[The meconium ileus equivalent in mucoviscidosis].

abstract：BACKGROUND:The prognosis of children with multisystem Langerhans cell histiocytosis (LCH) has improved with the application of chemotherapy. However, treatment strategies used varied from conservative approach with treatment only during disease exacerbation to intensive chemotherapy starting immediately after diagnosis...

journal_title：Klinische Padiatrie

authors： Minkov M,Grois N,Heitger A,Pötschger U,Westermeier T,Gadner H

更新日期：2000-07-01 00:00:00

abstract：BACKGROUND:17beta hydroxysteroid dehydrogenase deficiency is a presumable rare cause for a severe virilization disorder in children with 46,XY karyotype due to a defect in the testicular testosterone biosynthesis from androstenedione. PATIENT:We report on a 14 year old child with 46,XY karyotype with a predominantly f...

journal_title：Klinische Padiatrie

authors： Twesten W,Johannisson R,Holterhus PM,Hiort O

更新日期：2002-09-01 00:00:00

abstract：:The rapid institution of empirical broad-spectrum antibiotics has become the gold standard of treatment for febrile neutropenic children undergoing therapy for cancer. With this approach, morbidity and mortality have dropped significantly but have not been eliminated altogether. In recent randomized studies evaluating...

journal_title：Klinische Padiatrie

authors： Laws HJ,Ammann RA,Lehrnbecher T

更新日期：2005-11-01 00:00:00

abstract：:Longitudinal growth was assessed in 10 children aged 0.8 to 11.8 years with adrenocortical tumors. All children had signs of androgen excess. In addition, 5 children had glucocorticoid excess, 1 child had estrogen excess. Multiple height recordings, expressed as height standard deviation score for chronological age, w...

journal_title：Klinische Padiatrie

authors： Hauffa BP,Roll C,Mühlenberg R,Havers W

更新日期：1991-03-01 00:00:00

abstract：:Bacterial endocarditis belongs to the rare diseases in childhood. It occurs usually as a single episode and almost exclusively in children with congenital heart disease. In recent years, however, an increased number of renewed endocarditis after the first episode were reported, especially in drug addicts. We present a...

journal_title：Klinische Padiatrie

authors： Hunkert F,Handrick W,Kinzel P,Schneider P,Spencker FB,Günther E

更新日期：1995-01-01 00:00:00

abstract：:While leadpoisoning has been with mankind since the dawn of civilization, only in recent years this disease was recognized as a serious public health problem. It has been estimated that more than half a million children are suffering from lead intoxication in the U.S.A. In most instances this disease is caused by eati...

journal_title：Klinische Padiatrie

authors： Püschel SM

更新日期：1975-09-01 00:00:00

abstract：:Neurofibromatosis type 1 is the most common of the phakomatoses and the clinical follow-up is an interdisciplinary challenge. The data of 27 patients with NF1 were systematically reviewed and compared to data from the literature. All of our patients had clinical signs of NF1. Besides the classic criteria café-au-lait ...

journal_title：Klinische Padiatrie

authors： Syrbe S,Eberle K,Strenge S,Bernhard MK,Herbertz S,Bierbach U,Hirsch W,Froster UG,Kiess W,Merkenschlager A

更新日期：2007-11-01 00:00:00

abstract：:A two month old boy with Fournier's Gangrene of the scrotum as a result of unnecessary needle puncture of the hydrocele is being reported. The importance of appropriate diagnosis operation and drug-therapy is also described. ...

journal_title：Klinische Padiatrie

authors： Heemann KF,Homann W,Pistor K

更新日期：1984-11-01 00:00:00

abstract：:The normal values of the LH and FSH excretion in 12-h-overnight-urine-samples were measured by the commercial technique for the estimation of LH (Luteonosticon) and FSH (FSH-nosticon). These methods were used to determine the hormone excretion of these hormones in healthy individuals, 94 boys (0-18 years) and 48 girls...

journal_title：Klinische Padiatrie

authors： Bressensdorf DB,Knorr D

更新日期：1978-07-01 00:00:00

abstract：BACKGROUND:For Thrombasthenia Glanzmann (GT) patients presenting with a severe clinical phenotype due to complete lack of thrombocyte function or increased titres of anti-platelet antibodies hematopoietic stem cell transplantation (SCT) is the only curative therapy. CASE REPORT:We report the case of a 13-month-old boy...

journal_title：Klinische Padiatrie

authors： Wiegering V,Winkler B,Langhammer F,Wölfl M,Wirbelauer J,Sauer K,Kobsar A,Meyer T,Strauss A,Bakchoul T,Eyrich M,Schlegel PG

