Levosimendan as Rescue Therapy for Acute Heart Failure in a Patient with Duchenne Muscular Dystrophy.

abstract：:Acute pulmonary vasodilator testing (AVT) is essential to determining the initial therapy for children with pulmonary arterial hypertension (PAH). This study aimed to report the initial experience with inhaled treprostinil used for AVT in children with PAH and to evaluate the hemodynamic change after inhaled treprosti...

journal_title：Pediatric cardiology

authors： Takatsuki S,Parker DK,Doran AK,Friesen RH,Ivy DD

更新日期：2013-04-01 00:00:00

abstract：:For adults with sickle cell disease (SCD), cardiac changes are well described and may account for up to one-fourth of disease-related mortality. Much less is known about heart disease in pediatric SCD patients. This retrospective study analyzed a contemporary cohort of children with SCD followed at a single tertiary c...

journal_title：Pediatric cardiology

authors： Doshi AR,Pauliks LB

更新日期：2013-04-01 00:00:00

abstract：:Adrenomedullin (ADM) is a vasoactive peptide with potent dilatory effects. We studied whether perioperative myocardial injury could be altered by the presence of ADM. Blood samples from 19 children with congenital heart disease undergoing surgical repair were collected at six time points: preoperative, on cardiopulmon...

journal_title：Pediatric cardiology

authors： Szekely L,Vijay P,Sharp TG,Bando K,Brown JW

更新日期：2000-05-01 00:00:00

abstract：:Cardiopulmonary bypass (CPB) reduces coagulation factor levels through hemodilution and consumption. Differences in CPB-induced alterations of factor XIII (FXIII) levels in children with cyanotic and acyanotic congenital heart defects (CHDs) are not well characterized. FXIII activity (determined by Berichrom assay), p...

journal_title：Pediatric cardiology

authors： Bockeria LA,Samsonova NN,Yurlov IA,Klimovich LG,Kozar EF,Olsen EH,Zaets SB

更新日期：2014-10-01 00:00:00

abstract：:Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluati...

journal_title：Pediatric cardiology

authors： Kim JJ,Valdes SO,Kertesz NJ,Cannon BC

更新日期：2008-09-01 00:00:00

abstract：:Noonan syndrome is an autosomal dominant disease that manifests a wide variety of clinical characteristics. The syndrome is also associated with some cardiac defects. Half of all Noonan syndrome cases are caused by mutations in the PTPN11 gene, but only limited data are available regarding aortic involvement in these ...

journal_title：Pediatric cardiology

authors： Jefferies JL,Belmont JW,Pignatelli R,Towbin JA,Craigen WJ

更新日期：2010-01-01 00:00:00

abstract：:The vertebrate heart is innervated by the sympathetic and parasympathetic components of the peripheral autonomic nervous system, which regulates its contractile rate and force. Understanding the mechanisms that control sympathetic neuronal growth, differentiation, and innervation of the heart may provide insight into ...

journal_title：Pediatric cardiology

authors： Vincentz JW,Rubart M,Firulli AB

更新日期：2012-08-01 00:00:00

abstract：:The outcome in a series of 23 cases of tetralogy of Fallot diagnosed prenatally was compared to published figures for this condition when (a) identified postnatally or (b) treated surgically. There was a marked difference in the survival between these groups, with the highest mortality (75%) occurring when the diagnos...

journal_title：Pediatric cardiology

authors： Allan LD,Sharland GK

更新日期：1992-01-01 00:00:00

abstract：:This report aims to summarize and evaluate the efficacy and experience of reintervention for children with postoperative pulmonary venous restenosis. Clinical data from 61 patients with postoperative pulmonary venous restenosis who underwent reintervention at Shanghai Children's Medical Center (SCMC) from September 20...

journal_title：Pediatric cardiology

authors： Kai L,Xiaoyang Z,Jinghao Z,Zhongqun Z,Qi S,Xiaomin H,Zhiwei X,Jinfen L

更新日期：2019-06-01 00:00:00

abstract：:Congenital heart defects (CHDs) are the most prevalent of all birth defects and the leading cause of death in the first year of life. The molecular causes of most CHDs remain largely unknown. The LIM homeodomain transcriptor factor ISL1 is a marker for undifferentiated cardiac progenitor cells that give rise to both t...

journal_title：Pediatric cardiology

authors： Cresci M,Vecoli C,Foffa I,Pulignani S,Ait-Ali L,Andreassi MG

更新日期：2013-04-01 00:00:00

abstract：:The epidemiologic data for pediatric hypertrophic cardiomyopathy (HCM) needs to be periodically updated as diagnostic techniques and management strategies improve. Herein, the incidence, prevalence, and mortality rates of pediatric HCM in a population-based treatment system are described. Patients aged ≤ 17 years and ...

