Abstract：
INTRODUCTION:The Morgagni hernia (MH) accounts for 3-4% of congenital diaphragmatic hernias. There is a paucity of data regarding this rare defect. The purpose of this study is to describe the characteristics of children with MH, surgical approaches for repair, and patient outcomes. METHODS:Pediatric patients (ages 0-18) with a MH from 2002 to 2014 at a single, freestanding pediatric hospital were retrospectively reviewed. Patient presentation, demographics, operative methods and findings, and outcomes were evaluated. RESULTS:Twenty-six infants and children with a congenital MH were treated. There were 20 males (77%) and six females (23%) with a median age at diagnosis of 14.75 months (range 1 week to 13 years). Half were symptomatic. Sixteen hernias were repaired laparoscopically, nine by an open approach, and one laparoscopic converted to open. Colon was the most commonly herniated organ (N = 14). Hernia sacs were found in 22 patients of which, 20 were resected. Two patients underwent treatment with ECLS. There was one mortality in a patient who underwent repair on ECLS in the setting of an omphalocele and SVC obstruction. There were no recurrences in our sample. CONCLUSION:In this series, congenital MH appears to have a male predominance, frequently presents with pulmonary symptoms, and has excellent outcomes regardless of operative approach.
journal_name
Pediatr Surg Intjournal_title
Pediatric surgery internationalauthors
Golden J,Barry WE,Jang G,Nguyen N,Bliss Ddoi
10.1007/s00383-017-4078-3subject
Has Abstractpub_date
2017-07-01 00:00:00pages
771-775issue
7eissn
0179-0358issn
1437-9813pii
10.1007/s00383-017-4078-3journal_volume
33pub_type
杂志文章abstract：:The Thomsen-Friedenreich cryptantigen (TCA) is located on the surface of all red cells, but is concealed by a layer of neuraminic acid. When bacteria that produce neuraminidase disrupt this coating, the TCA can be exposed and activated. If blood products containing antibody to the TCA are subsequently administered, ha...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s003830050488
更新日期：1998-12-01 00:00:00
abstract：UNLABELLED:Anorectal malformation (ARM) is a group of significant birth defects with geographic variation in incidence, individual phenotypes and regional geographic subtypes occurring in approximately 1:5,000 live births. Anorectal atresia with gross terminal colonic distension in the presence of an absent anal canal ...
journal_title：Pediatric surgery international
pub_type： 杂志文章,多中心研究
doi：10.1007/s00383-013-3346-0
更新日期：2013-12-01 00:00:00
abstract：AIM:In chick embryos, administration of cadmium (Cd) induces ventral body wall defects (VBWD) similar to human omphalocele. It has been shown that failure of proper VBW formation may be due to disruption of somite development during early embryogenesis. In the VBWD chick model, Cd causes abnormal cell death in the somi...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-012-3202-7
更新日期：2013-01-01 00:00:00
abstract：PURPOSE:The purpose of this study was to test the susceptibility of human hepatoblastoma and neuroblastoma cells to photodynamic diagnostics (PDD) and photodynamic therapy (PDT) using 5-aminolevulinic acid (5-ALA) as a photosensitizer. METHODS:Cell cultures of human hepatoblastoma (HuH6) and neuroblastoma (MHH-NB-11) ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-008-2275-9
更新日期：2008-12-01 00:00:00
abstract：:To assess the relation between continence and the manometric and endosonographic state of the anorectal segment after surgery for anorectal anomalies (ARA), 33 adolescents operated upon for ARA and 14 controls were examined. Seventeen patients had low and 16 intermediate or high ARA. Fecal continence was recorded, and...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/BF01258715
更新日期：1997-09-01 00:00:00
abstract：:We present the case of a 14-year-old male with a history of small bowel transplantation for long segment Hirschsprung's disease who underwent Duhamel ileorectal pull-through procedure. In post-transplant, the patient had no restrictions and was not TPN-dependent. To improve his quality of life, he and his family were ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-017-4216-y
更新日期：2018-01-01 00:00:00
abstract：:"Variants of Hirschsprung's disease" are conditions that clinically resemble Hirschsprung's disease (HD), despite the presence of ganglion cells in rectal suction biopsies. The diagnosis and management of these patients can be challenging. Specific histological, immunohistochemical and electron microscopic investigati...
