The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant.

Abstract:

:We present the case of a 14-year-old male with a history of small bowel transplantation for long segment Hirschsprung's disease who underwent Duhamel ileorectal pull-through procedure. In post-transplant, the patient had no restrictions and was not TPN-dependent. To improve his quality of life, he and his family were interested in closing the ileostomy and undergoing pull-through surgery. The complexity of the case includes the presence of an aganglionic rectal segment-a short root of the mesentery due to the small bowel transplant-and significant immunosuppression. At the moment, he is continent, doing well, and has not had any remarkable complications.

journal_name

Pediatr Surg Int

authors

Jazi FS,Sinclair TJ,Thorson CM,Castillo R,Bonham AC,Esquivel CO,Bruzoni M

doi

10.1007/s00383-017-4216-y

subject

Has Abstract

pub_date

2018-01-01 00:00:00

pages

113-116

issue

1

eissn

0179-0358

issn

1437-9813

pii

10.1007/s00383-017-4216-y

journal_volume

34

pub_type

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