Abstract:
:The clinical and pathological features of primary pulmonary artery sarcoma in two children are reported. The first patient presented with right ventricular outflow obstruction and underwent successful surgical resection of his tumor. The second patient developed cardiac arrest following a relatively short period of symptoms of right heart failure and could not be revived. The pathological diagnosis in both patients was hemangiopericytoma. To the best of our knowledge, primary pulmonary artery sarcoma in children has not been previously reported.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Farooki ZQ,Chang CH,Jackson WL,Clapp SK,Hakimi M,Arciniegas E,Pinsky WWdoi
10.1007/BF02078416subject
Has Abstractpub_date
1988-01-01 00:00:00pages
243-51issue
4eissn
0172-0643issn
1432-1971journal_volume
9pub_type
杂志文章abstract::Inferior sinus venosus defects (SVDs) are rare imperfections located in the inferior portion of the atrial septum, leading to an overriding inferior vena cava (IVC) and an interatrial connection. These defects have increased risk of anomalous pulmonary venous return (PAPVR) and often are confused with secundum atrial ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0449-7
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abstract::Hospital volume has been associated with improved outcomes in congenital cardiac surgery. However, the relationship between hospital volume and hospitalization cost remains unclear. This study examines the relationship between hospital surgical volume and hospitalization costs, while accounting for measures of quality...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0987-2
更新日期:2015-01-01 00:00:00
abstract::Interruption of the aortic arch and hypoplastic left heart syndrome in the same patient is exceptional. In the combined collections of the Registry of Cardiovascular Disease (St. Paul, Minnesota, U.S.A.) and the Registry of Congenital Heart Defects of the Rijksuniversiteit Gent (Gent, Belgium) three specimens were fou...
journal_title:Pediatric cardiology
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abstract::Killian-Pallister syndrome is a rare dysmorphic condition characterized by specific clinical manifestations and tetrasomy 12p. Although the association of this condition with congenital heart disease has been previously documented, no cases have been reported in association with Fallot's tetralogy. We report one such ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900420
更新日期:1999-03-01 00:00:00
abstract::Cardiac surgery for congenital heart disease often necessitates a period of myocardial ischemia during cardiopulmonary bypass and cardioplegic arrest, followed by reperfusion after aortic cross-clamp removal. In experimental models, myocardial ischemia-reperfusion is associated with significant oxidative stress and ve...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2016-04-01 00:00:00
abstract::We report successful emergency pacing followed by permanent pacemaker implantation due to complete block in an otherwise healthy premature infant of 1,770 g. Via the umbilical vein a temporary bipolar pacing lead was placed in the right ventricle. The lack of spontaneous improvement warranted implantation of a permane...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010112
更新日期:2000-09-01 00:00:00
abstract::We report our findings in the microscopic examination of the conduction system in four infants with glycogen storage disease, one of whom had adequate electrophysiologic studies. The electrophysiologic studies in the latter case showed P-A and A-H intervals at the lower limits of normal, but the H-V interval was just ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:1982-01-01 00:00:00
abstract::Long-term ECG is widely used in diagnosis and assessment of many cardiac symptoms which may be caused by dangerous arrhythmias that sometimes can be difficult to document. The PocketECG system is a new technological solution for a long-term, noninvasive, continuous and real-time ECG monitoring that provides automatic ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1534-0
更新日期:2017-03-01 00:00:00
abstract::In a patient with single ventricle, mitral atresia, common atrium, pulmonary stenosis, azygos continuation of the inferior vena cava and bilateral systemic artery--pulmonary artery anastomoses, the systemic veins were connected directly to the pulmonary arteries to achieve physiologic repair; the child was discharged ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:
更新日期:1986-01-01 00:00:00
abstract::Marfan syndrome (MS) is a connective tissue disease involving the cardiovascular, ocular, and the musculoskeletal systems. MS has variable phenotypic expression and is most often diagnosed in adult life. Infantile-onset MS is rare and is associated with severe cardiovascular manifestations; there is an extremely high ...
