Acute mitral regurgitation due to chordal rupture in a patient with neonatal Marfan syndrome caused by a deletion in exon 29 of the FBN1 gene.

abstract：:A rare form of endocardial cushion defect is an atrioventricular (AV) canal-type ventricular septal defect with cleft mitral valve in the absence of a primum atrial septal defect. In two infants with Down's syndrome, preoperative delineation of this entity was accomplished. M-mode echocardiographic features included p...

journal_title：Pediatric cardiology

authors： LaCorte MA,Cooper RS,Kauffman SL,Schiller MS,Golinko RJ,Griepp RB

更新日期：1982-01-01 00:00:00

abstract：:We report a case of a 12-year-old boy with severe congenital aortic stenosis in whom magnetic resonance imaging (MRI) with delayed contrast enhancement demonstrated extensive subendocardial hyperenhancement within the left ventricle. The hyperenhancement was confirmed to be subendocardial infarct and fibrosis by histo...

journal_title：Pediatric cardiology

authors： La Salvia EA,Gilkeson RC,Dahms BB,Siwik E

更新日期：2006-05-01 00:00:00

abstract：:The etiology and pathogenesis of Kawasaki disease (KD) is largely unknown. Certain demographic factors and laboratory findings are predictive of the development of coronary artery (CA) aneurysms. The objectives of this study were to determine the epidemiology of KD patients in an urban hospital and determine risk fact...

journal_title：Pediatric cardiology

authors： Porcalla AR,Sable CA,Patel KM,Martin GR,Singh N

更新日期：2005-11-01 00:00:00

abstract：:Two cases of arrhythmogenic right ventricular dysplasia (ARVD) in siblings are reported. In the boy, 14 years old, the clinical history, ECG, echocardiography, and histopathological findings were consistent with ARVD. Premature ventricular contractions of left bundle branch block (LBBB) pattern were recorded but no ve...

journal_title：Pediatric cardiology

authors： Sabel KG,Blomström-Lundqvist C,Olsson SB,Eneström S

更新日期：1990-04-01 00:00:00

abstract：:This report describes an unusual case with tortuosity of the great vessels in a neonate who presented at birth with cyanosis. The diagnosis was made with magnetic resonance imaging (MRI), then confirmed by genetic analysis. ...

journal_title：Pediatric cardiology

authors： Pilati M,Luciani GB,Prioli MA,Puppini G

更新日期：2009-11-01 00:00:00

abstract：:Fetal echocardiography has impacted the fetus with congenital heart disease in many important ways. Advances in fetal echocardiography have allowed for more accurate and earlier detection of cardiac abnormalities. In turn, the prenatal diagnosis of cardiac abnormalities has improved the care and outcome of selected fe...

journal_title：Pediatric cardiology

authors： Kovalchin JP,Silverman NH

更新日期：2004-05-01 00:00:00

abstract：:We analyzed early and late results of surgical treatment of 100 consecutive children with Down's syndrome (DS) and congenital heart defect (CHD) who were operated on between 1990 and 1997. Fifty had common atrioventricular canal (CAVC), 24 ventricular septal defect, 8 the ostium primum atrial septal defect, 8 tetralog...

journal_title：Pediatric cardiology

authors： Malec E,Mroczek T,Pajak J,Januszewska K,Zdebska E

更新日期：1999-09-01 00:00:00

abstract：:The primary objective was to create a clinically relevant model of right ventricular hypertension and to study right ventricular myocardial pathophysiology in growing organism. The secondary objective was to analyse the effect of oral enoximone (phosphodiesterase inhibitor) therapy on right ventricular haemodynamic pa...

journal_title：Pediatric cardiology

authors： Kobr J,Slavik Z,Uemura H,Saeed I,Furck A,Pizingerová K,Fremuth J,Tonar Z

更新日期：2016-12-01 00:00:00

abstract：:In case of progressive cyanosis after modified Fontan procedure, intrahepatic shunting should be considered. Ligation of the hepatic vein is safe and effective in managing this condition, and it is important to ensure that the pressure difference between superior vena cava and the portal vein system remains minimal af...

journal_title：Pediatric cardiology

authors： Hishitani T,Ogawa K,Hoshino K,Nakamura Y

更新日期：1999-11-01 00:00:00

abstract：:The epinephrine test has been shown to be a powerful tool to predict the genotype of congenital long QT syndrome (LQTS). The aim of this study was to evaluate its role in the diagnosis and management of LQTS in children. The test (using the Shimizu protocol) was conducted in patients with some evidence of LQTS but in ...

journal_title：Pediatric cardiology

authors： Clur SA,Chockalingam P,Filippini LH,Widyanti AP,Van Cruijsen M,Blom NA,Alders M,Hofman N,Wilde AA