更新日期：2011-05-01 00:00:00

abstract：UNLABELLED:In the prophylaxis of stress ulcers with antacids in young infants there are no recommendations of dosages that consider the physiologic maturation of gastric acid secretion. During the first six month of life the amount of gastric acid secretion in relation to body weight and body surface area increases exp...

journal_title：Klinische Padiatrie

authors： Kentrup H,Skopnik H,Wolter L,Engelhart W,Nauert C,Heimann G

更新日期：1996-01-01 00:00:00

abstract：BACKGROUND:Currently there are 3 pneumococcal vaccines available in Germany. The aim of this study is to evaluate the potential of the three currently available pneumococcal vaccines to reduce the burden of invasive pneumococcal disease in children. SUBJECTS:Children younger than 16 years who have been hospitalized be...

journal_title：Klinische Padiatrie

authors： Rückinger S,van der Linden M,Siedler A,von Kries R

更新日期：2011-03-01 00:00:00

abstract：BACKGROUND:Most recent studies analyzing candidate biological prognostic factors in childhood medulloblastoma (MB) are limited by small patient numbers due to dependence on fresh-frozen tumor material. By contrast, large archives of formalin-fixed, paraffin-embedded MB samples exist from homogeneously treated patients....

journal_title：Klinische Padiatrie

authors： Grotzer MA,von Hoff K,von Bueren AO,Shalaby T,Hartmann W,Warmuth-Metz M,Emser A,Kortmann RD,Kuehl J,Pietsch T,Rutkowski S

更新日期：2007-11-01 00:00:00

abstract：:Since 1962, desferrioxamine (deferoxamine, DFO) has been utilized for the treatment of secondary hemosiderosis. For about 30 years, DFO therapy has been performed as nightly continuous subcutaneous infusion. About 20 years ago, the first oral iron chelator (deferiprone, DFP) was presented. Concerns about potential sid...

journal_title：Klinische Padiatrie

authors： Cario H,Janka-Schaub G,Janssen G,Jarisch A,Strauss G,Kohne E

更新日期：2007-05-01 00:00:00

abstract：:Short presentation of the common procedures to avoid transmission of human-immunodeficiency-virus (HIV) by hemoderivates especially clotting-factor-preparations. The stepwise seroconversion (ELISA, IFT, Western-blot) of HIV is shown in a 7 5/12 ys old boy with hemophilia A after administration of a dry-heated factor V...

journal_title：Klinische Padiatrie

authors： Weisser J

更新日期：1988-09-01 00:00:00

abstract：:The aetiology and pathogenesis of the Duchenne-type muscular dystrophy (pseudohypertrophic muscular dystrophy) are still largely unknown. The possibilities of treating the disease are rather limited. Treatment is the more successful, the earlier diagnosis was possible, and the earlier treatment is initiated. The CK-Sc...

journal_title：Klinische Padiatrie

authors： Beckmann R

更新日期：1978-11-01 00:00:00

abstract：:The aims of trial NHL-BFM 90 for patients (pts) suffering from B-cell neoplasms are to prove whether: 1. Treatment for pts with complete resection can be reduced from 3 to 2 therapy courses; 2. Results for pts of stage III with large abdominal tumors can be improved by high dose (HD) chemotherapy; 3. Survival for pts ...

journal_title：Klinische Padiatrie

authors： Reiter A,Schrappe M,Yakisan E,Sauter S,Ebell W,Zimmermann M,Hartmann W,Kremens B,Kuhn N,Claviez A

更新日期：1994-07-01 00:00:00

abstract：:From 1975-1986 6 boys with congenital nephrogenic diabetes insipidus were diagnosed at the age of 3 months to 10 years. Symptoms appeared within the first few weeks of life. The diagnosis was confirmed by polyuria, low urinary osmolality (97-225 mosm/kg H20), hypernatraemia (max. 171 mmol/l) and the missing response t...

journal_title：Klinische Padiatrie

authors： Kaulitz R,Brodehl J

更新日期：1989-11-01 00:00:00

abstract：:An increasing number of children suffering from cancer has been treated successfully during the last 25 years using therapy protocols of the Gesellschaft für Pädiatrische Onkologie und Hämatologie. The patients had to undergo an interdisciplinary treatment modality and a mostly intensive chemotherapy. Late effects cou...

journal_title：Klinische Padiatrie

authors： Beck JD,Winkler K,Niethammer D,Brandis M,Hertzberg H,von der Hardt K,Greil J,Uberall MA,Rossi R,Lamprecht-Dinnesen A

更新日期：1995-07-01 00:00:00

abstract：:The long term follow up of 55 children with allergy treated by specific hyposensitization therapy is reported. Hyposensitization therapy had been terminated from 2--7 years previously. The success of treatment was subjectively judged to be satisfactory of good in 62% of the cases. In the group of asthmatic children, a...

