Abstract:
:After surgical repair of an aortic coarctation a term infant presented with severe pulmonary hypertension and cyanosis unresponsive to treatment including extracorporeal membrane oxygenation. The atypical clinical course became apparent once the accompanying diagnosis of congenital alveolar capillary dysplasia with misalignment of the pulmonary veins had been established at autopsy. In infants with congenital heart defects and with refractory pulmonary hypertension unexplainable on anatomic findings, a lung biopsy at the time of cardiac repair should be considered to avoid further therapies that would not alter the uniformly fatal course of this rare lung disorder.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Gamillscheg A,Zobel G,Spuller E,Reiterer F,Beitzke Adoi
10.1007/s00246-007-9063-5subject
Has Abstractpub_date
2008-01-01 00:00:00pages
191-4issue
1eissn
0172-0643issn
1432-1971journal_volume
29pub_type
杂志文章abstract::The effect of patent ductus arteriosus (PDA) treatment with cyclooxygenase (COX) inhibitors (indomethacin [INDO] and ibuprofen [IBU]) on regional oxygenation requires further clarification. The authors hypothesized that both INDO and IBU reduce regional tissue oxygenation in preterm neonates with PDA but that the risk...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0309-5
更新日期:2012-12-01 00:00:00
abstract::Central venous pressure (CVP) measurement is a reliable method for evaluating intravascular volume status and cardiac function, but it is an invasive method that results in some complications such as arterial puncture, pneumothorax, and development of infection. The current study was performed to compare CVP measureme...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9067-1
更新日期:2008-03-01 00:00:00
abstract::Noonan syndrome is an autosomal dominant disease that manifests a wide variety of clinical characteristics. The syndrome is also associated with some cardiac defects. Half of all Noonan syndrome cases are caused by mutations in the PTPN11 gene, but only limited data are available regarding aortic involvement in these ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9537-8
更新日期:2010-01-01 00:00:00
abstract::An aneurysm of the fossa ovalis was identified at autopsy in 17 infants. In each case the aneurysm of the fossa ovalis was considered to have resulted from excessive elevation of pressure in that atrium contralateral to the side into which the aneurysm bulged. The aneurysms were divided into two types: intrinsic (thre...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02282740
更新日期:1985-01-01 00:00:00
abstract::The importance of myocardial bridging of a coronary artery in the setting of hypertrophic cardiomyopathy is controversial, although we have previously reported an association with myocardial ischemia and sudden death in children. We report five symptomatic children in whom symptoms or evidence of myocardial ischemia r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0576-2
更新日期:2004-07-01 00:00:00
abstract::Previous studies showed the reliability of cardiac magnetic resonance imaging (cMRI) in the quantification of aortic valve stenosis in adults. The aim of this retrospective study was to assess the ability of cMRI in the quantification of congenital aortic valve stenosis (CAS) in children. Nineteen patients (mean age 1...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0851-9
更新日期:2014-06-01 00:00:00
abstract::Intramural coronary artery is known to be a risk factor for early death after an arterial switch operation (ASO). We evaluated the early and mid-term results of ASO for patients with intramural coronary artery. From September 2008 to March 2012, seven patients with an intramural coronary artery underwent ASO at our ho...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0968-5
更新日期:2015-01-01 00:00:00
abstract::We report a patient with tricuspid atresia after total cavopulmonary connection who developed significant mitral valve regurgitation. Doppler myocardial echocardiography tracings showed "pseudonormalization" of diastolic velocities. After successful surgical reconstruction of the mitral valve, the diastolic myocardial...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-1283-6
更新日期:2006-07-01 00:00:00
abstract::We describe a patient diagnosed with a small atrial septal defect (3-4 mm) that had grown to 24 mm in diameter over a six-year period. Timing of transcatheter intervention may be affected by growth of the atrial septal defect and this reports the first case of an atrial septal defect outgrowing the possibility of tran...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-0068-1
更新日期:2002-09-01 00:00:00
abstract::Three cases of criss-cross heart with severe and complex congenital defects are reported. Precise preoperative diagnosis of the morphologic abnormalities made it possible to choose an optimal method of surgical treatment: all patients successfully underwent a Fontan-type surgical procedure. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02239574
更新日期:1990-04-01 00:00:00
abstract::Dexmedetomidine is a new sedative and analgesic agent that has a unique property of lack of respiratory depression. We describe a pediatric case in which the use of dexmedetomidine enabled us to successfully extubate a 12-year-old heart transplant patient with acute pneumonia after several failed attempts with the use...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0683-3
更新日期:2005-09-01 00:00:00
abstract::Percutaneous balloon aortic valvoplasty (BAV) and surgical aortic valvotomy (SAV) are palliative procedures in patients with non-critical congenital valve stenosis. The aim of the study was to evaluate long-term BAV and SAV results after up to 24 years of follow-up. From 1987 to 2013, 74 consecutive interventions were...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-1056-6
更新日期:2015-03-01 00:00:00
abstract::Rehospitalization following pediatric heart transplantation is common. However, existing data remain somewhat limited. Using a novel linkage between administrative and clinical databases, pediatric heart transplant (HT) recipients from 29 centers who survived to discharge were retrospectively reviewed to determine the...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02326-x
更新日期:2020-03-01 00:00:00
abstract::Non-invasive evaluation of right ventricular (RV) systolic function in neonates with pulmonary hypertension (PH) with traditional metrics including RV fractional area change (FAC) and tricuspid annular systolic plane excursion (TAPSE) has improved outcomes. Apical three-chamber (3C) RV-FAC, a novel tripartite assessme...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02376-1
