Prenatally Diagnosed Ventricular Inversion, Restrictive Ventricular Septal Defect, Pulmonary Stenosis, Hypertensive Left Ventricle and Double Outlet Right Ventricle: Case Report and Literature Review.

abstract：:Barth syndrome (BTHS) is an X-linked disorder characterised by cardiomyopathy, neutropenia, skeletal myopathy and growth delay. This study describes the UK national clinical experience and outcome of cardiomyopathy in BTHS. The clinical course and echocardiographic changes of all patients with BTHS in the UK were revi...

journal_title：Pediatric cardiology

authors： Kang SL,Forsey J,Dudley D,Steward CG,Tsai-Goodman B

更新日期：2016-01-01 00:00:00

abstract：:Sedation/anesthesia is critical to cardiac catheterization in the pediatric/congenital heart patient. We sought to identify current sedation/anesthesia practices, the serious adverse event rate related to airway, sedation, or anesthesia, and the rate of intra-procedural conversion from procedural sedation to the use o...

journal_title：Pediatric cardiology

authors： Lin CH,Desai S,Nicolas R,Gauvreau K,Foerster S,Sharma A,Armsby L,Marshall AC,Odegard K,DiNardo J,Vincent J,El-Said H,Spaeth J,Goldstein B,Holzer R,Kreutzer J,Balzer D,Bergersen L

更新日期：2015-10-01 00:00:00

abstract：:Respiratory viral infections in infants undergoing congenital heart surgery lead to prolonged intubation time, hospital (HLOS) and cardiac intensive care unit length of stay (CICU LOS). The objective of this study was to evaluate the prevalence of respiratory viruses using molecular testing in otherwise healthy infant...

journal_title：Pediatric cardiology

authors： Delgado-Corcoran C,Blaschke AJ,Ou Z,Presson AP,Burch PT,Pribble CG,Menon SC

更新日期：2019-02-01 00:00:00

abstract：:Angiotensin-converting enzyme inhibitors (ACEi) are commonly used for pediatric cardiology patients. However, studies examining their safety for neonates with cardiac disease are scarce. The current study aimed to test the hypothesis that ACEi-mediated nephrotoxicity occurs in neonates and may be underappreciated in t...

journal_title：Pediatric cardiology

authors： Lindle KA,Dinh K,Moffett BS,Kyle WB,Montgomery NM,Denfield SD,Knudson JD

更新日期：2014-03-01 00:00:00

abstract：:This report describes the case of two pediatric patients who demonstrated echocardiographic evidence of pulmonary hypertension (PH) during the acute phase of Kawasaki disease. The etiology of PH development in this setting is currently unknown, but the authors hypothesize that pulmonary vasculitis may play a significa...

journal_title：Pediatric cardiology

authors： Nicholson GT,Samai C,Kanaan U

更新日期：2013-01-01 00:00:00

abstract：:Recurrent congestive heart failure (CHF) attributable to myocarditis is a seldom-discussed entity in the scientific literature. This report describes the case of an 8-year-old girl who had three clinically identical episodes of CHF, beginning at the age of 5 years, with each episode preceded by a viral prodrome. The c...

journal_title：Pediatric cardiology

authors： Lee AF,Chiasson DA,Smythe JF,Sanatani S

更新日期：2012-01-01 00:00:00

abstract：:Dextro-transposition of the great arteries (D-TGA) is one of the most common cyanotic heart lesions. The arterial switch operation (ASO) is the preferred surgical palliation for D-TGA. One of the primary concerns following the ASO is complications arising from the coronary artery transfer. There is a need for myocardi...

journal_title：Pediatric cardiology

authors： Noel CV,Krishnamurthy R,Masand P,Moffett B,Schlingmann T,Cheong BY,Krishnamurthy R

更新日期：2018-08-01 00:00:00

abstract：:Apelin is an endogenous inotrope that decreased in heart failure (HF). We aimed to evaluate the prognostic value of its level in children with HF due to congenital heart disease (CHD). Sixty children with HF due to CHD were included as a patient group. Sixty healthy children matched for age, sex, and weight served as ...

journal_title：Pediatric cardiology

authors： El Amrousy D,El-Mahdy H

更新日期：2018-08-01 00:00:00

abstract：:It is documented that exercise can increase serum cardiac troponins in adults and adolescents; however, there is a lack of related studies concerning the release of cardiac troponins in children. This study investigated the influence of table tennis training on cardiac biomarkers in children. Twenty-eight male childre...

journal_title：Pediatric cardiology

authors： Ma G,Liu Y,Liu K

更新日期：2014-04-01 00:00:00

abstract：:The original version of the article unfortunately contained an alignment error in Table 1. The correct version of Table 1 is given below. ...