更新日期：2010-05-01 00:00:00

abstract：:Postoperative coarctation (CoA) patients are often found to have signs of persistent myocardial dysfunction. M-mode echocardiography was performed to study left ventricular (LV) size, mass, and systolic function and Doppler ultrasonography to study LV filling and flow velocity in the LV outflow tract and aorta in 28 "...

journal_title：Pediatric cardiology

authors： Sigurdardóttir LY,Helgason H

更新日期：1997-03-01 00:00:00

abstract：:Accessory atrioventricular pathways (AP) are the most common substrate for paroxysmal supraventricular tachycardia in infants and small children. Up-to-date data on AP ablation in infants and small children are limited. The aim of the present study was to gain additional insight into radiofrequency (RF) catheter ablat...

journal_title：Pediatric cardiology

authors： Backhoff D,Klehs S,Müller MJ,Schneider H,Kriebel T,Paul T,Krause U

更新日期：2016-06-01 00:00:00

abstract：:Percutaneous balloon aortic valvuloplasty was attempted in an eight-month-old infant with severe aortic valve stenosis. The procedure resulted in a fall in the resting transvalvular systolic pressure gradient from 106 mmHg to 40 mmHg and no aortic regurgitation. Clinical and Doppler echocardiography findings suggest p...

journal_title：Pediatric cardiology

authors： Sánchez GR,Mehta AV,Ewing LL,Brickley SE,Anderson TM,Black IF

更新日期：1985-01-01 00:00:00

abstract：:Congenital aneurysms of the thoracic venous system are rare. In particular, innominate venous aneurysms are extremely rare. We describe a 16-year-old girl whose chest x-ray suggested a mediastinal tumor. Three-dimensional contrast-enhancement magnetic resonance venography showed a giant sacciform aneurysm of the left ...

journal_title：Pediatric cardiology

authors： Tsuji A,Katada Y,Tanimoto M,Fujita I

更新日期：2004-07-01 00:00:00

abstract：:Ebstein anomaly of mitral valve (MV) is an extremely rare congenital heart disease. In the current report, we present a case of Ebstein of MV that was diagnosed prenatally. Fetal echocardiogram showed that the posterior leaflet of MV was tethered to the lateral wall of left ventricle (LV) with downward displacement in...

journal_title：Pediatric cardiology

authors： Aly S,Bokowski J,Diab K,Muller BA

更新日期：2018-08-01 00:00:00

abstract：:Rehospitalization following pediatric heart transplantation is common. However, existing data remain somewhat limited. Using a novel linkage between administrative and clinical databases, pediatric heart transplant (HT) recipients from 29 centers who survived to discharge were retrospectively reviewed to determine the...

journal_title：Pediatric cardiology

authors： Lambert AN,Weiner JG,Hall M,Thurm C,Dodd DA,Bearl DW,Soslow JH,Feingold B,Smith AH,Godown J

更新日期：2020-03-01 00:00:00

abstract：:Cardiopulmonary bypass (CPB) reduces coagulation factor levels through hemodilution and consumption. Differences in CPB-induced alterations of factor XIII (FXIII) levels in children with cyanotic and acyanotic congenital heart defects (CHDs) are not well characterized. FXIII activity (determined by Berichrom assay), p...

journal_title：Pediatric cardiology

authors： Bockeria LA,Samsonova NN,Yurlov IA,Klimovich LG,Kozar EF,Olsen EH,Zaets SB

更新日期：2014-10-01 00:00:00

abstract：:Three patients (ages 3, 5, and 8 years) with various forms of functionally univentricular heart lesions received a total cavopulmonary connection with an extracardiac conduit as a final reconstructive procedure. Failure of the Fontan circulation occurred immediately after surgery because of spontaneous closure of surg...

journal_title：Pediatric cardiology

authors： Michel-Behnke I,Luedemann M,Bauer J,Hagel KJ,Akintuerk H,Schranz D

更新日期：2005-01-01 00:00:00

abstract：:Requiring bilateral superior cavopulmonary anastomosis (bSCPA) instead of unilateral superior cavopulmonary anastomosis (uSCPA) could influence surgical timing and outcomes. We compared surgical timing and outcomes for patients who underwent uSCPA to those who underwent bSCPA through use of the Pediatric Heart Network...

journal_title：Pediatric cardiology

authors： Shuler JM,Statile C,Heydarian H,Lehenbauer DG,Hill GD

更新日期：2021-01-08 00:00:00

abstract：:Coronary artery anatomy represents a challenging and, often, determining predictor of outcome in an arterial switch operation (ASO). Impact of specific coronary artery variants, such as single, intramural and inverted, on time-related events following ASO, is, yet, to be determined. We sought to compare early and late...

