Abstract:
:In the classic scimitar syndrome, a pulmonary vein draining all or part of the right lung enters the inferior vena cava. A variant is described with the same roentgenographic appearance, but with drainage of the anomalous pulmonary vein into both the inferior vena cava and the left atrium; the atrial septum was intact. This case, together with six others reported elsewhere, reminds us that the scimitar sign has both false positives and false negatives. Therefore, the diagnosis of scimitar syndrome cannot be made with certainty from a plain x-ray film.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Pearl Wdoi
10.1007/BF02079472subject
Has Abstractpub_date
1987-01-01 00:00:00pages
139-41issue
2eissn
0172-0643issn
1432-1971journal_volume
8pub_type
杂志文章abstract::We report a 6-year-old girl with superoinferior ventricles, criss-cross atrioventricular (AV) relationships with solitus atria, a D-loop, L-transposition of the great arteries, subpulmonary stenosis, but without a ventricular septal defect (VSD). The diagnosis was made by echocardiographic examination and was strength...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00795379
更新日期:1993-10-01 00:00:00
abstract::A case report of a neonate with cardiac tumors in association with tuberous sclerosis is presented. The rare complication of pulmonary embolism and its successful treatment by anticoagulation and thrombolytic therapy is described. The treatment of these cardiac tumors is conservative, because the tumors regress sponta...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010247
更新日期:2001-07-01 00:00:00
abstract::Ebstein anomaly of mitral valve (MV) is an extremely rare congenital heart disease. In the current report, we present a case of Ebstein of MV that was diagnosed prenatally. Fetal echocardiogram showed that the posterior leaflet of MV was tethered to the lateral wall of left ventricle (LV) with downward displacement in...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1903-y
更新日期:2018-08-01 00:00:00
abstract::Congenital aneurysms of the thoracic venous system are rare. In particular, innominate venous aneurysms are extremely rare. We describe a 16-year-old girl whose chest x-ray suggested a mediastinal tumor. Three-dimensional contrast-enhancement magnetic resonance venography showed a giant sacciform aneurysm of the left ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0499-y
更新日期:2004-07-01 00:00:00
abstract::This review outlines the morphologic and pathogenetic characteristics of congenital polyvalvular disease. Two cases are used for exemplification. The macroscopic and histologic features of the valves as well as associated cardiac lesions and clinical syndromes are described, followed by a discussion of morphogenesis o...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s002460010169
更新日期:2001-03-01 00:00:00
abstract::Debilitating cardiomyocyte loss underlies the progression to heart failure. Although there have been significant advances in treatment, current therapies are intended to improve or preserve heart function rather than regenerate lost myocardium. A major hurdle in implementing a cell-based regenerative therapy is the in...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9409-2
更新日期:2009-07-01 00:00:00
abstract::This study aimed to assess the impact of integrating a simulation-based education module into an extracorporeal membrane oxygenation (ECMO) curriculum on novice learners and to test the duration of time that skills obtained during this training exercise were retained. The authors hypothesized that multidisciplinary, s...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0490-6
更新日期:2013-03-01 00:00:00
abstract::Tricuspid valve malformation is a rare congenital heart disease. Prenatal diagnosis of Ebstein's anomaly (EA) and tricuspid valve dysplasia (TVD) is associated with high mortality. There are conflicting reports concerning accurate prognostication after diagnosis in utero. The aim of our study was to assess prognostic ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0355-z
更新日期:2012-12-01 00:00:00
abstract::Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluati...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9134-7
更新日期:2008-09-01 00:00:00
abstract::Left-ventricular apical hypoplasia is a rare entity. Although it has typical imaging features on cardiovascular magnetic resonance, recognizing this condition on echocardiography can be challenging. This report describes an asymptomatic pediatric patient who initially presented with a left-ventricular mass on echocard...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0349-x
更新日期:2012-12-01 00:00:00
abstract::Calculating pulmonary vascular resistance is important in many fields of medicine. Although the influence of hematocrit on calculated resistance has been known for many years, it is rare to find the appropriate corrections in published articles. This review discusses the relationship between viscosity and resistance a...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-011-9954-3
更新日期:2011-06-01 00:00:00
abstract::Combination of right and left ventricular outflow tracts obstruction is extremely rare. Neonates with combined aortic stenosis (AS) and pulmonary stenosis (PS) present in critical condition and required urgent treatment. The management approach is not well defined. We report five female neonates with combined AS and P...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-1000-9
更新日期:2014-12-01 00:00:00
abstract::The mechanism of heart failure in patients with enterovirus 71 rhombencephalitis (brain stem encephalitis) remains unknown. Our previous reports hypothesized that a catecholamine storm induced by rhombencephalitis may account for the heart failure. The aim of this study was to develop a novel feline model of norepinep...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0915-6
更新日期:2006-09-01 00:00:00
abstract::Contrary to acquired arteriovenous fistulas, the congenital malformations are very rare. Here we report a case of congenital arteriovenous fistula forming a communication between the right subclavian artery to subclavian vein. To our knowledge, there is no similar case in which an infant has been successfully operated...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010056
更新日期:2000-05-01 00:00:00
