Aortic valvar atresia, interrupted aortic arch, and quadricuspid pulmonary valve: a rare combination.

Abstract:

:Aortic atresia and interrupted aortic arch is a rare cardiac combination. Review of the literature revealed nine cases. We present two patients with this combination and the additional finding of quadricuspid pulmonary valves, one of which was severely stenotic. In the latter patient, an aortopulmonary window was present. The other had a unique blood supply to the brachiocephalic arteries and ascending aorta from systemic collateral arteries. To the best of our knowledge, the association of a quadricuspid pulmonary valve with this combination has not been previously reported.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Yew G,Coleman D,Calder L

doi

10.1007/s00246-004-0754-x

subject

Has Abstract

pub_date

2005-07-01 00:00:00

pages

455-9

issue

4

eissn

0172-0643

issn

1432-1971

journal_volume

26

pub_type

杂志文章
  • Surgical ligation of anomalous hepatic vein in a case of heterotaxy syndrome with massive intrahepatic shunting after modified fontan operation.

    abstract::In case of progressive cyanosis after modified Fontan procedure, intrahepatic shunting should be considered. Ligation of the hepatic vein is safe and effective in managing this condition, and it is important to ensure that the pressure difference between superior vena cava and the portal vein system remains minimal af...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s002469900505

    authors: Hishitani T,Ogawa K,Hoshino K,Nakamura Y

    更新日期:1999-11-01 00:00:00

  • A viable therapeutic option: mechanical circulatory support of the failing Fontan physiology.

    abstract::A blood pump specifically designed to augment flow from the great veins through the lungs would ameliorate the poor physiology of the failing univentricular circulation and result in a paradigm shift in the treatment strategy for Fontan patients. This study is the first to examine mechanical cavopulmonary assistance w...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-013-0649-9

    authors: Throckmorton AL,Lopez-Isaza S,Downs EA,Chopski SG,Gangemi JJ,Moskowitz W

    更新日期:2013-08-01 00:00:00

  • Regression of Neonatal Cardiac Rhabdomyoma in Two Months Through Low-Dose Everolimus Therapy: A Report of Three Cases.

    abstract::Cardiac rhabdomyoma (CR) is the most common cardiac tumor in newborns. Approximately 75% of cases are associated with tuberous sclerosis complex. Although these tumors usually spontaneously regress after 2 years of age, they can be life-threatening when they obstruct major cardiac inflow or outflow pathways. Everolimu...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-017-1688-4

    authors: Chang JS,Chiou PY,Yao SH,Chou IC,Lin CY

    更新日期:2017-10-01 00:00:00

  • Hypoplastic left heart syndrome and valvar pulmonary stenosis: presentation and management.

    abstract::We describe the first report of an infant who was born with hypoplastic left heart syndrome and significant pulmonary stenosis. He was successfully palliated with multiple cardiac catheterization interventions while waiting for cardiac transplantation. This unusual constellation of heart defects is an entity that is r...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-004-0856-5

    authors: Farra H,Kort HW

    更新日期:2005-09-01 00:00:00

  • Surgical repair of truncus arteriosus.

    abstract::This paper reviews the initial experience of radical correction of truncus arteriosus in the Soviet Union. The anatomy, hemodynamics, diagnosis and surgical technique are described in detail. Five patients were operated on; three survived. The two deaths in this series were due to mistakes in evaluating the indication...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF02424960

    authors: Burakovsky VI,Falkovsky GE,Ivanitsky AV

    更新日期:1984-04-01 00:00:00

  • Intrapericardial and retrocardial implantation of implantable cardioverter-defibrillator lead in a child with type 3 long QT syndrome.

    abstract::A 6-year-old girl with type 3 long QT syndrome was safely and successfully implanted with an implantable cardioverter-defibrillator (ICD) system. Prior to implantation, she had experienced uncontrollable life-threatening arrhythmia in spite of high-dose administration of mexiletine. An ICD coil lead for transvenous us...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-011-0065-y

    authors: Ichikawa Y,Iwamoto M,Yanagi S,Masuda M

    更新日期:2011-10-01 00:00:00

  • Tricuspid atresia with progressive ductal restriction in a fetus.

