Pseudohypertrophic muscular dystrophy with pulmonary valve stenosis: an unusual association.

abstract：:Unilateral absence of a pulmonary artery is a rare anomaly. Patients may present with hemoptysis, recurrent respiratory infections, pulmonary hypertension, or congestive heart failure. This report describes the case of a missing right pulmonary artery associated with anomalous left pulmonary venous connection not prev...

journal_title：Pediatric cardiology

authors： Binnetoğlu K,Ayabakan C,Sarisoy O,Tokel K

更新日期：2012-01-01 00:00:00

abstract：:We report our experience with asymptomatic valvar aortic stenosis diagnosed during infancy. During the period between November 1, 1986 and October 31, 1992 a total of 13 infants were diagnosed with asymptomatic aortic stenosis, 5 of whom showed rapid progression over the first 2 years of life. Two of these asymptomati...

journal_title：Pediatric cardiology

authors： Anand R,Mehta AV

更新日期：1997-01-01 00:00:00

abstract：:Fluid overload and prolonged mechanical ventilation lead to worse outcomes in critically ill children. However, the association between these variables in children following congenital heart surgery is unknown. The objectives of this study were to describe the association between fluid overload and duration of mechani...

journal_title：Pediatric cardiology

authors： Sampaio TZ,O'Hearn K,Reddy D,Menon K

更新日期：2015-12-01 00:00:00

abstract：:Congenital heart disease (CHD) is the most common congenital anomaly, affecting 1 % of live births. The field of pediatric cardiology has witnessed major advances over the past 25 years triggered by research initiatives focusing on CHD. However, large disparities exist in research capabilities between Arab developing ...

journal_title：Pediatric cardiology

authors： Farhat T,Abdul-Sater Z,Obeid M,Arabi M,Diab K,Masri S,Al Haless Z,Nemer G,Bitar F

更新日期：2013-02-01 00:00:00

abstract：:Rheumatic heart disease (RHD) is an inflammatory disease that develops following streptococcal infections. IL10 helps to balance immune responses to pathogens. IL10 polymorphisms have been associated with RHD, although results remain inconclusive. Our aim was to investigate the association between IL10 polymorphisms a...

journal_title：Pediatric cardiology

authors： Abdallah AM,Alnuzha A,Al-Mazroea AH,Eldardear AE,AlSamman AY,Almohammadi Y,Al-Harbi KM

更新日期：2016-01-01 00:00:00

abstract：:Thrombus formation in the native aortic root is a rare but potentially life-threatening complication in patients with hypoplastic left heart syndrome. The native aortic root in these patients serves as a conduit for the retrograde filling of the coronary arteries. Thrombus in this location could result in myocardial i...

journal_title：Pediatric cardiology

authors： Owens ST,Gomez-Fifer C,Ensing GJ

更新日期：2006-05-01 00:00:00

abstract：:Catheter ablation in children requires placement of multiple large femoral venous sheaths and catheters. Magnetic resonance angiography (MRA) was used to evaluate the effect of indwelling lines on femoral venous blood flow. Between October 1993 and February 1994 a total of 17 patients scheduled for catheter ablation u...

journal_title：Pediatric cardiology

authors： Miga DE,McKellar LF,Denslow S,Wiles HB,Case CL,Gillette PC

更新日期：1997-05-01 00:00:00

abstract：:The objective of this study is to identify predictors of prolonged hospital length of stay (LOS) for single ventricle patients following stage 2 palliation (S2P), excluding patients who underwent a hybrid procedure. We explore the impact of demographic features, stage 1 palliation (S1P), interstage I (IS1) management,...

journal_title：Pediatric cardiology

authors： Baker-Smith CM,Goldberg SW,Rosenthal GL

更新日期：2015-12-01 00:00:00

abstract：:Sedation/anesthesia is critical to cardiac catheterization in the pediatric/congenital heart patient. We sought to identify current sedation/anesthesia practices, the serious adverse event rate related to airway, sedation, or anesthesia, and the rate of intra-procedural conversion from procedural sedation to the use o...

journal_title：Pediatric cardiology

authors： Lin CH,Desai S,Nicolas R,Gauvreau K,Foerster S,Sharma A,Armsby L,Marshall AC,Odegard K,DiNardo J,Vincent J,El-Said H,Spaeth J,Goldstein B,Holzer R,Kreutzer J,Balzer D,Bergersen L

更新日期：2015-10-01 00:00:00

abstract：:Device closure of atrial septal defects (ASDs) is rapidly becoming routine in children. Comparisons are often made to older surgical series with higher morbidities. However outcomes including reintervention, late failure, and the need for long-term follow-up must be considered and compared to those of a current surgic...