abstract::From 1981 through June 1989, 59 children had surgery for a complete atrioventricular (AV) canal defect at Oregon Health Sciences University. We compared the morbidity, mortality, and hemodynamic status of 47 children with and 12 without Down's syndrome through review of operative, clinical, and cardiac catheterization...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00798209
更新日期:1992-04-01 00:00:00
abstract::A 5-year-old boy born with a congenital heart defect had insertion of an epicardial pacemaker that was found on routine evaluation to have been displaced into the rectovesical pouch. He underwent transvenous insertion of another pacemaker, and the displaced pacemaker was successfully retrieved by laparoscopy without i...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-9972-1
更新日期:2011-12-01 00:00:00
abstract::Coronary artery fistula (CAF) is a rare congenital anomaly that can be complicated by endocarditis, myocardial infarction, or coronary aneurysms. This article reviews the clinical characteristics and surgical outcome of 10 patients with CAF in Rajae Heart Center. From 1990 to 2000, 10 patients (age, 6 months to 15 yea...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0656-y
更新日期:2005-07-01 00:00:00
abstract::Successful balloon valvuloplasty for critical pulmonary valve stenosis is described in an 800-g infant. A modified catheter was required to cross the valve in the smallest child known to undergo this procedure. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010288
更新日期:2001-11-01 00:00:00
abstract::A varying degree of impairment of ventricular performance is observed over the long-term after surgery for a congenital heart defect (CHD). Impaired ventricular performance has been shown to be of prognostic value for increased risk of cardiovascular events in adult CHD patients. This emphasizes the importance of deli...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-013-0802-5
更新日期:2014-01-01 00:00:00
abstract::Azygos continuation of inferior venacava (IVC) is well known in association with interrupted IVC. We report azygos connection of uninterrupted IVC in a young child with complex univentricular heart. This peculiar anatomy was made suitable for univentricular repair by combining percutaneous device closure of prehepatic...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-010-9802-x
更新日期:2011-01-01 00:00:00
abstract::The occurrence of familial heart disease in association with tricuspid atresia is rare. The first reported instance of tricuspid atresia and Ebstein's anomaly in siblings is presented. The presence of these two distinct pathologic variants of tricuspid valve malformations in siblings suggests that these malformations ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900072
更新日期:1996-09-01 00:00:00
abstract::Hammock mitral valve (MV), also known as anomalous mitral arcade, is a rare congenital anomaly. We report a case of a 10-month-old child who presented with congestive heart failure and was found to have severe mitral stenosis (MS) secondary to a hammock MV anomaly. Detailed advanced imaging with cardiac MRI and three-...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1797-0
更新日期:2018-03-01 00:00:00
abstract::We present a case of congenital pulmonary systemic collateral vein associated with truncus arteriosus. Pulmonary systemic collateral vein with nonobstructed left atrial egress is different from those with obstructed left atrial egress in that it is functionally redundant. Including this case, 8 patients among 33 repor...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-002-0439-2
更新日期:2004-01-01 00:00:00
abstract::The authors hypothesized that prospective, systematic Internet searches could identify occurrences of sudden cardiac death (SCD) in athletes and would be useful for establishing a system of active surveillance. Weekly advanced Google searches of the Internet were conducted for cases of SCD in young athletes during a 1...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0717-1
更新日期:2013-01-01 00:00:00
abstract::A two-year-old child who had had palliative surgery as a neonate for an absent right atrioventricular connection and double-inlet ventricle was shown to be developmentally retarded. Trisomy for the short arm of chromosome 8 was demonstrated, resulting from a familial 8:13 translocation, with a high risk of recurrence....
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02306750
更新日期:1984-01-01 00:00:00
abstract::Limited data exist on the impact of prenatal diagnosis and outcomes of fetal truncus arteriosus (TA). We sought to assess prenatal diagnostic accuracy and prenatal outcomes in fetuses with TA and compare postnatal outcomes in neonates with prenatally and postnatally diagnosed TA. Records were reviewed for patients dia...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9328-7
更新日期:2009-04-01 00:00:00
abstract::The epidemiologic data for pediatric hypertrophic cardiomyopathy (HCM) needs to be periodically updated as diagnostic techniques and management strategies improve. Herein, the incidence, prevalence, and mortality rates of pediatric HCM in a population-based treatment system are described. Patients aged ≤ 17 years and ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02472-2
更新日期:2020-10-03 00:00:00
abstract::Children with trisomy 21 have a high incidence of congenital heart disease that frequently requires surgical repair. These patients often require multiple and higher dosage sedatives during the postoperative period. Dexmedetomidine is an alpha(2)-adrenergic receptor agonist that has sedative, analgesic, and anxiolytic...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0072-6
更新日期:2007-09-01 00:00:00
abstract::The hybrid pathway for the management of patients with hypoplastic left heart syndrome was pioneered at our institution and is the preferred approach compared with the traditional Norwood pathway. Patients undergoing this surgery are generally <6 months of age, and pain management in this age group after surgery for c...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0233-8
更新日期:2012-10-01 00:00:00
abstract::Percutaneous balloon aortic valvoplasty (BAV) and surgical aortic valvotomy (SAV) are palliative procedures in patients with non-critical congenital valve stenosis. The aim of the study was to evaluate long-term BAV and SAV results after up to 24 years of follow-up. From 1987 to 2013, 74 consecutive interventions were...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-1056-6
更新日期:2015-03-01 00:00:00