Abstract:
:Panniculitis rarely occurs in the course of systemic lupus erythematosus (SLE). When it occurs, it is thought to be mainly lupus erythematosus panniculitis (LEP). Here we describe a 32-year old Japanese woman with chronic SLE, who simultaneously presented facial lymphocytic lobular panniculitis and pancytopenia due to haemophagocytic syndrome. She showed several auto-antibodies against trilineage haematopoetic cells, an anti-cardiolipin antibody, and no evidence of viral infection, indicating that her haemophagocytic syndrome might be autoimmune-associated haemophagocytic syndrome. The panniculitis and haemophagocytic syndrome presented simultaneously, and these manifestations were dramatically improved with corticosteroid therapy; therefore, the lymphocytic lobular panniculitis could be linked to autoimmune-associated haemophagocytic syndrome in this case.
journal_name
Lupusjournal_title
Lupusauthors
Deji N,Sugimoto T,Fujimoto T,Aoyama M,Takeda N,Sakaguchi M,Uzu T,Kashiwagi Adoi
10.1177/0961203307077560subject
Has Abstractpub_date
2007-01-01 00:00:00pages
363-5issue
5eissn
0961-2033issn
1477-0962pii
16/5/363journal_volume
16pub_type
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