Intra-utero diagnosis of anomalous right ventricular muscle bundles in association with a ventricular septal defect: a case report.


:The morphology and natural history of anomalous right ventricular muscle bundles (ARVMB) have been described in a number of postnatal studies. Whether this is a congenital or acquired cardiac lesion remains obscure. A fetal echocardiogram performed in a 32-week gestation mother showed a large ventricular septal defect and anomalous right ventricular muscle bundles, which were easily appreciated at the ostium-infundibular level. The diagnosis was confirmed postnatally and at 6 months of age the child underwent surgical repair. This report documents the presence of ARVMB in a fetus, at a time when hemodynamics cannot explain the development of right ventricular muscle bundles. It suggests that at least, the morphologic substrate for this disease is congenital.


Pediatr Cardiol


Pediatric cardiology


Leandro J,Dyck JD,Smallhorn JF




Has Abstract


1994-09-01 00:00:00












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    pub_type: 杂志文章


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    pub_type: 杂志文章


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    pub_type: 杂志文章


    authors: Plymale J,Kolinski K,Frommelt P,Bartz P,Tweddell J,Earing MG

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    journal_title:Pediatric cardiology

    pub_type: 杂志文章


    authors: Wu YR,Zhang YQ,Chen LJ,Wang SS,Zhong SW,Zhang ZF

    更新日期:2014-10-01 00:00:00