Abstract:
:We report a 6-year-old girl with superoinferior ventricles, criss-cross atrioventricular (AV) relationships with solitus atria, a D-loop, L-transposition of the great arteries, subpulmonary stenosis, but without a ventricular septal defect (VSD). The diagnosis was made by echocardiographic examination and was strengthened by cardiac catheterization and angiocardiography. Balloon atrial septostomy in the neonatal period and a modified Blalock-Taussig shunt at the age of 16 months were performed to alleviate hypoxia. Following the shunt operation, the clinical condition of the patient deteriorated with progressive cardiac enlargement, congestive heart failure, and tricuspid regurgitation. We assume that the absence of a VSD contributed to this deterioration. Subsequent improvement was obtained with balloon enlargement of the atrial septal defect and a bidirectional Glenn anastomosis.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Alday LE,Juaneda Edoi
10.1007/BF00795379subject
Has Abstractpub_date
1993-10-01 00:00:00pages
238-41issue
4eissn
0172-0643issn
1432-1971journal_volume
14pub_type
杂志文章abstract::This report describes the case of two pediatric patients who demonstrated echocardiographic evidence of pulmonary hypertension (PH) during the acute phase of Kawasaki disease. The etiology of PH development in this setting is currently unknown, but the authors hypothesize that pulmonary vasculitis may play a significa...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-012-0510-6
更新日期:2013-01-01 00:00:00
abstract::Coronary artery anatomy represents a challenging and, often, determining predictor of outcome in an arterial switch operation (ASO). Impact of specific coronary artery variants, such as single, intramural and inverted, on time-related events following ASO, is, yet, to be determined. We sought to compare early and late...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1543-z
更新日期:2017-03-01 00:00:00
abstract::Transient complete heart block (TCHB) is defined as complete interruption of atrioventricular conduction (AVC) after cardiac surgery followed by return of conduction. This study aimed to assess the risk for the development of late complete heart block (LCHB) after recovery of TCHB and to examine the electrocardiograph...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0595-y
更新日期:2013-04-01 00:00:00
abstract::Ebstein anomaly of mitral valve (MV) is an extremely rare congenital heart disease. In the current report, we present a case of Ebstein of MV that was diagnosed prenatally. Fetal echocardiogram showed that the posterior leaflet of MV was tethered to the lateral wall of left ventricle (LV) with downward displacement in...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1903-y
更新日期:2018-08-01 00:00:00
abstract::Use of extracorporeal membrane oxygenation (ECMO) in infants with congenital heart disease is becoming more frequent. We present the first reported use of balloon atrial septostomy during ECMO support and describe possible complications of such procedures unique to ECMO therapy. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00795647
更新日期:1993-07-01 00:00:00
abstract::Although recognized by pediatric cardiac surgeons, aortic insufficiency as a technical complication after tetralogy of Fallot repair is poorly documented, especially if it occurs late. The case of a boy with aortic insufficiency 10 years after complete tetralogy repair is described. No documentation in the literature ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00817618
更新日期:1994-03-01 00:00:00
abstract::In case of progressive cyanosis after modified Fontan procedure, intrahepatic shunting should be considered. Ligation of the hepatic vein is safe and effective in managing this condition, and it is important to ensure that the pressure difference between superior vena cava and the portal vein system remains minimal af...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900505
更新日期:1999-11-01 00:00:00
abstract::Color-coded two-dimensional (2D) echocardiography confirmed the presence of severe congenital mitral regurgitation in an 8-month-old infant. Intraoperative inspection revealed an isolated perforation in the anterior leaflet. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02239570
更新日期:1990-04-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469910028
更新日期:2000-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-2005-6
更新日期:2019-01-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900105
更新日期:1997-01-01 00:00:00
abstract::Killian-Pallister syndrome is a rare dysmorphic condition characterized by specific clinical manifestations and tetrasomy 12p. Although the association of this condition with congenital heart disease has been previously documented, no cases have been reported in association with Fallot's tetralogy. We report one such ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900420
更新日期:1999-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1322-2
更新日期:2016-03-01 00:00:00