journal_title：Pediatric cardiology

authors： Nandi D,Hayes EA,Wang Y,Jerrell JM

更新日期：2020-10-03 00:00:00

abstract：:All 91,823 children born in 1980 in Bohemia (population 6.314 million; area 52,478 square kilometers) were examined at least four times during infancy and at the age of three and four years. All children who died were autopsied and those with heart disease were selected. A total of 779 children (8.223/1000 live births...

journal_title：Pediatric cardiology

authors： Samánek M,Slavík Z,Zborilová B,Hrobonová V,Vorísková M,Skovránek J

更新日期：1989-10-01 00:00:00

abstract：:Fetal interventions have been performed for some congenital heart diseases. However, these procedures have not gained wide acceptance due to concerns about their efficacy and safety. The aim of this study was to report on a preliminary experience with fetal cardiac interventions in Brazil. Twenty-two cardiac intervent...

journal_title：Pediatric cardiology

authors： Pedra SR,Peralta CF,Crema L,Jatene IB,da Costa RN,Pedra CA

更新日期：2014-03-01 00:00:00

abstract：:Branch pulmonary artery stenosis (BPAS) in the setting of systemic-pulmonary artery shunts (SPS) may result in significant sequelae. Limited information exists regarding the safety and efficacy of pulmonary artery balloon angioplasty and stent implantation via SPS in neonates and infants. This study aimed to examine t...

journal_title：Pediatric cardiology

authors： Aregullin EO,Gutierrez Y,Osorio S,Nykanen DG,Khan DM,Zahn EM

更新日期：2013-08-01 00:00:00

abstract：:This study aimed to clarify the characteristics of pulmonary arterial resistance (Rp)-compliance (Cp) coupling in individuals with Down syndrome (DS), who have increased risks of pulmonary arterial hypertension (PAH). We performed cardiac catheterization before and after corrective surgery in 85 DS infants and 85 cont...

journal_title：Pediatric cardiology

authors： Iwaya Y,Muneuchi J,Inoue Y,Watanabe M,Okada S,Ochiai Y

更新日期：2019-04-01 00:00:00

abstract：:A very rare combination including tetralogy of Fallot (TOF), absent pulmonary valve, and isolated left pulmonary artery is described. A 4-month-old girl presented with mild cyanosis and severe dyspnea. Echocardiography established the diagnosis of TOF and absent pulmonary valve with severe pulmonary regurgitation and ...

journal_title：Pediatric cardiology

authors： Wu L

更新日期：2008-11-01 00:00:00

abstract：:Hypertrophic cardiomyopathy (HCM) is a rare presenting feature of congenital disorder of glycosylation type Ia (CDG-Ia). We report two female siblings with CDG-Ia and cardiomyopathy. Patient no. 1 died at 12 days of age from cardiac rupture and tamponade, which has not previously been reported in CDG-Ia. The second pa...

journal_title：Pediatric cardiology

authors： Rudaks LI,Andersen C,Khong TY,Kelly A,Fietz M,Barnett CP

更新日期：2012-06-01 00:00:00

abstract：:Left atrial isomerism includes a complex spectrum of cardiac and extracardiac anomalies. The records of all patients with left isomerism born during the period of 1973-2010 and treated at the Children's Hospital, Helsinki were reviewed. The short- and long-term outcomes were studied. The review included 38 patients (5...

journal_title：Pediatric cardiology

authors： Eronen MP,Aittomäki KA,Kajantie EO,Sairanen HI

更新日期：2012-04-01 00:00:00

abstract：:Ventricular arrhythmias (VAs) are common pediatric rhythm disorders requiring comprehensive laboratory evaluation. Although usually idiopathic, implying a benign character and favorable prognosis, the initial clinical approach is still not established in all cases. Considering their prognostic significance, exercise-i...

journal_title：Pediatric cardiology

authors： Bjelakovic B,Ilic S,Chouliaras K,Milovanovic B,Vukomanovic V,Bojic T,Bjelakovic L,Zaharov T

更新日期：2010-02-01 00:00:00

abstract：:In contrast to the percentile-based definitions of elevated blood pressure (BP) and hypertension for children and adolescents of all ages in the 2004 fourth report, the 2017 American Academy of Pediatrics (AAP) BP guideline recommends a change to single BP cut-offs for clinical diagnosis (120/< 80-129/< 80 mmHg for el...

journal_title：Pediatric cardiology

authors： Liu Q,Hou Y,Yang L,Zhao M,Li S,Xi B

更新日期：2019-04-01 00:00:00

abstract：:We sought to describe the use and outcomes of small, medium and large premounted stents in patients with congenital heart disease, including incidence of and risk factors for re-intervention and development of in-stent stenosis. Premounted stents offer several advantages over traditional manually crimped bare-metal st...

