Ventricular inversion and tricuspid atresia (VITA complex): long survival without surgical treatment.

Abstract:

:Five patients with ventricular inversion, corrected transposition of the great arteries, and atresia of the left-sided atrioventricular (tricuspid) valve have been observed. Three patients died in infancy, two had large interatrial communications, one with an early stage of arterial-type hypertensive pulmonary vascular disease, and the third patient had a very small interatrial communication and severe cyanosis. The other two patients survived into adulthood; both had small interatrial communications, and one had severe venous-type hypertensive pulmonary vascular disease. The longer survival of the two patients is attributed to a balance between resistance and blood flow in the pulmonary circulation influenced by the size of the interatrial communication.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Tazelaar HD,Moore GW,Hutchins GM

doi

10.1007/BF02310996

subject

Has Abstract

pub_date

1986-01-01 00:00:00

pages

187-91

issue

4

eissn

0172-0643

issn

1432-1971

journal_volume

6

pub_type

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