Recent developments in iron chelation therapy.

abstract：OBJECTIVE:To investigate the change of psychological symptoms and quality of life in children and adolescents with congenital heart disease, cancer, or cystic fibrosis after a family-oriented inpatient rehabilitation program. METHODS:302 participants in the intervention (aged 4-17 years, mean=8.7) were assessed using ...

journal_title：Klinische Padiatrie

authors： Goldbeck L,Hölling I,Schlack R,West C,Besier T

更新日期：2011-03-01 00:00:00

abstract：:In children with primary immunodeficiencies, the onset of symptoms precedes the diagnosis and the initiation of appropriate treatment by months or years. This delay in diagnosis is due to the fact that while these disorders are rare, some of the infections seen in immunodeficient patients are common. Defective antibod...

journal_title：Klinische Padiatrie

authors： Vancikova Z,Freiberger T,Vach W,Trojanek M,Rizzi M,Janda A

更新日期：2013-11-01 00:00:00

abstract：:Transfusion-induced hemochromatosis remains a major therapeutic complication in the management of patients with chronic hemolytic anemias. Red cell units harvested with blood cell separators have an average estimated mean cell age of 30 days, compared to 60 days for unfractionated blood. Our initial experience with tr...

journal_title：Klinische Padiatrie

authors： Heim MU,Eckstein R,Mittermüller H,Haas RJ,Schmidt P,Graebner E,Pape W,Mempel W

更新日期：1985-03-01 00:00:00

abstract：:Background: Transient synovitis is the most common hip joint disorder in children. Perthes disease occurs around the same age and may not be distinguishable to an episode of transient synovitis in the early stage. Therefore all children in our clinic with transient synovitis underwent a follow-up X-ray 3 months later ...

journal_title：Klinische Padiatrie

authors： Lenoir U,Slongo T,Aghayev E,Joeris A

更新日期：2017-03-01 00:00:00

abstract：:Five patients with arteriovenous angiomas in the head (2 galea angiomas, 1 mixed form with extracranial and intracranial localization of the arteriovenous fistulas and 2 intracranial arteriovenous fistulas) were described. Four patients were examined as newborns or infants. Oximetric data, intracardial pressure and ci...

journal_title：Klinische Padiatrie

authors： Pohl V

更新日期：1976-05-01 00:00:00

abstract：BACKGROUND:The medical care of pediatric cancer patients in the German health care system relies on special structures. All children and adolescents with a diagnosis of cancer receive uniform treatment within clinical studies or registers and exclusively at centers which can ensure interdisciplinary care by a multiprof...

journal_title：Klinische Padiatrie

authors： Reinke E,Jürgens H,Haier J,Froehlich B,Kontny U,Rossig C

更新日期：2020-11-01 00:00:00

abstract：BACKGROUND:Thyroglossal duct cysts arise from mucus production in an incomplete regressed thyroglossal duct. Often they are only noticed in case of infection or secondary fistulation. The operative management is a Sistrunk procedure. METHOD AND PATIENTS:In a retrospective study we analyse 26 patients aged 0,3 - 10 yea...

journal_title：Klinische Padiatrie

authors： von Bismarck S,Höllwarth ME

更新日期：2001-09-01 00:00:00

abstract：:An unbalanced structural chromosome aberration was found in a 6-year-old girl. Mother and maternal grandmother were shown to be carriers of a complex balanced translocation involving chromosomes 1, 5 and 15 and are of normal phenotype. The unbalanced status in the proband was defined as a partial trisomy 1p21-1p31. Pa...

journal_title：Klinische Padiatrie

authors： Schürmann M,Wethling H,Niemeyer ML,Schwinger E

更新日期：1987-01-01 00:00:00

abstract：:A case of arteriovenous aneurysm of the great vein of Galen with congestive heart failure in a newborn infant is presented. Efficiancy of medical management and stop of growth of the head circumference point towards a good prognosis. Patients with this malformation have been divided into four clinical groups presentin...

journal_title：Klinische Padiatrie

authors： Beitzke A,Zach M,Gypser G,Schreyer H

更新日期：1977-09-01 00:00:00

abstract：:The following paper is the manuscript of an oral presentation during the annual GPOH meeting on May 22nd, 2000 in Berlin. Following her experiences as a member of the psychosocial care team of a children's cancer unit the author discusses the emotional impact of stemcell or bone marrow transplantation in children. Psy...

journal_title：Klinische Padiatrie

authors： Griessmeier B

更新日期：2001-07-01 00:00:00

abstract：:A boy with dysplastic features had to be treated for recurrent diarrhoea and bronchitis since his tenth month of life. Defects in humoral and cellular immunity were found. The ecto-mesodermal abnormalities are so characteristic that in connection with the immunological changes it seems to be justified to assume a yet ...

