Hypertrophic cardiomyopathy with cardiac rupture and tamponade caused by congenital disorder of glycosylation type Ia.

abstract：:The neonatal Marfan syndrome is an autosomal dominantly inherited disease with an extremely poor prognosis. This report gives a clinical and echocardiographic description of an infant with a mutation in exon 29 of the fibrillin-1 gene (FBN1), a region in which this severe form of Marfan syndrome seems to cluster. The ...

journal_title：Pediatric cardiology

authors： Weidenbach M,Brenner R,Rantamäki T,Redel DA

更新日期：1999-09-01 00:00:00

abstract：:Cardiopulmonary bypass (CPB) reduces coagulation factor levels through hemodilution and consumption. Differences in CPB-induced alterations of factor XIII (FXIII) levels in children with cyanotic and acyanotic congenital heart defects (CHDs) are not well characterized. FXIII activity (determined by Berichrom assay), p...

journal_title：Pediatric cardiology

authors： Bockeria LA,Samsonova NN,Yurlov IA,Klimovich LG,Kozar EF,Olsen EH,Zaets SB

更新日期：2014-10-01 00:00:00

abstract：:This study aimed to assess the technical aspects of atrial septal defect (ASD) closure using the Amplatzer septal occluder (ASO) and the Gore Helex septal occluder (GHSO) for infants weighing less than 8 kg and to determine the safety, effectiveness, and near-to-intermediate-term outcome of the closure. The Mid-Atlant...

journal_title：Pediatric cardiology

authors： Bishnoi RN,Everett AD,Ringel RE,Owada CY,Holzer RJ,Chisolm JL,Radtke WA,Scott Lim D,Rhodes JF Jr,Coulson JD

更新日期：2014-10-01 00:00:00

abstract：:Aortic atresia and interrupted aortic arch is a rare cardiac combination. Review of the literature revealed nine cases. We present two patients with this combination and the additional finding of quadricuspid pulmonary valves, one of which was severely stenotic. In the latter patient, an aortopulmonary window was pres...

journal_title：Pediatric cardiology

authors： Yew G,Coleman D,Calder L

更新日期：2005-07-01 00:00:00

abstract：:This study aimed to clarify the characteristics of pulmonary arterial resistance (Rp)-compliance (Cp) coupling in individuals with Down syndrome (DS), who have increased risks of pulmonary arterial hypertension (PAH). We performed cardiac catheterization before and after corrective surgery in 85 DS infants and 85 cont...

journal_title：Pediatric cardiology

authors： Iwaya Y,Muneuchi J,Inoue Y,Watanabe M,Okada S,Ochiai Y

更新日期：2019-04-01 00:00:00

abstract：:A two-year-old child who had had palliative surgery as a neonate for an absent right atrioventricular connection and double-inlet ventricle was shown to be developmentally retarded. Trisomy for the short arm of chromosome 8 was demonstrated, resulting from a familial 8:13 translocation, with a high risk of recurrence....

journal_title：Pediatric cardiology

authors： Burn J,Baraitser M,Hughes DT,Saldana-Garcia P,Taylor JF

更新日期：1984-01-01 00:00:00

abstract：:Pseudohypertension has often been reported in elderly subjects, but is an unusual phenomenon in children. We report the case of a 5-year-old child who presented with features of Williams syndrome (characterized by elfin facies, supravalvar aortic stenosis, and peripheral pulmonary artery stenosis). Repeated blood pres...

journal_title：Pediatric cardiology

authors： Narasimhan C,Alexander T,Krishnaswami S

更新日期：1993-03-01 00:00:00

abstract：:Horseshoe lung is a rare malformation that is often associated with lung hypoplasia and/or vascular anomalies. We describe a 10-year-old girl with horseshoe lung and unique left pulmonary vein. This is the first reported case with this vascular feature. The patient presented with signs and symptoms of severe pulmonary...

journal_title：Pediatric cardiology

authors： Salerno T,Guccione P,Malena S,Cutrera R

更新日期：2010-08-01 00:00:00

abstract：:A 2100-g neonate underwent a two-ventricular surgical repair of a right ventricle-dominant unbalanced atrioventricular septal defect associated with the heterotaxy syndrome and sinus node dysfunction. Postoperative congestive heart failure persisted despite bradycardia management by temporary ventricular pacing. Spect...

journal_title：Pediatric cardiology

authors： Liske MR,Duffy CE,Gidding SS,Rocchini AP

更新日期：1999-05-01 00:00:00

abstract：:A vascular approach for balloon aortic dilatation in infants is of major concern due to the high risk of femoral artery injury. To overcome this problem, a surgical right carotid artery (RCA) approach has been advocated. No reports are available on RCA after neonatal cutdown. Since 1990, RCA cutdown has been performed...

