Abstract:
:Behçet disease (BD) is an inflammatory disorder of unknown origin. We present here an unusual case of juvenile Behçet with hemoptysis due to large pulmonary artery aneurysms (PAA), large intra-cardiac thrombus and prolonged fever, which posed several therapeutic challenges. In this case, a 14-year-old boy was admitted with a 3-month history of fever, painful oral ulcers, skin rash and intermittent hemoptysis. A high resolution helical computed tomography angiogram demonstrated thrombi in the right ventricle, two large aneurysms located in the right lung and two smaller ones in the left. The patient was successfully treated with colchicine, prednisone, cyclophosphamide and enoxaparine. A discussion about PAA and intracardiac thrombi and their role in BD is provided in this case.
journal_name
Rheumatol Intjournal_title
Rheumatology internationalauthors
Vivante A,Bujanover Y,Jacobson J,Padeh S,Berkun Ydoi
10.1007/s00296-008-0730-5subject
Has Abstractpub_date
2009-03-01 00:00:00pages
575-7issue
5eissn
0172-8172issn
1437-160Xjournal_volume
29pub_type
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