Abstract:
:Interruption of the aortic arch and hypoplastic left heart syndrome in the same patient is exceptional. In the combined collections of the Registry of Cardiovascular Disease (St. Paul, Minnesota, U.S.A.) and the Registry of Congenital Heart Defects of the Rijksuniversiteit Gent (Gent, Belgium) three specimens were found with this unusual combination. These cases are herein described and compared with four similar cases previously reported in the literature.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Devloo-Blancquaert A,Titus JL,Edwards JE,Vallaeys JH,De Gezelle HR,Coppens Mdoi
10.1007/BF00798068subject
Has Abstractpub_date
1995-11-01 00:00:00pages
304-8issue
6eissn
0172-0643issn
1432-1971journal_volume
16pub_type
杂志文章,评审abstract::The treatment of recurrent supraventricular tachycardia in a 3-week-old infant is described. Multiple doses of adenosine were used successfully to convert the dysrhythmia, without adverse effects or apparent tachyphylaxis. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900222
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abstract::Congenital left ventricular diverticulum is a rare cardiac malformation. The incidence of left ventricular diverticulum is reported to be 0.05% of all congenital heart malformations. This case series comprised three infants with the diagnosis of congenital left ventricular diverticulum determined by echocardiography. ...
journal_title:Pediatric cardiology
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abstract::Midodrine hydrochloride is a potent peripherally-acting alpha1 agonist that is well absorbed and rapidly metabolized to its active metabolite. It has been used for the treatment of refractory syncope but has the important side effect of supine hypertension. A 10-year-old boy with severe symptomatic orthostatic hypoten...
journal_title:Pediatric cardiology
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abstract::Adrenomedullin (ADM) is a vasoactive peptide with potent dilatory effects. We studied whether perioperative myocardial injury could be altered by the presence of ADM. Blood samples from 19 children with congenital heart disease undergoing surgical repair were collected at six time points: preoperative, on cardiopulmon...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010046
更新日期:2000-05-01 00:00:00
abstract::Patients with anomalies of the heart frequently suffer from arrhythmias that either are associated with a congenital heart defect or result from the course of the disease. For most of the bradyarrhythmias, appropriate timing of the initiation of treatment is more challenging than its eventual execution. In the case of...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s002460010134
更新日期:2000-11-01 00:00:00
abstract:OBJECTIVE:Heterotaxy syndrome is associated with complex cardiac malformations and cardiac conduction system abnormalities. Those with right atrial isomerism (RAI) have dual sinus nodes and dual atrioventricular nodes predisposing them to supraventricular tachycardia (SVT). Those with left atrial isomerism (LAI) lack a...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02087-2
更新日期:2019-06-01 00:00:00
abstract::Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluati...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9134-7
更新日期:2008-09-01 00:00:00
abstract::Despite improved outcomes following modifications to the Fontan technique, significant morbidity and mortality persist. We sought to determine if abnormal pre-Fontan catheterization hemodynamic data will predict postoperative prolonged hospital stay (PHLOS) and adverse post-discharge outcomes. This is a retrospective ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02430-y
更新日期:2020-12-01 00:00:00
abstract::Various agents have been suggested as causal or associated factors in the pathogenesis of Kawasaki disease (KD); however, the underlying factors of KD remain unknown. Plasma exchange is one of the most effective treatments for the acute phase of KD. This indicates that plasma may contain factors associated with the pa...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0329-1
更新日期:2012-12-01 00:00:00
abstract::For premature infants with congenital heart disease (CHD), it may be unclear when the burdens of treatment outweigh potential benefits. Parents may thus have to choose between comfort care at birth and medical stabilization until surgical repair is feasible. Better defined outcome data, including risk factors for mort...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1374-y
更新日期:2016-06-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0716-2
更新日期:2013-01-01 00:00:00
abstract::The aim of this study is to evaluate the relationship between maternal single nucleotide polymorphisms (SNPs) of methylenetetrahydrofolate reductase (MTHFR) gene with plasma homocysteine (HCY) level and offspring congenital heart diseases (CHDs). 338 mothers with offspring CHDs as case group and 306 mothers of normal ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02449-1