    abstract::We report a unique case of tricuspid and pulmonary atresia with idiopathic progressive ductus arteriosus restriction in utero. Diligent predelivery planning and a controlled delivery environment led to a favorable outcome. ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0391-8

    authors: Lowenthal A,Lal A,Selamet Tierney ES,Tacy TA

    更新日期:2013-08-01 00:00:00

  • Anastomosis of systemic veins to pulmonary arteries for physiologic repair of asplenia syndrome.

    abstract::In a patient with single ventricle, mitral atresia, common atrium, pulmonary stenosis, azygos continuation of the inferior vena cava and bilateral systemic artery--pulmonary artery anastomoses, the systemic veins were connected directly to the pulmonary arteries to achieve physiologic repair; the child was discharged ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:

    authors: Waldman JD,Lamberti JJ

    更新日期:1986-01-01 00:00:00

  • The myocardium of fetuses with endocardial fibroelastosis contains fewer B and T lymphocytes than normal control myocardium.

    abstract::The observation that endocardial fibroelastosis (EFE) can result from an immune response to maternal autoantibody deposition in the fetal myocardium raises the possibility that the fetal immune system may contribute to the pathogenesis of idiopathic EFE and dilated cardiomyopathy (DCM). This study sought to characteri...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-011-9980-1

    authors: Fernandes NM,Taylor GP,Manlhiot C,McCrindle BW,Ho M,Miner SE,Atkinson A,Jaeggi ET,Nield LE

    更新日期:2011-12-01 00:00:00

  • Ventricular performance after surgery for a congenital heart defect as assessed using advanced echocardiography: from doppler flow to 3D echocardiography and speckle-tracking strain imaging.

    abstract::A varying degree of impairment of ventricular performance is observed over the long-term after surgery for a congenital heart defect (CHD). Impaired ventricular performance has been shown to be of prognostic value for increased risk of cardiovascular events in adult CHD patients. This emphasizes the importance of deli...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章,评审

    doi:10.1007/s00246-013-0802-5

    authors: Klitsie LM,Roest AA,Blom NA,ten Harkel AD

    更新日期:2014-01-01 00:00:00

  • Partial anomalous pulmonary venous drainage in young pediatric patients: the role of magnetic resonance imaging.

    abstract::Studies of larger patient groups for systematic assessment of the anatomical accuracy of magnetic resonance imaging (MRI) for partial anomalous pulmonary venous drainage (PAPVD) have been performed so far only in adults. This study was undertaken to evaluate whether MRI can precisely depict pulmonary venous anatomy in...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-008-9367-0

    authors: Riesenkampff EM,Schmitt B,Schnackenburg B,Huebler M,Alexi-Meskishvili V,Hetzer R,Berger F,Kuehne T

    更新日期:2009-05-01 00:00:00

  • Development of a charge adjustment model for cardiac catheterization.

    abstract::A methodology that would allow for comparison of charges across institutions has not been developed for catheterization in congenital heart disease. A single institution catheterization database with prospectively collected case characteristics was linked to hospital charges related and limited to an episode of care i...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-014-0994-3

    authors: Brennan A,Gauvreau K,Connor J,O'Connell C,David S,Almodovar M,DiNardo J,Banka P,Mayer JE Jr,Marshall AC,Bergersen L

    更新日期:2015-02-01 00:00:00

  • Ventricular aneurysm or diverticulum? Clinical differential diagnosis.

    abstract::Intrathoracic ventricular aneurysms and diverticula can be differentiated by several criteria. Contractility is the only reliable parameter: aneurysms expand, whereas diverticula contract during ventricular systole. ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s002460010264

    authors: Krasemann T,Gehrmann J,Fenge H,Debus V,Loeser H,Vogt J

    更新日期:2001-09-01 00:00:00

  • Reliability of Peak Exercise Stroke Volume Assessment by Impedance Cardiography in Patients with Residual Right Outflow Tract Lesions After Congenital Heart Disease Repair.

    abstract::Global ventricular response to exercise may be useful in follow-up of patients with residual right outflow tract lesions after congenital heart disease repair. In this context, impedance cardiography is considered accurate for stroke volume (SV) measurement during exercise testing, however, to date, only partial asses...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-017-1725-3

    authors: Legendre A,Bonnet D,Bosquet L

    更新日期:2018-01-01 00:00:00

  • The role of transesophageal echocardiography during surgery for patients with tetralogy of Fallot.

