Hypoplastic left heart syndrome with male pseudohermaphroditism and bicornuate uterus bicollis.

Abstract:

:A 39-week-old phenotypically female infant was born with hypoplastic left heart syndrome and expired on the third day of life. An autopsy revealed the patient to also have male pseudohermaphroditism and uterus bicornis bicollis. The association of hypoplastic left heart syndrome and male pseudohermaphroditism has been reported in only two previous patients.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Calaluce RD,Huang TH,Quesenberry JT,Evans ML,Luger AM,O'Connor TA

doi

10.1007/BF00795715

subject

Has Abstract

pub_date

1995-09-01 00:00:00

pages

239-41

issue

5

eissn

0172-0643

issn

1432-1971

journal_volume

16

pub_type

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