all or part of the right lung enters the inferior vena cava. A variant is described with the same roentgenographic appearance, but with drainage of the anomalous pulmonary vein into both the inferior vena cava and the left atrium; the atrial septum was intact...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF02079472

    authors: Pearl W

    更新日期:1987-01-01 00:00:00

  • 1173C>T polymorphism in VKORC1 modulates the required warfarin dose.

    abstract::The response to warfarin is highly variable among individuals and such variability is likely to have some genetic basis. We evaluted the effect of VKORC1 polymorphisms on warfarin response among Japanese, taking advantage of its unique population structure in which CYP2C9 *2 and *3 alleles are relatively rare. Thirty-...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-005-1150-x

    authors: Kosaki K,Yamaghishi C,Sato R,Semejima H,Fuijita H,Tamura K,Maeyama K,Yamagishi H,Sugaya A,Dodo H,Tanigawara Y,Takahashi T

    更新日期:2006-11-01 00:00:00

  • Supracardiac total anomalous pulmonary venous connection with a descending vertical vein.

    abstract::The commonly used Darling classification for total anomalous pulmonary venous connection (TAPVC) consists of supracardiac, cardiac, infracardiac, and mixed types (Craig et al., Lab Invest 6:44-64, 1967). In supracardiac TAPVC, the common pulmonary vein drains superiorly into the left innominate vein, the superior vena...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-009-9509-z

    authors: Shah S,Singh M,John C,Maheshwari S

    更新日期:2009-10-01 00:00:00

  • The role of Shox2 in SAN development and function.

    abstract::Embryonic development is a tightly regulated process, and many families of genes functions to provide a regulatory genetic network to achieve such a program. The homeobox genes are an extensive family that encodes transcription factors with a characteristic 60-amino acid homeodomain. Mutations in these genes or in the...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0179-x

    authors: Liu H,Espinoza-Lewis RA,Chen C,Hu X,Zhang Y,Chen Y

    更新日期:2012-08-01 00:00:00

  • Progressive congenital valvar aortic stenosis during infancy: five cases.

    abstract::We report our experience with asymptomatic valvar aortic stenosis diagnosed during infancy. During the period between November 1, 1986 and October 31, 1992 a total of 13 infants were diagnosed with asymptomatic aortic stenosis, 5 of whom showed rapid progression over the first 2 years of life. Two of these asymptomati...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s002469900105

    authors: Anand R,Mehta AV

    更新日期:1997-01-01 00:00:00

  • Venous and intrapericardial thrombosis: secondary to transient protein C deficiency.

    abstract::We present a 2-month-old male infant with thrombosis in the superior vena cava and pericardium due to transient protein C deficiency. Protein C deficiency was related to sepsis and hepatitis-induced liver function impairment. The patient's cardiac anatomy was otherwise normal. The patient was referred to us with signs...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-006-1265-8

    authors: Demir T,Celkan T,Ahunbay G,Babaoglu A,Besikci R

    更新日期:2006-07-01 00:00:00

  • Long-term outcome of palliation with internal pulmonary artery bands after primary heart transplantation for hypoplastic left heart syndrome.

    abstract::The purpose of this study was to describe the long-term outcome of infants with hypoplastic left heart syndrome (HLHS) who underwent placement of internal pulmonary artery bands as part of a transcatheter palliation procedure followed by primary heart transplantation. Transcatheter palliation included stenting of the ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-009-9424-3

    authors: Miyamoto SD,Pietra BA,Chan KC,Ivy DD,Mashburn C,Campbell DN,Mitchell MB,Boucek MM

    更新日期:2009-05-01 00:00:00

  • Incidence of Echocardiographic Abnormalities Following Pediatric SVT Ablation: Comparison of Cases Utilizing Fluoroscopy Alone to Cases with Adjunctive 3D Electroanatomic Mapping.

    abstract::There are few data on the incidence of echocardiographic (echo) abnormalities following catheter ablation in children in the era of 3D mapping. Wide practice variation exists regarding routine post-ablation echo. We hypothesized a low incidence of clinically significant echo abnormalities following SVT ablation in oth...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-018-1999-0

    authors: Gartenberg AJ,Pass RH,Ceresnak S,Nappo L,Janson CM

    更新日期:2019-03-01 00:00:00