journal_title：Pediatric cardiology

authors： Al Anani S,Fughhi I,Taqatqa A,Elzein C,Ilbawi MN,Polimenakos AC

更新日期：2017-03-01 00:00:00

abstract：:Acute myopericarditis is a major cause of acquired heart disease worldwide in pediatric patients. Various viruses have been reported as the etiology, of which varicella zoster virus was first reported in 1953. However, since nationwide administration of the varicella vaccine, reports of varicella-associated myopericar...

journal_title：Pediatric cardiology

authors： Kao KL,Yeh SJ,Chen CC

更新日期：2010-07-01 00:00:00

abstract：:We studied the safety and efficacy of closing patent ductus arteriosus by Nit-Occlud coils via retrograde approach. This is a retrospective study of 46 attempts to close ducts by this method in two hospitals in Egypt and Iran. Ductus arteriosus was crossed by left or right Judkins or endhole catheters. The coil was de...

journal_title：Pediatric cardiology

authors： Zanjani KS,Sobhy R,El-Kaffas R,El-Sisi A

更新日期：2017-04-01 00:00:00

abstract：:A reduced exercise capacity is a common finding in adult congenital heart disease and is associated with cardiovascular morbidity and mortality. However, data on exercise capacity in patients after repair of coarctation of the aorta (CoA) are scarce. Furthermore, a high rate of exercise-induced hypertension has been d...

journal_title：Pediatric cardiology

authors： Dijkema EJ,Sieswerda GT,Breur JMPJ,Haas F,Slieker MG,Takken T

更新日期：2019-10-01 00:00:00

abstract：:Magnetic resonance imaging (MRI) is a powerful tool which enables the visualization of anatomy and the assessment of many physiological aspects of organ function. MRI and magnetic resonance angiography and magnetic resonance spectroscopy will play critical roles in cardiac applications during the next millennium. Thus...

journal_title：Pediatric cardiology

authors： Mulkern RV,Chung T

更新日期：2000-01-01 00:00:00

abstract：:To reveal the association between DNMT1 polymorphisms and congenital heart disease (CHD) in child patients, a total of 224 CHD child patients as well as 199 healthy individuals were enrolled in the present study. The DNA was extracted from whole blood, and four SNPs including rs16999593, rs2228612, rs2288349 and rs104...

journal_title：Pediatric cardiology

authors： Wang F,Zhou S,Wang Y,Wang L,Zhou J,Wang H,Li C,Chang M

更新日期：2015-06-01 00:00:00

abstract：:Circulating progenitor cells have been extensively studied in the context of heart disease in adults. In these patients, they have been demonstrated to be markers of myocardial injury and recovery as well as potential therapeutic agents. However, studies in children are much more limited. Here we review current knowle...

journal_title：Pediatric cardiology

authors： Kort EJ,Croskey L,Scibienski T,Rajasekaran S,Jovinge S

更新日期：2016-02-01 00:00:00

abstract：:A newborn infant with familial Wolff-Parkinson-White (WPW) syndrome presented with a supraventricular tachycardia of 300 beats/min, refractory to digoxin and flecainide administration. Serial electropharmacologic tests were performed via the esophagus before and during oral therapy with verapamil at 40, 80, and 60 mg ...

journal_title：Pediatric cardiology

authors： Colloridi V,Boscioni M,Patruno N,Pulignano G,Critelli G

更新日期：1990-10-01 00:00:00

abstract：BACKGROUND:Cardiac magnetic resonance imaging (MRI) is an important diagnostic tool for congenital heart disease (CHD), as reflected by class 1 recommendations for the use of cardiac MRI by various consensus panels. However, little is known about the safety and clinical utility of cardiac MRI for these critically ill i...

journal_title：Pediatric cardiology

authors： Sarikouch S,Schaeffler R,Körperich H,Dongas A,Haas NA,Beerbaum P

更新日期：2009-02-01 00:00:00

abstract：:Very young mammals have an impressive cardiac regeneration capacity. In contrast, cardiac regeneration is very limited in adult humans. The hearts of young children have a higher regenerative capacity compared with adults, as, for example, seen after surgical correction of an anomalous left coronary artery arising fro...

journal_title：Pediatric cardiology

authors： Rupp S,Schranz D

更新日期：2015-04-01 00:00:00

abstract：:Controversy exists as to whether a hemodynamically significant left-to-right shunt due to a patent ductus arteriosus (PDA) affects ventricular contractility. Load-dependent indices such as ejection fraction and shortening fraction have traditionally been used to assess contractility, but the relationship between the r...

journal_title：Pediatric cardiology

authors： Barlow AJ,Ward C,Webber SA,Sinclair BG,Potts JE,Sandor GG

更新日期：2004-03-01 00:00:00