    abstract::Routine use of intraoperative transesophageal echocardiography (TEE) is a safe monitoring and diagnostic method during pediatric congenital cardiac surgery. However, the question of whether intraoperative TEE is accurate and cost effective for patients with tetralogy of Fallot (TOF) has not been raised. This study aim...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0423-4

    authors: Kim SJ,Park SA,Song J,Shim WS,Choi EY,Lee SY

    更新日期:2013-02-01 00:00:00

  • Left ventricular function and myocardial mass after aortic valvotomy in infancy.

    abstract::Eighteen of 25 survivors of aortic valvotomy in infancy were reinvestigated by cross-sectional echocardiography a mean of 7.5 (2.3-13.4) years after surgery. They had been operated at a median age of 38 (5-330) days. At the follow-up examination the gradient across the aortic valve was 41 +/- 19 (15-85) mmHg and the e...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF00788221

    authors: Vogel M,Sebening F,Sauer U,Bühlmeyer K

    更新日期:1992-01-01 00:00:00

  • Retrograde transfemoral catheterization of the left ventricle in children with aortic valve stenosis.

    abstract::In 19 consecutive children with aortic valve stenosis, the left ventricle was entered retrogradely with a Gensini catheter guided by a tip-deflector guidewire which could produce any desirable degree of curvature at its tip. In all patients, the aortic valve was retrogradely traversed for measurement of the pressure g...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF02328955

    authors: Lau KC,Leung MP,Lo RN

    更新日期:1986-01-01 00:00:00

  • Inflammatory response and neurodevelopmental outcome after open-heart surgery in children.

    abstract::Long-term neurodevelopmental sequelae are commonly detectable in children after open-heart surgery with cardiopulmonary bypass (CPB). The objective of the study was to determine the neurodevelopmental outcome in these children in relation to postoperative inflammatory reaction. This is a prospective, observational stu...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-008-9354-5

    authors: Gessler P,Schmitt B,Prètre R,Latal B

    更新日期:2009-04-01 00:00:00

  • Long-distance transports of newborn infants with congenital heart disease.

    abstract::Little has been published about specific problems that may occur during long-distance transports of newborn cardiac patients. During a 4-year period after centralization of pediatric heart surgery in Sweden, 286 transports were prospectively investigated. A majority (77.3%) of the transports were carried out by nonspe...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s002460010254

    authors: Hellström-Westas L,Hanséus K,Jögi P,Lundström NR,Svenningsen N

    更新日期:2001-09-01 00:00:00

  • Age-Dependent Association Between Pre-transplant Blood Transfusion and Outcomes of Pediatric Heart Transplantation.

    abstract::Avoidance of red blood cell (RBC) transfusions in patients awaiting heart transplantation (HTx) has been suggested to minimize the risk of allosensitization. Although recent studies have suggested that an immature immune system in younger HTx recipients may reduce risks associated with RBC transfusion, the role of age...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-018-1814-y

    authors: McKee C,Tumin D,Alevriadou BR,Nicol KK,Yates AR,Hayes D Jr,Tobias JD

    更新日期:2018-04-01 00:00:00

  • Leadless Micra Pacemaker Use in the Pediatric Population: Device Implantation and Short-Term Outcomes.

    abstract::The development of Leadless cardiac pacemakers avoids the inherent complications that may occur secondary to lead insertion. A large number of devices have been inserted in adult patients although data in pediatric patients are lacking. We aimed to assess our experience with the Leadless device in the pediatric popula...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-019-02277-y

    authors: Breatnach CR,Dunne L,Al-Alawi K,Oslizlok P,Kenny D,Walsh KP

    更新日期:2020-04-01 00:00:00

  • Nesiritide for the treatment of pulmonary hypertension and cor pulmonale in an infant.

    abstract::Nesiritide is a synthetic form of B-type natriuretic peptide. It is approved for the treatment of acute exacerbations of congestive heart failure in hospitalized adult patients. It is currently under investigation for use in other settings and other patient populations. This article describes administration of nesirit...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-006-0064-6

    authors: Reynolds EW,Conely ET,Vranicar M

    更新日期:2007-05-01 00:00:00

  • Effective radiation dose in computed tomographic angiography of the chest and diagnostic cardiac catheterization in pediatric patients.