journal_title：Pediatric cardiology

authors： Şişli E,Tuncer ON,Şenkaya S,Doğan E,Şahin H,Ayık MF,Atay Y

更新日期：2019-01-01 00:00:00

abstract：:Congenital heart defects (CHDs) are the most prevalent of all birth defects and the leading cause of death in the first year of life. The molecular causes of most CHDs remain largely unknown. The LIM homeodomain transcriptor factor ISL1 is a marker for undifferentiated cardiac progenitor cells that give rise to both t...

journal_title：Pediatric cardiology

authors： Cresci M,Vecoli C,Foffa I,Pulignani S,Ait-Ali L,Andreassi MG

更新日期：2013-04-01 00:00:00

abstract：:Congenital heart defects (CHD) are the third leading cause of death in children <1 year of age in Mexico where there is a high prevalence of the 677C → T polymorphism of the MTHFR gene. This is important because the homozygous 677T/T MTHFR gene and deficiency of folic acid (FA) intake have been associated with CHD. Ou...

journal_title：Pediatric cardiology

authors： Balderrábano-Saucedo NA,Sánchez-Urbina R,Sierra-Ramírez JA,García-Hernández N,Sánchez-Boiso A,Klunder-Klunder M,Arenas-Aranda D,Bravo-Hernández G,Noriega-Zapata P,Vizcaíno-Alarcón A

更新日期：2013-01-01 00:00:00

abstract：:As a transcription factor mainly expressed in cardiovascular system, T-box 20 (TBX20) plays an important role in embryonic cardiovascular system development and adult heart function. Previous studies have identified associations of two SNPs in the T-box DNA-binding domain of TBX20 with congenital heart disease (CHD) i...

journal_title：Pediatric cardiology

authors： Chen J,Sun F,Fu J,Zhang H

更新日期：2015-04-01 00:00:00

abstract：:It is unclear if neonatal tetralogy of Fallot repair offers better outcomes compared to repair later in infancy. We therefore conducted a meta-analysis comparing outcomes of neonatal and non-neonatal repair. Manuscripts were identified and reviewed for quality and bias with favorably scored manuscripts being included ...

journal_title：Pediatric cardiology

authors： Loomba RS,Buelow MW,Woods RK

更新日期：2017-06-01 00:00:00

abstract：:The most common modes of medical education for congenital heart disease (CHD) rely heavily on 2-dimensional imaging. Three-dimensional (3D) printing technology allows for the creation of physical cardiac models that can be used for teaching trainees. 3D printed cardiac models were created for the following lesions: pu...

journal_title：Pediatric cardiology

authors： Smerling J,Marboe CC,Lefkowitch JH,Pavlicova M,Bacha E,Einstein AJ,Naka Y,Glickstein J,Farooqi KM

更新日期：2019-08-01 00:00:00

abstract：:Avoidance of red blood cell (RBC) transfusions in patients awaiting heart transplantation (HTx) has been suggested to minimize the risk of allosensitization. Although recent studies have suggested that an immature immune system in younger HTx recipients may reduce risks associated with RBC transfusion, the role of age...

journal_title：Pediatric cardiology

authors： McKee C,Tumin D,Alevriadou BR,Nicol KK,Yates AR,Hayes D Jr,Tobias JD

更新日期：2018-04-01 00:00:00

abstract：:Vasculopathy has been identified in young individuals with Turner syndrome (TS). No studies in young individuals with TS have investigated whether this vasculopathy progresses over time. The objective of this study is to describe the changes in vasculopathy over time in a cohort of young individuals with TS. Repeat ul...

journal_title：Pediatric cardiology

authors： Blunden CE,Urbina EM,Lawson SA,Gutmark-Little I,Shah AS,Khoury PR,Backeljauw PF

更新日期：2020-11-26 00:00:00

abstract：:This report describes a case involving the rare combination of persistent truncus arteriosus type A2, double aortic arch, and mitral stenosis. At the age of 26 days, the patient underwent division of the right-sided aortic arch with tracheal compression and bilateral pulmonary banding. Fontan completion was successful...

journal_title：Pediatric cardiology

authors： Imai K,Tsukuda K,Sakazaki H,Fujiwara K

更新日期：2013-01-01 00:00:00

abstract：:Noonan syndrome is an autosomal dominant disease that manifests a wide variety of clinical characteristics. The syndrome is also associated with some cardiac defects. Half of all Noonan syndrome cases are caused by mutations in the PTPN11 gene, but only limited data are available regarding aortic involvement in these ...

journal_title：Pediatric cardiology

authors： Jefferies JL,Belmont JW,Pignatelli R,Towbin JA,Craigen WJ

更新日期：2010-01-01 00:00:00

abstract：:Rheumatic heart disease (RHD) is an inflammatory disease that develops following streptococcal infections. IL10 helps to balance immune responses to pathogens. IL10 polymorphisms have been associated with RHD, although results remain inconclusive. Our aim was to investigate the association between IL10 polymorphisms a...

