Abstract:
:We report on a 4-kg infant with Alagille syndrome and congenital heart disease consisting of atrial septal defect (ASD), patent ductus arteriosus (PDA), and severe peripheral pulmonic stenosis. He underwent successful orthotopic liver transplant along with catheter closure of the ASD and PDA using the Amplatzer device and placement of Palmaz stents in both pulmonary arteries.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Harris M,Cao QL,Waight D,Hijazi ZMsubject
Has Abstractpub_date
2002-11-01 00:00:00pages
650-4issue
6eissn
0172-0643issn
1432-1971journal_volume
23pub_type
杂志文章abstract::Double outlet right ventricle (DORV) was produced experimentally in the chick embryo by preventing the incorporation of the posteromedial conus into the left ventricle. This was accomplished by placing a ligature around the caudal end of the conus at a stage in which it is exclusively continuous with the right ventric...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02240456
更新日期:1982-01-01 00:00:00
abstract::A 9-year-old girl was admitted because she had had palpitations for 2 years. Her electrocardiogram revealed multifocal ectopic beats with left bundle branch morphology, sinoatrial block, and first- and second-degree atrioventricular blocks. Cross-sectional echocardiography demonstrated an enlarged left ventricle and f...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02505810
更新日期:1996-01-01 00:00:00
abstract::Identification of heart transplant recipients at highest risk for a poor outcome could lead to improved posttransplantation survival. A chart review of primary heart transplantations from 1993 to 2006 was performed. Analysis was performed to evaluate the risk of graft loss for those with a transplantation age less tha...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0077-7
更新日期:2012-01-01 00:00:00
abstract::Renovascular hypertension is an uncommon disease, but it causes 5-10% of all childhood hypertension. The most common cause of renal artery stenosis is fibromuscular dysplasia, resulting in at least 60% of renovascular hypertension cases. This report describes a case of a renal artery stenosis confirmed by multidetecto...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-9944-5
更新日期:2011-06-01 00:00:00
abstract::We report a unique case of tricuspid and pulmonary atresia with idiopathic progressive ductus arteriosus restriction in utero. Diligent predelivery planning and a controlled delivery environment led to a favorable outcome. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0391-8
更新日期:2013-08-01 00:00:00
abstract::Long-term neurodevelopmental sequelae are commonly detectable in children after open-heart surgery with cardiopulmonary bypass (CPB). The objective of the study was to determine the neurodevelopmental outcome in these children in relation to postoperative inflammatory reaction. This is a prospective, observational stu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9354-5
更新日期:2009-04-01 00:00:00
abstract::Ventricular arrhythmias (VAs) are common pediatric rhythm disorders requiring comprehensive laboratory evaluation. Although usually idiopathic, implying a benign character and favorable prognosis, the initial clinical approach is still not established in all cases. Considering their prognostic significance, exercise-i...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9582-3
更新日期:2010-02-01 00:00:00
abstract::As a transcription factor mainly expressed in cardiovascular system, T-box 20 (TBX20) plays an important role in embryonic cardiovascular system development and adult heart function. Previous studies have identified associations of two SNPs in the T-box DNA-binding domain of TBX20 with congenital heart disease (CHD) i...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-1073-5
更新日期:2015-04-01 00:00:00
abstract::Recurrent congestive heart failure (CHF) attributable to myocarditis is a seldom-discussed entity in the scientific literature. This report describes the case of an 8-year-old girl who had three clinically identical episodes of CHF, beginning at the age of 5 years, with each episode preceded by a viral prodrome. The c...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-011-0109-3
更新日期:2012-01-01 00:00:00
abstract::Rhabdomyoma is the most common primary cardiac tumor in infants and children and is often associated with tuberous sclerosis. Surgical resection may be indicated and, if so, is usually curative. We describe a rhabdomyoma in an infant who presented with severe myocardial ischemia necessitating orthotopic heart transpla...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF00794197
更新日期:1995-07-01 00:00:00
abstract::Limited data exist on the impact of prenatal diagnosis and outcomes of fetal truncus arteriosus (TA). We sought to assess prenatal diagnostic accuracy and prenatal outcomes in fetuses with TA and compare postnatal outcomes in neonates with prenatally and postnatally diagnosed TA. Records were reviewed for patients dia...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9328-7
更新日期:2009-04-01 00:00:00
abstract::Cor triatriatum sinistrum (division of the left atrium) is a recognized clinical and surgical entity. Division of the right atrium, also known as cor triatriatum dexter, is an extremely rare congenital abnormality in which persistence of the right valve of the embryonic systemic sinus venosus divides the right atrium ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0443-0
更新日期:2013-01-01 00:00:00
abstract::Very young mammals have an impressive cardiac regeneration capacity. In contrast, cardiac regeneration is very limited in adult humans. The hearts of young children have a higher regenerative capacity compared with adults, as, for example, seen after surgical correction of an anomalous left coronary artery arising fro...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-015-1120-x
更新日期:2015-04-01 00:00:00
abstract::Enlarged bronchial arteries and/or systemic-to-pulmonary collaterals have been frequently demonstrated in association with transposition of the great arteries. They are usually clinically silent, although they might be large enough to cause accelerated pulmonary vascular obstructive disease or symptomatic cardiac volu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9183-y
更新日期:2008-07-01 00:00:00
