Abstract:
:A very rare combination including tetralogy of Fallot (TOF), absent pulmonary valve, and isolated left pulmonary artery is described. A 4-month-old girl presented with mild cyanosis and severe dyspnea. Echocardiography established the diagnosis of TOF and absent pulmonary valve with severe pulmonary regurgitation and moderate stenosis at the pulmonary valve site. A right ventricle angiogram showed the severe aneurismal dilation of the proximal right pulmonary artery and the remarkable pulmonary annular stenosis but failed to show the left pulmonary artery (LPA). An angiography after pulmonary vein wedge injection demonstrated the isolated and hypoplastic LPA.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Wu Ldoi
10.1007/s00246-008-9282-4subject
Has Abstractpub_date
2008-11-01 00:00:00pages
1129-30issue
6eissn
0172-0643issn
1432-1971journal_volume
29pub_type
杂志文章abstract::The hospitalization of a child for cardiac surgery is known to be a stressful experience for parents. However, little is known about the time course or the relationships between parental stress and the child's actual or perceived recovery. This research aimed to investigate pre- and postoperative parental stress and t...
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更新日期:2005-01-01 00:00:00
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pub_type: 杂志文章,已发布勘误
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更新日期:2009-07-01 00:00:00
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pub_type: 临床试验,杂志文章
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更新日期:2001-05-01 00:00:00
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journal_title:Pediatric cardiology
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