Absence of the right pulmonary artery associated with a partial anomalous pulmonary venous connection.

abstract：:Pulmonary artery thrombosis in neonates occurs rarely. This report describes the case of a term infant with a pulmonary artery thrombosis presenting as persistent pulmonary hypertension of the newborn. The risk factors identified in the case included maternal diabetes and heterozygous factor V Leiden deficiency. The p...

journal_title：Pediatric cardiology

authors： Sawyer T,Antle A,Studer M,Thompson M,Perry S,Mahnke CB

更新日期：2009-05-01 00:00:00

abstract：:The HOXA1 gene plays a fundamental role in embryonic morphogenesis. Recent studies in humans and mice have indicated that HOXA1 plays a previously unrecognized role in cardiovascular system development. Congenital heart disease (CHD), particularly ventricular septal defect (VSD), might be a clinically isolated manifes...

journal_title：Pediatric cardiology

authors： Liu J,Wang B,Chen X,Li H,Wang J,Cheng L,Ma X,Gao B

更新日期：2013-02-01 00:00:00

abstract：:The objective of this study was to evaluate the incidence of pre-existing catheterization left pulmonary artery (LPA) gradients and correlation of these gradients with later LPA stenosis after successful patent ductus arteriosus (PDA) occlusion. We performed a single-center review of 130 patients with PDA closure from...

journal_title：Pediatric cardiology

authors： Gowda ST,Kutty S,Ebeid M,Qureshi AM,Worley S,Latson LA

更新日期：2009-10-01 00:00:00

abstract：:Neo-aortic arch obstruction (NAAO) is a common complication following the Norwood/Sano procedure (NP) for hypoplastic left heart syndrome (HLHS) and is associated with increased morbidity and mortality. However, there is currently no objective method for predicting which patients will develop NAAO. This study was desi...

journal_title：Pediatric cardiology

authors： Raucci FJ Jr,Seckeler MD,Saunders C,Gangemi JJ,Peeler BB,Jayakumar KA

更新日期：2013-01-01 00:00:00

abstract：:Long-term ECG is widely used in diagnosis and assessment of many cardiac symptoms which may be caused by dangerous arrhythmias that sometimes can be difficult to document. The PocketECG system is a new technological solution for a long-term, noninvasive, continuous and real-time ECG monitoring that provides automatic ...

journal_title：Pediatric cardiology

authors： Bieganowska K,Kaszuba A,Bieganowski M,Kaczmarek K

更新日期：2017-03-01 00:00:00

abstract：:The neonatal Marfan syndrome is an autosomal dominantly inherited disease with an extremely poor prognosis. This report gives a clinical and echocardiographic description of an infant with a mutation in exon 29 of the fibrillin-1 gene (FBN1), a region in which this severe form of Marfan syndrome seems to cluster. The ...

journal_title：Pediatric cardiology

authors： Weidenbach M,Brenner R,Rantamäki T,Redel DA

更新日期：1999-09-01 00:00:00

abstract：:Echocardiography has previously been of limited use in visualizing the aorta in neonates and infants. Using a new technique--right parasternal scanning--the aortic arch and brachiocephalic vessels were studied in 50 children under 18 months of age. Complete visualization was accomplished in 47 patients including those...

journal_title：Pediatric cardiology

authors： George L,Waldman JD,Kirkpatrick SE,Turner SW,Pappelbaum SJ

更新日期：1982-01-01 00:00:00

abstract：:Congenital diverticulum of the ventricle is a rare disease, but most cases of congenital left ventricular diverticula are asymptomatic. We present a child with congenital left ventricular diverticulum whose routine electrocardiographic examination showed T-wave inversion in inferior and V4 to V6 leads. He was successf...

journal_title：Pediatric cardiology

authors： Wang W,Zhu W,Wang Y,Li J,Gong F

更新日期：2010-08-01 00:00:00

abstract：:A hemodynamically stable neonate with transposition of the great arteries suddenly went into cardiac arrest during preparation for transport to the operating room. Emergency echocardiography during cardiac massage detected coronary air embolism as the presumed cause of arrest. After about 15 minutes of resuscitation, ...

journal_title：Pediatric cardiology

authors： Weidenbach M,Riede FT,Dähnert I

更新日期：2011-12-01 00:00:00

abstract：:Numerous RNA-binding proteins (RBPs) are expressed in the heart, and mutations in several RBPs have been implicated in cardiovascular disease through genetic associations, animal modeling, and mechanistic studies. However, the functions of many more cardiac RBPs, and their relevance to disease states, remain to be elu...

