Isolated left pulmonary artery in absent pulmonary valve syndrome.

Abstract:

:A very rare combination including tetralogy of Fallot (TOF), absent pulmonary valve, and isolated left pulmonary artery is described. A 4-month-old girl presented with mild cyanosis and severe dyspnea. Echocardiography established the diagnosis of TOF and absent pulmonary valve with severe pulmonary regurgitation and moderate stenosis at the pulmonary valve site. A right ventricle angiogram showed the severe aneurismal dilation of the proximal right pulmonary artery and the remarkable pulmonary annular stenosis but failed to show the left pulmonary artery (LPA). An angiography after pulmonary vein wedge injection demonstrated the isolated and hypoplastic LPA.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Wu L

doi

10.1007/s00246-008-9282-4

subject

Has Abstract

pub_date

2008-11-01 00:00:00

pages

1129-30

issue

6

eissn

0172-0643

issn

1432-1971

journal_volume

29

pub_type

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