abstract::A fetal echocardiographic scan was performed when routine prenatal ultrasound screening failed to identify four cardiac chambers. The scan showed a single ventricle with an associated circoid varicosity. Because of these anomalies, amniocentesis was suggested and trisomy 18 confirmed. The presence of major cardiac str...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00794843
更新日期:1993-01-01 00:00:00
abstract::Plastic bronchitis is a rare, potentially life-threatening condition in which protein casts form within and occlude the bronchus, resulting in pulmonary failure, and has been identified as a complication after the Fontan procedure. We present a case of a 5-year-old girl who had undergone an extracardiac fenestrated Fo...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0913-8
更新日期:2005-09-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0169-y
更新日期:2007-07-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02505-w
更新日期:2020-11-26 00:00:00
abstract::The etiology and pathogenesis of Kawasaki disease (KD) is largely unknown. Certain demographic factors and laboratory findings are predictive of the development of coronary artery (CA) aneurysms. The objectives of this study were to determine the epidemiology of KD patients in an urban hospital and determine risk fact...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0916-5
更新日期:2005-11-01 00:00:00
abstract::Anomalous origin of left pulmonary artery (ALPA) from aorta with atrial septal defect (ASD) is a rare congenital cardiac malformation. We report a case of ALPA from the aorta with ASD in a 1.8-kg baby. Repair was needed at an early age due to progressive congestive heart failure. Surgical correction was performed with...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9234-z
更新日期:2008-07-01 00:00:00
abstract::This review examines the mechanism of estrogen signaling in cardiomyocytes, with an emphasis on mechanisms that might be important in cardioprotection. It investigates estrogen signaling mediated by the nuclear estrogen receptors alpha and beta and the G-protein-coupled receptor (GPR 30/GPER). Estrogen signaling via n...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-010-9877-4
更新日期:2011-03-01 00:00:00
abstract::We studied the safety and efficacy of closing patent ductus arteriosus by Nit-Occlud coils via retrograde approach. This is a retrospective study of 46 attempts to close ducts by this method in two hospitals in Egypt and Iran. Ductus arteriosus was crossed by left or right Judkins or endhole catheters. The coil was de...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章,多中心研究
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更新日期:2017-04-01 00:00:00
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journal_title:Pediatric cardiology
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doi:10.1007/s00246-012-0201-3
更新日期:2012-06-01 00:00:00
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journal_title:Pediatric cardiology
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更新日期:2020-03-01 00:00:00
abstract::Barth syndrome (BTHS) is an X-linked disorder characterised by cardiomyopathy, neutropenia, skeletal myopathy and growth delay. This study describes the UK national clinical experience and outcome of cardiomyopathy in BTHS. The clinical course and echocardiographic changes of all patients with BTHS in the UK were revi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1260-z
更新日期:2016-01-01 00:00:00
abstract::Complications, such as recoarctation or secondary hypertension, probably related to the loss of arterial elasticity, frequently occur after aortic coarctation surgery. This study aimed to investigate arterial compliance as evaluated by automated recording of the QKd interval in patients who underwent repair of coarcta...
journal_title:Pediatric cardiology
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abstract::Previous studies have indicated the importance of allometric scaling of VO2max for body size. However, no information is available on adjusting maximal cardiac output (Qmax) and stroke volume (SVmax) for body dimensions. The allometric exponent b was determined for the equation Y = aXb (where Y is the physiological ou...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章
doi:10.1007/s002460010102
更新日期:2000-09-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2016-12-01 00:00:00
abstract::This study aimed to assess the technical aspects of atrial septal defect (ASD) closure using the Amplatzer septal occluder (ASO) and the Gore Helex septal occluder (GHSO) for infants weighing less than 8 kg and to determine the safety, effectiveness, and near-to-intermediate-term outcome of the closure. The Mid-Atlant...
journal_title:Pediatric cardiology
pub_type: 杂志文章,多中心研究
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abstract::We aimed to investigate the complications after epicardial pacemaker (PM) implantation in neonates and infants and their relationship with factors such as device size and patient size. Between May 2010 and July 2018, 55 patients under 1 year of age who underwent epicardial PM placement were retrospectively evaluated. ...
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pub_type: 杂志文章
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02263455
更新日期:1987-01-01 00:00:00