journal_title：Pediatric surgery international
pub_type： 杂志文章,评审
doi：10.1007/s00383-013-3351-3
更新日期：2013-09-01 00:00:00
abstract：:A case of an epigastric giant-cell fibroblastoma is reported in a 6-year-old girl who had undergone a bone-marrow transplant for severe combined immunodeficiency secondary to adenosine deaminase deficiency. A small subcutaneous nodule had been excised from the epigastrium at age 12 months. ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-002-0827-y
更新日期：2003-08-01 00:00:00
abstract：AIM:The aim of this study was to examine the relationship between birth weight, pulmonary artery (PA) size, and outcome in congenital diaphragmatic hernia (CDH) to establish if PA size has prognostic value. METHODS:The subjects for this study were 39 consecutive left-sided CDH patients treated at our institution accor...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-011-2899-z
更新日期：2011-08-01 00:00:00
abstract：:Antral web is a rare cause of gastric-outlet obstruction. We report a case of gastric antral web with intermittent vomiting in a 10-year-old girl who received medical treatment for 6 months. The literature on this anomaly is reviewed with respect to differential diagnosis on the basis of upper gastrointestinal radiogr...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s003839900317
更新日期：2000-01-01 00:00:00
abstract：:Children with pyometrocolpos due to distal vaginal atresia may present as acutely ill, with severe obstructive uropathy and septicemia. In such patients the clinical course is markedly improved by urgent drainage of the infected cystic mass, and a temporary drainage procedure is required to allow local findings of inf...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-004-1323-3
更新日期：2005-03-01 00:00:00
abstract：AIM:To determine if follow-up by consultant pediatric surgeons (CPS) affects morbidity due to incarceration (INC) in children with indirect inguinal hernia (IH). METHODS:We educate parents so they can identify possible INC and advise them to attend our emergency department anytime for immediate review by on-call CPS. ...
journal_title：Pediatric surgery international
pub_type： 杂志文章,多中心研究
doi：10.1007/s00383-011-3005-2
更新日期：2012-01-01 00:00:00
abstract：:Repair of giant inguino-scrotal hernia (GISH) in male infants is a difficult operation, even in experienced hands. It requires an immaculate technique to avoid known complications such as tearing of the sac, injury to delicate testicular vessels and dividing of vas deferens. Moreover, a recurrence rate of 9% is noted ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-008-2145-5
更新日期：2008-06-01 00:00:00
abstract：:Intestinal neuronal dysplasia is a controversial form of dysganglionosis that has been described both as an isolated disorder and in association with Hirschsprung's disease. It has been blamed for the bad outcome of bowel function in patients operated on for Hirschsprung's disease. According to various authors, intest...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-003-1035-0
更新日期：2003-12-01 00:00:00
abstract：:To determine the incidence of cystic fibrosis (CF) in neonates with intestinal obstruction (NIO) secondary to meconium ileus (MI), jejunoileal atresia (JA), meconium plug syndrome (MPS), volvulus (V), and meconium peritonitis (MP) and analyze the correlation of ultrasonographic (US) signs with CF in NIO with a prenata...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-002-0781-8
更新日期：2003-04-01 00:00:00
abstract：:This study describes a subset of patients with posterior urethral valves (PUV) who presented late in childhood. The objective was to identify factors that lead to back-pressure effects on the upper tracts, which persist in spite of adequate valve ablation in some patients, and seek factors that may preserve the upper ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s003830050384
更新日期：1998-09-01 00:00:00
abstract：:A boy with a history of esophageal atresia repair received an esophagoesophagostomy at 14 months for a severe refractory anastomotic stricture, which had already required repeated balloon dilation with intralesional dexamethasone injection. Anastomotic leakage and stricture was again evident after the second surgery, ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-009-2367-1
更新日期：2009-06-01 00:00:00
abstract：:This study deals with the advancement process of neuroblastoma through clinical observations and circulating tumor cell exploration. Clinical feature, tumor biology, and circulating tumor cell detected by the previously described polymerase chain reaction (PCR) method were analyzed in 31 patients with advanced neurobl...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-005-1503-9
更新日期：2005-11-01 00:00:00
abstract：:A new technique for primary reconstruction of a congenital anterior urethral diverticulum is described. This operation eliminates the obstruction caused by the distal lip of the diverticulum and at the same time strengthens the unsupported urethral wall using tissue from the walls of the diverticulum. It has been used...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s003830050582
更新日期：1999-01-01 00:00:00
abstract：PURPOSE:The aim of this study was to analyze the outcomes of children added to the waiting list for deceased donor liver transplantation (DDLT) and the results of DDLT in a single Japanese center. METHODS:Forty-seven children were listed on the organ allocation system for DDLT. The priority points related to the medic...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-013-3381-x
更新日期：2013-11-01 00:00:00
abstract：AIM:The objective of the present study was to evaluate the diagnostic methods, concomitant organ injuries, factors affecting mortality and morbidity, treatment methods, and outcomes of patients treated for traumatic gastrointestinal (GI) perforation. MATERIALS AND METHODS:We conducted a retrospective review of the med...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-016-3963-5
更新日期：2016-11-01 00:00:00
abstract：INTRODUCTION:Objectively evaluating the lack of bowel control (fecal incontinence) continues to be a challenge. Many have attempted to measure the severity of fecal incontinence and to evaluate its impact on the quality of life by developing standardized scoring systems. Some of these systems have been validated but no...