journal_title：Klinische Padiatrie

authors： Tympner KD,Belohradsky B,Eife R,Klose PK

更新日期：1978-11-01 00:00:00

abstract：:A paralysis of the left vocal cord was seen by laryngoscopy in a 3-days-old boy with inspiratory stridor. A ductus aneurysm was established by angiocardiography, which was believed to be the cause of the vocal cord paralysis. Within 8 days after the angiocardiography the aneurysm became smaller and the stridor disappe...

journal_title：Klinische Padiatrie

authors： Scharf J,Richter K,Singer H,Deeg KH

更新日期：1986-01-01 00:00:00

abstract：BACKGROUND:Flank swelling and pseudotumors of the kidney are unusual manifestations of obstructive uropathies in small children. Our case illustrates typical problems and briefly reviews management options. CASE REPORT:A 5-week-old boy presented with a large, palpable urinoma due to posterior urethral valves. Sonograp...

journal_title：Klinische Padiatrie

authors： von Schnakenburg C,Dorn A,Jacobi C,Fisch D,Pohl M,Frankenschmidt A

更新日期：2006-09-01 00:00:00

abstract：BACKGROUND:The survival of infants born with esophageal atresia (EA) is > 90% at present. The purpose of this study was to evaluate early complications and long term outcome in children with EA treated at our institution. METHODS AND PATIENTS:Retrospective analysis of 111 children with EA undergoing repair of EA or tr...

journal_title：Klinische Padiatrie

authors： Lacher M,Froehlich S,von Schweinitz D,Dietz HG

更新日期：2010-09-01 00:00:00

abstract：:Hereditary Factor VII deficiency is one of the rare congenital coagulopathies. Prolonged prothrombin time (PT) with normal partial prothrombin time (PTT) may be an indicator for Factor VII deficiency. A family with hereditary heterozygous Factor VII deficiency is presented in whom no symptoms of a bleeding disorder we...

journal_title：Klinische Padiatrie

authors： Laws HJ,Harbrecht U,Köster B

更新日期：1992-11-01 00:00:00

abstract：:With the advent of prenatal diagnosis and the feasibility of intrauterine treatment, non-immune hydrops fetalis (NHIF) is gaining increasing importance. 14 patients are reported 10 of whom having been diagnosed prenatally. 13 were born prematurely severe asphyxia being a frequent occurrence. 7 out of 14 infants surviv...

journal_title：Klinische Padiatrie

authors： Kühl PG,Ulmer HE,Schmidt W,Wille L

更新日期：1985-07-01 00:00:00

abstract：:Objective: Toilet refusal syndrome (TRS) is a common disorder in toddlers, defined by use of diapers and refusal of toilet for defecation, while toilet phobia (TP) is a rare disorder in which toilets are avoided completely. Both disorders have not been described systematically in children, yet. Therefore, the aim was ...

journal_title：Klinische Padiatrie

authors： Wagner C,Niemczyk J,von Gontard A

更新日期：2017-01-01 00:00:00

abstract：:In 24 patients at risk for SIDS (12 infants with a near miss event and 12 infants with apnea and perioral cyanosis during sleep) respiratory and esophageal function were investigated by impedance pneumography (IP) and esophageal manometry combined with simultaneous pH-monitoring (EMPH). Both groups had ad early pathol...

journal_title：Klinische Padiatrie

authors： Landler U,Höllwarth ME,Uray E,Schober PH,Reiterer F,Schenkeli R

更新日期：1990-01-01 00:00:00

abstract：BACKGROUND:Children with Epidermolysis bullosa (EB) suffer from an intractable, burdensome skin disease that may result in cognitive as well as social and emotional problems. PATIENTS:To assess cognitive problems in patients with EB, we investigated 20 affected children and adolescents, 6-17 years of age (mean: 10.8 y...

journal_title：Klinische Padiatrie

authors： Feldmann R,Weglage J,Frosch M

更新日期：2012-01-01 00:00:00

abstract：:Purpose To determine the population prevalence and risk factors of myopia in children and adolescents in Germany. Methods The prevalence of myopia in Germany was computed using data from the 2003-2006 German Health Interview and Examination Survey for Children and Adolescents (N=17 640, 49% girls). Status of myopia wa...