journal_title:Pediatric cardiology
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doi:10.1007/s00246-006-0066-4
更新日期:2007-09-01 00:00:00
abstract::This study aimed to assess the impact of integrating a simulation-based education module into an extracorporeal membrane oxygenation (ECMO) curriculum on novice learners and to test the duration of time that skills obtained during this training exercise were retained. The authors hypothesized that multidisciplinary, s...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2013-03-01 00:00:00
abstract::Home international normalized ratio (INR) monitors are being increasingly used for monitoring the adequacy of anticoagulation in children on long-term warfarin. Their safety and effectiveness in the home setting has not been fully established. The purpose of this study was to explore the safety and effectiveness of ho...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9535-x
更新日期:2010-01-01 00:00:00
abstract::We present an infant with unusual anatomy and physiology of a persistent left superior vena cava (LSVC). The adverse physiologic consequences of the LSVC were corrected with percutaneous placement of vascular plugs. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9617-9
更新日期:2010-05-01 00:00:00
abstract::Accessory atrioventricular pathways (AP) are the most common substrate for paroxysmal supraventricular tachycardia in infants and small children. Up-to-date data on AP ablation in infants and small children are limited. The aim of the present study was to gain additional insight into radiofrequency (RF) catheter ablat...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1365-z
更新日期:2016-06-01 00:00:00
abstract::After surgical repair of an aortic coarctation a term infant presented with severe pulmonary hypertension and cyanosis unresponsive to treatment including extracorporeal membrane oxygenation. The atypical clinical course became apparent once the accompanying diagnosis of congenital alveolar capillary dysplasia with mi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9063-5
更新日期:2008-01-01 00:00:00
abstract::Percutaneous balloon aortic valvuloplasty was attempted in an eight-month-old infant with severe aortic valve stenosis. The procedure resulted in a fall in the resting transvalvular systolic pressure gradient from 106 mmHg to 40 mmHg and no aortic regurgitation. Clinical and Doppler echocardiography findings suggest p...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02282747
更新日期:1985-01-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0108-4
更新日期:2012-01-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s00246-011-9908-9
更新日期:2011-04-01 00:00:00
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journal_title:Pediatric cardiology
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doi:10.1007/s00246-019-02122-2
更新日期:2019-06-01 00:00:00
abstract::A rare case of isolated innominate artery arising from a left persistent arterial duct with a right aortic arch is presented. Of interest in this case is the retrograde flow in the left carotid system, the history of developmental delay, and the magnetic resonance image (MRI) brain findings suggestive of asymmetric vo...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-010-9739-0
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abstract::Aortic atresia and interrupted aortic arch is a rare cardiac combination. Review of the literature revealed nine cases. We present two patients with this combination and the additional finding of quadricuspid pulmonary valves, one of which was severely stenotic. In the latter patient, an aortopulmonary window was pres...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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abstract::Coronary artery anatomy represents a challenging and, often, determining predictor of outcome in an arterial switch operation (ASO). Impact of specific coronary artery variants, such as single, intramural and inverted, on time-related events following ASO, is, yet, to be determined. We sought to compare early and late...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1543-z
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journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
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更新日期:2012-08-01 00:00:00
abstract::In the very young child (less than eight years of age), transient loss of consciousness represents a diagnostic and management dilemma for clinicians. While most commonly benign, syncope may be due to cardiac dysfunction which can be life-threatening. It can be secondary to an underlying ion channelopathy, cardiac inf...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-020-02498-6
更新日期:2021-01-02 00:00:00
abstract::Acute kidney injury (AKI) is a potential complication for children with congenital heart disease (CHD) after cardiopulmonary bypass (CPB) surgery. This study was designed to investigate and compare the predictive values of urinary biomarkers for AKI after CPB surgery in infants and young children and to determine the ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0563-6
更新日期:2013-04-01 00:00:00
abstract::Pulmonary artery thrombosis in neonates occurs rarely. This report describes the case of a term infant with a pulmonary artery thrombosis presenting as persistent pulmonary hypertension of the newborn. The risk factors identified in the case included maternal diabetes and heterozygous factor V Leiden deficiency. The p...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9349-2
更新日期:2009-05-01 00:00:00
abstract::A neonate with pulmonary interstitial glycogenosis, pulmonary hypertension, and hypertrophic cardiomyopathy is described. The fatal outcome for this patient contrasts with the reported favorable prognosis associated with isolated pulmonary interstitial glycogenosis. To the authors' knowledge, the association of pulmon...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0311-y
更新日期:2013-02-01 00:00:00
abstract::Various agents have been suggested as causal or associated factors in the pathogenesis of Kawasaki disease (KD); however, the underlying factors of KD remain unknown. Plasma exchange is one of the most effective treatments for the acute phase of KD. This indicates that plasma may contain factors associated with the pa...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0329-1
更新日期:2012-12-01 00:00:00
abstract::Postpericardiotomy syndrome is a frequent complication following cardiac surgery. It is characterized by fever, chest pain, pericardial friction rub or pericardial effusion, and laboratory signs of inflammation. Treatment includes the use of nonsteroidal antiinflammatory agents, corticosteroids, and pericardial draina...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9025-y
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0179-x
更新日期:2012-08-01 00:00:00