journal_title：Pediatric cardiology

authors： Baskett RJ,Tancock E,Ross DB

更新日期：2003-09-01 00:00:00

abstract：:The cardiac NK-2 transcription factors are the vertebrate relatives of the Drosophila tinman gene. Without the Drosophila tinman gene, fruit flies fail to form their heart ("dorsal vessel"), and mutations or altered expression of cardiac NK-2 genes may lead to abnormal heart formation in vertebrates. Although the card...

journal_title：Pediatric cardiology

authors： Bartlett H,Veenstra GJ,Weeks DL

更新日期：2010-04-01 00:00:00

abstract：BACKGROUND:This study aimed to provide descriptive information about off-label treatment practice with clopidogrel in a pediatric population. METHODS:Patients less than 18 years of age prescribed clopidogrel between March 2002 and August 2005 were retrospectively identified at Children's Hospital, Boston. Data from th...

journal_title：Pediatric cardiology

authors： Maltz LA,Gauvreau K,Connor JA,Jenkins KJ

更新日期：2009-02-01 00:00:00

abstract：:During the development of so-called aneurysmal transformation of perimembranous ventricular septal defects (pmVSD), tricuspid valve (TV) morphology and function may be altered resulting in left ventricular (LV) to right atrial (RA) shunting. The feasibility and outcome of interventional closure of these pmVSD has not ...

journal_title：Pediatric cardiology

authors： Kerst G,Moysich A,Ho SY,Apitz C,Latus H,Schranz D

更新日期：2015-10-01 00:00:00

abstract：:Arrhythmias in pregnancy are becoming more common given more available and effective medical, ablation and device treatment options. Several changes associated with pregnancy, increased blood volume, cardiac output, and heart rate secondary to an increased sympathetic state, facilitate more frequent occurrences of arr...

journal_title：Pediatric cardiology

authors： Friday KP,Moak JP,Fries MH,Iqbal SN

更新日期：2015-10-01 00:00:00

abstract：:The data on the outcomes of children with heart disease and Down syndrome receiving extracorporeal membrane oxygenation (ECMO) for cardiac or respiratory failure are limited. This study aimed to evaluate morbidity and mortality associated with ECMO in children with Down syndrome and heart disease. Children younger tha...

journal_title：Pediatric cardiology

authors： Gupta P,Gossett JM,Rycus PT,Prodhan P

更新日期：2014-12-01 00:00:00

abstract：:A very rare combination including tetralogy of Fallot (TOF), absent pulmonary valve, and isolated left pulmonary artery is described. A 4-month-old girl presented with mild cyanosis and severe dyspnea. Echocardiography established the diagnosis of TOF and absent pulmonary valve with severe pulmonary regurgitation and ...

journal_title：Pediatric cardiology

authors： Wu L

更新日期：2008-11-01 00:00:00

abstract：:A blood pump specifically designed to augment flow from the great veins through the lungs would ameliorate the poor physiology of the failing univentricular circulation and result in a paradigm shift in the treatment strategy for Fontan patients. This study is the first to examine mechanical cavopulmonary assistance w...

journal_title：Pediatric cardiology

authors： Throckmorton AL,Lopez-Isaza S,Downs EA,Chopski SG,Gangemi JJ,Moskowitz W

更新日期：2013-08-01 00:00:00

abstract：:A two-year-old child who had had palliative surgery as a neonate for an absent right atrioventricular connection and double-inlet ventricle was shown to be developmentally retarded. Trisomy for the short arm of chromosome 8 was demonstrated, resulting from a familial 8:13 translocation, with a high risk of recurrence....

journal_title：Pediatric cardiology

authors： Burn J,Baraitser M,Hughes DT,Saldana-Garcia P,Taylor JF

更新日期：1984-01-01 00:00:00

abstract：:This study identified tracheobronchial cartilage calcification in children with congenital heart disease. Calcification of the tracheobronchial airways has been found previously in adults receiving warfarin and in children receiving warfarin after mitral valve replacement. A 9-year-old girl who had received a Fontan r...

journal_title：Pediatric cardiology

authors： Eckersley L,Stirling J,Occleshaw C,Wilson N

更新日期：2014-08-01 00:00:00

abstract：:This case report describes a boy who had Kawasaki disease (KD) at age 12 months and had a recurrence one year later. The coronary arteries were normal following the initial episode; however, during the second episode he developed coronary aneurysms. Gallium-67 radionuclide imaging, echocardiography, and angiography we...