journal_title：Klinische Padiatrie

authors： Schuster AK,Elflein HM,Pokora R,Urschitz MS

更新日期：2017-07-01 00:00:00

abstract：:In case of painful scoliosis, a search for etiologic factors in the vertebral spinal canal and adjacent structures should be made. MRI with Gadolinium is useful to look for various pathology in and around the spine in particular of spinal cord. CT scanning is indispensible for bony details. Thus CT and MRI are complem...

journal_title：Klinische Padiatrie

authors： Hoeffel C,Gaucher H,Hoeffel JC,Galloy MA,Arnould V

更新日期：1997-03-01 00:00:00

abstract：:From 1975-1986 6 boys with congenital nephrogenic diabetes insipidus were diagnosed at the age of 3 months to 10 years. Symptoms appeared within the first few weeks of life. The diagnosis was confirmed by polyuria, low urinary osmolality (97-225 mosm/kg H20), hypernatraemia (max. 171 mmol/l) and the missing response t...

journal_title：Klinische Padiatrie

authors： Kaulitz R,Brodehl J

更新日期：1989-11-01 00:00:00

abstract：:Problems of terminology, differential diagnosis, etiology and therapy of language development disorders are demonstrated by a casuistic example. Besides the importance of clinical date special attention was laid on neuropsychological diagnostic procedures and their therapeutic implications. Therapeutic interventions c...

journal_title：Klinische Padiatrie

authors： Niebergall G,Wiesse J

更新日期：1978-09-01 00:00:00

abstract：BACKGROUND:The considerable increase of obesity in children and adolescents poses a major challenge to the health care system. METHODS:In an observation study of the Bundeszentrale für gesundheitliche Aufklärung (BZgA) somatic data of 1916 overweight and obese children and adolescents aged 8-17 years were compared to ...

journal_title：Klinische Padiatrie

authors： Flechtner-Mors M,Thamm M,Rosario AS,Goldapp C,Hoffmeister U,Mann R,Bullinger M,van Egmond-Fröhlich A,Ravens-Sieberer U,Reinehr T,Westenhöfer J,Holl RW

更新日期：2011-12-01 00:00:00

abstract：:Severe combined immunodeficiency (SCID) is a heterogeneous group of congenital diseases characterized by their presentation with life threatening infections in the first months of life. The clinical presentation and the therapeutic outcome is influenced by multiple factors: the genetic defect, infectious complications...

journal_title：Klinische Padiatrie

authors： Hönig M,Schulz A,Friedrich W

更新日期：2011-11-01 00:00:00

abstract：BACKGROUND:Transumbilical laparoscopic-assisted appendectomy (TULAA) is fast and cost-effective since no endoloops, staplers or wound protection devices are used. We analyzed the effects of TULAA as first approach for perforated (PA) and non-perforated (NPA) appendicitis in children. PATIENTS:We performed a retrospect...

journal_title：Klinische Padiatrie

authors： Dübbers M,Nikolaou E,Fuchs H,Fischer J,Alakus H,Leers J,Bruns C,Cernaianu G

更新日期：2018-07-01 00:00:00

abstract：:Tumors of the central nervous system account for 15.7% of all malignancies registered at the documentation center for childhood malignancies in Western Germany. This group constitutes the largest entity of solid tumors. With the exception of medulloblastoma the five-year survival probability of children with cns tumor...

journal_title：Klinische Padiatrie

authors： Kühl J

更新日期：1987-05-01 00:00:00

abstract：:Report of a case with congenital right sided intrapericardial diaphragmatic hernia. This type of a congenital diaphragmatic hernia occurs only rarely. Until 1984 30 cases are recorded in the available literature. ...

journal_title：Klinische Padiatrie

authors： Langer R,Kaufmann HJ

更新日期：1986-07-01 00:00:00

abstract：UNLABELLED:It was the aim of the cooperative therapy study HD-82 for children with Hodgkin's disease to reduce chemo- and radiotherapy and to investigate of a strategy for selective splenectomy previously developed in the Hodgkin study HD-78. Between December 1981 and December 1984 207 patients (131 boys and 76 girls) ...

journal_title：Klinische Padiatrie

authors： Schellong G,Brämswig J,Ludwig R,Gerein V,Jobke A,Jürgens H,Kabisch H,Stollmann B,Weinel P,Gadner H

更新日期：1986-05-01 00:00:00

abstract：:Immune neutropenia in infancy comprises alloimmune neutropenia and autoimmune neutropenia. Both diseases are caused by granulocyte-specific antibodies. Patients are newborns and children, often being younger than three years. Neutropenia usually leads to recurrent mild bacterial infections. Beside the blood count and ...

journal_title：Klinische Padiatrie

authors： Bux J,Mueller-Eckhardt C

更新日期：1989-11-01 00:00:00