abstract::Various surgical techniques have been proposed for the repair of supravalvular pulmonary stenosis (SVPS) in pediatric populations. Whereas growth potential should be promised, excessive expansion under the presence of undiminished high pulmonary arterial pressure should be avoided. The authors applied all-autologous t...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0698-0
更新日期:2013-10-01 00:00:00
abstract::A large ductus arteriosus aneurysm can lead to potentially serious and life-threatening complications. We report a case of aneurysmal dilatation of the ductus arteriosus in a premature infant that was successfully treated with indomethacin. Thus, surgical intervention with general anesthesia could be avoided. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-1164-4
更新日期:2006-01-01 00:00:00
abstract::Twenty-three children with diabetes mellitus, their ages ranging from 0.2-9.8 years, but with no sign of diabetic microvascular disease were investigated by M-mode and Doppler echocardiography, along with a comparable group of control subjects. In the diabetics, the fractional shortening and the mean velocity of fract...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02238405
更新日期:1991-04-01 00:00:00
abstract::Although Kawasaki disease (KD) was first discovered and identified in Japan by Kawasaki in the 1960s, fatal KD cases resulting from coronary artery aneurysms had been identified retrospectively in the West as early as 1871. Kawasaki initially postulated that this disease was a new, as yet unidentified, self-limiting i...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9625-9
更新日期:2010-05-01 00:00:00
abstract::Kearns-Sayre syndrome (KSS) is a rare mitochondrial disorder characterized by large-scale deletions of mitochondrial DNA. Neuromuscular and cardiac conduction systems are most commonly involved in these patients. Here, we discuss a 10-year-old patient with diabetes mellitus who presented in complete heart block leadin...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9040-z
更新日期:2008-05-01 00:00:00
abstract::Three patients (ages 3, 5, and 8 years) with various forms of functionally univentricular heart lesions received a total cavopulmonary connection with an extracardiac conduit as a final reconstructive procedure. Failure of the Fontan circulation occurred immediately after surgery because of spontaneous closure of surg...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0693-6
更新日期:2005-01-01 00:00:00
abstract::Operative survival after the Norwood procedure has significantly improved during the past 10 years. However, there remains attrition among Norwood survivors before reaching planned second-stage palliation. The purpose of this study was to evaluate potential risk factors for interstage mortality among Norwood survivors...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0776-4
更新日期:2005-07-01 00:00:00
abstract::Postoperative arrhythmia is a common complication after open heart surgery in children. JET is the most common and dangerous arrhythmia. We aimed to assess safety and efficacy of prophylactic amiodarone in preventing JET in children underwent cardiac surgery and to assess risk factors for JET among our patients. In to...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1343-5
更新日期:2016-04-01 00:00:00
abstract::Ventriculo-coronary arterial connections are frequently observed in pulmonary atresia with intact interventricular septum. Sustained right ventricular hypertension during cardiac morphogenesis is thought to be responsible for persistence of myocardial sinusoidal-coronary artery connections. Considering an unusual obse...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900305
更新日期:1998-05-01 00:00:00
abstract::A case of cerebral hemorrhage associated with sildenafil (Revatio) use in an infant is presented. Sildenafil is increasingly used in the treatment of primary and secondary pulmonary arterial hypertension and pulmonary arteriovenous fistula. In the reported case, sildenafil used to treat pulmonary arteriovenous fistula...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9460-z
更新日期:2009-10-01 00:00:00
abstract::To examine factors associated with low high-density lipoprotein cholesterol (HDL-C) levels among middle school children. HDL-C levels were the primary outcome of interest. A total of 1,104 middle-school children (mean age 11.6 years, 51.2% female) were included in this analysis, of whom 177 (16%) had an HDL-C level ≤4...
journal_title:Pediatric cardiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s00246-013-0814-1
更新日期:2014-03-01 00:00:00
abstract::To evaluate the feasibility of implementing a pulse oximetry screening protocol at a city of mild elevation with a specific focus on the false-positive screening rate. Pulse oximetry screening was performed according to the proposed guidelines endorsed by the American Academy of Pediatrics at a center in Tucson, AZ, a...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0716-2
更新日期:2013-01-01 00:00:00
abstract::Paroxysmal non-reentrant supraventricular tachycardia due to double ventricular response through antegrade dual atrioventricular nodal pathways by a single atrial excitation has been reported in limited adult cases but not in pediatric patients with structurally normal hearts or with congenital heart defects. We repor...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0326-4
更新日期:2013-03-01 00:00:00
abstract::The clinical and pathological features of primary pulmonary artery sarcoma in two children are reported. The first patient presented with right ventricular outflow obstruction and underwent successful surgical resection of his tumor. The second patient developed cardiac arrest following a relatively short period of sy...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02078416
更新日期:1988-01-01 00:00:00
abstract::Long-term ECG is widely used in diagnosis and assessment of many cardiac symptoms which may be caused by dangerous arrhythmias that sometimes can be difficult to document. The PocketECG system is a new technological solution for a long-term, noninvasive, continuous and real-time ECG monitoring that provides automatic ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1534-0
更新日期:2017-03-01 00:00:00
abstract::Avoidance of red blood cell (RBC) transfusions in patients awaiting heart transplantation (HTx) has been suggested to minimize the risk of allosensitization. Although recent studies have suggested that an immature immune system in younger HTx recipients may reduce risks associated with RBC transfusion, the role of age...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1814-y
更新日期:2018-04-01 00:00:00