Scapulo-peroneal muscular atrophy. Full autopsy report. Unusual findings in the anterior horn of the spinal cord. Lipid storage in muscle.

abstract：:A 21-year-old male developed back pain, fever, and rapidly progressive quadriparesis. Lumbar tap yielded frank pus which was confirmed on magnetic resonance imaging (MRI) to be located mainly in the cervical epidural space. Conservative antibiotic remedy was partially effective for restoration of the neurological defi...

journal_title：European neurology

authors： Fukui T,Ichikawa H,Kawate N,Nozawa T,Sugita K

更新日期：1992-01-01 00:00:00

abstract：BACKGROUND:The profile and degree of cognitive impairment in Multiple System Atrophy (MSA) and the impact of sleep disorders, REM sleep behavior disorder (RBD) in particular, in parkinsonism-related cognitive deficits are currently being debated. SUMMARY:We reviewed the cognitive, affective and sleep findings in MSA a...

journal_title：European neurology

authors： Stanzani-Maserati M,Gallassi R,Calandra-Buonaura G,Alessandria M,Oppi F,Poda R,Sambati L,Provini F,Cortelli P

更新日期：2014-01-01 00:00:00

abstract：BACKGROUND AND AIMS:Cardiac myxomas may present clinically with many different features. Since highly effective treatments exist, it is important that they are diagnosed quickly in order to avoid further complications. Our aim was to determine the influence of neurological presentation in diagnosis and prognosis of car...

journal_title：European neurology

authors： Alvarez-Sabín J,Lozano M,Sastre-Garriga J,Montoyo J,Murtra M,Abilleira S,Codina A

更新日期：2001-01-01 00:00:00

abstract：INTRODUCTION:Cardiovascular autonomic failure is commonly associated with Parkinson's disease (PD), affecting the daily lives of patients. Rotigotine was recently reported not to influence cardiovascular autonomic responses in contrast to other dopaminergic drugs. The effect of rotigotine on daily blood pressure (BP) f...

journal_title：European neurology

authors： Oka H,Nakahara A,Umehara T

更新日期：2018-01-01 00:00:00

abstract：:In 167 patients with cerebrovascular disorders 323 carotid bifurcations were investigated by Duplex ultrasound. In 100 of these patients, additionally intravenous digital subtraction angiography (DSA) was performed and in 35 patients, also intra-arterial DSA was carried out. In 32 patients all three procedures were pe...

journal_title：European neurology

authors： Boné G,Ladurner G,Karas I,Grobovschek M,Punzengruber J

更新日期：1988-01-01 00:00:00

abstract：:We present a long-term follow-up examination concerning patients with isolated extra-ocular muscle involvement in thyroid-related orbitopathy. Within the previous 13 years we observed 7 patients with endocrine orbitopathy and marked myopathy of the extra-ocular muscles. Five of these patients had no detectable proptos...

journal_title：European neurology

authors： Gerlach M,Ferbert A

更新日期：2008-01-01 00:00:00

abstract：:Early traumatic epilepsy, whose frequency is rather high, especially in children, is usually characterized by focal motor seizures (57%) or by generalized seizures (43%). The association of both running and laughing fits in the same patient on the contrary is quite exceptional, as only three cases have been reported i...

journal_title：European neurology

authors： Jandolo B,Gessini L,Occhipinti E,Pompili A

更新日期：1977-01-01 00:00:00

abstract：:Ten patients with left-sided visuospatial neglect due to cerebrovascular accident were monitored using the Behavioural Inattention Test (BIT) at weekly intervals, on a long-term basis. The novel finding was that some patients showed occasional but transitory marked improvement in their visuospatial neglect at times pr...

journal_title：European neurology

authors： Small M,Ellis S

更新日期：1994-01-01 00:00:00

abstract：:Reduction in caeruloplasmin (Cp) levels is sometimes found in other sporadic movement disorders, not limited to Wilson's disease (WD). Serum levels of Cp, copper, iron and gamma-glutamyl transpeptidase were measured in 71 patients with various diagnoses of movement disorders, including Parkinson's disease (PD), atypic...

journal_title：European neurology

authors： Ling H,Bhidayasiri R

更新日期：2011-01-01 00:00:00

abstract：:This study aimed at examining correlations between quantitative REM sleep EEG, regional cerebral blood flow measured by single photon emission computerized tomography (SPECT) and global cognitive functioning in nine patients with mild to moderate Alzheimer's disease. REM sleep EEG was not correlated with SPECT measure...

