Abstract:
:The inauguration of Sequential Segmental Analysis (SSA) a few decades ago provides basic conditions to establish a universally applicable classification system for cardiac malformations. To gain practical experience, we used this method to classify a collection of 292 congenitally malformed human hearts. Our aims were to determine advantages and problems of the SSA and to make recommendations for a better practical usability and documentation. SSA is an appropriate instrument for the description of complex cardiac malformations because it is a logical step-by-step approach based on the heart morphology. The method optimizes the diagnosis of different malformed hearts. However, there are some disadvantages of SSA concerning terminology, localization of simple septal defects and exact topographic description of heart structures. For these reasons, we recommend a graphic description of the malformed heart using symbols based on the SSA. The most important prerequisite for an interdisciplinary acceptable classification system of cardiac malformations is to include morphological as well as functional aspects of the hearts.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Craatz S,Künzel E,Spanel-Borowski Kdoi
10.1007/pl00021002subject
Has Abstractpub_date
2002-09-01 00:00:00pages
483-90issue
5eissn
0172-0643issn
1432-1971journal_volume
23pub_type
杂志文章abstract::The observation that endocardial fibroelastosis (EFE) can result from an immune response to maternal autoantibody deposition in the fetal myocardium raises the possibility that the fetal immune system may contribute to the pathogenesis of idiopathic EFE and dilated cardiomyopathy (DCM). This study sought to characteri...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-9980-1
更新日期:2011-12-01 00:00:00
abstract::Different devices have been used for percutaneous closure of ventricular septal defects (VSDs). Over the past 6 months, we have used the Amplatzer duct occluder for VSDs associated with tunnel-shaped aneurysm in three patients here at our institution. Due to the anatomic resemblance between such VSDs and the duct occl...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9092-0
更新日期:2008-03-01 00:00:00
abstract::For premature infants with congenital heart disease (CHD), it may be unclear when the burdens of treatment outweigh potential benefits. Parents may thus have to choose between comfort care at birth and medical stabilization until surgical repair is feasible. Better defined outcome data, including risk factors for mort...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1374-y
更新日期:2016-06-01 00:00:00
abstract::Long-term prostaglandin use is commonly associated with side effects such as cortical proliferation of the bones, hypertrophic pyloric stenosis, and soft tissue swelling of the extremities. We report a neonate with critical coarctation of the aorta, who developed second and third degree atrioventricular blocks associa...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1633-6
更新日期:2017-10-01 00:00:00
abstract::Echocardiography has previously been of limited use in visualizing the aorta in neonates and infants. Using a new technique--right parasternal scanning--the aortic arch and brachiocephalic vessels were studied in 50 children under 18 months of age. Complete visualization was accomplished in 47 patients including those...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02426973
更新日期:1982-01-01 00:00:00
abstract::Successful balloon valvuloplasty for critical pulmonary valve stenosis is described in an 800-g infant. A modified catheter was required to cross the valve in the smallest child known to undergo this procedure. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010288
更新日期:2001-11-01 00:00:00
abstract::We report the case of a fetus diagnosed at 24 weeks' gestation with complete heart block associated with maternal collagen vascular disease and Sjögren's antibody. Serial fetal echocardiograms noted increased echogenicity along the tricuspid and mitral valves without insufficiency. Postnatally, severe tricuspid insuff...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00800677
更新日期:1994-07-01 00:00:00
abstract::Central venous pressure (CVP) measurement is a reliable method for evaluating intravascular volume status and cardiac function, but it is an invasive method that results in some complications such as arterial puncture, pneumothorax, and development of infection. The current study was performed to compare CVP measureme...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9067-1
更新日期:2008-03-01 00:00:00
abstract::The effect of patent ductus arteriosus (PDA) treatment with cyclooxygenase (COX) inhibitors (indomethacin [INDO] and ibuprofen [IBU]) on regional oxygenation requires further clarification. The authors hypothesized that both INDO and IBU reduce regional tissue oxygenation in preterm neonates with PDA but that the risk...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0309-5
更新日期:2012-12-01 00:00:00
abstract::Two cases of arrhythmogenic right ventricular dysplasia (ARVD) in siblings are reported. In the boy, 14 years old, the clinical history, ECG, echocardiography, and histopathological findings were consistent with ARVD. Premature ventricular contractions of left bundle branch block (LBBB) pattern were recorded but no ve...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02239576
更新日期:1990-04-01 00:00:00
abstract::We studied the safety and efficacy of closing patent ductus arteriosus by Nit-Occlud coils via retrograde approach. This is a retrospective study of 46 attempts to close ducts by this method in two hospitals in Egypt and Iran. Ductus arteriosus was crossed by left or right Judkins or endhole catheters. The coil was de...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章,多中心研究
doi:10.1007/s00246-017-1589-6
更新日期:2017-04-01 00:00:00
abstract::The timing of pulmonary valve replacement (PVR) in asymptomatic patients with repaired tetralogy of Fallot (TOF) is typically based on cardiac magnetic resonance imaging-derived ventricular volume measurements. Current criteria do not account for sex-based differences in chamber size. The purpose of this study was to ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02181-5
更新日期:2019-10-01 00:00:00
abstract::Calculating pulmonary vascular resistance is important in many fields of medicine. Although the influence of hematocrit on calculated resistance has been known for many years, it is rare to find the appropriate corrections in published articles. This review discusses the relationship between viscosity and resistance a...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-011-9954-3
更新日期:2011-06-01 00:00:00