journal_title：Pediatric surgery international
pub_type： 杂志文章,评审
doi：10.1007/s00383-016-3909-y
更新日期：2016-08-01 00:00:00
abstract：PURPOSE:Neuroblastoma is a biological, genetic and morphological heterogeneous tumor with a variable clinical course. NCAM is a cell adhesion molecule belonging to the immunoglobulin superfamily with structural similarities to cell adhesion molecule L1. The aim of this study was to determine the expression of NCAM in n...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-008-2264-z
更新日期：2008-12-01 00:00:00
abstract：PURPOSE:We investigated the associations between hsMAD2 mRNA expression in tumor cells and sensitivity to paclitaxel or patient prognosis in neuroblastoma. METHODS:Fifty-one formalin-fixed paraffin-embedded tumor samples were manually microdissected to collect tumor cells, and RNA was purified. Nineteen clinical sampl...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-010-2780-5
更新日期：2011-02-01 00:00:00
abstract：:Two patients who presented with a history of right inguinal hernia and a third with an impalpable left testis were found to have transverse testicular ectopia. Both testes were fixed in their own scrotum, through a modified Ombredanne operation in two patients and a subdartos pouch in one. ...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：
更新日期：1997-02-01 00:00:00
abstract：:Manual reduction with the index finger (modified Hutchinson's maneuver) enabling simple and safe manual reduction of infantile intussusception is described. The procedure was used in four patients, two boys and two girls, ranging in age from 2 to 15 months, as greater than normal compression was necessary and/or seros...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s003830050301
更新日期：1998-03-01 00:00:00
abstract：PURPOSE:Laparoscopic-assisted anorectoplasty (LAARP) is a minimally invasive procedure in which the levator ani muscle is left to potentially improve postoperative fecal continence. This study aimed to retrospectively evaluate postoperative complications and long-term outcomes of fecal continence after LAARP and compar...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-018-4323-4
更新日期：2018-10-01 00:00:00
abstract：OBJECTIVE:For esophagus tissue engineering, isolation and proliferation of esophageal epithelial cells (EEC) is a pre-requisite for scaffold seeding to create constructs. The aim of this study was to sort EEC expressing cytokeratin markers and their proliferative subpopulations; also, to investigate the viability of di...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-009-2512-x
更新日期：2010-01-01 00:00:00
abstract：PURPOSE:Although Rex shunt is an effective treatment for extrahepatic portal venous obstruction (EHPVO), 4-20% children develop rebleeding postoperatively. This study was used to evaluate the surgical treatment of rebleeding after Rex shunt in our center. METHOD:From June 2008 to Jan 2017, 12 of 122 children with EHPV...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-018-4246-0
更新日期：2018-05-01 00:00:00
abstract：BACKGROUND/PURPOSE:To determine the frequency and characteristics of suspected cow's milk protein allergy (CMPA) in infants with gastroschisis and response to change in milk. METHODS:A retrospective cohort study of 111 consecutive infants with gastroschisis. RESULTS:64 episodes suggesting non-IgE-mediated CMPA occurr...
journal_title：Pediatric surgery international
pub_type： 杂志文章
doi：10.1007/s00383-015-3664-5
更新日期：2015-03-01 00:00:00
