Abstract:
:This report describes an unusual case with tortuosity of the great vessels in a neonate who presented at birth with cyanosis. The diagnosis was made with magnetic resonance imaging (MRI), then confirmed by genetic analysis.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Pilati M,Luciani GB,Prioli MA,Puppini Gdoi
10.1007/s00246-009-9486-2subject
Has Abstractpub_date
2009-11-01 00:00:00pages
1146-9issue
8eissn
0172-0643issn
1432-1971journal_volume
30pub_type
杂志文章abstract::Twelve years after an apparently successful surgical correction of infradiaphragmatic (obstructed) total anomalous pulmonary venous drainage, a 12-year-old boy developed evidence of pulmonary artery hypertension secondary to pulmonary venous obstruction due to an apparent lack of growth at the anastomotic site. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02080561
更新日期:1988-01-01 00:00:00
abstract::Debilitating cardiomyocyte loss underlies the progression to heart failure. Although there have been significant advances in treatment, current therapies are intended to improve or preserve heart function rather than regenerate lost myocardium. A major hurdle in implementing a cell-based regenerative therapy is the in...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9409-2
更新日期:2009-07-01 00:00:00
abstract::We report the case of a fetus diagnosed at 24 weeks' gestation with complete heart block associated with maternal collagen vascular disease and Sjögren's antibody. Serial fetal echocardiograms noted increased echogenicity along the tricuspid and mitral valves without insufficiency. Postnatally, severe tricuspid insuff...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00800677
更新日期:1994-07-01 00:00:00
abstract::A 6-year-old girl was found to have a combination of accessory mitral valve tissue and subaortic membrane. The association caused left ventricular outflow tract obstruction leading to severe left ventricular dysfunction. Surgical relief of the obstruction resulted in immediate improvement of ventricular function. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-5023-7
更新日期:2002-01-01 00:00:00
abstract::We present a case of congenital pulmonary systemic collateral vein associated with truncus arteriosus. Pulmonary systemic collateral vein with nonobstructed left atrial egress is different from those with obstructed left atrial egress in that it is functionally redundant. Including this case, 8 patients among 33 repor...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-002-0439-2
更新日期:2004-01-01 00:00:00
abstract::We performed a Waterston's anastomosis on a patient with complicated tricuspid atresia when she was two months of age. At age 14 years she required left pneumonectomy for massive, idiopathic hemoptysis. Four months after the pneumonectomy we substituted a modified Fontan anastomosis for the Waterston anastomosis. Rest...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02238530
更新日期:1991-07-01 00:00:00
abstract::Quantification of left ventricular (LV) mass by echocardiography has not been validated against the gold standard of cardiac magnetic resonance imaging (CMR) in the pediatric population. The purpose of this study was to compare LV mass by two-dimensional and conventional M-mode echocardiography versus CMR in children....
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1991-8
更新日期:2019-02-01 00:00:00
abstract::From 1981 through June 1989, 59 children had surgery for a complete atrioventricular (AV) canal defect at Oregon Health Sciences University. We compared the morbidity, mortality, and hemodynamic status of 47 children with and 12 without Down's syndrome through review of operative, clinical, and cardiac catheterization...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00798209
更新日期:1992-04-01 00:00:00
abstract::This report describes a case involving the rare combination of persistent truncus arteriosus type A2, double aortic arch, and mitral stenosis. At the age of 26 days, the patient underwent division of the right-sided aortic arch with tracheal compression and bilateral pulmonary banding. Fontan completion was successful...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0572-5
更新日期:2013-01-01 00:00:00
abstract::Rehospitalization following pediatric heart transplantation is common. However, existing data remain somewhat limited. Using a novel linkage between administrative and clinical databases, pediatric heart transplant (HT) recipients from 29 centers who survived to discharge were retrospectively reviewed to determine the...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02326-x
更新日期:2020-03-01 00:00:00
abstract::Dextro-transposition of the great arteries (D-TGA) is one of the most common cyanotic heart lesions. The arterial switch operation (ASO) is the preferred surgical palliation for D-TGA. One of the primary concerns following the ASO is complications arising from the coronary artery transfer. There is a need for myocardi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1890-z
更新日期:2018-08-01 00:00:00
abstract::The HOXA1 gene plays a fundamental role in embryonic morphogenesis. Recent studies in humans and mice have indicated that HOXA1 plays a previously unrecognized role in cardiovascular system development. Congenital heart disease (CHD), particularly ventricular septal defect (VSD), might be a clinically isolated manifes...
