Abstract:
:Five patients with ventricular inversion, corrected transposition of the great arteries, and atresia of the left-sided atrioventricular (tricuspid) valve have been observed. Three patients died in infancy, two had large interatrial communications, one with an early stage of arterial-type hypertensive pulmonary vascular disease, and the third patient had a very small interatrial communication and severe cyanosis. The other two patients survived into adulthood; both had small interatrial communications, and one had severe venous-type hypertensive pulmonary vascular disease. The longer survival of the two patients is attributed to a balance between resistance and blood flow in the pulmonary circulation influenced by the size of the interatrial communication.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Tazelaar HD,Moore GW,Hutchins GMdoi
10.1007/BF02310996subject
Has Abstractpub_date
1986-01-01 00:00:00pages
187-91issue
4eissn
0172-0643issn
1432-1971journal_volume
6pub_type
杂志文章abstract::Assessment of ventricular dysfunction and asynchrony is very important in predicting the outcome for children with a single right ventricle. However, the assessment is inaccurate and subjective because of the unusual ventricular shape. This study aimed to evaluate the feasibility and clinical value of velocity vector ...
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journal_title:Pediatric cardiology
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