journal_title：Pediatric cardiology

authors： Akerberg AA,Burns CE,Burns CG

更新日期：2019-10-01 00:00:00

abstract：:In the classic scimitar syndrome, a pulmonary vein draining all or part of the right lung enters the inferior vena cava. A variant is described with the same roentgenographic appearance, but with drainage of the anomalous pulmonary vein into both the inferior vena cava and the left atrium; the atrial septum was intact...

journal_title：Pediatric cardiology

authors： Pearl W

更新日期：1987-01-01 00:00:00

abstract：:Although liver fibrosis causes significant morbidity in the late postoperative period of the Fontan procedure, the diagnostic value of hyaluronic acid (HA), a serum marker of liver fibrosis, has not been established in Fontan patients. The purpose of this study was to determine whether increased serum HA concentration...

journal_title：Pediatric cardiology

authors： Hayashi T,Inuzuka R,Shindo T,Hirata Y,Shimizu N,Oka A

更新日期：2014-04-01 00:00:00

abstract：:We retrospectively investigated the effect of warfarin therapy in improving the clinical outcome of Kawasaki disease (KD) patients with giant coronary aneurysms (GAs). We followed 2350 KD patients from 1973 to 2004. The GAs (> or =8 mm in diameter) were diagnosed by coronary angiography. Sixty-eight patients (54 males...

journal_title：Pediatric cardiology

authors： Sugahara Y,Ishii M,Muta H,Iemura M,Matsuishi T,Kato H

更新日期：2008-03-01 00:00:00

abstract：:As our ability to diagnosis cardiomyopathy matures and genetic testing becomes more widespread, there has been an increase in the number of children followed for cardiomyopathy. The purpose of this study was to compare health-related quality of life (HRQoL) between children with cardiomyopathy and healthy controls and...

journal_title：Pediatric cardiology

authors： Friess MR,Marino BS,Cassedy A,Wilmot I,Jefferies JL,Lorts A

更新日期：2015-03-01 00:00:00

abstract：:We sought to describe the use and outcomes of small, medium and large premounted stents in patients with congenital heart disease, including incidence of and risk factors for re-intervention and development of in-stent stenosis. Premounted stents offer several advantages over traditional manually crimped bare-metal st...

journal_title：Pediatric cardiology

authors： Boe BA,Zampi JD,Schumacher KR,Yu S,Armstrong AK

更新日期：2016-12-01 00:00:00

abstract：:Over the past decade, revolutionary advances in ultrasound imaging technology have allowed the study of the evolution of congenital heart disease during fetal life. The frustration arising from watching the prenatal progression of severe semilunar valve obstructions and therapy-refractory fetal arrhythmias has prompte...

journal_title：Pediatric cardiology

authors： Kohl T

更新日期：2002-05-01 00:00:00

abstract：:We report a patient with tricuspid atresia after total cavopulmonary connection who developed significant mitral valve regurgitation. Doppler myocardial echocardiography tracings showed "pseudonormalization" of diastolic velocities. After successful surgical reconstruction of the mitral valve, the diastolic myocardial...

journal_title：Pediatric cardiology

authors： Petzuch K,Eicken A,Marek J,Vogel M,Schreiber C,Hess J

更新日期：2006-07-01 00:00:00

abstract：:The prevalence of obesity in long-term survivors with complex congenital heart disease may be increasing, and little is known about the timing and onset of weight gain and growth patterns in these high-risk patients. Prevalence rates of overweight/obesity and longitudinal changes in body mass index (BMI) with age were...

journal_title：Pediatric cardiology

authors： Chung ST,Hong B,Patterson L,Petit CJ,Ham JN

更新日期：2016-01-01 00:00:00

abstract：:A cohort of 52 French unrelated infant cases who died unexpectedly before they reached 12 months of age was blindly investigated to better quantify the contribution of long-QT syndrome (LQTS) genetic variants in French cases of sudden infant death syndrome (SIDS). After a standardized autopsy protocol, a blinded molec...

journal_title：Pediatric cardiology

authors： Millat G,Kugener B,Chevalier P,Chahine M,Huang H,Malicier D,Rodriguez-Lafrasse C,Rousson R

更新日期：2009-05-01 00:00:00

abstract：:In other cardiomyopathies, cardiac magnetic resonance imaging (CMR)-derived myocardial delayed enhancement (MDE), a marker of myocardial fibrosis, is a risk factor for sudden cardiac death (SCD). In Duchenne muscular dystrophy (DMD), the prognostic value of MDE for ventricular arrhythmias and death is unknown. This st...

journal_title：Pediatric cardiology

authors： Menon SC,Etheridge SP,Liesemer KN,Williams RV,Bardsley T,Heywood MC,Puchalski MD