journal_title：European neurology

authors： Montplaisir J,Petit D,McNamara D,Gauthier S

更新日期：1996-01-01 00:00:00

abstract：:Camptocormia (bent spine syndrome, cyphose hystérique) is an abnormality characterized by severe forward flexion of the thoracolumbar spine which typically increases during walking or standing and completely disappears in supine position. Camptocormia can be due to central nervous system diseases, such as Parkinson's ...

journal_title：European neurology

authors： Finsterer J,Strobl W

更新日期：2010-01-01 00:00:00

abstract：:In a previous retrospective study, we demonstrated that falls are common and often injurious in dominant spinocerebellar ataxias (SCAs) and that nonataxia features play an important role in these falls. Retrospective surveys are plagued by recall bias for the presence and details of prior falls. We therefore sought to...

journal_title：European neurology

authors： Fonteyn EM,Schmitz-Hübsch T,Verstappen CC,Baliko L,Bloem BR,Boesch S,Bunn L,Giunti P,Globas C,Klockgether T,Melegh B,Pandolfo M,Schöls L,Timmann D,van de Warrenburg BP

更新日期：2013-01-01 00:00:00

abstract：OBJECTIVES:Cerebral arteriovenous malformations (AVMs) harbor a network of abnormal vasculatures, namely the nidus between arterial and venous components. The pressure gradient between these two components results in abnormal high-velocity arteriovenous shunts flowing through the nidus and alternate intracranial hemody...

journal_title：European neurology

authors： Chuang YM,Guo W,Lin CP

更新日期：2010-01-01 00:00:00

abstract：BACKGROUND:Dizziness and vertigo are frequent complaints of outpatients in the neurological department. Our objective was to explore the epidemiological category and clinical features of patients with dizziness or vertigo in the neurological outpatient department of a tertiary hospital. METHODS:We consecutively recrui...

journal_title：European neurology

authors： Pan Q,Zhang Y,Long T,He W,Zhang S,Fan Y,Zhou J

更新日期：2018-01-01 00:00:00

abstract：:Previous findings regarding the role of TNF-alpha-308 gene polymorphism in multiple sclerosis (MS) are contradictory. The aim of this study was to investigate the possible influence of TNF-alpha-308 polymorphism on MS susceptibility and the MS disease process in a Croatian and Slovenian population. Genotyping was perf...

journal_title：European neurology

authors： Ristić S,Lovrecić L,Starcević-Cizmarević N,Brajenović-Milić B,Sega Jazbec S,Sepcić J,Kapović M,Peterlin B

更新日期：2007-01-01 00:00:00

abstract：:In the last 2 years we have systematically treated 31 sleep apnea patients with 25-50 mg imipramine HCl given 30 min before bedtime. Imipramine treatment was attempted for nonoverweight patients with negative ear, nose and throat (ENT) findings and for patients who had not responded to weight reduction or ENT surgery ...

journal_title：European neurology

authors： Rubin AH,Alroy GG,Peled R,Lavie P

更新日期：1986-01-01 00:00:00

abstract：:Temporal arteritis (TA) is a vasculitis involving mainly cranial branches of the aorta that can lead to ischemic complications such as amaurosis or ischemic stroke. Increment in the platelet count has been described in the acute period of the disease. We studied retrospectively the platelet count in patients with TA, ...

journal_title：European neurology

authors： Gonzalez-Alegre P,Ruiz-Lopez AD,Abarca-Costalago M,Gonzalez-Santos P

更新日期：2001-01-01 00:00:00

abstract：:The lupus anticoagulant, an immunoglobulin of the IgG or IgM class, is one of a group of antiphospholipid antibodies. Although an anticoagulant in vitro, its action in vivo is that of a procoagulant. This procoagulant activity may involve many organ systems including the nervous system. Thus far cerebral thrombosis, s...

journal_title：European neurology

authors： Englert H,Derue G,Hughes GR

更新日期：1985-01-01 00:00:00

abstract：:Reviewing the angiograms of 100 patients with RIA or stroke we found intracranial lesions in 67%, extracranial lesions in 64%, and normal angiograms in 13% of the cases. Risk factors occurred more often as the angiographic lesions were more extensive. These findings confirm the importance of angiographic examination o...

journal_title：European neurology

authors： van Oudenaarden WF,Tans JT,Hoogland PH

更新日期：1980-01-01 00:00:00

abstract：BACKGROUND:We aimed at measuring the positive predictive value (PPV) of data in the French Hospital Medical Information Database (FHD). SUMMARY:This retrospective multicenter study included 31 hospitals from where 56 hospital stays were randomly selected among all hospitalizations for the years 2009 and 2010 with at l...

journal_title：European neurology

authors： Giroud M,Hommel M,Benzenine E,Fauconnier J,Béjot Y,Quantin C,FRESCO Study.