journal_title：Pediatric cardiology

authors： Boe BA,Zampi JD,Schumacher KR,Yu S,Armstrong AK

更新日期：2016-12-01 00:00:00

abstract：:A case of cerebral hemorrhage associated with sildenafil (Revatio) use in an infant is presented. Sildenafil is increasingly used in the treatment of primary and secondary pulmonary arterial hypertension and pulmonary arteriovenous fistula. In the reported case, sildenafil used to treat pulmonary arteriovenous fistula...

journal_title：Pediatric cardiology

authors： Samada K,Shiraishi H,Aoyagi J,Momoi MY

更新日期：2009-10-01 00:00:00

abstract：:Dilated cardiomyopathy (DCM) is an important cause of chronic congestive cardiac failure in children. In patients with idiopathic DCM, endothelium vasomotor function is disturbed. There are many studies on the roles of nitric oxide (NO) and adrenomedullin (AM) in adult patients with DCM. However, to our knowledge, no ...

journal_title：Pediatric cardiology

authors： Kilinç M,Balat A,Cekmen M,Yürekli M,Yilmaz K,Sahinöz S

更新日期：2003-07-01 00:00:00

abstract：:A blood pump specifically designed to augment flow from the great veins through the lungs would ameliorate the poor physiology of the failing univentricular circulation and result in a paradigm shift in the treatment strategy for Fontan patients. This study is the first to examine mechanical cavopulmonary assistance w...

journal_title：Pediatric cardiology

authors： Throckmorton AL,Lopez-Isaza S,Downs EA,Chopski SG,Gangemi JJ,Moskowitz W

更新日期：2013-08-01 00:00:00

abstract：:Hyperplastic left heart syndrome (HLHS) patients are palliated by creating a Fontan-type circulation passing from different surgical stages. The aim of this work is to describe the evolution of ventricular energetics parameters in HLHS patients during the different stages of palliation including the hybrid, the Norwoo...

journal_title：Pediatric cardiology

authors： Di Molfetta A,Iacobelli R,Guccione P,Di Chiara L,Rocchi M,Cobianchi Belisari F,Campanale M,Gagliardi MG,Filippelli S,Ferrari G,Amodeo A

更新日期：2017-12-01 00:00:00

abstract：:This prospective observational study conducted in a neonatal intensive care unit aimed to evaluate echocardiographic changes provoked by anemia and transfusion of packed red blood cells (pRBCs) in premature infants. In this study, 32 anemic premature infants had serial echocardiographic assessment of left ventricular ...

journal_title：Pediatric cardiology

authors： Radicioni M,Troiani S,Mezzetti D

更新日期：2012-04-01 00:00:00

abstract：:The reported prenatal detection rates (PDRs) for significant congenital heart disease (sCHD) have been suboptimal, even in the current era. Changes in prenatal ultrasound policy and training may lead to improved prenatal detection of sCHD. This study analyzed the results of a policy to assess fetal cardiac outflow tra...

journal_title：Pediatric cardiology

authors： Levy DJ,Pretorius DH,Rothman A,Gonzales M,Rao C,Nunes ME,Bendelstein J,Mehalek K,Thomas A,Nehlsen C,Ehr J,Burchette RJ,Sklansky MS

更新日期：2013-03-01 00:00:00

abstract：BACKGROUND:The optimal surgical strategy for pulmonary atresia with ventricular septal defect (PA/VSD) in neonates and young infants is controversial. Staged repair may be associated with a higher risk of inter-stage mortality, while primary repair may lead to frequent post-repair re-interventions. METHODS:From 2004 t...

journal_title：Pediatric cardiology

authors： Lee WY,Kang SR,Im YM,Yun TJ

更新日期：2020-06-01 00:00:00

abstract：:Pediatric cardiothoracic surgery is often associated with low cardiac output in the postoperative period. This study sought to determine whether increasing heart rate via temporary atrial pacing is beneficial in augmenting cardiac output. Patients younger than 18 years who underwent cardiothoracic surgery and had no p...

journal_title：Pediatric cardiology

authors： Barker GM,Affolter J,Saenz J,Cox CS,Forbess JM,Scott WA,Zeltser I

更新日期：2013-10-01 00:00:00

abstract：:A rare form of endocardial cushion defect is an atrioventricular (AV) canal-type ventricular septal defect with cleft mitral valve in the absence of a primum atrial septal defect. In two infants with Down's syndrome, preoperative delineation of this entity was accomplished. M-mode echocardiographic features included p...

journal_title：Pediatric cardiology

authors： LaCorte MA,Cooper RS,Kauffman SL,Schiller MS,Golinko RJ,Griepp RB

更新日期：1982-01-01 00:00:00