journal_title:Pediatric cardiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s00246-012-0418-1
更新日期:2013-02-01 00:00:00
abstract::Children with congenital heart defects often demonstrate a reduced capacity for exercise, even after surgical intervention. Forty subjects, with various heart defects, completed a 5-year study to evaluate the impact of a postoperative training program on their physical exercise capacity. All of the patients were signi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02238841
更新日期:1990-07-01 00:00:00
abstract::The etiology and pathogenesis of Kawasaki disease (KD) is largely unknown. Certain demographic factors and laboratory findings are predictive of the development of coronary artery (CA) aneurysms. The objectives of this study were to determine the epidemiology of KD patients in an urban hospital and determine risk fact...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0916-5
更新日期:2005-11-01 00:00:00
abstract::The objective of this investigation was to compare how two modes of positive pressure ventilation affect cardiac output, airway pressures, oxygenation, and carbon dioxide removal in children with congenital heart disease in the immediate postoperative period. The investigation used a one group pretest-post-test study ...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章
doi:10.1007/s002460010210
更新日期:2001-05-01 00:00:00
abstract::Central venous pressure (CVP) measurement is a reliable method for evaluating intravascular volume status and cardiac function, but it is an invasive method that results in some complications such as arterial puncture, pneumothorax, and development of infection. The current study was performed to compare CVP measureme...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9067-1
更新日期:2008-03-01 00:00:00
abstract::Atherosclerotic cardiovascular disease (CVD), a leading cause of death globally, has origins in childhood. Major risk factors include family history of premature CVD, dyslipidemia, diabetes mellitus, and hypertension. Lipoprotein (a) [Lp(a)], an inherited lipoprotein, is associated with premature CVD, but its impact o...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1927-3
更新日期:2018-12-01 00:00:00
abstract::This study examined the age-related criteria of signal-averaged electrocardiographic (SA-ECG) parameters in children. SA-ECGs were obtained in 82 healthy volunteers in six groups depending on age (group 1: 1 day to < 1 month; group 2: 1 month to < 1 year; group 3: 1 to < 6 years; group 4: 6 to < 12 years; group 5: 12 ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00796320
更新日期:1994-05-01 00:00:00
abstract::Controversy exists as to whether a hemodynamically significant left-to-right shunt due to a patent ductus arteriosus (PDA) affects ventricular contractility. Load-dependent indices such as ejection fraction and shortening fraction have traditionally been used to assess contractility, but the relationship between the r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0452-0
更新日期:2004-03-01 00:00:00
abstract::To determine whether diastolic ventricular interdependence mechanisms would act in the presence of an open pericardial sac, as during cardiac surgery, moderate acute right ventricle afterload increases were applied to eight dogs with the chest and pericardium open while left ventricular filling dynamics were being ass...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02505087
更新日期:1996-03-01 00:00:00
abstract::Little has been published about specific problems that may occur during long-distance transports of newborn cardiac patients. During a 4-year period after centralization of pediatric heart surgery in Sweden, 286 transports were prospectively investigated. A majority (77.3%) of the transports were carried out by nonspe...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010254
更新日期:2001-09-01 00:00:00
abstract::We undertook a study to identify the hemodynamic significance of a Doppler-derived gradient across a stenotic pulmonary valve. Furthermore, we attempted to define the optimal plane for velocity data acquisition. A total of 17 children with valvar pulmonary stenosis were evaluated using Doppler echocardiography. Flow-v...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02081678
更新日期:1989-07-01 00:00:00
abstract::To reveal the association between DNMT1 polymorphisms and congenital heart disease (CHD) in child patients, a total of 224 CHD child patients as well as 199 healthy individuals were enrolled in the present study. The DNA was extracted from whole blood, and four SNPs including rs16999593, rs2228612, rs2288349 and rs104...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1093-9
更新日期:2015-06-01 00:00:00
abstract::There is often a diagnostic dilemma in pediatric patients presenting with depressed ventricular function, as myocarditis and dilated cardiomyopathy (DCM) of other etiologies can appear very similar. Accurate identification is critical to guide treatment and to provide families with the most accurate expectation of lon...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1867-y
更新日期:2018-08-01 00:00:00
abstract::Interventional occluder implantation has become the preferred mode of treatment in children with clinically significant atrial septal defect (ASD). The continuous increase in the number of patients treated calls for long-term data on device integrity and biocompatibility. We report a child who underwent successful int...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-010-9757-y
更新日期:2010-10-01 00:00:00
abstract::Adult studies suggest a better functional outcome after aortic valve replacement with a pulmonary autograft compared with mechanical or homograft valves. Little is known about functional results after Ross surgery in growing children. This study reports formal exercise stress echocardiographic data from 26 pediatric R...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0218-7
更新日期:2012-06-01 00:00:00
abstract::Congenital diverticulum of the left ventricle, a rare malformation, is usually associated with midline thoracoabdominal defect. We describe a case with congenital left ventricular diverticulum presenting as an isolated lesion. The lesion was suspected on two-dimensional echocardiography and was confirmed by cardiac ca...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02524804
更新日期:1996-07-01 00:00:00
abstract::Radiation exposure from pediatric cardiac catheterization may be substantial, although published estimates vary. We sought to report patient radiation dose across a range of diagnostic and interventional cases in a modern, high-volume pediatric catheterization laboratory. We retrospectively reviewed diagnostic and int...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0869-7
更新日期:2014-06-01 00:00:00
abstract::Ischemic myocardial damage was identified as a complicating feature in the clinical course of 12 newborn infants who died in congestive failure with cerebral arteriovenous malformation. Electrocardiograms of 11 patients showed signs of chamber hypertrophy and T wave and ST segment features of varying degree compatible...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02281003
更新日期:1983-01-01 00:00:00
abstract::Ultrasound Doppler was used to establish time of ductal closure, normal values for blood flow velocity in the pulmonary artery (PA), and time interval between pulmonary valve closure (Pc) and tricuspid valve opening (To) in 37 healthy neonates. Ductal closure had occurred in 23% of the children within 12 h after deliv...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:
更新日期:1986-01-01 00:00:00