更新日期：2015-01-01 00:00:00

abstract：:The serum concentration of S-100B is reported to reflect the severity of brain damage. The purpose of this study was to determine whether elevated serum S-100B concentrations were related to neuropsychological test performance of patients in the subacute phase of recovery from mild traumatic brain injury (TBI). S-100B...

journal_title：European neurology

authors： Stapert S,de Kruijk J,Houx P,Menheere P,Twijnstra A,Jolles J

更新日期：2005-01-01 00:00:00

abstract：BACKGROUND:Profound cellular and biochemical remodeling processes occur in the brain following an ischemic stroke, raising the possibility that we may be able to promote neurological recovery by harnessing the brain's endogenous recovery processes with pharmacological or cell-based therapies. There is a compelling body...

journal_title：European neurology

authors： Hermann DM,Chopp M

更新日期：2014-01-01 00:00:00

abstract：:L-Dopa pioneered the symptomatic therapy of Parkinson's disease. While this treatment proved effective in the treatment of parkinsonian akinesia, rigidity and tremor, prolonged L-dopa treatment was often noted to result in dyskinesia, psychosis and 'on-off' phenomena. This increasing disability of L-Dopa-treated parki...

journal_title：European neurology

authors： Kuno S

更新日期：1994-01-01 00:00:00

abstract：:Two cases are presented with a long clinical history of multiple sclerosis (MS) before the diagnosis of an intracranial brain tumor. In the subsequent brain autopsy, however, both cases presented a diffusely growing anaplastic astrocytoma, only, and no changes similar to MS were seen. Diffuse tumor growth was noted in...

journal_title：European neurology

authors： Röyttä M,Latvala M

更新日期：1986-01-01 00:00:00

abstract：BACKGROUND/AIM:Although most late-onset seizures (LS) appear within 2 years after stroke, some of them occur later and their characteristics are unknown. The aim of this study was to compare the characteristics of patients with very-late-onset seizures (VLS) to those with early-onset seizures (ES) and those with LS. P...

journal_title：European neurology

authors： De Reuck J,Sieben A,Van Maele G

更新日期：2008-01-01 00:00:00

abstract：:T lymphocytes were determined according to their ability to form rosettes with sheep erythrocytes, in cerebrospinal fluid (CSF) from 120 patients, and in peripheral blood from 59 patients. Normal CSF contained 74.9 +/- 9.6% T lymphocytes. Increased T lymphocyte percentage was found in CSF from patients with active mul...

journal_title：European neurology

authors： Naess A

更新日期：1979-01-01 00:00:00

abstract：:Nicorandil, an ATP-sensitive potassium (KATP) channel opener, is known to have protective effects on ischemic injury in heart and brain. One of the most important protective mechanisms is the anti-apoptotic effect on cardiomyocytes and neurons. This study explored the anti-apoptotic effect of nicorandil against neurot...

journal_title：European neurology

authors： Kong J,Ren G,Jia N,Wang Y,Zhang H,Zhang W,Chen B,Cao Y

更新日期：2013-01-01 00:00:00

abstract：:The binding of the dopamine uptake inhibitor [3H]GBR-12935 to postmortem putamen from a control group and patients with Alzheimer's disease/senile dementia of Alzheimer type (AD/SDAT) or vascular dementia (VD) was studied. The binding density (Bmax) in AD/SDAT was significantly reduced to 50% of control. A reduction o...

journal_title：European neurology

authors： Allard P,Alafuzoff I,Carlsson A,Eriksson K,Ericson E,Gottfries CG,Marcusson JO

更新日期：1990-01-01 00:00:00

abstract：:The effect of thoracic duct lymph drainage (5-34 days) in 12 patients with myasthenia gravis on muscular function has been followed for 5-43 months. Among the results obtained were: (1) During the drainage the myasthenic symptoms decreased markedly after 1-4 days and remained so during the drainage. (2) The doses of c...

journal_title：European neurology

authors： Bergström K,Franksson C,Matell G,Nilsson BY,Persson A,von Reis G,Stensman R

更新日期：1975-01-01 00:00:00

abstract：BACKGROUND:One of the hallmarks of the α-synucleinopathies is the degeneration of the autonomic nervous system. SUMMARY:This review discusses the diagnosis and management of cardiovascular autonomic failure within the context of the α-synucleinopathies. In addition, it outlines the utility of various laboratory assess...

journal_title：European neurology

authors： Sambati L,Calandra-Buonaura G,Doria A,Cortelli P

更新日期：2015-01-01 00:00:00