Abstract:
:This review discusses the historical aspects, current state of the art, and potential future advances in the areas of nomenclature and databases for congenital heart disease. Five areas will be reviewed: (1) common language = nomenclature, (2) mechanism of data collection (database or registry) with an established uniform core data set, (3) mechanism of evaluating case complexity, (4) mechanism to ensure and verify data completeness and accuracy, and (5) collaboration between medical subspecialties. During the 1990s, both the Society of Thoracic Surgeons (STS) and the European Association for Cardiothoracic Surgery (EACTS) created congenital heart surgery outcomes databases. Beginning in 1998, the EACTS and STS collaborated in the work of the International Congenital Heart Surgery Nomenclature and Database Project. By 2000, a common congenital heart surgery nomenclature, along with a common core minimal data set, were adopted by the EACTS and the STS and published in the Annals of Thoracic Surgery. In 2000, the International Nomenclature Committee for Pediatric and Congenital Heart Disease was established; this committee eventually evolved into the International Society for Nomenclature of Paediatric and Congenital Heart Disease (ISNPCHD). The working component of ISNPCHD is the International Working Group for Mapping and Coding of Nomenclatures for Paediatric and Congenital Heart Disease, also known as the Nomenclature Working Group (NWG). By 2005, the NWG cross-mapped the EACTS-STS nomenclature with the European Paediatric Cardiac Code of the Association for European Paediatric Cardiology and created the International Paediatric and Congenital Cardiac Code (IPCCC) ( http://www.IPCCC.NET ). This common nomenclature (IPCCC), and the common minimum database data set created by the International Congenital Heart Surgery Nomenclature and Database Project, are now utilized by both EACTS and STS; since 1998, this nomenclature and database have been used by both the STS and EACTS to analyze outcomes of more than 75,000 patients. Two major multi-institutional efforts have attempted to measure case complexity; the Risk Adjustment in Congenital Heart Surgery-1 and the Aristotle Complexity Score. Efforts to unify these two scoring systems are in their early stages but are encouraging. Collaborative efforts involving the EACTS and STS are under way to develop mechanisms to verify data completeness and accuracy. Further collaborative efforts are also ongoing between pediatric and congenital heart surgeons and other subspecialties, including pediatric cardiac anesthesiologists (via the Congenital Cardiac Anesthesia Society), pediatric cardiac intensivists (via the Pediatric Cardiac Intensive Care Society), and pediatric cardiologists (via the Joint Council on Congenital Heart Disease). Clearly, methods of congenital heart disease outcomes analysis continue to evolve, with continued advances in five areas: nomenclature, database, complexity adjustment, data verification, and subspecialty collaboration.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Jacobs JP,Mavroudis C,Jacobs ML,Maruszewski B,Tchervenkov CI,Lacour-Gayet FG,Clarke DR,Gaynor JW,Spray TL,Kurosawa H,Stellin G,Ebels T,Bacha EA,Walters HL 3rd,Elliott MJdoi
10.1007/s00246-006-1447-4subject
Has Abstractpub_date
2007-03-01 00:00:00pages
105-15issue
2eissn
0172-0643issn
1432-1971journal_volume
28pub_type
杂志文章,评审abstract::We report a case of isolated ventricular inversion in a 42-year-old woman. This rare congenital cardiac anomaly was corrected by an intraatrial baffle procedure. She also underwent left-sided double-chamber endocardial pacemaker implantation for postoperative tachycardia bradycardia syndrome. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0583-3
更新日期:2004-09-01 00:00:00
abstract::Atherosclerotic cardiovascular disease (CVD), a leading cause of death globally, has origins in childhood. Major risk factors include family history of premature CVD, dyslipidemia, diabetes mellitus, and hypertension. Lipoprotein (a) [Lp(a)], an inherited lipoprotein, is associated with premature CVD, but its impact o...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1927-3
更新日期:2018-12-01 00:00:00
abstract::Congenital heart defects (CHDs) are the most prevalent of all birth defects and the leading cause of death in the first year of life. The molecular causes of most CHDs remain largely unknown. The LIM homeodomain transcriptor factor ISL1 is a marker for undifferentiated cardiac progenitor cells that give rise to both t...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0578-z
更新日期:2013-04-01 00:00:00
abstract::Left-ventricular apical hypoplasia is a rare entity. Although it has typical imaging features on cardiovascular magnetic resonance, recognizing this condition on echocardiography can be challenging. This report describes an asymptomatic pediatric patient who initially presented with a left-ventricular mass on echocard...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0349-x
更新日期:2012-12-01 00:00:00