journal_title：Pediatric cardiology

authors： Borghi A,Agnoletti G,Poggiani C

更新日期：2001-05-01 00:00:00

abstract：:The commonly used Darling classification for total anomalous pulmonary venous connection (TAPVC) consists of supracardiac, cardiac, infracardiac, and mixed types (Craig et al., Lab Invest 6:44-64, 1967). In supracardiac TAPVC, the common pulmonary vein drains superiorly into the left innominate vein, the superior vena...

journal_title：Pediatric cardiology

authors： Shah S,Singh M,John C,Maheshwari S

更新日期：2009-10-01 00:00:00

abstract：:Hammock mitral valve (MV), also known as anomalous mitral arcade, is a rare congenital anomaly. We report a case of a 10-month-old child who presented with congestive heart failure and was found to have severe mitral stenosis (MS) secondary to a hammock MV anomaly. Detailed advanced imaging with cardiac MRI and three-...

journal_title：Pediatric cardiology

authors： VanLoozen D,McCafferty S,Lutin WA,Polimenakos AC

更新日期：2018-03-01 00:00:00

abstract：:Ionizing radiation exposure is a necessary risk entailed during congenital cardiac catheterizations. The congenital catheterization lab at Yale New Haven Children's Hospital employed quality improvement strategies to minimize radiation exposure in this vulnerable population. In two phases, we implemented six intervent...

journal_title：Pediatric cardiology

authors： Patel C,Grossman M,Shabanova V,Asnes J

更新日期：2019-03-01 00:00:00

abstract：:Presented is a retrospective outcome study of a 15-year single institutional experience with a contemporary cohort of patients with hypoplastic left heart syndrome and complex that underwent a "Giessen Hybrid" stage I as initial palliation. Hybrid approach consisting of surgical bilateral pulmonary artery banding and ...

journal_title：Pediatric cardiology

authors： Schranz D,Bauer A,Reich B,Steinbrenner B,Recla S,Schmidt D,Apitz C,Thul J,Valeske K,Bauer J,Müller M,Jux C,Michel-Behnke I,Akintürk H

更新日期：2015-02-01 00:00:00

abstract：:Long-term prostaglandin use is commonly associated with side effects such as cortical proliferation of the bones, hypertrophic pyloric stenosis, and soft tissue swelling of the extremities. We report a neonate with critical coarctation of the aorta, who developed second and third degree atrioventricular blocks associa...

journal_title：Pediatric cardiology

authors： Aly SA,Awad SM,Abdulla RI,Kazmouz S,Nguyen HH

更新日期：2017-10-01 00:00:00

abstract：:Regional wall motion patterns in tetralogy of Fallot and its postoperative modifications by electrical and hemodynamic factors were assessed by Fourier analysis of gated radionuclide angiograms in 24 studies performed in children after surgical correction of tetralogy of Fallot. The range of right ventricular (RV) pha...

journal_title：Pediatric cardiology

authors： Ratib O,Friedli B,Righetti A,Oberhaensli I

更新日期：1989-01-01 00:00:00

abstract：:A five-day-old infant with transposition of the great arteries, ventricular septal defect, and an interrupted right aortic arch underwent successful balloon septostomy, pulmonary artery banding, and aortic arch repair. The infant also had abnormal facies with severe refractory hypocalcemia and depressed T-lymphocyte n...

journal_title：Pediatric cardiology

authors： Duncan WJ,Tyrrell MJ,Bharadwaj B,Rosenberg AM,Schroeder ML,Bingham WT

更新日期：1984-07-01 00:00:00

abstract：:Assessment of ventricular dysfunction and asynchrony is very important in predicting the outcome for children with a single right ventricle. However, the assessment is inaccurate and subjective because of the unusual ventricular shape. This study aimed to evaluate the feasibility and clinical value of velocity vector ...

journal_title：Pediatric cardiology

authors： Wu YR,Zhang YQ,Chen LJ,Wang SS,Zhong SW,Zhang ZF

更新日期：2014-10-01 00:00:00

abstract：:Congenital left ventricular diverticulum is a rare cardiac malformation. The incidence of left ventricular diverticulum is reported to be 0.05% of all congenital heart malformations. This case series comprised three infants with the diagnosis of congenital left ventricular diverticulum determined by echocardiography. ...

journal_title：Pediatric cardiology

authors： Yang H,Zhu Q,Chen J,Guo N

更新日期：2012-04-01 00:00:00

abstract：:Although liver fibrosis causes significant morbidity in the late postoperative period of the Fontan procedure, the diagnostic value of hyaluronic acid (HA), a serum marker of liver fibrosis, has not been established in Fontan patients. The purpose of this study was to determine whether increased serum HA concentration...

