[Arthogryposis multiplex congenita with neurogenic atrophy and brachydactyly (author's transl)].

abstract：:Transfusion-induced hemochromatosis remains a major therapeutic complication in the management of patients with chronic hemolytic anemias. Red cell units harvested with blood cell separators have an average estimated mean cell age of 30 days, compared to 60 days for unfractionated blood. Our initial experience with tr...

journal_title：Klinische Padiatrie

authors： Heim MU,Eckstein R,Mittermüller H,Haas RJ,Schmidt P,Graebner E,Pape W,Mempel W

更新日期：1985-03-01 00:00:00

abstract：:Ten to fifteen percent of infants of myasthenic mothers develop neonatal myasthenia independent of the severity of the maternal disease. The antiacetylcholin receptor-protein antibodytiter (AChR-AK) was followed through the first twelve months in a boy who's mother suffered from myasthenia gravis (M.G.) since twelve y...

journal_title：Klinische Padiatrie

authors： Lischka A,Grisold W,Pollak A,Zeitelhofer J,Riegler R,Weninger M

更新日期：1984-09-01 00:00:00

abstract：:More than 40 years ago, Toxocara ssp. was identified as the cause of larva migrans visceralis and ocular larva migrans, which mainly affect infants and children. Although widespread in most parts of the world, the parasitic disease is rarely diagnosed in Germany. Focusing on clinical and pathophysiological similaritie...

journal_title：Klinische Padiatrie

authors： Hohenschild S

更新日期：1998-05-01 00:00:00

abstract：:160 children aged 1 to 12 years with clinical diagnosis of bacterial pharyngitis and/or tonsillitis were treated either with cefixime ready-to-use-suspension or penicillin V in an open, controlled and randomized multicenter study. Before treatment a rapid antigen detection test was accomplished and throat swabs were t...

journal_title：Klinische Padiatrie

authors： Adam D,Hostalek U,Tröster K

更新日期：1996-09-01 00:00:00

abstract：:The German Society of Pediatric Oncology (GPO) designed a cooperative study to improve the outlook of patients with malignant (testicular) germ cell tumors. According to stage and histology of the tumor different surgical approaches to retroperitoneal lymphadenectomy are suggested. Local radiotherapy is not recommende...

journal_title：Klinische Padiatrie

authors： Haas RJ,Brämswig J,Göbel U,Harms D,Janka G,Weissbach L

更新日期：1983-05-01 00:00:00

abstract：:Radionuclide lumbar cisternography with 111In-DTPA was utilized as a bedside procedure to evaluate CSF dynamics and the patency of the ventricular system in 29 preterm infants with hydrocephalus. Serial images of the brain were obtained at 0, 1, 2, 6, 24 and 48 hours after instillation of the isotope in the lumbar sub...

journal_title：Klinische Padiatrie

authors： Roloff DW

更新日期：1985-03-01 00:00:00

abstract：:In case of painful scoliosis, a search for etiologic factors in the vertebral spinal canal and adjacent structures should be made. MRI with Gadolinium is useful to look for various pathology in and around the spine in particular of spinal cord. CT scanning is indispensible for bony details. Thus CT and MRI are complem...

journal_title：Klinische Padiatrie

authors： Hoeffel C,Gaucher H,Hoeffel JC,Galloy MA,Arnould V

更新日期：1997-03-01 00:00:00

abstract：:Autoimmune hemolytic anaemia (AIHA) in childhood is associated with antibodies produced by the patient himself, which coat his red cells causing their hemolysis. Although in some cases no underlying disease could be found, in the majority of children a virus etiology is apparent. There are very few reports regarding t...

journal_title：Klinische Padiatrie

authors： Haas RJ,Pöschl U,Christ M,Schaub J,Belohradsky BH

更新日期：1977-05-01 00:00:00

abstract：:The integration of colleagues from psychosocial occupations into the traditional team of doctors and nurses demands a holistic treatment concept, the general desire for interdisciplinary action, and readiness for patience in the process of mutual learning. The acceptance of the psychosocial services by the patient and...

journal_title：Klinische Padiatrie

authors： Janssen F

更新日期：1989-07-01 00:00:00

abstract：:From 1975-1986 6 boys with congenital nephrogenic diabetes insipidus were diagnosed at the age of 3 months to 10 years. Symptoms appeared within the first few weeks of life. The diagnosis was confirmed by polyuria, low urinary osmolality (97-225 mosm/kg H20), hypernatraemia (max. 171 mmol/l) and the missing response t...

journal_title：Klinische Padiatrie

authors： Kaulitz R,Brodehl J

更新日期：1989-11-01 00:00:00

abstract：BACKGROUND:The prevalence of asthma and overweight/obesity in children and adolescents is continuously increasing over the last decades. It remains unclear if overweight/obesity raises the risk of developing asthma or if an uncontrolled asthma increases the risk of developing overweight/obesity by restricting physical ...

