Abstract:
:Congenitally corrected transposition of the great arteries is a rare anomaly that is thought to arise from a defect in looping of the primitive cardiac tube. Cor triatriatum is another rare congenital cardiac anomaly due to faulty incorporation of the common pulmonary vein into the left atrium. We present a rare case comprising both disorders in one patient.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Jayranganath M,Subramanian A,Manjunath CNdoi
10.1007/s00246-011-9912-0subject
Has Abstractpub_date
2011-04-01 00:00:00pages
515-7issue
4eissn
0172-0643issn
1432-1971journal_volume
32pub_type
杂志文章abstract::Cardiopulmonary bypass (CPB) reduces coagulation factor levels through hemodilution and consumption. Differences in CPB-induced alterations of factor XIII (FXIII) levels in children with cyanotic and acyanotic congenital heart defects (CHDs) are not well characterized. FXIII activity (determined by Berichrom assay), p...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0903-9
更新日期:2014-10-01 00:00:00
abstract::Left ventricular (LV) function is impaired by increased afterload in neonates with severe coarctation of the aorta, which may result in endocardial fibroelastosis. Repair of the coarctation usually solves the problem, with LV function normalizing after a few weeks. This report describes a patient who underwent success...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9595-y
更新日期:2010-02-01 00:00:00
abstract::This review discusses the historical aspects, current state of the art, and potential future advances in the areas of nomenclature and databases for congenital heart disease. Five areas will be reviewed: (1) common language = nomenclature, (2) mechanism of data collection (database or registry) with an established uni...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-006-1447-4
更新日期:2007-03-01 00:00:00
abstract::Sudden cardiac death in young competitive athletes is tragic and usually due to unsuspected cardiovascular disease. Screening programs for athletes remain debatable, and restriction of athletes from sports can have physical, emotional, and legal ramifications. In this article, we review the epidemiology of the more co...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-012-0170-6
更新日期:2012-03-01 00:00:00
abstract::The slope of the relation between the unadjusted QT interval and heart rate during the face immersion test has been reported to be useful as an index for predicting an abnormal lengthening of the QT interval for children with nonfamilial long QT syndrome. Our goals were to determine whether we can replace the slope of...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-0034-y
更新日期:2002-03-01 00:00:00
abstract::The congenital anomaly of aortopulmonary window is rare. Its combination with interruption of the aortic arch has been previously recognized and reported in infants and children. Early and complete repair of such a congenital anomaly may prevent progression to cardiac failure and premature death. We describe the succe...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/BF02505097
更新日期:1996-03-01 00:00:00
abstract::Electrocardiograms (heart rate, QRS voltage, QRS axis in the frontal plane. Q-Tc interval) echocardiograms [left ventricular fractional shortening (LVFS); preejection period (PEP); PEP/left ventricular ejection time (PEP/LVET) ratio; end-diastolic left ventricular free wall and interventricular septum thickness; prese...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02238495
更新日期:1991-01-01 00:00:00
abstract::From 1981 through June 1989, 59 children had surgery for a complete atrioventricular (AV) canal defect at Oregon Health Sciences University. We compared the morbidity, mortality, and hemodynamic status of 47 children with and 12 without Down's syndrome through review of operative, clinical, and cardiac catheterization...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00798209
更新日期:1992-04-01 00:00:00
abstract::Exercise testing can highlight repolarisation abnormalities in adults with coronary artery disease. Late after Kawasaki disease (KD), increased QT dispersion (QTd) has been reported on resting ECG in children, but there are no reported studies of QTd during exercise. Our objective was to determine the pattern of QTd r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0201-3
更新日期:2012-06-01 00:00:00
abstract::A fetal echocardiographic scan was performed when routine prenatal ultrasound screening failed to identify four cardiac chambers. The scan showed a single ventricle with an associated circoid varicosity. Because of these anomalies, amniocentesis was suggested and trisomy 18 confirmed. The presence of major cardiac str...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00794843
更新日期:1993-01-01 00:00:00
abstract::Adrenomedullin (ADM) is a vasoactive peptide with potent dilatory effects. We studied whether perioperative myocardial injury could be altered by the presence of ADM. Blood samples from 19 children with congenital heart disease undergoing surgical repair were collected at six time points: preoperative, on cardiopulmon...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010046
更新日期:2000-05-01 00:00:00
abstract::Right ventricular (RV) pacing can be associated with impairment of left ventricular (LV) function due to electrical dyssynchrony and myocardial remodeling (Janousek et al. in J Cardiovasc Electrophysiol 15:470-474, 2004). RV-pacing induced ventricular dysfunction is reversible by techniques such as biventricular pacin...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1629-2
更新日期:2017-08-01 00:00:00
abstract::Noonan syndrome is an autosomal dominant disease that manifests a wide variety of clinical characteristics. The syndrome is also associated with some cardiac defects. Half of all Noonan syndrome cases are caused by mutations in the PTPN11 gene, but only limited data are available regarding aortic involvement in these ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9537-8
更新日期:2010-01-01 00:00:00