journal_title：Klinische Padiatrie

authors： Urbanek R,Karitzky D

更新日期：1975-11-01 00:00:00

abstract：OBJECTIVE:To identify obstetric and neonatal risk factors associated with the development of germinal matrix-intraventricular hemorrhage (GM-IVH) in high-risk preterm neonates. METHODS AND PATIENTS:Data from 279 preterm infants (246 mothers) with a gestational age≤28+0 weeks admitted to our NICU between January 2004 a...

journal_title：Klinische Padiatrie

authors： Waitz M,Nusser S,Schmid MB,Dreyhaupt J,Reister F,Hummler H

更新日期：2016-09-01 00:00:00

abstract：BACKGROUND:The medical care of pediatric cancer patients in the German health care system relies on special structures. All children and adolescents with a diagnosis of cancer receive uniform treatment within clinical studies or registers and exclusively at centers which can ensure interdisciplinary care by a multiprof...

journal_title：Klinische Padiatrie

authors： Reinke E,Jürgens H,Haier J,Froehlich B,Kontny U,Rossig C

更新日期：2020-11-01 00:00:00

abstract：:Purpose To determine the population prevalence and risk factors of myopia in children and adolescents in Germany. Methods The prevalence of myopia in Germany was computed using data from the 2003-2006 German Health Interview and Examination Survey for Children and Adolescents (N=17 640, 49% girls). Status of myopia wa...

journal_title：Klinische Padiatrie

authors： Schuster AK,Elflein HM,Pokora R,Urschitz MS

更新日期：2017-07-01 00:00:00

abstract：UNLABELLED:After corrective surgery for congenital heart defects (CHD) many patients suffer from residual defects, some with reduced cardiorespiratory capacity and possible impairment of their health related quality of life (HRQoL). The aim of our study is to evaluate, how children after surgery for CHD rate their HRQo...

journal_title：Klinische Padiatrie

authors： Heusch A,Calaminus G,Kahl J,Schmidt K

更新日期：2014-09-01 00:00:00

abstract：BACKGROUND:Spinal compression can be a complication of neuroblastoma (NBL). Delayed or insufficient treatment of this condition may lead to permanent neurological sequelae. Therefore, appropriate treatment should be introduced promptly. Therapeutic options include neurosurgery, chemotherapy, and radiation therapy. CAS...

journal_title：Klinische Padiatrie

authors： Walter KN,Kratz C,Uhl M,Niemeyer C

更新日期：2008-05-01 00:00:00

abstract：:Several randomized controlled trials (RCTs) have investigated the prophylactic use of probiotics in preterm infants aimed at reducing the rate of necrotising enterocolitis (NEC). There are 4 meta-analyses on this subject. 2 more RCTs have been published since these meta-analyses were completed. Each meta-analysis, as ...

journal_title：Klinische Padiatrie

authors： Guthmann F,Kluthe C,Bührer C

更新日期：2010-09-01 00:00:00

abstract：:Polycythemia vera - the most frequent form of a primary erythrocytosis in adult patients - represents an extremely rare disease in pediatric and juvenile patients as do congenital primary and secondary erythrocytoses. Frequently, in patients with these diseases clinical problems do not occur before adulthood. Systemat...

journal_title：Klinische Padiatrie

authors： Cario H,Schwarz K,Debatin KM,Kohne E

更新日期：2004-05-01 00:00:00

abstract：:Centralized treatment of critically ill pediatric patients and related problems are presented. Pediatric intensive care allows to overbridge deranged or interrupted organ functions while simultaneously treating the disease causing the disturbance. Its efficiency depends on continuity of medical care. Medical and nursi...

journal_title：Klinische Padiatrie

authors： Wille L

更新日期：1980-09-01 00:00:00

abstract：OBJECTIVES:Despite about 3 decades of clinical experience with the therapy of inherited thrombocytopathies (HTP) with desmopressin (DDAVP) the mechanisms of haemostatic effects of DDAVP in these diseases remain unclear. Therefore platelet function diagnostics was carried out in whole blood (WB) from children with aspir...

journal_title：Klinische Padiatrie

authors： Tauer JT,Gneuss A,Lohse JE,Jürgens T,Knöfler R

更新日期：2011-05-01 00:00:00

abstract：:Possibilities of recognizing cerebral function disturbances in newborns as early as the acute phase of the condition, and of prognosticating permanent brain damage are described. Clinical findings such as lethargy or spasms in the second and third weeks of life following hypoxia indicate severe function disturbances w...

journal_title：Klinische Padiatrie

authors： Karch D

更新日期：1984-11-01 00:00:00