abstract::Two fetuses of approximately 11 weeks development with aplasia of the pulmonary as well as the aortic valve leaflets are reported. Both cases showed additional cardiac malformations. Case 1, with all leaflets missing, also had double-outlet right ventricle, hypoplastic left ventricle, large ventricular septal defect, ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02238416
更新日期:1991-04-01 00:00:00
abstract::A 6-year-old girl with type 3 long QT syndrome was safely and successfully implanted with an implantable cardioverter-defibrillator (ICD) system. Prior to implantation, she had experienced uncontrollable life-threatening arrhythmia in spite of high-dose administration of mexiletine. An ICD coil lead for transvenous us...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0065-y
更新日期:2011-10-01 00:00:00
abstract::A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0483-5
更新日期:2013-01-01 00:00:00
abstract::Cardiac involvement of Duchenne and Becker muscular dystrophies (DMD/BMD) is the most common cause of fatal outcomes. It is still unclear whether some DMD/BMD gene mutations might be predictive of cardiac involvement. In this study, we provide a comprehensive overview on genotypes of cardiac disease in DMD/BMD. We sys...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02470-4
更新日期:2020-10-09 00:00:00
abstract::This paper reviews the initial experience of radical correction of truncus arteriosus in the Soviet Union. The anatomy, hemodynamics, diagnosis and surgical technique are described in detail. Five patients were operated on; three survived. The two deaths in this series were due to mistakes in evaluating the indication...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02424960
更新日期:1984-04-01 00:00:00
abstract::This report describes a rare case of complete transposition of the great arteries (TGA) with an intramural right coronary artery arising well above the sinotubular junction. Additionally in this case, the left circumflex artery arose anomalously as a branch from the right coronary. Identification of this anatomic anom...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0108-4
更新日期:2012-01-01 00:00:00
abstract::Device closure of atrial septal defects (ASDs) is rapidly becoming routine in children. Comparisons are often made to older surgical series with higher morbidities. However outcomes including reintervention, late failure, and the need for long-term follow-up must be considered and compared to those of a current surgic...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-002-0131-6
更新日期:2003-09-01 00:00:00
abstract::We report our experience with asymptomatic valvar aortic stenosis diagnosed during infancy. During the period between November 1, 1986 and October 31, 1992 a total of 13 infants were diagnosed with asymptomatic aortic stenosis, 5 of whom showed rapid progression over the first 2 years of life. Two of these asymptomati...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900105
更新日期:1997-01-01 00:00:00
abstract::Magnetic resonance imaging (MRI) is a powerful tool which enables the visualization of anatomy and the assessment of many physiological aspects of organ function. MRI and magnetic resonance angiography and magnetic resonance spectroscopy will play critical roles in cardiac applications during the next millennium. Thus...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469910003
更新日期:2000-01-01 00:00:00
abstract::Radiation exposure from pediatric cardiac catheterization may be substantial, although published estimates vary. We sought to report patient radiation dose across a range of diagnostic and interventional cases in a modern, high-volume pediatric catheterization laboratory. We retrospectively reviewed diagnostic and int...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0869-7
更新日期:2014-06-01 00:00:00
abstract::The aim of this study was to clarify the association of clinical characteristics of unexplained syncope with the outcome of the head-up tilt test (HUT) in children. A total of 47 patients with unexplained syncope were classified into two groups according to their outcomes of HUT: the positive response group and the ne...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0513-4
更新日期:2004-07-01 00:00:00
abstract::Three infants, each with a clinical picture of dilated cardiomyopathy, underwent endomyocardial biopsy. Immunohistologic analysis revealed chronic myocarditis. In one infant, a postviral etiology of chronic myocarditis could be assessed on the basis of molecular techniques. Therapy with azathioprine and prednisone res...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900292
更新日期:1998-05-01 00:00:00
abstract:INTRODUCTION:Newborns with congenital diaphragmatic hernia (CDH) have varying degrees of pulmonary hypoplasia and pulmonary hypertension (PH), and there is limited evidence that cardiac dysfunction is present. We sought to study early neonatal biventricular function and performance in these patients by reviewing early ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1850-7
更新日期:2018-06-01 00:00:00
abstract::The original version of this article unfortunately contained a mistake. The presentation of Table 2 was incorrect .The corrected table is given below. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章,已发布勘误
