Abstract:
:The morphology and natural history of anomalous right ventricular muscle bundles (ARVMB) have been described in a number of postnatal studies. Whether this is a congenital or acquired cardiac lesion remains obscure. A fetal echocardiogram performed in a 32-week gestation mother showed a large ventricular septal defect and anomalous right ventricular muscle bundles, which were easily appreciated at the ostium-infundibular level. The diagnosis was confirmed postnatally and at 6 months of age the child underwent surgical repair. This report documents the presence of ARVMB in a fetus, at a time when hemodynamics cannot explain the development of right ventricular muscle bundles. It suggests that at least, the morphologic substrate for this disease is congenital.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Leandro J,Dyck JD,Smallhorn JFdoi
10.1007/BF00795736subject
Has Abstractpub_date
1994-09-01 00:00:00pages
246-8issue
5eissn
0172-0643issn
1432-1971journal_volume
15pub_type
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journal_title:Pediatric cardiology
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journal_title:Pediatric cardiology
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journal_title:Pediatric cardiology
pub_type: 杂志文章
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journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
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