abstract::The importance of myocardial bridging of a coronary artery in the setting of hypertrophic cardiomyopathy is controversial, although we have previously reported an association with myocardial ischemia and sudden death in children. We report five symptomatic children in whom symptoms or evidence of myocardial ischemia r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0576-2
更新日期:2004-07-01 00:00:00
abstract::Congenital aneurysms of the thoracic venous system are rare. In particular, innominate venous aneurysms are extremely rare. We describe a 16-year-old girl whose chest x-ray suggested a mediastinal tumor. Three-dimensional contrast-enhancement magnetic resonance venography showed a giant sacciform aneurysm of the left ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0499-y
更新日期:2004-07-01 00:00:00
abstract::Presented is a retrospective outcome study of a 15-year single institutional experience with a contemporary cohort of patients with hypoplastic left heart syndrome and complex that underwent a "Giessen Hybrid" stage I as initial palliation. Hybrid approach consisting of surgical bilateral pulmonary artery banding and ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-1015-2
更新日期:2015-02-01 00:00:00
abstract::Various echocardiographic parameters are determined in the assessment and evaluation of a patent ductus arteriosus. In isolation, many of these parameters have a low sensitivity and specificity for ductal hemodynamic significance compared with ductal size. This study aimed to correlate various echocardiographic parame...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0640-5
更新日期:2013-06-01 00:00:00
abstract::To reveal the association between DNMT1 polymorphisms and congenital heart disease (CHD) in child patients, a total of 224 CHD child patients as well as 199 healthy individuals were enrolled in the present study. The DNA was extracted from whole blood, and four SNPs including rs16999593, rs2228612, rs2288349 and rs104...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1093-9
更新日期:2015-06-01 00:00:00
abstract::This study reviewed different types of primary cardiac and mediastinal tumors in infants and children as well as their clinical presentation and management. Altogether, 34 consecutive patients followed from 1976 through December 2005 were analyzed. Of these 34 patients, 14 (41%) underwent surgery and 20 (59%) with rha...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9256-6
更新日期:2008-11-01 00:00:00
abstract::This report describes the case of two pediatric patients who demonstrated echocardiographic evidence of pulmonary hypertension (PH) during the acute phase of Kawasaki disease. The etiology of PH development in this setting is currently unknown, but the authors hypothesize that pulmonary vasculitis may play a significa...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-012-0510-6
更新日期:2013-01-01 00:00:00
abstract::Severe atrioventricular valve (AVV) or semilunar valve (SLV) regurgitation in the setting of a single ventricle physiology may proceed to valve replacement if repair strategies fail. Outcome data for these children are limited. We present transplant-free survival of a case series of children with single ventricle phys...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02234-9
更新日期:2020-01-01 00:00:00
abstract::We report a patient with tricuspid atresia after total cavopulmonary connection who developed significant mitral valve regurgitation. Doppler myocardial echocardiography tracings showed "pseudonormalization" of diastolic velocities. After successful surgical reconstruction of the mitral valve, the diastolic myocardial...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-1283-6
更新日期:2006-07-01 00:00:00
abstract::A 12-year-old male presented with a 6-week history of apparent digital vasculitis with color changes of the distal fingers and erythematous macules of the palms and soles. Physical examination revealed skin findings of Carney complex and an abnormal cardiac examination. Echocardiography demonstrated a large left atria...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-1238-3
更新日期:2006-03-01 00:00:00
abstract::Plastic bronchitis is a rare, potentially life-threatening condition in which protein casts form within and occlude the bronchus, resulting in pulmonary failure, and has been identified as a complication after the Fontan procedure. We present a case of a 5-year-old girl who had undergone an extracardiac fenestrated Fo...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0913-8
更新日期:2005-09-01 00:00:00
abstract::Rho-kinase (ROCK) belongs to the AGC (protein kinase A/protein kinase G/protein kinase C, PKA/PKG/PKC) family of serine/threonine kinases and is a major downstream effector of small GTPase RhoA. Rho-kinase is involved in a wide range of fundamental cellular functions such as contraction, adhesion, migration, and proli...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-011-9920-0
更新日期:2011-03-01 00:00:00
abstract::Percutaneous balloon aortic valvuloplasty was attempted in an eight-month-old infant with severe aortic valve stenosis. The procedure resulted in a fall in the resting transvalvular systolic pressure gradient from 106 mmHg to 40 mmHg and no aortic regurgitation. Clinical and Doppler echocardiography findings suggest p...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02282747
更新日期:1985-01-01 00:00:00
abstract::Right ventricular (RV) remodeling in hypoplastic left heart syndrome (HLHS) begins prenatally and continues through staged palliations. However, it is unclear if the most marked observed remodeling post-Norwood is secondary to cardiopulmonary bypass (CPB) exposure or if it is an adaptation intrinsic to the systemic RV...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02482-0
更新日期:2020-10-10 00:00:00
abstract::B-type natriuretic peptide (BNP) reflects volume overload on left ventricle and pulmonary hypertension (PH) in patients with ventricular septal defect (VSD). Pulmonary vascular resistance (PVR) has been reported to correlate positively with BNP in VSD patients with various degrees of PH. We aimed to investigate the re...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9037-7
更新日期:2008-01-01 00:00:00
abstract::Dexmedetomidine is a new sedative and analgesic agent that has a unique property of lack of respiratory depression. We describe a pediatric case in which the use of dexmedetomidine enabled us to successfully extubate a 12-year-old heart transplant patient with acute pneumonia after several failed attempts with the use...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0683-3
更新日期:2005-09-01 00:00:00
abstract::Pediatric primary cardiomyopathy is rare but serious, having high mortality; hypertrophic and dilated types are the most common. Its etiology has been mainly considered idiopathic; however, next generation sequencing techniques have revealed nearly half of idiopathic pediatric cases arose from specific genetic mutatio...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02240-x
更新日期:2020-01-01 00:00:00