[Autoimmune hemolytic anaemia in childhood. Review and report of one case (author's transl)].

Abstract:

:Autoimmune hemolytic anaemia (AIHA) in childhood is associated with antibodies produced by the patient himself, which coat his red cells causing their hemolysis. Although in some cases no underlying disease could be found, in the majority of children a virus etiology is apparent. There are very few reports regarding the use of treatment with immunsuppressive agents and the possible benefit. The article reports one case of AIHA. The patient developed at age 6 months a prolonged chronic form of AIHA complicated by thrombopenic purpura. The recent knowledge about pathogenesis, clinical phenomena, serology and prognosis is discussed. Treatment with corticosteroids, azathioprine or cyclophosphamide failed to benefit. Splenectomy and 6-mercaptopurin therapy (3 months) resulted in a complete remission.

journal_name

Klin Padiatr

journal_title

Klinische Padiatrie

authors

Haas RJ,Pöschl U,Christ M,Schaub J,Belohradsky BH

subject

Has Abstract

pub_date

1977-05-01 00:00:00

pages

276-82

issue

3

eissn

0300-8630

issn

1439-3824

journal_volume

189

pub_type

杂志文章
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    authors: Weglage J,Kurlemann G

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  • Survival after an antiangiogenetic therapy and surgery in a wide spread growing teratoma originating from a testicular mixed malignant germ cell tumor.

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  • [D-penicillamine-induced IgA deficiency in the therapy of Wilson's disease].

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    doi:10.1055/s-2007-1025560

    authors: Ibel H,Feist D,Endres W,Belohradsky BH

    更新日期:1990-11-01 00:00:00

  • [Waardenburg syndrome type I--autosomal dominant hereditary combination of multiple facial anomalies with cochlear deafness (author's transl)].

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    pub_type: 杂志文章

    doi:10.1055/s-2008-1033785

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    更新日期:1982-03-01 00:00:00

  • [Measuring accuracy of commercial respiratory function equipment and ventilation monitors for newborn infants].

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  • [Diagnostic and differential-diagnostic considerations regarding the assessment of children's reactions within the scope of psychosocial care in paediatric oncology and haematology].

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  • [Potential coulometry, a new methodology for the determination of iron concentration in serum. Comparison with the bathophenanthroline method in protein-free solution (author's transl)].

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    pub_type: 杂志文章

    doi:10.1055/s-2008-1033773

    authors: Liappis N

    更新日期:1982-01-01 00:00:00

  • [Achalasia, alacrimia and cortisol deficiency--Allgrove syndrome].

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  • Diagnostic value of immature myeloid information in early-onset bacterial infection in term and preterm neonates.

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    更新日期:2015-03-01 00:00:00

  • [Severe 46,XY virilization deficit due to 17beta-hydroxysteroid dehydrogenase deficiency].

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    更新日期:2002-09-01 00:00:00

  • [Supplementary intravenous nutrition in term and preterm neonates (author's transl)].

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    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:

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    更新日期:1979-07-01 00:00:00

  • [Intensive care in pediatrics (author's transl)].

    abstract::Centralized treatment of critically ill pediatric patients and related problems are presented. Pediatric intensive care allows to overbridge deranged or interrupted organ functions while simultaneously treating the disease causing the disturbance. Its efficiency depends on continuity of medical care. Medical and nursi...

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    doi:10.1055/s-2008-1035616

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  • A massive intestinal vaso-occlusive crisis or "girdle syndrome" in a 6-year-old boy observed as a first manifestation of sickle cell disease.

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  • [No motivation, no time, no money--does oncologic graduate and continuing education still have a future? Presentation at the 50th Scientific Session of the Society of Pediatric Oncology and Hematology within the scope of the KOK and PSAPOH general session

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    doi:10.1055/s-2008-1043896

    authors: Voss H

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  • [A case of X/X translocation: t(X;X) (q26;p11)].

    abstract::An eight-year old girl showing a X/X-translocation (45,X/46,Xt(X;X)(q26;p11)) is presented. Besides short stature and congenital heart-anomaly no other phenotypical abnormalities were present. In all cells containing the abnormal X-chromosome, the latter was late labeling as shown by autoradiography and BrdU-labeling....

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:

    authors: Wagenbichler P,Frisch H,Schnedl W

    更新日期:1975-11-01 00:00:00

  • [The meconium ileus equivalent in mucoviscidosis].

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    doi:10.1055/s-2008-1034390

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  • [Therapy-related pamphlet for patients in pediatric oncology].

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  • [Initial response to therapy as an important prognostic factor in acute lymphoblastic leukemia in childhood. COALL study group].

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  • Calcium and phosphor intake in preterm infants: sensitivity and specifity of 6-hour urine samples to detect deficiency.

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  • [Non-immunologic hydrops fetalis (NIHF)--case report of double partial trisomy 15q and 17q resulting from familial translocation 15/17 and cytogenetic findings in 50 cases with hydrops fetalis].

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    更新日期:1987-07-01 00:00:00

  • Congenital Central Hypoventilation Syndrome due to PHOX2b gene defects: inheritance from asymptomatic parents.

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    更新日期:2009-09-01 00:00:00

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    doi:10.1055/s-2008-1035594

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    更新日期:1980-05-01 00:00:00

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    journal_title:Klinische Padiatrie

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  • [Wiedemann-Beckwith syndrome: clinical characteristics, constitutional chromosome abnormalities and tumor incidence].

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    doi:10.1055/s-2008-1026804

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    更新日期:1987-07-01 00:00:00