更新日期:2020-11-21 00:00:00
abstract::Little data are published about right ventricular (RV) growth and function in infants and neonates after balloon pulmonary valvuloplasty (BPV) for critical valvular pulmonary stenosis (PS). We aimed to assess the RV growth and function during 1 year after BPV for critical valvular PS in neonates and infants. A total o...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02314-1
更新日期:2020-04-01 00:00:00
abstract::The prevalence of obesity in long-term survivors with complex congenital heart disease may be increasing, and little is known about the timing and onset of weight gain and growth patterns in these high-risk patients. Prevalence rates of overweight/obesity and longitudinal changes in body mass index (BMI) with age were...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1265-7
更新日期:2016-01-01 00:00:00
abstract::M-mode and 2-dimensional (2D) echocardiographic imaging are routinely used to quantify left-ventricular (LV) size and function in pediatric patients with dilated cardiomyopathy (DCM). The reproducibility of and correlation between these techniques are unknown. This analysis sought to compare interreader, intrareader, ...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章,多中心研究
doi:10.1007/s00246-013-0835-9
更新日期:2014-04-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0226-8
更新日期:2004-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0224-9
更新日期:2012-06-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-017-1610-0
更新日期:2017-06-01 00:00:00
abstract::Arrhythmias in pregnancy are becoming more common given more available and effective medical, ablation and device treatment options. Several changes associated with pregnancy, increased blood volume, cardiac output, and heart rate secondary to an increased sympathetic state, facilitate more frequent occurrences of arr...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-015-1232-3
更新日期:2015-10-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
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journal_title:Pediatric cardiology
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journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2000-05-01 00:00:00
abstract::Congenital diverticulum of the left ventricle, a rare malformation, is usually associated with midline thoracoabdominal defect. We describe a case with congenital left ventricular diverticulum presenting as an isolated lesion. The lesion was suspected on two-dimensional echocardiography and was confirmed by cardiac ca...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02524804
更新日期:1996-07-01 00:00:00
abstract::We report the placement of an implantable cardiac defibrillator as preventative treatment in a 2-year-old with long QT syndrome. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-5230-5
更新日期:2004-07-01 00:00:00
abstract::Apelin is an endogenous inotrope that decreased in heart failure (HF). We aimed to evaluate the prognostic value of its level in children with HF due to congenital heart disease (CHD). Sixty children with HF due to CHD were included as a patient group. Sixty healthy children matched for age, sex, and weight served as ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1879-7
更新日期:2018-08-01 00:00:00
abstract::Chylous effusions frequently occur after cardiac surgery due to severe damage to the lymphatic system, thus indicating that the insertion of a chest tube may be necessary. Factor XIII (FXIII) is discussed as being essential for wound healing. The aim of this retrospective study was to evaluate whether the application ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0993-5
更新日期:2006-01-01 00:00:00
abstract::A cohort of 52 French unrelated infant cases who died unexpectedly before they reached 12 months of age was blindly investigated to better quantify the contribution of long-QT syndrome (LQTS) genetic variants in French cases of sudden infant death syndrome (SIDS). After a standardized autopsy protocol, a blinded molec...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9417-2
更新日期:2009-05-01 00:00:00
abstract::The objective of this study is to identify predictors of prolonged hospital length of stay (LOS) for single ventricle patients following stage 2 palliation (S2P), excluding patients who underwent a hybrid procedure. We explore the impact of demographic features, stage 1 palliation (S1P), interstage I (IS1) management,...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1208-3
更新日期:2015-12-01 00:00:00
abstract::The neonatal Marfan syndrome is an autosomal dominantly inherited disease with an extremely poor prognosis. This report gives a clinical and echocardiographic description of an infant with a mutation in exon 29 of the fibrillin-1 gene (FBN1), a region in which this severe form of Marfan syndrome seems to cluster. The ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900493
更新日期:1999-09-01 00:00:00