Abstract:
:Modifications of the Fontan operation can afford excellent palliation for many patients with a variety of forms of single ventricle. In properly selected patients who are good candidates, early and late survival can be as high as 95-97%. However, mortality is considerably higher for patients with risk factors for poor outcome. For high-risk patients, inclusion of a fenestration may reduce morbidity and mortality. Important long-term undesirable events include the ongoing risk of death, arrhythmias, protein-losing enteropathy, and cardiac failure. The key to excellent long-term outcome is proper selection of patients for the operation.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Driscoll DJdoi
10.1007/s00246-007-9003-4subject
Has Abstractpub_date
2007-11-01 00:00:00pages
438-42issue
6eissn
0172-0643issn
1432-1971journal_volume
28pub_type
杂志文章,评审abstract::In adult heart failure (HF) patients, a higher ventricular arterial (VA) coupling ratio measured non-invasively is associated with worse HF prognosis and response to treatment. There are no data regarding the relationship of VA coupling to outcome in pediatric dilated cardiomyopathy (DCM) patients. We investigated the...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-2021-6
更新日期:2019-02-01 00:00:00
abstract::Barth syndrome (BTHS) is an X-linked disorder characterised by cardiomyopathy, neutropenia, skeletal myopathy and growth delay. This study describes the UK national clinical experience and outcome of cardiomyopathy in BTHS. The clinical course and echocardiographic changes of all patients with BTHS in the UK were revi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1260-z
更新日期:2016-01-01 00:00:00
abstract:INTRODUCTION:Newborns with congenital diaphragmatic hernia (CDH) have varying degrees of pulmonary hypoplasia and pulmonary hypertension (PH), and there is limited evidence that cardiac dysfunction is present. We sought to study early neonatal biventricular function and performance in these patients by reviewing early ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1850-7
更新日期:2018-06-01 00:00:00
abstract::Congenital left ventricular diverticulum is a rare cardiac malformation. The incidence of left ventricular diverticulum is reported to be 0.05% of all congenital heart malformations. This case series comprised three infants with the diagnosis of congenital left ventricular diverticulum determined by echocardiography. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0153-7
更新日期:2012-04-01 00:00:00
abstract::Complications, such as recoarctation or secondary hypertension, probably related to the loss of arterial elasticity, frequently occur after aortic coarctation surgery. This study aimed to investigate arterial compliance as evaluated by automated recording of the QKd interval in patients who underwent repair of coarcta...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9381-2
更新日期:2009-05-01 00:00:00
abstract::Intrathoracic ventricular aneurysms and diverticula can be differentiated by several criteria. Contractility is the only reliable parameter: aneurysms expand, whereas diverticula contract during ventricular systole. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010264
更新日期:2001-09-01 00:00:00
abstract::Sleep-disordered breathing (SDB) is described in patients with acquired heart failure but its prevalence in adults with congenital heart disease is not well documented. It is likely that single-ventricle patients who have undergone Fontan palliation poorly tolerate the additional stress of SDB on their fragile cardiac...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02403-1
更新日期:2020-10-01 00:00:00
abstract::Once a mainstay in the treatment of neonates with d-transposition of the great arteries (d-TGA), the application of balloon atrial septostomy (BAS) in the d-TGA population has become more selective. Currently, there is no clear evidence for or against a selective BAS strategy. The aims of this single-center retrospect...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02520-x
更新日期:2021-01-25 00:00:00
abstract::We sought to characterize the shifting epidemiology and resource utilization of Lyme disease and associated carditis in US children's hospitals. We hypothesized that the Lyme carditis burden has increased and that hospitalizations for Lyme carditis are costlier than those for Lyme disease without carditis. The PHIS da...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02250-9
更新日期:2020-02-01 00:00:00
abstract::The case report describes a 9-year-old boy who presented with an acute cerebrovascular accident and was found to have cardiac tamponade caused by cardiac rhabdomyosarcoma. Symptoms of rhabdomyosarcoma can be indolent and nonspecific, even with metastatic disease. Echocardiography and cardiac magnetic resonance imaging...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0549-4
更新日期:2013-03-01 00:00:00
abstract::Isolation of the left innominate artery arising from the ductus arteriosus is a rare clinical entity with only nine cases being reported in the literature [5, 7, 8]. We describe a case consisting of tetralogy of Fallot, right aortic arch, and isolation of the left innominate artery arising from a left-sided ductus art...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010154
更新日期:2001-01-01 00:00:00
abstract::Internationally, there have been isolated case reports published of children presenting with dilated cardiomyopathy (DCM) in the setting of undiagnosed rickets. Although there has been an increased prevalence of rickets in the United States, there has been only one documented case of associated DCM. At our institution...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9444-z
更新日期:2009-08-01 00:00:00
abstract::This review discusses the historical aspects, current state of the art, and potential future advances in the areas of nomenclature and databases for congenital heart disease. Five areas will be reviewed: (1) common language = nomenclature, (2) mechanism of data collection (database or registry) with an established uni...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-006-1447-4
更新日期:2007-03-01 00:00:00
abstract::Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a heritable cardiomyopathy characterized by fibro-fatty replacement of right ventricular myocardium. Diagnostic criteria, established in 1994 and modified in 2010, are based on predominately adult manifestations of ARVC/D. The goal of this paper is ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1327-x