doi:10.1007/s00246-018-1816-9
更新日期:2018-03-01 00:00:00
abstract::A 6-year-old girl presented with respiratory distress. Chest radiographs exhibited calcifications in the mediastinum. Further imaging revealed extensive cardiac calcifications on computed tomography of the chest. The laboratory parameters were consistent with findings of secondary hyperparathyroidism. Detailed review ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0765-7
更新日期:2005-07-01 00:00:00
abstract::For premature infants with congenital heart disease (CHD), it may be unclear when the burdens of treatment outweigh potential benefits. Parents may thus have to choose between comfort care at birth and medical stabilization until surgical repair is feasible. Better defined outcome data, including risk factors for mort...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1374-y
更新日期:2016-06-01 00:00:00
abstract::An atrial septal aneurysm (ASA) is an increasingly recognized entity that involves septal tissue significantly bulging into either atria instead of remaining in a relatively neutral position. ASAs may be described based on the length of the segment of atrial septal tissue involved as well as the distance and direction...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-2017-2
更新日期:2019-01-01 00:00:00
abstract::The inauguration of Sequential Segmental Analysis (SSA) a few decades ago provides basic conditions to establish a universally applicable classification system for cardiac malformations. To gain practical experience, we used this method to classify a collection of 292 congenitally malformed human hearts. Our aims were...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/pl00021002
更新日期:2002-09-01 00:00:00
abstract::Little has been published about specific problems that may occur during long-distance transports of newborn cardiac patients. During a 4-year period after centralization of pediatric heart surgery in Sweden, 286 transports were prospectively investigated. A majority (77.3%) of the transports were carried out by nonspe...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010254
更新日期:2001-09-01 00:00:00
abstract::Contrary to acquired arteriovenous fistulas, the congenital malformations are very rare. Here we report a case of congenital arteriovenous fistula forming a communication between the right subclavian artery to subclavian vein. To our knowledge, there is no similar case in which an infant has been successfully operated...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010056
更新日期:2000-05-01 00:00:00
abstract::Nesiritide is a synthetic form of B-type natriuretic peptide. It is approved for the treatment of acute exacerbations of congestive heart failure in hospitalized adult patients. It is currently under investigation for use in other settings and other patient populations. This article describes administration of nesirit...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0064-6
更新日期:2007-05-01 00:00:00
abstract::Different devices have been used for percutaneous closure of ventricular septal defects (VSDs). Over the past 6 months, we have used the Amplatzer duct occluder for VSDs associated with tunnel-shaped aneurysm in three patients here at our institution. Due to the anatomic resemblance between such VSDs and the duct occl...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9092-0
更新日期:2008-03-01 00:00:00
abstract::Congenital aneurysms of the thoracic venous system are rare. In particular, innominate venous aneurysms are extremely rare. We describe a 16-year-old girl whose chest x-ray suggested a mediastinal tumor. Three-dimensional contrast-enhancement magnetic resonance venography showed a giant sacciform aneurysm of the left ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0499-y
更新日期:2004-07-01 00:00:00
abstract::Ruptured sinus Valsalva aneurysm (SVA) in a patient with tetralogy of Fallot is a very rare cardiac complication. This report describes the case of a 10-year-old Hispanic girl who presented to her cardiologist for a routine transthoracic echocardiography (TTE), which showed a ruptured sinus of Valsalva, with left-to-r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0457-7
更新日期:2013-01-01 00:00:00
abstract::In the classic scimitar syndrome, a pulmonary vein draining all or part of the right lung enters the inferior vena cava. A variant is described with the same roentgenographic appearance, but with drainage of the anomalous pulmonary vein into both the inferior vena cava and the left atrium; the atrial septum was intact...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02079472
更新日期:1987-01-01 00:00:00
abstract::Isolation of the left innominate artery arising from the ductus arteriosus is a rare clinical entity with only nine cases being reported in the literature [5, 7, 8]. We describe a case consisting of tetralogy of Fallot, right aortic arch, and isolation of the left innominate artery arising from a left-sided ductus art...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010154
更新日期:2001-01-01 00:00:00