    abstract::Computed tomographic angiography (CTA) and cardiac catheterization are useful adjuncts to echocardiography for delineating cardiovascular anatomy in pediatric patients. These studies require ionizing radiation, and it is paramount to understand the amount of radiation pediatric patients receive when these tests are pe...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0486-2

    authors: Watson TG,Mah E,Joseph Schoepf U,King L,Huda W,Hlavacek AM

    更新日期:2013-03-01 00:00:00

  • Functional echocardiographic assessment of myocardial performance in anemic premature infants: a pilot study.

    abstract::This prospective observational study conducted in a neonatal intensive care unit aimed to evaluate echocardiographic changes provoked by anemia and transfusion of packed red blood cells (pRBCs) in premature infants. In this study, 32 anemic premature infants had serial echocardiographic assessment of left ventricular ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-012-0154-6

    authors: Radicioni M,Troiani S,Mezzetti D

    更新日期:2012-04-01 00:00:00

  • Doppler echocardiography with extended transesophageal atrial pacing: predicting the efficacy of permanent atrial pacing in the patient with a small left ventricle and sinus node dysfunction.

    abstract::A 2100-g neonate underwent a two-ventricular surgical repair of a right ventricle-dominant unbalanced atrioventricular septal defect associated with the heterotaxy syndrome and sinus node dysfunction. Postoperative congestive heart failure persisted despite bradycardia management by temporary ventricular pacing. Spect...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s002469900446

    authors: Liske MR,Duffy CE,Gidding SS,Rocchini AP

    更新日期:1999-05-01 00:00:00

  • Secondary residual shunt after atrial septal defect closure with an amplatzer occluder: surgical removal and evaluation of device biocompatibility after 7 years.

    abstract::Interventional occluder implantation has become the preferred mode of treatment in children with clinically significant atrial septal defect (ASD). The continuous increase in the number of patients treated calls for long-term data on device integrity and biocompatibility. We report a child who underwent successful int...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-010-9757-y

    authors: Zhu W,Neubauer H

    更新日期:2010-10-01 00:00:00

  • Reintervention Burden and Vessel Growth After Surgical Reimplantation of a Pulmonary Artery During Childhood.

    abstract::Children requiring reimplantation of a branch pulmonary artery (PA) are at risk for postoperative stenosis and impaired growth of the reimplanted PA. Outcomes and risk factors for reintervention and impaired growth are incompletely described. We reviewed data on patients who underwent reimplantation of a branch PA bet...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-017-1767-6

    authors: Wu SJ,Downing T,Mascio C,Gillespie MJ,Dori Y,Rome JJ,Glatz AC

    更新日期:2018-02-01 00:00:00

  • Predictors of Prolonged Hospital Length of Stay Following Stage II Palliation of Hypoplastic Left Heart Syndrome (and Variants): Analysis of the National Pediatric Cardiology Quality Improvement Collaborative (NPC-QIC) Database.

    abstract::The objective of this study is to identify predictors of prolonged hospital length of stay (LOS) for single ventricle patients following stage 2 palliation (S2P), excluding patients who underwent a hybrid procedure. We explore the impact of demographic features, stage 1 palliation (S1P), interstage I (IS1) management,...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/s00246-015-1208-3

    authors: Baker-Smith CM,Goldberg SW,Rosenthal GL

    更新日期:2015-12-01 00:00:00

  • Age-related criteria for signal-averaged electrocardiographic late potentials in children.

    abstract::This study examined the age-related criteria of signal-averaged electrocardiographic (SA-ECG) parameters in children. SA-ECGs were obtained in 82 healthy volunteers in six groups depending on age (group 1: 1 day to < 1 month; group 2: 1 month to < 1 year; group 3: 1 to < 6 years; group 4: 6 to < 12 years; group 5: 12 ...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章

    doi:10.1007/BF00796320

    authors: Hayabuchi Y,Matsuoka S,Kubo M,Akita H,Kuroda Y

    更新日期:1994-05-01 00:00:00

  • Radiofrequency catheter ablation of tachycardia in patients with congenital heart disease.

    abstract::Patients with anomalies of the heart frequently suffer from arrhythmias that either are associated with a congenital heart defect or result from the course of the disease. For most of the bradyarrhythmias, appropriate timing of the initiation of treatment is more challenging than its eventual execution. In the case of...

    journal_title:Pediatric cardiology

    pub_type: 杂志文章,评审

    doi:10.1007/s002460010134

    authors: Hebe J,Hansen P,Ouyang F,Volkmer M,Kuck KH

    更新日期:2000-11-01 00:00:00