journal_title：Klinische Padiatrie

authors： Schmauck-Gómez JS,Menrath I,Kaiser MM,Herz A,Kopp MV

更新日期：2016-07-01 00:00:00

abstract：:The Austrian Screening Program performed during the last 12 years 5,833.381 tests in 1,003.841 newborns to detect at last 10 different disorders. 225 cases were uncovered: 81 PKU, 1 Dihydropteridine-Reductase-Deficiency, 37 Hyperphenylalaninemias of long duration, 23 Galactosemias by Transferase deficiency, 6 by Kinas...

journal_title：Klinische Padiatrie

authors： Thalhammer O,Scheibenreiter S,Knoll E,Wehle E,Schön R

更新日期：1980-11-01 00:00:00

abstract：:During angiogenesis new blood vessels sprout from an existing vascular bed. This is a prerequisite for tumor growth beyond a certain size and for metastasis formation. Tumors produce a number of cytokines. The development of in vivo bio-assays for angiogenesis and in vitro analysis of endothelial cells permits charact...

journal_title：Klinische Padiatrie

authors： Hotfilder M,Nowak-Göttl U,Wolff JE

更新日期：1997-07-01 00:00:00

abstract：UNLABELLED:We present updated results of stem cell transplantation with highly purified stem cells from haploidentical parental donors and infection with human adenovirus (HAdV) post stem cell transplantation (SCT). Survival post SCT is primarily determined by relapse, infections and far less by GvHD or other transplan...

journal_title：Klinische Padiatrie

authors： Feuchtinger T,Richard C,Pfeiffer M,Neuhäuser F,Lücke J,Handgretinger R,Greil J,Bader P,Klingebiel T,Schlegel PG,Jahn G,Niethammer D,Lang P

更新日期：2005-11-01 00:00:00

abstract：:Prognostic factors to estimate the risk of relapse are crucial for risk-adapted therapy in acute lymphoblastic leukemia (ALL). In a cooperative multicenter treatment study for childhood ALL (COALL-03-85) the prognostic relevance of the bone marrow (BM) blast count at day 28 was evaluated. Treatment was adjusted to the...

journal_title：Klinische Padiatrie

authors： Janka-Schaub GE,Stührk H,Kortüm B,Graubner U,Jürgens H,Spaar HJ,Schöck V,Dohrn B,Bahr R,Winkler K

更新日期：1991-07-01 00:00:00

abstract：:The present paper reports on a striking increase in undesirable drug induced reactions during simultaneous administration of high-dosage phenobarbital and beta-lactam antibiotics to children in intensive care. In a 30-month study period, reactions which had to be classified as drug-induced were seen in 24 out of a tot...

journal_title：Klinische Padiatrie

authors： Harder S,Schneider W,Bae ZU,Bock U,Zielen S

更新日期：1990-11-01 00:00:00

abstract：:In approximately 10% of the children suffering from juvenile chronic arthritis (JCA), rheumatic iridocyclitis was also diagnosed. In 90 JCA and iridocyclitis patients we studied relative risk, clinical course and prognosis by means of several clinical and immunological parameters. Antinuclear antibodies (ANA), selecti...

journal_title：Klinische Padiatrie

authors： Michels H,Schuchmann L,Truckenbrodt H,Renz K

更新日期：1982-03-01 00:00:00

abstract：BACKGROUND:Alcoholism during pregnancy is one of the most common factors in western societies causing persisting congenital and multiple physical as well as neurological impairments. Finding the diagnosis at first sight puts medical professionals into a demanding situation. Therefore the objective of this study was to ...

journal_title：Klinische Padiatrie

authors： Alex K,Feldmann R

更新日期：2012-03-01 00:00:00

abstract：:Aim of this study was to describe the course of perinatal factors in neonates with meconium aspiration syndrome (MAS) from 1990 to 2010 and to determine risk factors for a severe course of the disease.All neonates with MAS hospitalized in our level III neonatal intensive care unit from 1990 to 2010.Retrospective analy...

journal_title：Klinische Padiatrie

authors： Hofer N,Jank K,Resch E,Urlesberger B,Reiterer F,Resch B

更新日期：2013-12-01 00:00:00

abstract：BACKGROUND:Thyroglossal duct cysts arise from mucus production in an incomplete regressed thyroglossal duct. Often they are only noticed in case of infection or secondary fistulation. The operative management is a Sistrunk procedure. METHOD AND PATIENTS:In a retrospective study we analyse 26 patients aged 0,3 - 10 yea...

