Recent advances in the management of cystic fibrosis.

Abstract:

:Cystic fibrosis is a disease that still causes a reduced life expectancy. The treatment burden remains high for affected individuals with often a combination of multiple oral and inhaled medications, as well as physiotherapy, required on a daily basis. In this article, we look at an overview of the pathogenesis, how this might lead to treatment options and look at some of the available new therapies, all in the aim of increasing life expectancy and reducing treatment burden.

journal_name

Arch Dis Child

authors

Davies JC,Ebdon AM,Orchard C

doi

10.1136/archdischild-2013-304400

subject

Has Abstract

pub_date

2014-11-01 00:00:00

pages

1033-6

issue

11

eissn

0003-9888

issn

1468-2044

pii

archdischild-2013-304400

journal_volume

99

pub_type

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