Abstract:
:We report hemodynamic findings in two patients with pulmonary atresia and intact ventricular septum (PAIVS) after "one-and-a-half ventricle repair" and placement of a bidirectional Glenn shunt using four-dimensional (4D) flow magnetic resonance imaging. Quantification of flow and analysis of flow patterns revealed the hemodynamic "battle" between the right ventricle (RV) and the Glenn shunt. Moreover, with a novel approach we calculated during Glenn anastomosis the flow distribution from the superior vena cava (SVC) to the pulmonary arteries. Our results showed a highly asymmetric flow distribution, with most of the flow from the SVC toward the RV and not to the lungs. The evidence provided by 4D flow demonstrates poor efficiency of this system and suggests that both patients might benefit from adding an artificial pulmonary valve to avoid right heart failure.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Uribe S,Bächler P,Valverde I,Crelier GR,Beerbaum P,Tejos C,Irarrazaval Pdoi
10.1007/s00246-012-0288-6subject
Has Abstractpub_date
2013-02-01 00:00:00pages
447-51issue
2eissn
0172-0643issn
1432-1971journal_volume
34pub_type
杂志文章abstract::A 3 1/2-year-old female child presented with massive hemoptysis 5 months after a modified Blalock-Taussig (BT) shunt for double-outlet right ventricle with pulmonary stenosis. Computerized tomographic scan and angiography showed a false aneurysm of the subclavian artery at the insertion of the shunt. Successful surgic...
journal_title:Pediatric cardiology
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更新日期:2002-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0928-6
更新日期:2007-01-01 00:00:00
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journal_title:Pediatric cardiology
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更新日期:2002-07-01 00:00:00
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journal_title:Pediatric cardiology
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doi:10.1007/s00246-016-1466-8
更新日期:2016-12-01 00:00:00
abstract::Mammalian cardiomyocytes withdraw from the cell cycle soon after birth. This process is called terminal differentiation. The c-kit, a receptor tyrosine kinase, is expressed on cardiomyocytes immediately after birth but for only a few days. In mice with genetic c-kit dysfunction, adult cardiomyocytes are phenotypically...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0224-9
更新日期:2012-06-01 00:00:00
abstract::Current guidelines recommend that all neonates with Down syndrome (DS) be screened for congenital heart disease (CHD) with an echocardiogram. We sought to determine the effectiveness of a more accessible and less expensive screening strategy consisting of physical examination, electrocardiogram (ECG), and chest X-ray....
journal_title:Pediatric cardiology
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更新日期:2016-10-01 00:00:00
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journal_title:Pediatric cardiology
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更新日期:2018-12-01 00:00:00
abstract::Chylous effusions frequently occur after cardiac surgery due to severe damage to the lymphatic system, thus indicating that the insertion of a chest tube may be necessary. Factor XIII (FXIII) is discussed as being essential for wound healing. The aim of this retrospective study was to evaluate whether the application ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0993-5
更新日期:2006-01-01 00:00:00
abstract::Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0280-1
更新日期:2013-01-01 00:00:00
abstract::We report the placement of an implantable cardiac defibrillator as preventative treatment in a 2-year-old with long QT syndrome. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2004-07-01 00:00:00
abstract::The most common modes of medical education for congenital heart disease (CHD) rely heavily on 2-dimensional imaging. Three-dimensional (3D) printing technology allows for the creation of physical cardiac models that can be used for teaching trainees. 3D printed cardiac models were created for the following lesions: pu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02146-8
更新日期:2019-08-01 00:00:00
abstract::As a transcription factor mainly expressed in cardiovascular system, T-box 20 (TBX20) plays an important role in embryonic cardiovascular system development and adult heart function. Previous studies have identified associations of two SNPs in the T-box DNA-binding domain of TBX20 with congenital heart disease (CHD) i...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2015-04-01 00:00:00
abstract::Long-term prostaglandin use is commonly associated with side effects such as cortical proliferation of the bones, hypertrophic pyloric stenosis, and soft tissue swelling of the extremities. We report a neonate with critical coarctation of the aorta, who developed second and third degree atrioventricular blocks associa...
journal_title:Pediatric cardiology
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更新日期:2017-10-01 00:00:00
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journal_title:Pediatric cardiology
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doi:10.1007/s00246-009-9460-z
更新日期:2009-10-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0827-9
更新日期:2014-04-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2013-10-01 00:00:00
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journal_title:Pediatric cardiology
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更新日期:2017-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2013-01-01 00:00:00
abstract::For neonates with right atrial isomerism (RAI), functional single ventricle (f-SV), and obstructive total anomalous pulmonary venous connection (TAPVC), primary TAPVC repair (TAPVCR) has a poor outcome. At our hospital, the survival rate at 1 year of such neonates undergoing primary TAPVCR between 1999 and 2010 (TAPVC...
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pub_type: 杂志文章,收录出版
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journal_title:Pediatric cardiology
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更新日期:2007-05-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
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更新日期:2007-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02310333
更新日期:1995-01-01 00:00:00
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更新日期:2019-06-01 00:00:00
abstract::Nesiritide is a synthetic form of B-type natriuretic peptide. It is approved for the treatment of acute exacerbations of congestive heart failure in hospitalized adult patients. It is currently under investigation for use in other settings and other patient populations. This article describes administration of nesirit...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0064-6
更新日期:2007-05-01 00:00:00