Pseudohypertension in a child with Williams syndrome.

Abstract:

:Pseudohypertension has often been reported in elderly subjects, but is an unusual phenomenon in children. We report the case of a 5-year-old child who presented with features of Williams syndrome (characterized by elfin facies, supravalvar aortic stenosis, and peripheral pulmonary artery stenosis). Repeated blood pressure recordings made with appropriately sized blood pressure cuffs were very high, while simultaneous intraarterial blood pressure was normal, confirming the presence of pseudohypertension. This was shown to be caused by excessively thickened arterial vessels.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Narasimhan C,Alexander T,Krishnaswami S

doi

10.1007/BF00796994

subject

Has Abstract

pub_date

1993-03-01 00:00:00

pages

124-6

issue

2

eissn

0172-0643

issn

1432-1971

journal_volume

14

pub_type

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