journal_title：Pediatric cardiology

authors： Vargo TA,Huhta JC,Moore WH,Person DA,Edwards MS

更新日期：1986-01-01 00:00:00

abstract：:We report hemodynamic findings in two patients with pulmonary atresia and intact ventricular septum (PAIVS) after "one-and-a-half ventricle repair" and placement of a bidirectional Glenn shunt using four-dimensional (4D) flow magnetic resonance imaging. Quantification of flow and analysis of flow patterns revealed the...

journal_title：Pediatric cardiology

authors： Uribe S,Bächler P,Valverde I,Crelier GR,Beerbaum P,Tejos C,Irarrazaval P

更新日期：2013-02-01 00:00:00

abstract：:A five-day-old infant with transposition of the great arteries, ventricular septal defect, and an interrupted right aortic arch underwent successful balloon septostomy, pulmonary artery banding, and aortic arch repair. The infant also had abnormal facies with severe refractory hypocalcemia and depressed T-lymphocyte n...

journal_title：Pediatric cardiology

authors： Duncan WJ,Tyrrell MJ,Bharadwaj B,Rosenberg AM,Schroeder ML,Bingham WT

更新日期：1984-07-01 00:00:00

abstract：:Children with congenital heart defects often demonstrate a reduced capacity for exercise, even after surgical intervention. Forty subjects, with various heart defects, completed a 5-year study to evaluate the impact of a postoperative training program on their physical exercise capacity. All of the patients were signi...

journal_title：Pediatric cardiology

authors： Longmuir PE,Tremblay MS,Goode RC

更新日期：1990-07-01 00:00:00

abstract：:We report on a 4-kg infant with Alagille syndrome and congenital heart disease consisting of atrial septal defect (ASD), patent ductus arteriosus (PDA), and severe peripheral pulmonic stenosis. He underwent successful orthotopic liver transplant along with catheter closure of the ASD and PDA using the Amplatzer device...

journal_title：Pediatric cardiology

authors： Harris M,Cao QL,Waight D,Hijazi ZM

更新日期：2002-11-01 00:00:00

abstract：:This review outlines the morphologic and pathogenetic characteristics of congenital polyvalvular disease. Two cases are used for exemplification. The macroscopic and histologic features of the valves as well as associated cardiac lesions and clinical syndromes are described, followed by a discussion of morphogenesis o...

journal_title：Pediatric cardiology

authors： Bartram U,Bartelings MM,Kramer HH,Gittenberger-de Groot AC

更新日期：2001-03-01 00:00:00

abstract：:Pulmonary artery banding (PAB) is used as a surgical palliation to reduce excessive pulmonary blood flow caused by congenital heart defects. Due to the lack of microscopic studies dealing with the tissue remodeling caused by contemporary PAB materials, this study aimed to assess histologic changes associated with PAB ...

journal_title：Pediatric cardiology

authors： Nedorost L,Uemura H,Furck A,Saeed I,Slavik Z,Kobr J,Tonar Z

更新日期：2013-10-01 00:00:00

abstract：:All 91,823 children born in 1980 in Bohemia (population 6.314 million; area 52,478 square kilometers) were examined at least four times during infancy and at the age of three and four years. All children who died were autopsied and those with heart disease were selected. A total of 779 children (8.223/1000 live births...

journal_title：Pediatric cardiology

authors： Samánek M,Slavík Z,Zborilová B,Hrobonová V,Vorísková M,Skovránek J

更新日期：1989-10-01 00:00:00

abstract：:The epinephrine test has been shown to be a powerful tool to predict the genotype of congenital long QT syndrome (LQTS). The aim of this study was to evaluate its role in the diagnosis and management of LQTS in children. The test (using the Shimizu protocol) was conducted in patients with some evidence of LQTS but in ...

journal_title：Pediatric cardiology

authors： Clur SA,Chockalingam P,Filippini LH,Widyanti AP,Van Cruijsen M,Blom NA,Alders M,Hofman N,Wilde AA

更新日期：2010-05-01 00:00:00

abstract：:We report our findings in the microscopic examination of the conduction system in four infants with glycogen storage disease, one of whom had adequate electrophysiologic studies. The electrophysiologic studies in the latter case showed P-A and A-H intervals at the lower limits of normal, but the H-V interval was just ...

journal_title：Pediatric cardiology

authors： Bharati S,Serratto M,DuBrow I,Paul MH,Swiryn S,Miller RA,Rosen K,Lev M

更新日期：1982-01-01 00:00:00

abstract：:A vascular approach for balloon aortic dilatation in infants is of major concern due to the high risk of femoral artery injury. To overcome this problem, a surgical right carotid artery (RCA) approach has been advocated. No reports are available on RCA after neonatal cutdown. Since 1990, RCA cutdown has been performed...

journal_title：Pediatric cardiology

authors： Borghi A,Agnoletti G,Poggiani C

更新日期：2001-05-01 00:00:00