journal_title：Pediatric cardiology

authors： Hayashi T,Inuzuka R,Shindo T,Hirata Y,Shimizu N,Oka A

更新日期：2014-04-01 00:00:00

abstract：:Angiotensin-converting enzyme inhibitors (ACEi) are commonly used for pediatric cardiology patients. However, studies examining their safety for neonates with cardiac disease are scarce. The current study aimed to test the hypothesis that ACEi-mediated nephrotoxicity occurs in neonates and may be underappreciated in t...

journal_title：Pediatric cardiology

authors： Lindle KA,Dinh K,Moffett BS,Kyle WB,Montgomery NM,Denfield SD,Knudson JD

更新日期：2014-03-01 00:00:00

abstract：:Acute myopericarditis is a major cause of acquired heart disease worldwide in pediatric patients. Various viruses have been reported as the etiology, of which varicella zoster virus was first reported in 1953. However, since nationwide administration of the varicella vaccine, reports of varicella-associated myopericar...

journal_title：Pediatric cardiology

authors： Kao KL,Yeh SJ,Chen CC

更新日期：2010-07-01 00:00:00

abstract：:Magnetocardiographic mapping was performed on a 2-year-old boy who suffered from the Wolff-Parkinson-White syndrome in association with a complex congenital heart defect. The pre-excitation site was determined noninvasively from the measured cardiac magnetic fields. The location was in the same anatomic region as foun...

journal_title：Pediatric cardiology

authors： Nenonen J,Rovamo L,Toivonen L,Ilmoniemi R,Järvinen A,Leiniö M,Montonen J,Nisula L

更新日期：1995-01-01 00:00:00

abstract：:Congenital heart defects (CHD) are the third leading cause of death in children <1 year of age in Mexico where there is a high prevalence of the 677C → T polymorphism of the MTHFR gene. This is important because the homozygous 677T/T MTHFR gene and deficiency of folic acid (FA) intake have been associated with CHD. Ou...

journal_title：Pediatric cardiology

authors： Balderrábano-Saucedo NA,Sánchez-Urbina R,Sierra-Ramírez JA,García-Hernández N,Sánchez-Boiso A,Klunder-Klunder M,Arenas-Aranda D,Bravo-Hernández G,Noriega-Zapata P,Vizcaíno-Alarcón A

更新日期：2013-01-01 00:00:00

abstract：:We report successful emergency pacing followed by permanent pacemaker implantation due to complete block in an otherwise healthy premature infant of 1,770 g. Via the umbilical vein a temporary bipolar pacing lead was placed in the right ventricle. The lack of spontaneous improvement warranted implantation of a permane...

journal_title：Pediatric cardiology

authors： Hanséus K,Sandström S,Schüller H

更新日期：2000-09-01 00:00:00

abstract：:Right-ventricular diverticula (RVD), although rare, have particular characteristics. Our study describes the morphology of anterosuperior diverticula of the right ventricle (RV) and patient outcome for this anomaly. Retrospective analysis was performed on all patients with anterosuperior RVD diagnosed in two tertiary ...

journal_title：Pediatric cardiology

authors： Wiegand G,Rauch R,Singer H,Koch A,Hofbeck M

更新日期：2014-08-01 00:00:00

abstract：:Unroofed coronary sinus is a rare cardiac anomaly in which communication occurs between the coronary sinus and the left atrium due to the partial or complete absence of the roof of the coronary sinus. It is usually associated with other cardiovascular anomalies, especially persistent left superior vena cava. It is oft...

journal_title：Pediatric cardiology

authors： Hahm JK,Park YW,Lee JK,Choi JY,Sul JH,Lee SK,Cho BK,Choe KO

更新日期：2000-07-01 00:00:00

abstract：:Fluid overload and prolonged mechanical ventilation lead to worse outcomes in critically ill children. However, the association between these variables in children following congenital heart surgery is unknown. The objectives of this study were to describe the association between fluid overload and duration of mechani...

journal_title：Pediatric cardiology

authors： Sampaio TZ,O'Hearn K,Reddy D,Menon K

更新日期：2015-12-01 00:00:00

abstract：:Although recognized by pediatric cardiac surgeons, aortic insufficiency as a technical complication after tetralogy of Fallot repair is poorly documented, especially if it occurs late. The case of a boy with aortic insufficiency 10 years after complete tetralogy repair is described. No documentation in the literature ...

journal_title：Pediatric cardiology

authors： Bilfinger TV,Seifert FC,Vallone AM,Biancaniello TM

更新日期：1994-03-01 00:00:00

abstract：:It is documented that exercise can increase serum cardiac troponins in adults and adolescents; however, there is a lack of related studies concerning the release of cardiac troponins in children. This study investigated the influence of table tennis training on cardiac biomarkers in children. Twenty-eight male childre...

journal_title：Pediatric cardiology

authors： Ma G,Liu Y,Liu K

更新日期：2014-04-01 00:00:00