Intestinal lymphangiectasia. Long-term results with MCT diet.

Abstract:

:The clinical course of 6 children with primary intestinal lymphangiectuasia who have been treated with low fat medium chain triglyceride-supplemented diets for between 3 and 8 years (4 for longer than 5 years) is described. Though laboratory findings indicate continuing chyle leak, evidence for long-term benefit from dietary treatment is provided by symptomatic relief while on the diet, clinical relapse upon relaxation of t,e regimen, and improvement in growth rates. In most patients the underlying lymphatic defect, and thus the need for dietary treatment, appears to be permanent.

journal_name

Arch Dis Child

authors

Tift WL,Lloyd JK

doi

10.1136/adc.50.4.269

subject

Has Abstract

pub_date

1975-04-01 00:00:00

pages

269-76

issue

4

eissn

0003-9888

issn

1468-2044

journal_volume

50

pub_type

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