更新日期:2016-04-01 00:00:00
abstract::In case of progressive cyanosis after modified Fontan procedure, intrahepatic shunting should be considered. Ligation of the hepatic vein is safe and effective in managing this condition, and it is important to ensure that the pressure difference between superior vena cava and the portal vein system remains minimal af...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900505
更新日期:1999-11-01 00:00:00
abstract::The occurrence of familial heart disease in association with tricuspid atresia is rare. The first reported instance of tricuspid atresia and Ebstein's anomaly in siblings is presented. The presence of these two distinct pathologic variants of tricuspid valve malformations in siblings suggests that these malformations ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900072
更新日期:1996-09-01 00:00:00
abstract::A rare form of endocardial cushion defect is an atrioventricular (AV) canal-type ventricular septal defect with cleft mitral valve in the absence of a primum atrial septal defect. In two infants with Down's syndrome, preoperative delineation of this entity was accomplished. M-mode echocardiographic features included p...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02426975
更新日期:1982-01-01 00:00:00
abstract::We report a newborn with a congenital aneurysm of the muscular interventricular septum, a conduction system abnormality involving variable left and right bundle branch block, and an abnormality of the short arm of chromosome 20, This combination of anomalies has not been previously reported. To date, the infant has pr...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0928-6
更新日期:2007-01-01 00:00:00
abstract::A 2-year-old girl with cor triatriatum with unroofed coronary sinus and persistent left superior vena cava underwent preoperative radiofrequency catheter ablation for atrial tachycardia attack that developed after admission to our hospital. The procedure was not successful. Cryoablation was successfully performed duri...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-002-0376-0
更新日期:2003-09-01 00:00:00
abstract::Limited data exist on the impact of prenatal diagnosis and outcomes of fetal truncus arteriosus (TA). We sought to assess prenatal diagnostic accuracy and prenatal outcomes in fetuses with TA and compare postnatal outcomes in neonates with prenatally and postnatally diagnosed TA. Records were reviewed for patients dia...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9328-7
更新日期:2009-04-01 00:00:00
abstract::The original version of this article unfortunately contained a mistake. The presentation of Table 2 was incorrect .The corrected table is given below. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章,已发布勘误
doi:10.1007/s00246-018-1816-9
更新日期:2018-03-01 00:00:00
abstract::We herein describe, for the first time, the fetal presentation of a case of ventricular inversion, restrictive ventricular septal defect, pulmonary stenosis, hypertensive left ventricle and double outlet right ventricle at 34 weeks of gestational age. Postnatal echocardiography confirmed the prenatal diagnosis. The pa...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-018-2048-8
更新日期:2019-01-01 00:00:00
abstract:OBJECTIVES:The aim of this article is to examine the frequency, timing of formation of aneurysm of the ventricular membranous septum (AVMS), and prognosis in patients with a perimembranous ventricular septal defect (VSD). PATIENTS:One hundred forty-eight patients were diagnosed with a perimembranous VSD within 90 days...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0572-6
更新日期:2004-07-01 00:00:00
abstract::There has been substantial controversy regarding treatment of congenital heart defects in infants with trisomies 13 and 18. Most reports have focused on surgical outcomes versus expectant treatment, and rarely there has been an effort to consolidate existing evidence into a more coherent way to help clinicians with de...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-020-02444-6
更新日期:2020-10-01 00:00:00
abstract::This report describes the case of a 29-day-old infant with Kawasaki's disease who presented in extremis with multiple coronary aneurysms and coronary thromboses, myocardial ischemia, and congestive heart failure. The infant successfully underwent emergent coronary thrombolysis with tissue plasminogen activator. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-010-9781-y
更新日期:2010-11-01 00:00:00
abstract::Recurrent congestive heart failure (CHF) attributable to myocarditis is a seldom-discussed entity in the scientific literature. This report describes the case of an 8-year-old girl who had three clinically identical episodes of CHF, beginning at the age of 5 years, with each episode preceded by a viral prodrome. The c...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0109-3
更新日期:2012-01-01 00:00:00
abstract::Noninvasive measurement of cardiac output (CO) and particularly stroke volume (SV) remain difficult but potentially valuable. These variables can be particularly challenging to measure in children with congenital heart disease (CHD). Impedance cardiography (IC) is a technique shown to be accurate in measuring SV in ad...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1456-x
更新日期:2016-12-01 00:00:00
abstract::A case of aneurysmal enlargement of the right atrium was found accidentally during a routine examination. The patient was asymptomatic and free of palpitations or proven rhythm disturbances. The results of echocardiography, magnetic resonance imaging, and cardiac catheterization excluded cardiac malformation, which co...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900341
更新日期:1998-09-01 00:00:00
abstract::Dilated cardiomyopathy in children still has a poor prognosis with high rates of mortality and cardiac transplantation (resp. around 20 and 25%). Awaiting transplantation or possible recovery, these pediatric patients are mechanically supported with extracorporeal membrane oxygenation or a paracorporeal ventricular as...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-017-1610-0
更新日期:2017-06-01 00:00:00
abstract::Tricuspid valve malformation is a rare congenital heart disease. Prenatal diagnosis of Ebstein's anomaly (EA) and tricuspid valve dysplasia (TVD) is associated with high mortality. There are conflicting reports concerning accurate prognostication after diagnosis in utero. The aim of our study was to assess prognostic ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0355-z
更新日期:2012-12-01 00:00:00