journal_title：Klinische Padiatrie

authors： von Bismarck S,Höllwarth ME

更新日期：2001-09-01 00:00:00

abstract：:We report of an previously unpublished combination of partial trisomy 9 and a membranous pulmonary atresia with a large conotruncal ventricular septal defect. The dystrophic female, term newborn presented after delivery with microcephaly, prominent nose and several other facial and skeletal deformities. The echocardio...

journal_title：Klinische Padiatrie

authors： Nekarda T,Kececioglu D,Kehl HG,Gehrmann J,Miny P,Vogt J

更新日期：1997-05-01 00:00:00

abstract：:We analyzed episodes of peritonitis and/or sepsis associated with the idiopathic nephrotic syndrome (ns) in 23 children treated between 1975 and 1985 at our clinic. 37.5% of the children with infantile ns, 16% of those with steroidsensible ns, and 13.6% of those with steroidresistant ns developed peritonitis. Children...

journal_title：Klinische Padiatrie

authors： Feldhoff C,Kleine L,Bachmann H

更新日期：1988-01-01 00:00:00

abstract：:Since reliable diagnosis of cystic fibrosis (CF) is still difficult, the occurrence of serum markers CA 19-9, CA 50 and elastase 1 was analysed. Serum levels of CA 19-9, CA 50, CA 125 and elastase 1 were estimated in 54 CF patients as well as in a control group of 66 children of similar age suffering from various othe...

journal_title：Klinische Padiatrie

authors： Uhlenbruck G,Scheuring U,Dienst C,Kaiser D,Roth B,Skopnik H

更新日期：1988-03-01 00:00:00

abstract：:Standard for diagnosis of inflammatory bowel disease (IBD) is the endoscopy of the stomach and the intestine. Aim of this study was to determine the value of 18F-fluorodeoxyglucose positron emission tomography (FDG-PET) in pediatric patients with mild to moderate IBD.We included 23 children and adolescents between 8 a...

journal_title：Klinische Padiatrie

authors： Berthold LD,Steiner D,Scholz D,Alzen G,Zimmer KP

更新日期：2013-07-01 00:00:00

abstract：:The biologic behaviour of teratomas depends on various interdependent clinical and epidemiologic variables such as the age at diagnosis, sex, tumor site, histology which all correlate to different cytogenetic and molecular biologic aberrations. Thus, testicular teratomas of infancy are generally benign. Accordingly, p...

journal_title：Klinische Padiatrie

authors： Harms D,Zahn S,Göbel U,Schneider DT

更新日期：2006-11-01 00:00:00

abstract：:An increasing number of children with acute leukemia show cerebral complications. 10 out of 78 children treated in our hospital for acute lymphoblastic leukemia or non-Hodgkin's lymphoma who underwent remission induction therapy or were in continuous complete remission developed central nervous system complications. D...

journal_title：Klinische Padiatrie

authors： Ludwig R,Meyer E,Brandeis WE

更新日期：1980-07-01 00:00:00

abstract：HINTERGRUND: Die zeitliche Verzögerung zwischen Symptombeginn und Diagnose ist eine Herausforderung in der Behandlung von Kindern mit arteriell ischämischem Schlaganfall. Frühere Studien zur klinischen Präsentation beschäftigten sich v. a. mit kumulativen Symptomen. ZIELSETZUNG: Ziel dieser Studie ist es, mögliche Sym...

journal_title：Klinische Padiatrie

authors： Gerstl L,Weinberger R,von Kries R,Heinen F,Sebastian Schroeder A,Veronika Bonfert M,Borggräfe I,Tacke M,Vill K,N Landgraf M,Kurnik K,Olivieri M

更新日期：2018-10-01 00:00:00

abstract：BACKGROUND:Current resuscitation guidelines recommend the use of simulation-based medical education (SBME) as an instructional methodology to improve patient safety and health. We sought to investigate the evidence-base for the effectiveness of SBME for neonatal and pediatric resuscitation training. METHOD:Therefore, ...

journal_title：Klinische Padiatrie

authors： Mileder LP,Urlesberger B,Szyld EG,Roehr CC,Schmölzer GM

更新日期：2014-09-01 00:00:00

abstract：:Crohn's Disease and Ulcerative Colitis play a vital role in the differential diagnosis of inflammatory diseases of the colon during childhood. Pediatricians, radiologists, pediatric surgions and pediatric pathologists have been frequently confronted with the problem of distinguishing the two diseases. Morphologically,...

journal_title：Klinische Padiatrie

authors： Födisch HJ,Toledo R

更新日期：1978-03-01 00:00:00

abstract：BACKGROUND:Up to now, reliable data has not been available on the actual costs of treating oncological patients. However, such data material is urgently required in view of the institution of the health service reform with the concomitant introduction of the G-DRG remuneration system. PATIENTS:The medical services and...

journal_title：Klinische Padiatrie

authors： Stäbler W,Wagner B

更新日期：2003-05-01 00:00:00