更新日期:2020-08-01 00:00:00
abstract::This case report describes a boy who had Kawasaki disease (KD) at age 12 months and had a recurrence one year later. The coronary arteries were normal following the initial episode; however, during the second episode he developed coronary aneurysms. Gallium-67 radionuclide imaging, echocardiography, and angiography we...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02310998
更新日期:1986-01-01 00:00:00
abstract::Twelve years after an apparently successful surgical correction of infradiaphragmatic (obstructed) total anomalous pulmonary venous drainage, a 12-year-old boy developed evidence of pulmonary artery hypertension secondary to pulmonary venous obstruction due to an apparent lack of growth at the anastomotic site. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02080561
更新日期:1988-01-01 00:00:00
abstract::Cardiac rhabdomyoma (CR) is the most common cardiac tumor in newborns. Approximately 75% of cases are associated with tuberous sclerosis complex. Although these tumors usually spontaneously regress after 2 years of age, they can be life-threatening when they obstruct major cardiac inflow or outflow pathways. Everolimu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1688-4
更新日期:2017-10-01 00:00:00
abstract::M-mode and 2-dimensional (2D) echocardiographic imaging are routinely used to quantify left-ventricular (LV) size and function in pediatric patients with dilated cardiomyopathy (DCM). The reproducibility of and correlation between these techniques are unknown. This analysis sought to compare interreader, intrareader, ...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章,多中心研究
doi:10.1007/s00246-013-0835-9
更新日期:2014-04-01 00:00:00
abstract::Although recognized by pediatric cardiac surgeons, aortic insufficiency as a technical complication after tetralogy of Fallot repair is poorly documented, especially if it occurs late. The case of a boy with aortic insufficiency 10 years after complete tetralogy repair is described. No documentation in the literature ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00817618
更新日期:1994-03-01 00:00:00
abstract::Inhaled nitric oxide (NO) has been used in the preoperative evaluation of patients with congenital heart disease and pulmonary hypertension. The purpose of this study was to characterize responses in pulmonary vascular resistance (PVR) to oxygen and increasing doses of NO during cardiac catheterization and to determin...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0767-5
更新日期:2005-09-01 00:00:00
abstract:BACKGROUND:The purpose of this study was to investigate the associations between clinical factors and cardiac function as measured by pressure-volume loops (PVLs) in a pediatric heart transplant cohort. METHODS:Patients (age < 20 years) who underwent heart transplantation presenting for a clinically indicated catheter...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1758-7
更新日期:2018-02-01 00:00:00
abstract::Dilated cardiomyopathy in children still has a poor prognosis with high rates of mortality and cardiac transplantation (resp. around 20 and 25%). Awaiting transplantation or possible recovery, these pediatric patients are mechanically supported with extracorporeal membrane oxygenation or a paracorporeal ventricular as...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-017-1610-0
更新日期:2017-06-01 00:00:00
abstract::The commonly used Darling classification for total anomalous pulmonary venous connection (TAPVC) consists of supracardiac, cardiac, infracardiac, and mixed types (Craig et al., Lab Invest 6:44-64, 1967). In supracardiac TAPVC, the common pulmonary vein drains superiorly into the left innominate vein, the superior vena...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9509-z
更新日期:2009-10-01 00:00:00
abstract::Ultrasound Doppler was used to establish time of ductal closure, normal values for blood flow velocity in the pulmonary artery (PA), and time interval between pulmonary valve closure (Pc) and tricuspid valve opening (To) in 37 healthy neonates. Ductal closure had occurred in 23% of the children within 12 h after deliv...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:
更新日期:1986-01-01 00:00:00
abstract::We measured the coronary flow reserve in a 13-year-old girl with the rare anomaly of an absent left circumflex coronary artery. Although the coronary flow volume of the right coronary artery was at the same level as that of the left anterior descending coronary artery, the coronary flow reserve of the patient's right ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010188
更新日期:2001-03-01 00:00:00
abstract::We describe the first report of an infant who was born with hypoplastic left heart syndrome and significant pulmonary stenosis. He was successfully palliated with multiple cardiac catheterization interventions while waiting for cardiac transplantation. This unusual constellation of heart defects is an entity that is r...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0856-5
更新日期:2005-09-01 00:00:00
abstract::The observation that endocardial fibroelastosis (EFE) can result from an immune response to maternal autoantibody deposition in the fetal myocardium raises the possibility that the fetal immune system may contribute to the pathogenesis of idiopathic EFE and dilated cardiomyopathy (DCM). This study sought to characteri...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-9980-1
更新日期:2011-12-01 00:00:00
abstract::The objective of this study was to evaluate the incidence of pre-existing catheterization left pulmonary artery (LPA) gradients and correlation of these gradients with later LPA stenosis after successful patent ductus arteriosus (PDA) occlusion. We performed a single-center review of 130 patients with PDA closure from...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9448-8
更新日期:2009-10-01 00:00:00
abstract::Right ventricular (RV) remodeling in hypoplastic left heart syndrome (HLHS) begins prenatally and continues through staged palliations. However, it is unclear if the most marked observed remodeling post-Norwood is secondary to cardiopulmonary bypass (CPB) exposure or if it is an adaptation intrinsic to the systemic RV...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02482-0
更新日期:2020-10-10 00:00:00
abstract::Aortic atresia and interrupted aortic arch is a rare cardiac combination. Review of the literature revealed nine cases. We present two patients with this combination and the additional finding of quadricuspid pulmonary valves, one of which was severely stenotic. In the latter patient, an aortopulmonary window was pres...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0754-x
更新日期:2005-07-01 00:00:00