journal_title：Pediatric cardiology

authors： Abdallah AM,Alnuzha A,Al-Mazroea AH,Eldardear AE,AlSamman AY,Almohammadi Y,Al-Harbi KM

更新日期：2016-01-01 00:00:00

abstract：:A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy ...

journal_title：Pediatric cardiology

authors： Singla M,Al-Radi O,Mertens L

更新日期：2013-01-01 00:00:00

abstract：:Subtotal cor triatriatum sinister (partially divided left atrium) is characterized by a membrane dividing the left atrium into two portions: a dorsal accessory proximal chamber that receives part of the pulmonary venous return and a small restrictive defect in the membrane that obstructs blood flow from the accessory ...

journal_title：Pediatric cardiology

authors： Sivakumar K,Satish R,Tailor K,Coelho R

更新日期：2008-07-01 00:00:00

abstract：:There has been substantial controversy regarding treatment of congenital heart defects in infants with trisomies 13 and 18. Most reports have focused on surgical outcomes versus expectant treatment, and rarely there has been an effort to consolidate existing evidence into a more coherent way to help clinicians with de...

journal_title：Pediatric cardiology

authors： Carvajal HG,Callahan CP,Miller JR,Rensink BL,Eghtesady P

更新日期：2020-10-01 00:00:00

abstract：:Once a mainstay in the treatment of neonates with d-transposition of the great arteries (d-TGA), the application of balloon atrial septostomy (BAS) in the d-TGA population has become more selective. Currently, there is no clear evidence for or against a selective BAS strategy. The aims of this single-center retrospect...

journal_title：Pediatric cardiology

authors： Zaleski KL,McMullen CL,Staffa SJ,Thiagarajan RR,Maschietto N,DiNardo JA,Nasr VG

更新日期：2021-01-25 00:00:00

abstract：:Color-coded two-dimensional (2D) echocardiography confirmed the presence of severe congenital mitral regurgitation in an 8-month-old infant. Intraoperative inspection revealed an isolated perforation in the anterior leaflet. ...

journal_title：Pediatric cardiology

authors： Schranz D,Oelert H,Iversen S,Schuind A,Huth R,Jüngst BK,Stopfkuchen H,Erbel R

更新日期：1990-04-01 00:00:00

abstract：:Various surgical techniques have been proposed for the repair of supravalvular pulmonary stenosis (SVPS) in pediatric populations. Whereas growth potential should be promised, excessive expansion under the presence of undiminished high pulmonary arterial pressure should be avoided. The authors applied all-autologous t...

journal_title：Pediatric cardiology

authors： Fujiyoshi T,Hoashi T,Kagisaki K,Kurosaki K,Shiraishi I,Ichikawa H

更新日期：2013-10-01 00:00:00

abstract：:The purpose of this study was to describe the long-term outcome of infants with hypoplastic left heart syndrome (HLHS) who underwent placement of internal pulmonary artery bands as part of a transcatheter palliation procedure followed by primary heart transplantation. Transcatheter palliation included stenting of the ...

journal_title：Pediatric cardiology

authors： Miyamoto SD,Pietra BA,Chan KC,Ivy DD,Mashburn C,Campbell DN,Mitchell MB,Boucek MM

更新日期：2009-05-01 00:00:00

abstract：:Coronary artery fistula (CAF) is a rare congenital anomaly that can be complicated by endocarditis, myocardial infarction, or coronary aneurysms. This article reviews the clinical characteristics and surgical outcome of 10 patients with CAF in Rajae Heart Center. From 1990 to 2000, 10 patients (age, 6 months to 15 yea...

journal_title：Pediatric cardiology

authors： Malekahmadi M,Shahmohammadi A

更新日期：2005-07-01 00:00:00

abstract：:Noninvasive Doppler-derived cardiac output was measured with the pulsed Doppler method in 22 healthy newborns during their first four days of life. Maximal blood flow velocity in the aorta was measured with the Doppler ultrasound method. The mean Doppler-derived cardiac output was 273 +/- 59 ml/min/kg. Ductal left-to-...

journal_title：Pediatric cardiology

authors： Hirsimäki H,Kero P,Wanne O,Erkkola R,Makoi Z

更新日期：1988-01-01 00:00:00

abstract：:We retrospectively investigated the effect of warfarin therapy in improving the clinical outcome of Kawasaki disease (KD) patients with giant coronary aneurysms (GAs). We followed 2350 KD patients from 1973 to 2004. The GAs (> or =8 mm in diameter) were diagnosed by coronary angiography. Sixty-eight patients (54 males...

journal_title：Pediatric cardiology

authors： Sugahara Y,Ishii M,Muta H,Iemura M,Matsuishi T,Kato H

更新日期：2008-03-01 00:00:00