更新日期：2014-10-01 00:00:00

abstract：:We describe the first report of an infant who was born with hypoplastic left heart syndrome and significant pulmonary stenosis. He was successfully palliated with multiple cardiac catheterization interventions while waiting for cardiac transplantation. This unusual constellation of heart defects is an entity that is r...

journal_title：Pediatric cardiology

authors： Farra H,Kort HW

更新日期：2005-09-01 00:00:00

abstract：:Congenital heart defect (CHD) represents the most prevalent birth defect, and accounts for substantial morbidity and mortality in humans. Aggregating evidence demonstrates the genetic basis for CHD. However, CHD is a heterogeneous disease, and the genetic determinants underlying CHD in most patients remain unknown. In...

journal_title：Pediatric cardiology

authors： Lu CX,Wang W,Wang Q,Liu XY,Yang YQ

更新日期：2018-04-01 00:00:00

abstract：:Dexmedetomidine is a new sedative and analgesic agent that has a unique property of lack of respiratory depression. We describe a pediatric case in which the use of dexmedetomidine enabled us to successfully extubate a 12-year-old heart transplant patient with acute pneumonia after several failed attempts with the use...

journal_title：Pediatric cardiology

authors： Chrysostomou C,Zeballos T

更新日期：2005-09-01 00:00:00

abstract：:Magnetocardiographic mapping was performed on a 2-year-old boy who suffered from the Wolff-Parkinson-White syndrome in association with a complex congenital heart defect. The pre-excitation site was determined noninvasively from the measured cardiac magnetic fields. The location was in the same anatomic region as foun...

journal_title：Pediatric cardiology

authors： Nenonen J,Rovamo L,Toivonen L,Ilmoniemi R,Järvinen A,Leiniö M,Montonen J,Nisula L

更新日期：1995-01-01 00:00:00

abstract：:We report a 6-year-old girl with superoinferior ventricles, criss-cross atrioventricular (AV) relationships with solitus atria, a D-loop, L-transposition of the great arteries, subpulmonary stenosis, but without a ventricular septal defect (VSD). The diagnosis was made by echocardiographic examination and was strength...

journal_title：Pediatric cardiology

authors： Alday LE,Juaneda E

更新日期：1993-10-01 00:00:00

abstract：:Acute respiratory distress syndrome (ARDS) in children after open heart surgery, although uncommon, can be a significant source of morbidity. Because high-frequency oscillatory ventilation (HFOV) had been used successfully with pediatric patients who had no congenital heart defects, this therapy was used in our unit. ...

journal_title：Pediatric cardiology

authors： Li S,Wang X,Li S,Yan J

更新日期：2013-08-01 00:00:00

abstract：:The current pulse-oximetry screening (POS) protocol for detection of critical congenital heart defects (CCHDs) is recommended only for newborns in well-infant and intermediate care nurseries, and there is no evidence-based protocol for infants discharged from the neonatal intensive care unit (NICU). The objectives of ...

journal_title：Pediatric cardiology

authors： Iyengar H,Kumar P,Kumar P

更新日期：2014-03-01 00:00:00

abstract：:Myocardial blood flow (MBF) was investigated in children (14.2 +/- 5.01 years) with "resolved" coronary involvement after the onset of Kawasaki disease and angiographically normal epicardial coronary arteries. Ten asymptomatic children with a history of Kawasaki disease had electrocardiography, echocardiography, and p...

journal_title：Pediatric cardiology

authors： Hauser M,Bengel F,Kuehn A,Nekolla S,Kaemmerer H,Schwaiger M,Hess J

更新日期：2004-03-01 00:00:00

abstract：:Sudden death accounts for up to 43% of all deaths in patients with familial dysautonomia (FD). The classic features of FD, namely, autonomic dysfunction, high blood pressure, and blood pressure labiality, are all risk factors for cardiac remodeling and hypertrophy. Myocardial remodeling and hypertrophy are independent...

journal_title：Pediatric cardiology

authors： Nussinovitch U,Katz U,Nussinovitch M,Blieden L,Nussinovitch N

更新日期：2009-11-01 00:00:00

abstract：:Our objective was to evaluate and highlight the significance of epigastric tenderness in children and adolescents with chest pain. In a 26-months period, patients who were referred for pediatri cardiology evaluation at Shiraz University of Medical Sciences with chief complaint of chest pain were studied. Patients with...

journal_title：Pediatric cardiology

authors： Sabri MR,Ghavanini AA,Haghighat M,Imanieh MH

更新日期：2003-01-01 00:00:00