Myasthenic neuromyopathy. An unusual neuromuscular disorder.

Abstract:

:4 cases with an identical neuromuscular disorder are presented. The disorder was characterized by slowly progressive weakness and wasting of the proximal muscles together with either ocular or bulbar symptoms, fatigability, positive tensilon test, myasthenic response on repetitive nerve stimulations, elevated serum creatine phosphokinase, and neuropathic and myopathic muscle pathology. All the patients showed a fairly good response to anti-ChE medications and steroid administration. Serum creatine phosphokinase levels returned to normal values after steroid therapy. Myasthenia, polymyositis or other neuromuscular disorders were discussed in the differential diagnosis.

journal_name

Eur Neurol

journal_title

European neurology

authors

Kinoshita M,Nakazato H,Wakata N,Satoyoshi E

doi

10.1159/000115454

subject

Has Abstract

pub_date

1982-01-01 00:00:00

pages

52-8

issue

1

eissn

0014-3022

issn

1421-9913

journal_volume

21

pub_type

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