abstract::Ductal stenting (DS) palliates duct-dependent lesions using coronary stents. Sirolimus-eluting stents have replaced bare-metal stents in coronary interventions. Concerns exist about sirolimus levels in neonates. Therapeutic immunosuppressive sirolimus level is 5-15 ng/ml. After neonatal DS, drug levels were assessed a...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02381-4
更新日期:2020-10-01 00:00:00
abstract::Although recognized by pediatric cardiac surgeons, aortic insufficiency as a technical complication after tetralogy of Fallot repair is poorly documented, especially if it occurs late. The case of a boy with aortic insufficiency 10 years after complete tetralogy repair is described. No documentation in the literature ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00817618
更新日期:1994-03-01 00:00:00
abstract::The original version of this article unfortunately contained a mistake. The presentation of Table 2 was incorrect .The corrected table is given below. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章,已发布勘误
doi:10.1007/s00246-018-1816-9
更新日期:2018-03-01 00:00:00
abstract::Previous studies have indicated the importance of allometric scaling of VO2max for body size. However, no information is available on adjusting maximal cardiac output (Qmax) and stroke volume (SVmax) for body dimensions. The allometric exponent b was determined for the equation Y = aXb (where Y is the physiological ou...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章
doi:10.1007/s002460010102
更新日期:2000-09-01 00:00:00
abstract::Many different types of potassium channels with various functions exist in pulmonary artery smooth muscle cells, contributing to many physiological actions and pathological conditions. The deep involvement of these channels in the onset and exacerbation of pulmonary arterial hypertension (PAH) also continues to be rev...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-016-1491-7
更新日期:2017-01-01 00:00:00
abstract::Persistent pulmonary hypertension of the newborn (PPHN) complicated with transposition of the great arteries (TGA) and an intact ventricular septum (IVS) often is therapy resistant and associated with an extremely poor prognosis. For this condition, opening of the ductus arteriosus (DA) by prostaglandin-E1 in conjunct...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9475-5
更新日期:2009-10-01 00:00:00
abstract::The importance of myocardial bridging of a coronary artery in the setting of hypertrophic cardiomyopathy is controversial, although we have previously reported an association with myocardial ischemia and sudden death in children. We report five symptomatic children in whom symptoms or evidence of myocardial ischemia r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0576-2
更新日期:2004-07-01 00:00:00
abstract::Human pluripotent stem cells (hPSCs) offer a multifaceted platform to study cardiac developmental biology, understand disease mechanisms, and develop novel therapies. Remarkable progress over the last two decades has led to methods to obtain highly pure hPSC-derived cardiomyocytes (hPSC-CMs) with reasonable ease and s...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-019-02165-5
更新日期:2019-10-01 00:00:00
abstract::Using the Doppler technique, this study compared the prenatal and postnatal flow patterns of an infant with cerebral arteriovenous (AV) malformation. Fetal right ventricular end-diastolic dimension was 1.7 cm with right ventricular ejection equaling 66% of the combined cardiac output. Diastolic flow was reversed in th...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00801914
更新日期:1995-05-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s00246-003-0471-x
更新日期:2004-01-01 00:00:00
abstract::Operative survival after the Norwood procedure has significantly improved during the past 10 years. However, there remains attrition among Norwood survivors before reaching planned second-stage palliation. The purpose of this study was to evaluate potential risk factors for interstage mortality among Norwood survivors...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0776-4
更新日期:2005-07-01 00:00:00
abstract::A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0483-5
更新日期:2013-01-01 00:00:00
abstract::Two children with acute symptomatic pericardial effusion had unusual echocardiographic findings. In each case, the pericardial effusion was hemorrhagic. Echocardiography displayed numerous linear bands coursing across the pericardial space. Recognition of this characteristic image may predict that an acute effusion is...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00817614
更新日期:1994-03-01 00:00:00
abstract::Rehospitalization following pediatric heart transplantation is common. However, existing data remain somewhat limited. Using a novel linkage between administrative and clinical databases, pediatric heart transplant (HT) recipients from 29 centers who survived to discharge were retrospectively reviewed to determine the...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02326-x
更新日期:2020-03-01 00:00:00
abstract::We undertook a study to identify the hemodynamic significance of a Doppler-derived gradient across a stenotic pulmonary valve. Furthermore, we attempted to define the optimal plane for velocity data acquisition. A total of 17 children with valvar pulmonary stenosis were evaluated using Doppler echocardiography. Flow-v...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02081678
更新日期:1989-07-01 00:00:00
abstract::Postoperative arrhythmia is a common complication after open heart surgery in children. JET is the most common and dangerous arrhythmia. We aimed to assess safety and efficacy of prophylactic amiodarone in preventing JET in children underwent cardiac surgery and to assess risk factors for JET among our patients. In to...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1343-5
更新日期:2016-04-01 00:00:00
abstract:BACKGROUND:The optimal surgical strategy for pulmonary atresia with ventricular septal defect (PA/VSD) in neonates and young infants is controversial. Staged repair may be associated with a higher risk of inter-stage mortality, while primary repair may lead to frequent post-repair re-interventions. METHODS:From 2004 t...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02352-9
更新日期:2020-06-01 00:00:00